Ziyab Sarfaraz, Sarah Stuart, Amritha Nair, Andrea Giulio Quarti
{"title":"Reoperative Aortic Root Surgery in Adults with Prior Conotruncal Repair.","authors":"Ziyab Sarfaraz, Sarah Stuart, Amritha Nair, Andrea Giulio Quarti","doi":"10.14797/mdcvj.1812","DOIUrl":"10.14797/mdcvj.1812","url":null,"abstract":"<p><p>Conotruncal anomalies comprise a heterogeneous group of congenital heart defects arising from abnormal embryologic development of the cardiac outflow tract and the great arteries. Aortic root dilatation represents a frequent yet comparatively underexplored finding in this population, and clear guidelines regarding surveillance and surgical treatment remain limited. This article reviews mechanisms of aortic root dilatation, diagnostic evaluation, and surgical indications and principles for aortic root surgery in adults with conotruncal anomalies, including lesion-specific considerations for Tetralogy of Fallot, d-transposition of the great arteries, truncus arteriosus, and double outlet right ventricle.</p>","PeriodicalId":39207,"journal":{"name":"Methodist DeBakey cardiovascular journal","volume":"22 3","pages":"78-87"},"PeriodicalIF":0.0,"publicationDate":"2026-06-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13330924/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"148392063","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Heart Failure in Adult Congenital Heart Disease.","authors":"Jessica N Richardson, Cindy M Martin","doi":"10.14797/mdcvj.1815","DOIUrl":"10.14797/mdcvj.1815","url":null,"abstract":"<p><p>Advances in the management of congenital heart disease have resulted in a rapidly expanding population of adults with congenital heart disease (ACHD), among whom heart failure (HF) has emerged as a leading cause of morbidity and mortality. HF in ACHD represents a distinct and heterogeneous clinical entity shaped by lifelong abnormal loading conditions, prior surgical interventions, arrhythmogenic substrates, and limited representation in randomized clinical trials. The systemic ventricle may be morphologically left, right, or single, each conferring unique susceptibility to maladaptive remodeling, myocardial fibrosis, valvular dysfunction, and progressive contractile decline. Accurate diagnosis requires longitudinal, multimodal assessment incorporating echocardiography, cardiovascular magnetic resonance, cardiopulmonary exercise testing, biomarkers, rhythm surveillance, and selective invasive hemodynamic evaluation. Management prioritizes identification and correction of reversible contributors, including residual structural lesions, atrioventricular valve regurgitation, arrhythmias, pulmonary vascular disease, and extracardiac comorbidities. Pharmacologic therapy remains largely extrapolated from acquired HF paradigms and demonstrates variable efficacy across ACHD subgroups, underscoring the need for physiology-driven individualized care within specialized centers. Advanced therapies, including heart transplantation and mechanical circulatory support, are increasingly utilized, with improving outcomes despite higher perioperative complexity. This review presents a ventricle-based framework for understanding the pathophysiology, evaluation, and management of HF in ACHD and highlights critical gaps requiring further investigation.</p>","PeriodicalId":39207,"journal":{"name":"Methodist DeBakey cardiovascular journal","volume":"22 3","pages":"124-135"},"PeriodicalIF":0.0,"publicationDate":"2026-06-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13330930/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"148392049","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Lifelong Bonds.","authors":"Philip Alexander","doi":"10.14797/mdcvj.1885","DOIUrl":"https://doi.org/10.14797/mdcvj.1885","url":null,"abstract":"<p><p>These contrasting images are presented by Philip Alexander, MD, a native Texan, retired physician, and accomplished musician and artist. After 41 years as an internal medicine physician, Dr. Phil retired from his practice in College Station in 2016. A lifelong musician and former music professor, he often performs as an oboe soloist for the Brazos Valley Symphony Orchestra. He began exploring visual art in 1980, evolving from pencil sketches-including an official White House portrait of President Ronald Reagan-to the computer-generated drawings featured in this journal. His images, which first appeared in this journal in the spring of 2012, are his own original creations. If you would like to see your art published in the <i>Methodist DeBakey Cardiovascular Journal</i>, submit your creation online at journal.houstonmethodist.org as a \"Humanities\" entry.</p>","PeriodicalId":39207,"journal":{"name":"Methodist DeBakey cardiovascular journal","volume":"22 3","pages":"153-155"},"PeriodicalIF":0.0,"publicationDate":"2026-06-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13330915/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"148392096","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Alicia Rangosch, Aneesh Dhore-Patil, Valeria E Duarte
{"title":"The Initial Diagnostic Approach to Adult Congenital Heart Disease: A Practical Imaging Pathway for General Cardiologists and Cardiac Imagers.","authors":"Alicia Rangosch, Aneesh Dhore-Patil, Valeria E Duarte","doi":"10.14797/mdcvj.1868","DOIUrl":"10.14797/mdcvj.1868","url":null,"abstract":"<p><p>Adult congenital heart disease (ACHD) is among the most anatomically and physiologically complex domains in cardiovascular medicine. Advances in pediatric cardiac surgery and cardiology have shifted congenital heart disease (CHD) from a predominantly pediatric condition to a lifelong disease, resulting in a growing adult population that now outnumbers the affected children. In addition, increased detection of CHD in adulthood has broadened the spectrum of ACHD encountered outside specialized centers, underscoring the importance of familiarity among general cardiologists and cardiac imagers. This state-of-the-art review outlines a structured imaging approach for adults with suspected or known CHD. The proposed pathway includes four stages: (1) clinical-anatomic orientation with systematic review of prior data including operative notes and prior imaging; (2) protocolized adult congenital transthoracic echocardiography using sequential segmental analysis; (3) question-driven cardiac magnetic resonance (CMR) with flow quantification; and (4) selective use of cardiac computed tomography (CCT) for detailed cardiac and extracardiac anatomy, coronary artery origins, surgical planning, sternal re-entry and cannulation or in cases of hardware-related imaging limitations. Beyond modality selection, we address the specialized protocol requirements, training milestones, and competency standards expected of ACHD sonographers, CMR, and CCT technologists-all personnel whose expertise is central to diagnostic quality and accuracy in this patient population. Lesion-specific scenarios and case examples illustrate application in practice. A multimodality and team-based strategy supported by standardized protocols and structured reporting is the foundation of accurate, safe, and efficient ACHD imaging in contemporary cardiovascular practice.</p>","PeriodicalId":39207,"journal":{"name":"Methodist DeBakey cardiovascular journal","volume":"22 3","pages":"5-27"},"PeriodicalIF":0.0,"publicationDate":"2026-06-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13330995/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"148392091","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Unrepaired Congenital Shunt Lesions in Adults: Principles for Clinical Management.","authors":"Diana Mariela Mouratian, Judith Beatriz Ackerman, Laura Mariana Riznyk, Carla Pasinato, Florencia Giacomozzi, Amalia Elizari","doi":"10.14797/mdcvj.1801","DOIUrl":"10.14797/mdcvj.1801","url":null,"abstract":"<p><p>This review article summarizes the pathophysiology, clinical presentation, diagnostic approach, and management principles of unrepaired congenital shunt lesions in adulthood, with emphasis on individualized decision-making and indications and contraindications for defect closure.</p>","PeriodicalId":39207,"journal":{"name":"Methodist DeBakey cardiovascular journal","volume":"22 3","pages":"40-53"},"PeriodicalIF":0.0,"publicationDate":"2026-06-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13331039/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"148392079","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Common Clinical Scenarios in Adult Congenital Heart Disease: A Practical Guide for General Cardiologists.","authors":"Tripti Gupta, Matthew R Carazo","doi":"10.14797/mdcvj.1800","DOIUrl":"10.14797/mdcvj.1800","url":null,"abstract":"<p><p>Adults with congenital heart disease (ACHD) represent a growing population of adults in the United States, necessitating lifelong care by ACHD specialists. Often, patients may be lost to follow-up after pediatric care or elude detection until adulthood, presenting to the emergency room with common clinical complaints such as chest pain, dyspnea on exertion, or palpitations. This review demystifies common clinical presentations in pulmonary stenosis, branch pulmonary stenosis, coarctation of the aorta, and subaortic stenosis and their associated pathophysiology, salient clinical features, multimodality diagnostic findings, and indication for intervention.</p>","PeriodicalId":39207,"journal":{"name":"Methodist DeBakey cardiovascular journal","volume":"22 3","pages":"28-39"},"PeriodicalIF":0.0,"publicationDate":"2026-06-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13330932/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"148392085","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Chloe Kharsa, Fatima Qamar, Joseph Elias, Karl Abou Zeid, Sachin S Goel, Joe Aoun
{"title":"Embolization Followed by Self-Repositioning of a CardioMEMS™ Wireless Pulmonary Artery Hemodynamic Monitoring Sensor Device.","authors":"Chloe Kharsa, Fatima Qamar, Joseph Elias, Karl Abou Zeid, Sachin S Goel, Joe Aoun","doi":"10.14797/mdcvj.1765","DOIUrl":"10.14797/mdcvj.1765","url":null,"abstract":"<p><p>We report a case of early migration of a CardioMEMS™ heart failure device (Abbott) from the right to the left pulmonary artery, which then spontaneously repositioned itself within the left pulmonary artery without the need for intervention. A balloon Swan-Ganz catheter was then used to reposition the device, successfully lodging it into a more distal position. This case underscores the importance of close device monitoring and demonstrates an effective technique for repositioning without device retrieval.</p>","PeriodicalId":39207,"journal":{"name":"Methodist DeBakey cardiovascular journal","volume":"22 1","pages":"37-41"},"PeriodicalIF":0.0,"publicationDate":"2026-04-16","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13089364/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147724277","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Anomalous Origin of the Vertebral Artery from Thyrocervical Trunk: A Rare Anatomical Variant.","authors":"Arun Sharma, Gurkawal Kaur, Mansi Verma, Manphool Singhal","doi":"10.14797/mdcvj.1810","DOIUrl":"10.14797/mdcvj.1810","url":null,"abstract":"<p><p>This case describes a 55-year-old man who presented with complaints of claudication in his left upper limb. Computed tomography angiography revealed a rare anatomical variant in which the left vertebral artery originated from the left thyrocervical trunk.</p>","PeriodicalId":39207,"journal":{"name":"Methodist DeBakey cardiovascular journal","volume":"22 1","pages":"34-36"},"PeriodicalIF":0.0,"publicationDate":"2026-04-06","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13068082/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147677485","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Julianna West, Ihab Hamzeh, Jonathan You, Efstratios Koutroumpakis, Cezar Iliescu, Leslie Ynalvez, Hyeon-Ju Ali, Anita Deswal, Shaden Khalaf
{"title":"Value of Myocardial Strain in Assessing Cardiac Masses: A Case Report.","authors":"Julianna West, Ihab Hamzeh, Jonathan You, Efstratios Koutroumpakis, Cezar Iliescu, Leslie Ynalvez, Hyeon-Ju Ali, Anita Deswal, Shaden Khalaf","doi":"10.14797/mdcvj.1768","DOIUrl":"10.14797/mdcvj.1768","url":null,"abstract":"<p><p>Transthoracic echocardiography and global longitudinal strain are pivotal in evaluating myocardial structure and function in cardio-oncology patients, but there are limited reports of using global longitudinal strain to identify intracardiac masses. This case presents a patient with metastatic renal cell carcinoma and cardiac metastasis that was identified using global longitudinal strain on transthoracic echocardiography and subsequently confirmed by cardiac magnetic resonance imaging.</p>","PeriodicalId":39207,"journal":{"name":"Methodist DeBakey cardiovascular journal","volume":"22 1","pages":"30-33"},"PeriodicalIF":0.0,"publicationDate":"2026-04-02","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13045788/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147624053","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Transient Cortical Blindness and Hemi-Spatial Neglect Following Watchman Device Implantation.","authors":"Mansunderbir Singh, Divleen Sidhu, Priyanka Anvekar, Shubhika Jain, Harnoor Katyal, Vijaywant Brar","doi":"10.14797/mdcvj.1769","DOIUrl":"10.14797/mdcvj.1769","url":null,"abstract":"<p><p>A 66-year-old male with prior right middle cerebral artery stroke status post thrombectomy-as well as right internal carotid artery (ICA) stenting and chronic occlusion, paroxysmal atrial fibrillation, and hypertension-underwent left atrial appendage occlusion with a Watchman device for stroke prevention. Immediately following the procedure, he developed acute bilateral vision loss accompanied by headache and worsening left-sided weakness. Emergent computed tomography (CT) and CT angiography demonstrated no hemorrhagic stroke or new large-vessel occlusion and confirmed the previously known chronic right ICA occlusion. The patient was not a candidate for thrombolysis due to recent heparin exposure during his procedure, and thrombectomy was not pursued given the absence of any new large vessel occlusion. In the context of contrast exposure and negative initial imaging, contrast-induced cortical blindness was considered the leading diagnosis, with embolism, hypoperfusion, and post-stroke recrudescence as alternative considerations. This case highlights the diagnostic complexity of acute cortical blindness and hemispatial neglect following Watchman implantation. Mechanisms may include microembolic shower, transient hypoperfusion, seizure-related cortical dysfunction, post-stroke recrudescence, or contrast induced cortical blindness. Negative initial CT imaging should not preclude suspicion for ischemia, especially in patients with preexisting cerebrovascular compromise. Early magnetic resonance imaging and multidisciplinary coordination are essential.</p>","PeriodicalId":39207,"journal":{"name":"Methodist DeBakey cardiovascular journal","volume":"22 1","pages":"26-29"},"PeriodicalIF":0.0,"publicationDate":"2026-04-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13045789/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147624040","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}