COCHLEAR IMPLANTS INTERNATIONAL最新文献

{"title":"The impact of prematurity on cochlear implant outcomes: A case-control study.","authors":"Idit Tessler, Yehonatan Adler, Nir A Gecel, Noam Symon, Ziva Yakir, Yael Henkin, Yisgav Shapira, Eldar Carmel, Amit Wolfovitz","doi":"10.1080/14670100.2025.2494922","DOIUrl":"https://doi.org/10.1080/14670100.2025.2494922","url":null,"abstract":"<p><strong>Objective: </strong>Despite a higher prevalence of hearing loss in preterm-born infants, cochlear implantation (CI) outcome remains underexplored in this unique subpopulation. We aimed to compare long-term hearing outcomes between preterm- and term-born infants undergoing CI and identify prognostic factors of hearing outcomes among preterm infants post-CI.</p><p><strong>Methods: </strong>This retrospective case-control study compared preterm infants (study group) with two control groups who underwent CI: One group of term infants was matched for hearing loss etiology and the other group was comprised of term infants with a genetic etiology [connexin-26 (GJB2)], the benchmark for favorable CI outcomes. Subgroup analyses were based upon birth weight and gestational age. Primary outcomes included long-term speech reception threshold (SRT) and monosyllabic word identification (HAB) scores.</p><p><strong>Results: </strong>A total of 161 implanted ears were included: 35 (22%) in the study group, 63 (39%) in the etiology-matched control group, and 63 (39%) in the GJB2 group. SRT was significantly lower in the GJB2 group compared to the study group (<i>p</i> = 0.007) but not between the study and the etiology-matched control group (<i>p</i> = 0.79). HAB scores were comparable among the three groups. A subgroup analysis revealed significant differences in word identification by birth weight, particularly in the <1000 g group. A linear mixed model analysis indicated significant improvements in HAB scores over time for all groups (<i>p</i> < 0.0001), with comparable HAB progress (<i>p</i> = 0.98).</p><p><strong>Conclusion: </strong>Our findings suggest that prematurity does not significantly impact speech perception outcomes among CI recipients. Low birth weight in preterm infants, however, emerged as a negative prognostic factor for language perception outcomes.</p>","PeriodicalId":53553,"journal":{"name":"COCHLEAR IMPLANTS INTERNATIONAL","volume":" ","pages":"1-9"},"PeriodicalIF":1.4,"publicationDate":"2025-06-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144227603","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Reading abilities of adolescents with cochlear implants: the role of early speech perception in a longitudinal study.","authors":"Lisa S Davidson, Ann E Geers, Rosalie M Uchanski","doi":"10.1080/14670100.2025.2507477","DOIUrl":"https://doi.org/10.1080/14670100.2025.2507477","url":null,"abstract":"<p><strong>Objective: </strong>To examine reading skills of adolescents who use cochlear implants (CIs) and who were implanted early. Three questions are asked: (1) Do these pediatric CI recipients read at age-appropriate levels at adolescence, as they had done at elementary-ages (Grantham et al. [2022]. Effects of segmental and suprasegmental speech perception on reading in pediatric cochlear implant recipients. <i>Journal of Speech, Language and Hearing Research</i>, <i>65</i>(9), 3583-3594. https://doi.org/10.1044/2022_JSLHR-22-00035 )? (2) Are the previously documented effects of early segmental and suprasegmental speech perception on elementary-age reading skills obtained for adolescent reading skills? (3) Do the effects on adolescent reading differ for early speech perception versus elementary-age speech perception?</p><p><strong>Design: </strong>Eighty-six orally educated children with a mean age of CI of 2 years completed a standardized reading comprehension test at elementary ages (7-11 years) and at adolescent ages (11-16 years). They completed speech perception tests when they were 5-9 years old (early) and again at 7-11 years of age (elementary-age). Reading comprehension scores from elementary and adolescent ages were compared, and the effects of early and elementary-age speech perception on adolescent reading were examined.</p><p><strong>Results: </strong>The mean reading passage comprehension standard score was within the normative range for typically hearing age-mates at both elementary-age and adolescent testing. Early suprasegmental speech perception was the only significant speech perception predictor of adolescent reading skills, after controlling for demographic and audiological variables.</p><p><strong>Conclusions: </strong>These data bolster the recent literature reporting good reading skills, on average, for children who received early CIs and highlight the long-term benefits of good early suprasegmental speech perception skills. Both segmental and suprasegmental perception should be included in audiological candidacy criteria and educational intervention for children with CIs.</p>","PeriodicalId":53553,"journal":{"name":"COCHLEAR IMPLANTS INTERNATIONAL","volume":" ","pages":"1-10"},"PeriodicalIF":1.4,"publicationDate":"2025-05-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144183030","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Cryoablation of the superficial cervical plexus for post cochlear implantation lesser occipital neuralgia.","authors":"Gabriel Ricardo Lichtenstein, Basher Mwassi, Amit Wolfovitz, Michelle Nigri Levitan, Ofir Morag, Yisgav Shapira","doi":"10.1080/14670100.2025.2491918","DOIUrl":"https://doi.org/10.1080/14670100.2025.2491918","url":null,"abstract":"<p><strong>Objective and importance: </strong>Chronic pain following cochlear implantation (CI) is a notable complication that can lead to device explantation. This case report describes the successful treatment of post-CI lesser occipital neuralgia using cryoablation of the superficial cervical plexus (SCP).</p><p><strong>Clinical presentation: </strong>A 25-year-old female patient developed localized pain following CI reimplantation, presenting with allodynia and dysesthesia in the left lesser occipital nerve distribution. After a positive diagnostic SCP block providing temporary relief, ultrasound-guided cryoablation was performed.</p><p><strong>Conclusion: </strong>The procedure resulted in complete pain resolution and anesthesia in the distribution of the lesser occipital, greater auricular, and transverse cervical nerves. While pain recurrence occurred after seven months necessitating repeat treatment, the intervention proved to be a safe and effective management strategy for post-CI neuralgia. This case demonstrates that SCP cryoablation may offer a viable, minimally invasive solution for patients experiencing post-CI neuralgic pain, with the potential for repeated applications as needed.</p>","PeriodicalId":53553,"journal":{"name":"COCHLEAR IMPLANTS INTERNATIONAL","volume":" ","pages":"1-4"},"PeriodicalIF":1.4,"publicationDate":"2025-05-23","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144129118","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Hospital service utilisation and treatment costs before and after cochlear implantation in adults with hearing loss: a retrospective cohort study.","authors":"Tolesa Okuba, Reidar P Lystad, Isabelle Boisvert, Anne McMaugh, Robyn Cantle Moore, Peter Wolnizer, Cassidy Chow, Ramya Walsan, Rebecca Mitchell","doi":"10.1080/14670100.2025.2504265","DOIUrl":"https://doi.org/10.1080/14670100.2025.2504265","url":null,"abstract":"<p><strong>Objective: </strong>Hearing loss can lead to a higher health service use which may be reduced by using hearing technology. This study aimed to examine pre- and post-cochlear implant hospital service use and treatment costs of adults with hearing loss.</p><p><strong>Methods: </strong>A retrospective cohort study was conducted using linked hospital admission and mortality data in New South Wales, Australia. Adults aged ≥18 years who received a cochlear implant between 2015- and 2017 were included. Outcomes included all-cause hospital admissions, total hospital length of stay (LOS) and treatment costs in 4 years prior to- and 4 years post-implant. A negative binomial regression model was used to examine characteristics associated with hospitalisation.</p><p><strong>Results: </strong>There were 1159 individuals who received a cochlear implant between 2015- and 2017. Adults aged ≥65 years had a higher number of all-cause hospitalisations post-implant (65.7%) compared with pre-implant (57.9%). The median hospital LOS was 5.0 days (IQR 13.0) pre- and 6.0 days (IQR 19.0) post-implant. Being of aged ≥65 years, having comorbidity and a fall-related injury were associated with both pre- and post-implant hospitalisations. Having a mental health disorder was additionally associated with pre-implant hospitalisations. The median treatment costs were AUD$10,790 (IQR 27,595) pre- and AUD$9,444 (IQR 31,945) post-implant.</p><p><strong>Conclusion: </strong>Adults aged ≥65 years, with comorbidities, fall-related injuries and mental health disorders faced higher hospitalisation. Adults encountered higher treatment costs pre-implantation, but these costs decreased post-implant. This suggests a need for tailored pre- and post-operative care strategies to mitigate risks and manage costs effectively.</p>","PeriodicalId":53553,"journal":{"name":"COCHLEAR IMPLANTS INTERNATIONAL","volume":" ","pages":"1-10"},"PeriodicalIF":1.4,"publicationDate":"2025-05-18","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144095809","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Cochlear implant services for Spanish speaking patients: language access and organizational health literacy of programs in the United States of America.","authors":"Alejandra Ullauri, Tessa Kramer, Valeriy Shafiro","doi":"10.1080/14670100.2025.2500830","DOIUrl":"https://doi.org/10.1080/14670100.2025.2500830","url":null,"abstract":"<p><strong>Objective: </strong>To examine the accessibility of online information about cochlear implant (CI) services for Spanish speakers and evaluate organizational health literacy practices in CI programs in the United States (USA).</p><p><strong>Method: </strong>From a list provided by Cochlear, CI programs working with at least two of three CI manufacturers were identified in eight states. Selected states had the highest and lowest Hispanic populations in each of the four US geographic regions. Online information access was evaluated based on whether programs' website links were a) listed on manufacturers' 'Find-a-Clinic' tabs, b) led directly to the CI program website, c) provided information about CIs in Spanish, and d) the readability level of such information. To examine language access, researchers determined if listed programs' phone numbers connected to the department providing CI services and the availability of Spanish speaking schedulers, audiologists, ENT surgeons, and professional interpreters (PIs).</p><p><strong>Results: </strong>122 CI programs met the inclusion criteria. Only 4-9% of listed programs had a link connecting directly to the CI program's website, and only 11% had Spanish-language CI information. Spanish text averaged 10th grade readability (Flesch-Kincaid). Phone contacts showed 78% of numbers connected directly to the ENT/Audiology department, while only 27% offered an initial Spanish option. PIs were available in 68% of programs.</p><p><strong>Conclusions: </strong>Results indicate reduced language access for Spanish speakers seeking CI services in the USA, exemplified by limited access to PIs and bilingual providers, insufficient availability of information about CIs on programs' websites, and low organization health literacy practices in CI programs.</p>","PeriodicalId":53553,"journal":{"name":"COCHLEAR IMPLANTS INTERNATIONAL","volume":" ","pages":"1-9"},"PeriodicalIF":1.4,"publicationDate":"2025-05-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144082057","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Customized strategies for managing cochlear implant stimulation side effects.","authors":"Xianhui Wang, Phillip Tran, Michelle R Kapolowicz, Thomas Lu, Ginger Stickney, Arnold Starr, Hamid Djalilian, Fan-Gang Zeng","doi":"10.1080/14670100.2025.2484860","DOIUrl":"https://doi.org/10.1080/14670100.2025.2484860","url":null,"abstract":"<p><strong>Objectives: </strong>Cochlear implants restore functional hearing but may cause side effects like facial nerve stimulation, sound sensitivity or reactive tinnitus. The present study aimed to establish a general framework for optimizing stimulation parameters to manage these side effects while maximizing speech perception performance. A second objective was to understand how side effect origins impact treatment outcomes.</p><p><strong>Methods: </strong>Eight adult cochlear implant subjects had intolerable side effects that rendered device usage difficult or even impossible. New maps were created by reducing stimulation levels, increasing pulse duration, reducing stimulation rate, altering channel gains and frequency maps, deactivating problematic electrodes, or a combination of the above. Outcomes were measured in terms of side effect reduction and changes in speech performance.</p><p><strong>Results: </strong>Facial nerve stimulation was reduced or eliminated in five of five subjects. Sound hypersensitivity was eliminated in two of two subjects. Tinnitus was alleviated in three of four subjects, while the remaining one with cerebellar malformation experienced no change. Speech performance was either maintained or improved in all subjects. Except for the subject with cerebellar malformation who chose to explant the device, all subjects were able to use the implant effectively without bothersome side effects.</p><p><strong>Discussion: </strong>Facial nerve stimulation is usually related to electric current spread on the same side, which can be effectively managed by customized strategies. In contrast, the origins of sound sensitivity and reactive tinnitus are more variable and likely more difficult to manage.</p><p><strong>Conclusion: </strong>Customized mapping can alleviate cochlear implant side effects without compromising speech performance.</p>","PeriodicalId":53553,"journal":{"name":"COCHLEAR IMPLANTS INTERNATIONAL","volume":" ","pages":"1-14"},"PeriodicalIF":1.4,"publicationDate":"2025-04-03","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143774873","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"The effect of current amplitude and multi-electrode stimulation on eSRT for auditory fitting in cochlear implants with pulse-width loudness coding.","authors":"Behnam Molaee-Ardekani, Pedro Goiana-Martins, Manuel Segovia-Martinez, Leonel Luís","doi":"10.1080/14670100.2025.2457200","DOIUrl":"10.1080/14670100.2025.2457200","url":null,"abstract":"<p><strong>Objective: </strong>Neurophysiologic measures like the electrically evoked Stapedius Reflex Threshold (eSRT) offer valuable insights into personalized responses to Cochlear Implant (CI) stimuli. This study evaluates the effects of stimulation current amplitude and the number of stimulating electrodes on eSRT and its correlation with the Most Comfortable Loudness level (MCL or C-level) in all-polar, pseudo-monophasic, pulse-width loudness coded stimulations.</p><p><strong>Approach: </strong>The study was conducted on seventeen adult patients with Oticon Medical implants. In these implants, current amplitude remains constant while loudness is coded through pulse-width. Stimulation amplitudes were set to low (default clinical) and high values, using single or multi electrode groups of 1, 3, and 5 (G1, G3, and G5) across five cochlear regions, spanning from apical to basal. For each amplitude and group, the eSRT detection rate and correlation with MCL were analyzed regionally and overall.</p><p><strong>Results: </strong>Higher eSRT detection rates were observed in the contra-lateral ear, with G3 and G5 significantly enhancing detection over G1 for both low and high amplitudes. The current amplitude facilitated eSRT invocation, particularly for G1 and patients with higher MCLs. The correlation between eSRT and MCL was relatively high (<i>r</i> = 0.64-0.87) across all conditions, indicating accurate MCL estimation from eSRT at both low and high amplitudes.</p><p><strong>Discussions: </strong>Among all condition interactions (amplitude, side, electrodes), low-amplitude contra-lateral G5 and high-amplitude contra-lateral G3 showed optimal modes for estimating MCL from eSRT, with linear slopes near 1.0, and detection rates of 54% and 63%, respectively. High-amplitude contra-lateral G5 further increased detection to 68%, though with a slope of 0.8, requiring a correction factor. These findings provide insights into eSRT mechanisms and its application in pseudo-monophasic all-polar CI programming.</p><p><strong>Conclusion: </strong>The eSRT detection rate can be improved in pulse-width modulation cochlear implants by using multi-electrode stimulation and/or increasing the stimulation amplitude beyond the default clinical value, without significantly affecting the correlation coefficient between eSRT and MCL.</p>","PeriodicalId":53553,"journal":{"name":"COCHLEAR IMPLANTS INTERNATIONAL","volume":" ","pages":"30-42"},"PeriodicalIF":1.4,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143076559","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Effects of electro-acoustic stimulation on gated word recognition.","authors":"Chhayakanta Patro, Ellen Shephard, Nirmal Kumar Srinivasan","doi":"10.1080/14670100.2025.2475618","DOIUrl":"10.1080/14670100.2025.2475618","url":null,"abstract":"<p><strong>Objective: </strong>The objective of this study was to determine how the presentation of unprocessed speech, either ipsilaterally (to simulate electro-acoustic stimulation, EAS) or contralaterally (to simulate bimodal stimulation), alongside vocoder-processed speech affects the efficiency of spoken word processing.</p><p><strong>Method: </strong>Gated word recognition was performed under four listening conditions: full-spectrum speech, vocoder-processed speech, electro-acoustic stimulation (EAS), and bimodal stimulation. In the EAS condition, low-frequency unprocessed speech and high-frequency vocoder-processed speech were presented to the same ear, while in the bimodal condition, full-spectrum speech was presented to one ear and vocoder-processed speech to the other.</p><p><strong>Results: </strong>Listeners identified target words accurately with just over half of the word duration in the full-spectrum condition, whereas nearly the entire word was required for correct identification with vocoder-processed speech. Combining full-spectrum speech and vocoder-processed speech, whether ipsilaterally or contralaterally, led to significant improvements in gated word recognition. Full-spectrum speech yielded the best-gated word recognition performance, followed by bimodal stimulation, with intermediate results from EAS and the lowest performance from the vocoder condition.</p><p><strong>Conclusion: </strong>Inherent limitations in CI spectral resolution can impair spoken word processing. Adding acoustic stimulation can improve gated word recognition performance. Bimodal stimulation significantly enhances lexical processing timing compared to EAS in one ear.</p>","PeriodicalId":53553,"journal":{"name":"COCHLEAR IMPLANTS INTERNATIONAL","volume":" ","pages":"63-72"},"PeriodicalIF":1.4,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143607237","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"The relationship between AutoNRT thresholds and subjective programming levels revisited.","authors":"Andreas Björsne, Lennart Magnusson","doi":"10.1080/14670100.2025.2455891","DOIUrl":"10.1080/14670100.2025.2455891","url":null,"abstract":"<p><strong>Objectives: </strong>The aim of this study wasto systemically examine the relationship between AutoNRT thresholds and subjective programming levels by controlling for individual subject variation, and further, to propose an alternative way to calculate the AutoNRT threshold profile for programming purposes.</p><p><strong>Methods: </strong>The study was a prospective observational study. AutoNRT thresholds, T- and C-levels were recorded at six and twelve months after activation. All subjects had received a CI24RE implant.</p><p><strong>Results: </strong>Forty-one adults participated in the study. A linear mixed-effects model analysis of the relationship between the AutoNRT thresholds and the T-and C-levels resulted in a large unexplainable variation between subjects, the standard deviation was between 15.42 and 18.89 CL. However, the study showed that the profiles for the T- and C-levels could be predicted with an acceptable accuracy from AutoNRT. A model for calculating profiles from AutoNRT thresholds based on linear regression resulted in the lowest deviation from the subjective programming thresholds, with somewhat better results for C-levels than T-levels.</p><p><strong>Conclusion: </strong>The results from this study showed that the predictability was reasonable when calculating the profiles for the T- and C-levels based on AutoNRT. And, further, that AutoNRT thresholds can be used when programming cochlear implants, to make global adjustments without predicting actual T- or C-levels.</p>","PeriodicalId":53553,"journal":{"name":"COCHLEAR IMPLANTS INTERNATIONAL","volume":" ","pages":"1-11"},"PeriodicalIF":1.4,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143069484","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Audiological profile in children with congenital inner ear anomalies.","authors":"Mohamed Mohamed El-Badry, Amira Fawzy, Mohamed Makhlouf Hasan, Fatma Refat","doi":"10.1080/14670100.2025.2457202","DOIUrl":"10.1080/14670100.2025.2457202","url":null,"abstract":"<p><strong>Objectives: </strong>The current study aims to describe subjects and audiological profiles of children with congenital inner ear anomalies (IEAs).</p><p><strong>Materials and methods: </strong>A total of 193 children with sensorineural hearing loss (SNHL) and radiological evidence of one or more congenital IEAs were included.</p><p><strong>Results and discussion: </strong>The most common IEAs in the current study was enlarged vestibular aqueduct (EVA) either isolated or associated with other IEAs. Incomplete partition (IP) with its three types (IP I, IP II, and IP III) was the second common anomaly, followed by cochlear hypoplasia (CH). At the time of radiological diagnosis, hearing loss degrees ranged from mild to profound in children with EVA, CH III, and CH IV with the majority having severe or profound degrees. The prevalence of severe and profound degree of hearing loss was higher in children with IP than children with isolated EVA or CH III and CH IV. In children with isolated EVA, hearing loss was asymmetric in 52.2% and progressive in 58%. In children with CH III and CH IV, hearing loss was asymmetric but stationary. Only children with EVA and IP III had air-bone gab (ABG) at low frequencies, while children with other IEAs did not have ABG except if there was an association with EVA. Children with severe anomalies such as CH I, CH II, common cavity, and cochlear nerve hypoplasia had profound degrees of hearing loss or just sound detection.</p><p><strong>Conclusions: </strong>Knowing the audiological profile of children with IEAs has important clinical implications in the management of those children.</p>","PeriodicalId":53553,"journal":{"name":"COCHLEAR IMPLANTS INTERNATIONAL","volume":" ","pages":"43-62"},"PeriodicalIF":1.4,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143076558","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}