Cardiology in the Young最新文献

{"title":"Infracardiac total anomalous pulmonary venous drainage with concomitant hypoplastic aortic arch in a preterm neonate: a rare and complex surgical challenge.","authors":"Munavvar Gasimova, Bahruz Aliyev, Aynur Abbasaliyeva, Cabir Gulmaliyev, Khayala Mammadova, Shiraslan Bakhshaliyev","doi":"10.1017/S104795112510053X","DOIUrl":"10.1017/S104795112510053X","url":null,"abstract":"<p><p>Total anomalous pulmonary venous drainage associated with hypoplastic aortic arch represents an exceptionally rare and intricate congenital cardiac anomaly. We report the case of a 13-day-old late preterm neonate presenting with infracardiac total anomalous pulmonary venous drainage, severe pulmonary hypertension, and a hypoplastic aortic arch. The patient underwent single-stage surgical correction involving rerouting of the pulmonary venous confluence to the left atrium and aortic arch reconstruction using autologous pericardial patch under cardiopulmonary bypass with selective cerebral perfusion. Postoperative recovery was favourable, marked by successful extubation, resolution of pulmonary hypertension, and absence of residual anatomical obstruction. This case highlights the feasibility and effectiveness of early, comprehensive surgical repair and the necessity of coordinated multidisciplinary perioperative care. Long-term follow-up remains vital for monitoring functional outcomes and detecting late complications.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1944-1946"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144599524","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Resolution of severe pulmonary artery obstruction secondary to ductus arteriosus aneurysm: a case report with long-term follow-up and balloon angioplasty.","authors":"Takafumi Seo, Takeshi Sasaki, Hisashi Sugiyama","doi":"10.1017/S1047951125101418","DOIUrl":"10.1017/S1047951125101418","url":null,"abstract":"<p><p>Ductus arteriosus aneurysm typically resolves spontaneously; surgical resection is required when it compresses surrounding structures and causes symptoms. In our neonatal case, the ductus arteriosus gradually regressed, but the left pulmonary artery stenosis persisted; therefore, balloon dilation was performed to address the ongoing imbalance in bilateral pulmonary perfusion. This case underscores the potential for non-surgical management of ductus arteriosus aneurysms.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1947-1949"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144815798","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Relationship between anaesthesia strategy and intracardiac hemodynamics during paediatric cardiac catheterisation.","authors":"Andrew H Smith, Steven J Healan, Genevieve E Staudt, George T Nicholson, Dana R Janssen, Thomas P Doyle, Heidi A Smith, William A McEachern, Nathan E Hill, Fred S Lamb","doi":"10.1017/S1047951125109360","DOIUrl":"10.1017/S1047951125109360","url":null,"abstract":"<p><strong>Objectives: </strong>Describe the hemodynamic implications of anaesthetic choice among children with heart disease undergoing cardiac catheterisation.</p><p><strong>Methods: </strong>Study 1 was a secondary analysis of data obtained during catheterisation-based hemodynamic assessment of infants with hypoplastic left heart syndrome following Stage 1 palliation, randomised in the Single Ventricle Reconstruction trial. Measured and calculated hemodynamics including pulmonary and systemic vascular resistance indexed to body surface area (PVRi and SVRi respectively) and pulmonary/systemic blood flow (Qp/Qs) were analysed with respect to anaesthetic employed during catheterisation, classified as moderate sedation or general anaesthesia. Study 2 consisted of a single centre, prospective analysis of patients requiring percutaneous closure of a patent ductus arteriosus or endomyocardial biopsy after orthotopic heart transplant. Participants underwent hemodynamic assessment first using inhaled volatile anaesthesia (IA), and then transitioned to total intravenous anaesthesia, comparing hemodynamic measures with respect to anaesthetic approach.</p><p><strong>Results: </strong>In Study 1, independent of shunt type, PVRi, and patient size, moderate sedation was associated with a greater than two-fold odds of a Qp/Qs >1 (OR 2.12, 95%CI 1.18-3.87, <i>p</i> = 0.013). In Study 2, while PVRi was similar, SVRi was significantly higher using total intravenous anaesthesia. Among the patent ductus arteriosus subgroup, Qp/Qs increased significantly with a total intravenous anaesthesia relative to IA (<i>p</i> = 0.003); additionally, among the orthotopic heart transplant subgroup, left ventricular end diastolic pressure increased following a transition to total intravenous anaesthesia (<i>p</i> = 0.002).</p><p><strong>Conclusions: </strong>Analyses of hemodynamics during catheterisation support a significant impact of anaesthetic type on hemodynamic values including SVRi, left ventricular end diastolic pressure, and Qp/Qs. Anaesthesia choice and intraprocedural management of SVRi are important considerations when making clinical decisions based on hemodynamic data.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1863-1870"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144943442","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"\"Like everybody else\": Adolescent perceptions of safe, independent driving with a CHD - ERRATUM.","authors":"Leigh Ann DiFusco, Rachel A Solomon, Lindsey H Lee, Chelsea M Ward McIntosh, Catherine C McDonald","doi":"10.1017/S1047951125109177","DOIUrl":"https://doi.org/10.1017/S1047951125109177","url":null,"abstract":"","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":"35 9","pages":"1968"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145211860","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Prioritising gaps in care in the real-life journey of single ventricle CHD - CORRIGENDUM.","authors":"Maria E Hoyos, Mario O'Connor, Carlos M Mery, Kathleen Carberry, Alexandra Lamari-Fisher, Eileen Steward, Christine Dillingham, Charles D Fraser, Andrew Well","doi":"10.1017/S1047951125109438","DOIUrl":"https://doi.org/10.1017/S1047951125109438","url":null,"abstract":"","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":"35 9","pages":"1881"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145211932","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"What is the best surgical strategy for aortic valve disease in children.","authors":"Zhangwei Wang, Honghao Fu, Shoujun Li","doi":"10.1017/S1047951125101121","DOIUrl":"10.1017/S1047951125101121","url":null,"abstract":"<p><p>Aortic valve disease in children is a hot topic in the field of cardiac surgery. The surgical treatment of aortic valve disease in children is affected by age, severity of the disease, and technology. The main purpose of surgical repair is to improve the symptoms of children and avoid or delay prosthetic valve replacement and reoperation as much as possible. At the same time, surgical repair should take into account the sustainability of the surgical effect and the growth ability of the aortic valve after surgery. At present, there is still a lack of a consistent surgical treatment concept and a universal surgical treatment strategy. Based on the current published literature, we conclude that for children younger than 1 year, valve repair is the first choice to avoid premature valve replacement. However, for experienced medical centres and surgeons, the Ross procedure can be attempted to treat aortic valve disease in children younger than 1 year and the long-term effect is comparable to aortic repair. In children older than 1 year, overall outcomes were similar with repair and the Ross procedure. When an acceptable intraoperative result was achieved, the outcomes of repair were favourable. However, when the intraoperative result of repair was suboptimal, the Ross procedure showed better results. For patients with suboptimal aortic valve repair, contraindications to the Ross procedure, and unwillingness to take anticoagulants, Ozaki procedure may also be an option to delay mechanical valve replacement. Compared with aortic valve repair and the Ross procedure, mechanical or homograft aortic valve replacement has a poor prognosis and is considered as a last resort option for surgical treatment of aortic valve disease in children. This article reviews the current status, advantages and disadvantages, and suitable population of several different surgical procedures for aortic valve disease in children.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1766-1772"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144752497","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Pseudoaneurysm formation at the right ventricular anastomosis of a pulmonary homograft following tetralogy of Fallot repair: a rare late complication.","authors":"Kenan Öztürker, Eylem Tunçer, Abdullah Urve Köksal","doi":"10.1017/S1047951125101467","DOIUrl":"10.1017/S1047951125101467","url":null,"abstract":"<p><p>We report a 7-year-old boy with tetralogy of Fallot who developed a right ventricular pseudoaneurysm one year after right ventricular outflow tract reconstruction with a 17 mm pulmonary homograft. Urgent reoperation revealed proximal homograft dehiscence. Repair was performed using an Invengenx® pericardial patch. This rare complication highlights the importance of long-term surveillance following homograft implantation in congenital heart surgery.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1950-1952"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144774725","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Thoracotomy-assisted arterial duct stenting in a 1.6-kg infant with Kleefstra syndrome: a case report.","authors":"Atsushi Maruyama, Taisuke Nabeshima, Takuro Kojima","doi":"10.1017/S1047951125109323","DOIUrl":"10.1017/S1047951125109323","url":null,"abstract":"<p><p>Thoracotomy-assisted arterial duct stenting is a palliative option for patent ductus arteriosus-dependent systemic circulation, typically reserved for infants at high risk for open-heart surgery, such as those with genetic syndromes or very low birth weight. We report the first documented case of thoracotomy-assisted arterial duct stenting in a patient with Kleefstra syndrome, resulting in systemic stabilisation and long-term survival.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1932-1933"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144943791","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"The economic burden of complex CHD in the United States.","authors":"Diane M Pickles, Kirstie Keller","doi":"10.1017/S1047951125109256","DOIUrl":"10.1017/S1047951125109256","url":null,"abstract":"<p><p>In the United States, about 1 in 100 children are born with a CHD, with complex cases requiring intensive, lifelong care. Despite medical severity, little data exist on economic burden, driving low impact scores in federal research funding applications, a lack of specific funding appropriations, and minimal research investment. Here, the financial and economic impact was quantified by identifying direct, indirect, and mortality costs of six complex CHDs and compared to two common cardiovascular diseases: coronary heart disease and congestive heart failure. Despite lower prevalence, complex CHDs exert disproportionate, often invisible financial burdens on families and the healthcare system. Annually, per patient, direct and indirect costs of complex CHDs are four times higher than coronary heart disease and eight times higher than congestive heart failure. The average lifetime direct and indirect cost for complex CHDs is $2.1 million per patient-nearly 44 times that of congestive heart failure. 31% of lifetime costs for complex CHDs are incurred in the first five years of life with families paying an average of $190,000 out-of-pocket. Many caregivers are forced to reduce employment hours, change jobs, or completely withdraw from the labour force. The annual national cost of complex CHDs is $74 billion, and the total lifetime economic impact exceeds $3.35 trillion. Systemic under-recognition has led to chronic underinvestment in research and stagnant patient outcomes. The biomedical community can catalyse an interdisciplinary response from research institutions, policymakers, and clinical systems to alleviate the economic and human toll of complex CHDs.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1751-1758"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144999785","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Neonatal transposition of the great arteries associated with abnormal right pulmonary artery.","authors":"Xinrui Deng, Lingyi Wen, Chuan Fu","doi":"10.1017/S1047951125109384","DOIUrl":"10.1017/S1047951125109384","url":null,"abstract":"<p><p>An anomalous origin of the right pulmonary artery is a rare phenomenon in neonates with transposition of the great arteries. We report a case of dextro-transposition of the great arteries with an anomalous right pulmonary artery originating from the innominate artery, diagnosed by cardiac CT angiography and the cinematic rendering technique. Although surgical correction was possible, it was deferred due to complex anatomy and parental preference. This case highlights the diagnostic value and role of advanced imaging in complex congenital heart disease.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1923-1925"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145112021","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}