{"title":"Ileo-Sigmoid-Vesical Fistula in a Patient with Williams Syndrome Treated Using One-Stage Surgery: A Case Report","authors":"Shuhei Kii, Tatsushi Shimokuni, Yuki Kuratani, Sunao Fijiyoshi, Makoto Nishikawa, Masahiko Koike, Katsuya Nakanishi, Masahiro Takahashi","doi":"10.5833/jjgs.2022.0050","DOIUrl":"https://doi.org/10.5833/jjgs.2022.0050","url":null,"abstract":"症例は37歳の男性で,幼少時にWilliams症候群と診断され近医に定期通院していた.持続する血膿尿と頻尿を主訴に当院泌尿器科を受診した.腹部CTでS状結腸癌による膀胱浸潤が疑われ,当院消化器内科に紹介された.精査の結果,S状結腸憩室炎による回腸S状結腸膀胱瘻の診断で当科に紹介となった.術中所見で下行結腸,S状結腸に多発憩室を認め,開腹左半結腸切除術,小腸部分切除術,膀胱部分切除術を行った.経過良好で術後11日目に退院した.Williams症候群は染色体7q11.23の微小欠失が原因の比較的まれな疾患である.エラスチンの異常に伴い大腸憩室症を発症しやすいが,大腸憩室炎から回腸S状結腸膀胱瘻を生じた報告例はまれである.心血管系の合併症から麻酔リスクがあること,精神発達遅滞や不安障害の頻度が高いことなどが,周術期の管理に留意すべき点と考えられた.","PeriodicalId":405769,"journal":{"name":"The Japanese Journal of Gastroenterological Surgery","volume":"138 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"134995468","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"編集後記","authors":"Yuko Takami","doi":"10.5833/jjgs.2023.en009","DOIUrl":"https://doi.org/10.5833/jjgs.2023.en009","url":null,"abstract":"","PeriodicalId":405769,"journal":{"name":"The Japanese Journal of Gastroenterological Surgery","volume":"53 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"134995471","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"A Case of Treves’ Field Pouch Hernia with Meckel’s Diverticulum","authors":"Takahiro Kamiga","doi":"10.5833/jjgs.2022.0078","DOIUrl":"https://doi.org/10.5833/jjgs.2022.0078","url":null,"abstract":"症例は25歳の男性で,心窩部痛にて当院を受診した.腹部CTにて回腸末端近くで腸管の急峻な口径差と腫大した虫垂を認めた.急性虫垂炎と腸閉塞の診断となり,緊急手術を施行した.Treves’ field(回結腸動脈とその最終回腸枝との吻合枝に囲まれた部位)に袋状の線維性膜があり,メッケル憩室基部の回腸から回腸末端までが覆われる内ヘルニアであった.メッケル憩室はヘルニア門に沿って背側を走行し,先端は腹側に回り込んで回腸腸間膜に癒着していた.ヘルニア囊を開放してメッケル憩室を基部で切離した.本症例は,Treves’ field に生じたヘルニア囊を有する内ヘルニアであり,Treves’ field pouch hernia(以下,TFPHと略記)であった.TFPHはメッケル憩室と同じく先天性疾患であり,それらの合併の報告は本症例を含めて4例あり,ヘルニア囊の成因にメッケル憩室の関与が考えられる.","PeriodicalId":405769,"journal":{"name":"The Japanese Journal of Gastroenterological Surgery","volume":"29 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"134992631","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}