Cardiology in the Young最新文献

{"title":"Use of right axillary thoracotomy approach for minimally invasive tricuspid valve repair in the setting of paediatric infective endocarditis.","authors":"Aanya Chopra, Lindsay Nitsche, Nikia Toomey, Katsuhide Maeda, Constantine Mavroudis","doi":"10.1017/S104795112510156X","DOIUrl":"https://doi.org/10.1017/S104795112510156X","url":null,"abstract":"<p><p>Tricuspid valve repair in paediatric infective endocarditis using a right axillary thoracotomy approach has never been reported. This report describes the minimally invasive treatment of infective endocarditis using this approach in a previously healthy paediatric patient. The patient underwent successful tricuspid valve repair and was discharged with an outpatient antibiotic regimen. He remains well seven months postoperatively.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":"35 9","pages":"1956-1958"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145211902","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Prioritising gaps in care in the real-life journey of single ventricle CHD.","authors":"Maria E Hoyos, Mario O'Connor, Carlos M Mery, Kathleen Carberry, Alexandra Lamari-Fisher, Eileen Steward, Christine Dillingham, Charles D Fraser, Andrew Well","doi":"10.1017/S1047951125101157","DOIUrl":"10.1017/S1047951125101157","url":null,"abstract":"<p><strong>Background: </strong>Single ventricle CHD requires lifelong care, yet its broader impact on patients and families remains unclear. Engaging patients in care improvement can strengthen relationships and outcomes.</p><p><strong>Objectives: </strong>This study evaluates how individuals with single ventricle CHD prioritise gaps in care based on personal and family impact.</p><p><strong>Methods: </strong>Using Mery et al.'s identified care gaps, a survey was distributed to parents of children with single ventricle CHD and adults with single ventricle CHD in English or Spanish. Participants rated each gap from 1(not important) to 10(extremely important), with a \"Not Applicable\" option. Responses were analysed using median, weighted, and total rating scores. Sociodemographic data were examined, and univariate analysis and a race/ethnicity and insurance matrix were conducted on parent responses.</p><p><strong>Results: </strong>Among 36 complete responses, 30(83.3%) were parents and 6(16.7%) patients. Most parents were female(29,96.7%), White non-Hispanic(24,80.0%), with 17(6.7%) having privately insured children. Median child age was 6.5[interquartile range: 3.0-12.8] years, and 55.3% had Hypoplastic Left Heart Syndrome. The highest-rated gap was \"Uncertainty of prognosis in adulthood\" (9.5[interquartile range: 8.0-10.0]). The lowest was \"Pregnancy termination presented repeatedly\" (1.0[interquartile range: 1.0-7.0]). Non-White parents rated \"Transition to adult healthcare\" (<i>p</i> = 0.017) and \"Navigating resources\" (<i>p</i> = 0.037) higher. Patients (median age 33.0 years) prioritised \"Rescheduling surgical procedures\" and \"Transition to adult healthcare\" (both 10.0). \"Support in family planning\" had the highest total rating score(12). The lowest-rated was \"Limited guidance on transition to adolescence\" (0.0[interquartile range:0.0-0.0]).</p><p><strong>Conclusions: </strong>Patients and families prioritise care gaps differently. Aligning their perspectives with clinical expertise can guide tailored solutions to improve outcomes for single ventricle CHD patients.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1871-1880"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144752481","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"New triple combination therapy approach for children with advanced heart failure despite having received standard heart failure treatment.","authors":"Isa Ozyilmaz, Halise Zeynep Genc, Senay Coban, Ahmet Saki Oguz, Nurullah Yilmaz, Ibrahim Cansaran Tanidir, Erkut Ozturk, Ali Can Hatemi","doi":"10.1017/S1047951125109335","DOIUrl":"10.1017/S1047951125109335","url":null,"abstract":"<p><strong>Aim: </strong>The limited efficacy of monotherapy and the insufficient clinical experience with triple therapy (levosimendan, dapagliflozin, and sacubitril/valsartan) warrant further investigation. The aim of this study was to evaluate the effects of triple therapy on left ventricular function in children with advanced heart failure whose left ventricular function had not improved despite classical heart failure treatment and who remained dependent on inotropes.</p><p><strong>Methods: </strong>The study included children who were admitted to the hospital with advanced heart failure and who were still inotrope-dependent at a mean of 42 days after the start of classical heart failure treatment and then started triple therapy at our hospital.</p><p><strong>Results: </strong>The study included 18 patients, 8 (44%) males, with a median age of 4 years (2-7 years). Before and after classical treatment and after triple treatment, statistically significant improvement in two-dimensional left ventricular ejection fraction (%) (median values 30; 38; 55, respectively), left ventricular end-diastolic diameter (median values 44; 45; 40 mm), left ventricular end-systolic diameter (median values 38; 36; 29 mm), left ventricular end-diastolic diameter (z score) (median values 4.2; 3.2; 2.7), left ventricular end-systolic diameter (z score) (median values 5.8; 4.8; 3.2), Simpson left ventricular ejection fraction (%) (median values 29; 36.5; 55), Simpson left ventricular end-diastolic volume (median values 60; 55; 43 ml), left ventricular end-systolic volume (median values 43; 40; 18. 5 ml), left ventricular global longitudinal strain four-chamber (median values -8.1;-10;-19), left ventricular global longitudinal strain three-chamber (median values -5.9;-8.9;-14), and left ventricular global longitudinal strain mean (median values -6.9;-9.7;-19) values was observed ( <b><i>all values p < 0.05</i></b> ).</p><p><strong>Conclusions: </strong>In children admitted to the hospital with advanced heart failure whose left ventricular function has not improved with classical therapy, it seems likely that both left ventricular systolic and diastolic function will improve, inotrope dependency will resolve, and patients can be discharged with the new triple drug therapy.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1882-1888"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144943921","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Opportunities and challenges surrounding the use of implantable haemodynamic monitor in paediatric Fontan patients living in high-altitude, rural settings.","authors":"Deepti Pagare Bhat, Arash A Sabati, Saleem Almasarweh, Joseph N Graziano","doi":"10.1017/S104795112510927X","DOIUrl":"10.1017/S104795112510927X","url":null,"abstract":"<p><strong>Background: </strong>Implantable haemodynamic monitors allow remote monitoring of Fontan circulation. We report unique opportunities and challenges related to device use in rural, high-altitude regions.</p><p><strong>Objectives: </strong>Assess the performance of implantable haemodynamic monitor in Fontan circulation and identify potential sources of measurement discrepancy defined as non-physiological, negative, or significantly lower reading than baseline.</p><p><strong>Methods: </strong>We performed a retrospective review of patients who underwent implantable haemodynamic monitor implantation from September 2021 to April 2024 (<i>n</i> = 17) at our centre (∼1,000 feet above sea level; ASL) and identified those with sensor discrepancies.</p><p><strong>Results: </strong>During a mean follow-up duration of 26 months (range 13-44 months), there were no procedure-related complications, thromboembolism, or device displacement. Ten patients lived in rural, higher-altitude regions (average altitude 5100 feet above sea level, average distance from centre ∼160 miles, range = 100-400 miles). Challenges in remote monitoring included unreliable home-internet connection, non-compliance, and difficulty performing device recalibration at patient's home altitude. Sensor discrepancies were noted in 7 patients (41%), of whom 6 (86%) lived remotely. Manual review of the waveforms identified sources of discrepancy, including misinterpretation of the non-pulsatile pressure waveform (<i>n</i> = 3), offset due to change in hospital-interrogation unit (<i>n</i> = 4), and sensor drift (<i>n</i> = 1). Altitude change did not directly affect sensor performance. We were able to apply corrective interventions in 4/7 sensors, including Fontan-specific settings (overriding pulsatility), and back-end recalibration, which were effective in improving device accuracy.</p><p><strong>Conclusions: </strong>Implantable haemodynamic monitors are a promising tool for monitoring Fontan circulation but may require modified settings and careful attention to potential interpretation errors. Home monitoring remains challenging for rural, high-altitude residents with limited resources.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1815-1823"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144943938","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"A rare case of parachute mitral valve and dual drainage of the left upper pulmonary vein in a patient with Kabuki syndrome.","authors":"Mustafa Nalbant, Sezen Ugan Atik, Pelin Ayyıldız, Sertaç Haydin, Alper Güzeltaş","doi":"10.1017/S1047951125109281","DOIUrl":"10.1017/S1047951125109281","url":null,"abstract":"<p><p>A patient with Kabuki syndrome and a parachute mitral valve was referred for mitral stenosis. Echocardiography indicated right ventricular dilatation and a suspected vertical ascending vein. Cardiac CT confirmed dual drainage of the left upper pulmonary vein and hemiazygos vein continuity. Despite echocardiographic limitations, surgery was performed. This rare case is reported due to its unique anatomical variation.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1937-1939"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144943958","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Does age matter? Echocardiographic assessment after isolated atrial septal defect surgery.","authors":"Kenan Öztürker, Hakan Ceyran, Veysel Başar, Ayhan Güneş, Mustafa Akbbulut, Abdullah Urve Köksal","doi":"10.1017/S1047951125101601","DOIUrl":"10.1017/S1047951125101601","url":null,"abstract":"<p><strong>Objective: </strong>Atrial septal defect is the second most common CHD in adults. This study aimed to evaluate the relationship between age and early postoperative changes in cardiac function-including right ventricular function, tricuspid regurgitation, pulmonary artery pressure, mitral regurgitation, and left ventricular ejection fraction-in adult patients undergoing surgical atrial septal defect repair.</p><p><strong>Methods: </strong>This retrospective study included 214 patients aged 16-65 years who underwent isolated atrial septal defect repair between 2014 and 2024. Patients were divided into five age groups. Echocardiographic parameters were compared at three time points: preoperative, 1-month, and 6-month postoperative.</p><p><strong>Results: </strong>Of the patients, 60.7% were female. A significant postoperative left ventricular ejection fraction decrease was observed only in the 56-65 age group. Preoperative tricuspid regurgitation severity and pulmonary artery pressure values increased with age, but both showed significant postoperative improvement across all age groups. Postoperative pulmonary artery pressure reduction was most prominent in the youngest and oldest groups. Mitral regurgitation was mildly increased in all groups, without progression to moderate severity. Tricuspid annular plane systolic excursion values, inversely correlated with age, decreased in younger patients postoperatively but improved in older patients, indicating enhanced right ventricular function after volume unloading.</p><p><strong>Conclusion: </strong>Surgical atrial septal defect repair leads to early improvement in several cardiac parameters. However, the benefit is more pronounced in younger patients. These findings support early surgical intervention to preserve right ventricular function and prevent long-term complications, particularly in asymptomatic adults.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1799-1808"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144943884","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"A change of heart: the evolution of care for children with Trisomy 21 and CHD.","authors":"Madeline Petrikas, Sumin Choi, Katherine Cavanaugh, Nevaeh Gomez, Cheyenne Ahamed, Davi Freitas Tenorio, Roderick Yang, Jiyong Moon, Charles D Fraser, Charles D Fraser, Constantine D Mavroudis","doi":"10.1017/S1047951125109347","DOIUrl":"10.1017/S1047951125109347","url":null,"abstract":"<p><p>Trisomy 21 is the most common chromosomal anomaly worldwide, and nearly half of the affected individuals are born with CHD, making cardiac complications a leading cause of morbidity and mortality in this population. Over the past century, the management of CHD in patients with Trisomy 21 has evolved dramatically, shaped by shifting societal attitudes, advances in diagnostic and surgical techniques, and landmark legal and ethical milestones. Historically, children with Trisomy 21 faced significant barriers to cardiac care, including delayed referrals and denial of surgical intervention, often rooted in discrimination rather than medical evidence. However, improvements in perioperative management and early surgical repair have led to survival outcomes for many forms of CHD that now approach those of the general population. Despite these advances, challenges persist, particularly in access to heart transplantation, where disparities in referral and eligibility remain. This review provides a historical overview of the evolution of CHD management in individuals with Trisomy 21, highlighting key medical, ethical, and societal developments that have shaped current standards of care.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1759-1765"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144943960","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"The current state of paediatric publishing utilising high-fidelity physiologic data streaming with sickbay or etiometry: a systematic review.","authors":"Rohit S Loomba, Wesam Sourour, Saul Flores, Juan S Farias, Michael Goldsmith, Javier J Lasa, Orkun Baloglu","doi":"10.1017/S1047951125109219","DOIUrl":"10.1017/S1047951125109219","url":null,"abstract":"<p><strong>Background: </strong>Physiologic data streaming and aggregation platforms such as Sickbay® and Etiometry are becoming increasingly used in the paediatric acute care setting. As these platforms gain popularity in clinical settings, there has been a parallel growth in scholarly interest. The primary aim of this study is to characterise research productivity utilising high-fidelity physiologic streaming data with Sickbay® or Etiometry in the acute care paediatric setting.</p><p><strong>Methods: </strong>A systematic review of the literature was conducted to identify paediatric publications using data from Sickbay® or Etiometry. The resulting publications were reviewed to characterise them and identify trends in these publications.</p><p><strong>Results: </strong>A total of 41 papers have been published over 9 years using either platform. This involved 179 authors across 21 institutions. Most studies utilised Sickbay®, involved cardiac patients, were single-centre, and did not utilise machine learning or artificial intelligence methods. The number of publications has been significantly increasing over the past 9 years, and the average number of citations for each publication was 7.9.</p><p><strong>Conclusion: </strong>A total of 41 papers have been published over 9 years using Sickbay<u>®</u> or Etiometry data in the paediatric setting. Although the majority of these are single-centre and pertain to cardiac patients, growth in publication volume suggests growing utilisation of high-fidelity physiologic data beyond clinical applications. Multicentre efforts may help increase the number of centres that can do such work and help drive improvements in clinical care.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1809-1814"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144999746","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Origin of the left circumflex artery from pulmonary artery discovered post-ventricular septal defect repair.","authors":"Dealla Samadi, Shaun Mohan, Jess Randall","doi":"10.1017/S1047951125109372","DOIUrl":"10.1017/S1047951125109372","url":null,"abstract":"","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1926-1928"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144999764","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Sternal cleft with surgical repair and 3-year follow-up: case report and literature review.","authors":"Kevin Gianaris, Amy Heincker, Constantine Mavroudis","doi":"10.1017/S1047951125100917","DOIUrl":"10.1017/S1047951125100917","url":null,"abstract":"<p><p>Sternal cleft is a rare congenital condition associated with unprotected viscera and respiratory failure. We present a case of a sternal cleft, absent right clavicle, and congenital diaphragmatic paresis in a neonate. The sternum was closed primarily, and the patient was taken back for plication of the diaphragm. At 3 years follow-up, the patient is free from complications.</p>","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":" ","pages":"1940-1943"},"PeriodicalIF":0.7,"publicationDate":"2025-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144706418","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}