Cardiology in the Young最新文献_第8页

Multiple recurrent supraventricular tachycardia in infantile tuberous sclerosis complex: management requiring triple-drug therapy. 婴幼儿结节性硬化症复合体多发性复发性室上性心动过速：需要三联药物治疗。

IF 1 4区医学

Cardiology in the Young Pub Date : 2024-05-24 DOI: 10.1017/S1047951124000325

Xander Jacquemyn, Shelby Kutty, Mitchell I Cohen, Keyur K Mehta

引用次数: 0

In Memoriam-Dr. Juan León-Wyss (10 January, 1963-18 January, 2024). 悼念胡安-莱昂-维斯博士（1963 年 1 月 10 日至 2024 年 1 月 18 日）。

IF 1 4区医学

Cardiology in the Young Pub Date : 2024-05-22 DOI: 10.1017/S1047951124000520

Tom R Karl, Rodrigo Soto, Rebeca Pérez González, Joseph Turek, Giles Peek

引用次数: 0

Device closure of residual aortopulmonary window using Konar-MF occluder device: an attractive new option. 使用 Konar-MF 封堵器对残留的主动脉肺窗进行器械封堵：一种极具吸引力的新选择。

IF 1 4区医学

Cardiology in the Young Pub Date : 2024-05-22 DOI: 10.1017/S1047951124025010

Ahmad Usaid Qureshi, Tehmina Kazmi, Masood Sadiq

引用次数: 0

Mitochondrial cardiomyopathy: a puzzle for the final diagnosis. 线粒体心肌病：最终诊断之谜。

IF 1 4区医学

Cardiology in the Young Pub Date : 2024-05-16 DOI: 10.1017/S1047951124025095

Andreia Duarte Constante, Susana Martins Abreu, Conceição Trigo

引用次数: 0

Periods of low renal perfusion pressure are associated with acute kidney injury following paediatric cardiac surgery. 肾灌注压过低与小儿心脏手术后急性肾损伤有关。

IF 1 4区医学

Cardiology in the Young Pub Date : 2024-05-16 DOI: 10.1017/S1047951124025149

Jamie S Penk, Katja M Gist, Matthew Barhight, Karl Migally, Santiago Borasino, Wendy F Torres, Siyuan Dong, Bradley S Marino, Catherine D Krawczeski

{"title":"Periods of low renal perfusion pressure are associated with acute kidney injury following paediatric cardiac surgery.","authors":"Jamie S Penk, Katja M Gist, Matthew Barhight, Karl Migally, Santiago Borasino, Wendy F Torres, Siyuan Dong, Bradley S Marino, Catherine D Krawczeski","doi":"10.1017/S1047951124025149","DOIUrl":"https://doi.org/10.1017/S1047951124025149","url":null,"abstract":"Introduction: Acute kidney injury is associated with worse outcomes after cardiac surgery. The haemodynamic goals to ameliorate kidney injury are not clear. Low post-operative renal perfusion pressure has been associated with acute kidney injury in adults. Inadequate oxygen delivery may also cause kidney injury. This study evaluates pressure and oximetric haemodynamics after paediatric cardiac surgery and their association with acute kidney injury.Materials and methods: Retrospective case-control study at a children's hospital. Patients were < 6 months of age who underwent a Society of Thoracic Surgery-European Association for Cardio-Thoracic Surgery Congenital Heart Surgery categories ≥ 3. Low renal perfusion pressure was time and depth below several tested thresholds. The primary outcome was serum creatine-defined acute kidney injury in the first 7 days.Results: Sixty-six patients (median age 8 days) were included. Acute kidney injury occurred in 36%. The time and depth of renal perfusion pressure < 42 mmHg in the first 24 hours was greater in acute kidney injury patients (94 versus 35 mmHg*minutes of low renal perfusion pressure/hour, p = 0.008). In the multivariable model, renal perfusion pressure < 42 mmHg was associated with acute kidney injury (aOR: 2.07, 95%CI: 1.25-3.82, p = 0.009). Mean arterial pressure, central venous pressure, and measures of inadequate oxygen delivery were not associated with acute kidney injury.Conclusion: Periods of low renal perfusion pressure (<42 mmHg) in the first 24 post-operative hours are associated with acute kidney injury. Renal perfusion pressure is a potential modifiable target that may mitigate the impact of acute kidney injury after paediatric cardiac surgery.","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":null,"pages":null},"PeriodicalIF":1.0,"publicationDate":"2024-05-16","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"140944091","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Native aortic root thrombus leading to myocardial infarction in a single ventricle patient. 单心室患者主动脉根部血栓导致心肌梗死。

IF 1 4区医学

Cardiology in the Young Pub Date : 2024-05-16 DOI: 10.1017/S1047951124025150

Rod M Shinozaki, Mark C Johnson, Avihu Z Gazit

引用次数: 0

Human milk, breastfeeding, and early neurodevelopmental outcomes for infants with critical CHD. 人乳、母乳喂养和患有严重先天性心脏病婴儿的早期神经发育结果。

IF 1 4区医学

Cardiology in the Young Pub Date : 2024-05-13 DOI: 10.1017/S1047951124025228

Kristin M Elgersma, Melissa L Engel, Sara E Ramel, Jessica A Davis, Anne C McKechnie, Katie M Pfister

{"title":"Human milk, breastfeeding, and early neurodevelopmental outcomes for infants with critical CHD.","authors":"Kristin M Elgersma, Melissa L Engel, Sara E Ramel, Jessica A Davis, Anne C McKechnie, Katie M Pfister","doi":"10.1017/S1047951124025228","DOIUrl":"https://doi.org/10.1017/S1047951124025228","url":null,"abstract":"Human milk improves neurodevelopment for preterm infants, but relationships between human milk and neurodevelopment for infants with critical CHD are unknown. We aimed to (1) explore associations between human milk/direct breastfeeding and neurodevelopment at 1-year and 2-year follow-up and (2) describe patterns of human milk (maternal, donor) and commercial formula during hospitalisation in the first year of life.This retrospective cohort study included infants who underwent surgery for CHD < 6 months old. The primary outcome was neurodevelopment via Bayley Scales of Infant Development-IV. Analysis included adjusted linear regression for associations between exclusive human milk while inpatient during the first 6 months or any direct breastfeeding while inpatient during the first year of life and 1-year Bayley-IV scores. Models were adjusted for race, insurance type, genetic diagnosis, and length of stay.Of 98 eligible infants, 40% followed up at 1 year; 27% at 2 years. There were differences in follow-up related to demographics (race, ethnicity) and social determinants of health (insurance type, distance from clinic). In adjusted models, infants who directly breastfed had 13.18 points higher cognition (95% CI: 0.84-25.53, p = 0.037); 14.04 points higher language (2.55-25.53, p = 0.018); and 15.80 points higher motor scores (3.27-28.34, p = 0.015) at 1-year follow-up. Infants fed exclusive human milk had 12.64 points higher cognition scores (-0.53-25.82, p = 0.059).Future investigation into nutrition and neurodevelopment in the context of critical CHD is warranted. As neurodevelopmental follow-up becomes standard of care in this population, efforts are needed to mitigate disparities in access to this care.","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":null,"pages":null},"PeriodicalIF":1.0,"publicationDate":"2024-05-13","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"140911425","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Truncus arteriosus from prenatal diagnosis to clinical outcome: a single-centre experience. 动脉导管未闭从产前诊断到临床结果：单中心经验。

IF 1 4区医学

Cardiology in the Young Pub Date : 2024-05-13 DOI: 10.1017/S1047951124025071

Nina A Korsuize, Wouter Bakhuis, Bram van Wijk, Heynric B Grotenhuis, Henriëtte Ter Heide, Michelle Cohen de Lara, Zina Fejzic, Paul H Schoof, Felix Haas, Trinette J Steenhuis

{"title":"Truncus arteriosus from prenatal diagnosis to clinical outcome: a single-centre experience.","authors":"Nina A Korsuize, Wouter Bakhuis, Bram van Wijk, Heynric B Grotenhuis, Henriëtte Ter Heide, Michelle Cohen de Lara, Zina Fejzic, Paul H Schoof, Felix Haas, Trinette J Steenhuis","doi":"10.1017/S1047951124025071","DOIUrl":"https://doi.org/10.1017/S1047951124025071","url":null,"abstract":"Background: The aim of this study was to review our institution's experience with truncus arteriosus from prenatal diagnosis to clinical outcome.Methods: and results: We conducted a single-centre retrospective cohort study for the years 2005-2020. Truncus arteriosus antenatal echocardiographic diagnostic accuracy within our institution was 92.3%. After antenatal diagnosis, five parents (31%) decided to terminate the pregnancy. After inclusion from referring hospitals, 16 patients were offered surgery and were available for follow-up. Right ventricle-to-pulmonary artery continuity was preferably established without the use of a valve (direct connection), which was possible in 14 patients (88%). There was no early or late mortality. Reinterventions were performed in half of the patients at latest follow-up (median follow-up of 5.4 years). At a median age of 5.5 years, 13 out of 14 patients were still without right ventricle-to-pulmonary artery valve, which was well tolerated without signs of right heart failure. The right ventricle demonstrated preserved systolic function as expressed by tricuspid annular plane systolic excursion z-score (-1.4 ± 1.7) and fractional area change (44 ± 12%). The dimensions and function of the left ventricle were normal at latest follow-up (ejection fraction 64.4 ± 6.2%, fractional shortening 34.3 ± 4.3%).Conclusions: This study demonstrates good prenatal diagnostic accuracy of truncus arteriosus. There was no mortality and favourable clinical outcomes at mid-term follow-up, with little interventions on the right ventricle-to-pulmonary artery connection and no right ventricle deterioration. This supports the notion that current perspectives of patients with truncus arteriosus are good, in contrast to the poor historic outcome series. This insight can be used in counselling and surgical decision-making.","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":null,"pages":null},"PeriodicalIF":1.0,"publicationDate":"2024-05-13","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"140911426","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Against all odds: successful pregnancy in an adult patient with unrepaired coarctation of the aorta. 排除万难：主动脉闭塞未修复的成年患者成功怀孕。

IF 1 4区医学

Cardiology in the Young Pub Date : 2024-05-13 DOI: 10.1017/S1047951124025113

Davide Sorice, Rosaria Barracano, Berardo Sarubbi

引用次数: 0

The efficacy of the use of atropine in children with reflex anoxic syncope during pallid breath-holding spells: can cardiac pacemaker implantation be avoided? 使用阿托品治疗苍白性憋气时反射性缺氧晕厥患儿的疗效：能否避免植入心脏起搏器？

IF 1 4区医学

Cardiology in the Young Pub Date : 2024-05-10 DOI: 10.1017/S1047951124025101

Marieke Donné, Kristof Vandekerckhove, Hans De Wilde

{"title":"The efficacy of the use of atropine in children with reflex anoxic syncope during pallid breath-holding spells: can cardiac pacemaker implantation be avoided?","authors":"Marieke Donné, Kristof Vandekerckhove, Hans De Wilde","doi":"10.1017/S1047951124025101","DOIUrl":"https://doi.org/10.1017/S1047951124025101","url":null,"abstract":"Objectives: Reflex anoxic syncope is the result of an overreaction of the vagal system, resulting in hypotension and bradycardia or brief cardiac arrest. Because of the benign character and the absence of complications in short or long term, treatment is only necessary in case of frequent or severe clinical presentation. Treatment options are anticholinergic drugs or cardiac pacemaker placement. We investigated atropine treatment and aimed to examine if pacemaker placement can be avoided.Methods: We retrospectively reviewed patients treated with atropine for severe reflex anoxic syncope in our centre from January 2017 until May 2023, and compared our results to those in the literature.Results: The study population consisted of 10 children, 70% female, with an age ranging from 5 months to 3 years (mean 14.5 months) when atropine treatment was started (dose 17-50 microg/kg/day). All patient's parents reported adequate symptom management during atropine treatment, with complete resolution in 10%. Minor side effects were reported in 60% (dry mucosa in 40%, obstipation in 20%, and nausea or blurry vision in 10%).Discussion: We consider atropine a safe and effective treatment to manage reflex anoxic syncope with similar success rate to pacemaker implantation. However, pacemaker implantation entails substantial risk for complications (up to 25%) such as infection or technical problems and morbidity such as scar formation. This might be considered redundant for a benign and temporary condition, certainly given the possibility of other efficient treatment options. Consequently, we recommend atropine treatment over implantation of a cardiac pacemaker in children with severe reflex anoxic syncope.","PeriodicalId":9435,"journal":{"name":"Cardiology in the Young","volume":null,"pages":null},"PeriodicalIF":1.0,"publicationDate":"2024-05-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"140897270","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0