JPGN reportsPub Date : 2024-02-05eCollection Date: 2024-05-01DOI: 10.1002/jpr3.12027
Rachel B Schenker, Brian Kim, George Yanni
{"title":"Letter to the editor: A response to Hildreth and Schwimmer.","authors":"Rachel B Schenker, Brian Kim, George Yanni","doi":"10.1002/jpr3.12027","DOIUrl":"10.1002/jpr3.12027","url":null,"abstract":"","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"5 2","pages":"236-237"},"PeriodicalIF":0.0,"publicationDate":"2024-02-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11093906/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"140961449","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
JPGN reportsPub Date : 2024-02-05DOI: 10.1002/jpr3.12047
Daniel M. O'Connell, Jonathan Moses
{"title":"Invited commentary to immunotherapy withdrawal by step‐down to mesalamine in pediatrics patients with ulcerative colitis","authors":"Daniel M. O'Connell, Jonathan Moses","doi":"10.1002/jpr3.12047","DOIUrl":"https://doi.org/10.1002/jpr3.12047","url":null,"abstract":"","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"69 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2024-02-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139863233","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
JPGN reportsPub Date : 2024-01-30DOI: 10.1002/jpr3.12018
Mindy Huynh, Rodolfo Silva, Nikhil Thiruvengadam, K. Parashette
{"title":"Idiopathic fibrosing pancreatitis: A rare cause of obstructive jaundice","authors":"Mindy Huynh, Rodolfo Silva, Nikhil Thiruvengadam, K. Parashette","doi":"10.1002/jpr3.12018","DOIUrl":"https://doi.org/10.1002/jpr3.12018","url":null,"abstract":"Jaundice is an important physiologic manifestation of both benign and insidious diseases. We report on the case of an 11‐year‐old male who presented with diffuse pruritis, jaundice, and later abdominal pain. Initial work‐up revealed an obstructive cholestatic pattern, warranting investigation for structural anomalies. Extensive imaging revealed a lesion on the pancreatic head, and biopsy of the lesion confirmed the diagnosis of idiopathic fibrosing pancreatitis (IFP). Temporary stenting of the common bile duct successfully treated our patient's symptomatic IFP.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"229 ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2024-01-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"140480830","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Mucosal prolapse syndrome mimicking Peutz–Jeghers syndrome in a pediatric patient","authors":"Phinga Do, Claudia Phen, Michele Alkalay, Vivekanand Singh, Isabel Rojas","doi":"10.1002/jpr3.12022","DOIUrl":"https://doi.org/10.1002/jpr3.12022","url":null,"abstract":"Mucosal prolapse syndrome (MPS) is a rare group of benign conditions characterized by a set of unifying histologic findings thought to be the result of repeated mucosal shearing and submucosal vascular congestion caused by straining. This set of conditions is often misdiagnosed as other polyposis syndromes, inflammatory bowel disease, or malignancy due to its clinical presentation, appearance, and rarity. We report a case of a 15‐year‐old male who presented with painless rectal bleeding. He was found to have four rectal polyps thought to be due to Peutz–Jeghers syndrome. A repeat colonoscopy with biopsies a year later revealed a diagnosis of MPS. Our case highlights the morphologic similarity between hamartomatous polyp and mucosal prolapse histology. Since MPS is a rare diagnosis even among the adult population, it has not been well described in pediatrics. This syndrome should be on the differential diagnosis for pediatric rectal polyps to prevent unnecessary invasive testing and a delay in treatment.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"57 15","pages":""},"PeriodicalIF":0.0,"publicationDate":"2024-01-29","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"140487245","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
JPGN reportsPub Date : 2024-01-25DOI: 10.1002/jpr3.12039
Ahmad Miri, Shahab Abdessalam, Andria M. Powers, Ruben E. Quiros‐Tejeira, Chinenye R Dike
{"title":"Gallbladder remnant: A potential source for biliary stones postcholecystectomy; a case report in a child with sickle cell disease","authors":"Ahmad Miri, Shahab Abdessalam, Andria M. Powers, Ruben E. Quiros‐Tejeira, Chinenye R Dike","doi":"10.1002/jpr3.12039","DOIUrl":"https://doi.org/10.1002/jpr3.12039","url":null,"abstract":"Stone formation in a gallbladder remnant is a rare postcholecystectomy complication. This report describes the case of gallstones in a gallbladder remnant of an adolescent with sickle cell disease (SCD) years after laparoscopic cholecystectomy. A 15‐year‐old female with SCD presented to our gastroenterology clinic with concerns of recurrent choledocholithiasis despite cholecystectomy 2 years before presentation. About 4 months before presentation to our clinic, she was evaluated at the referring physician's emergency department for recurrent severe abdominal pain of 1 month duration. After admission to the hospital, common bile duct stones were seen on magnetic resonance cholangiopancreatography (MCRP) imaging and subsequently removed via endoscopic retrograde cholangiopancreatography (ERCP). On review of her MRCP and ERCP at our hospital, a remnant of gallbladder containing multiple stones was identified. She subsequently underwent a laparoscopic resection of the gallbladder remnant. Clinicians should consider biliary duct imaging in children with biliary colic following cholecystectomy, especially those with history of chronic hemolysis.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"3 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2024-01-25","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139596886","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
JPGN reportsPub Date : 2024-01-25DOI: 10.1002/jpr3.12042
Katia N. Estrada‐Medrano, Sergio J. Fernández‐Ortiz, Oscar Tamez-Rivera, E. Villarreal
{"title":"Congenital mixed hiatal hernia: A case report of an atypical cause of neonatal vomiting","authors":"Katia N. Estrada‐Medrano, Sergio J. Fernández‐Ortiz, Oscar Tamez-Rivera, E. Villarreal","doi":"10.1002/jpr3.12042","DOIUrl":"https://doi.org/10.1002/jpr3.12042","url":null,"abstract":"Congenital mixed hiatal hernia is a disorder that combines features of both sliding and paraoesophageal hernias. The precise incidence of congenital mixed hiatal hernia during the pediatric and neonatal period remains uncertain, making diagnosis challenging within this age cohort. This case presents a 15‐day‐old female with an 8% postnatal weight loss and apost‐feeding vomiting. An upper gastrointestinal series, computer tomography, and upper endoscopy revealed a mixed hiatal hernia. The patient underwent a laparoscopic herniorrhaphy and Nissen fundoplication achieving successful resumption of complete oral feeding before discharge. Diagnosis and management of this condition in neonates remain challenging due to its rarity and variable clinical presentations. This report emphasizes the importance of early recognition, accurate diagnosis, and tailored management strategies in the neonatal period. Further research, with a collaborative effort between pediatricians and surgeons, is needed to refine diagnostic criteria, establish evidence‐based management approaches, and improve outcomes for affected children.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"54 6","pages":""},"PeriodicalIF":0.0,"publicationDate":"2024-01-25","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139598682","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
JPGN reportsPub Date : 2024-01-25DOI: 10.1002/jpr3.12033
Olivier Goulet, E. Payen, C. Talbotec, C. Poisson, Amélia Rocha, Karina Brion, Marie‐Bernadette Madras, Isabelle Eicher, Isabelle Martinez, Clémence Bégo, Céline Chasport, Julie Ollivier, Cécile Godot, Claude Villain, Francisca Joly, C. Lambe
{"title":"An innovative educational program for adolescents on home parenteral nutrition for the “transition” to adulthood","authors":"Olivier Goulet, E. Payen, C. Talbotec, C. Poisson, Amélia Rocha, Karina Brion, Marie‐Bernadette Madras, Isabelle Eicher, Isabelle Martinez, Clémence Bégo, Céline Chasport, Julie Ollivier, Cécile Godot, Claude Villain, Francisca Joly, C. Lambe","doi":"10.1002/jpr3.12033","DOIUrl":"https://doi.org/10.1002/jpr3.12033","url":null,"abstract":"Facing with an increasing demand for transition to adult care management, our home parenteral nutrition (HPN) team designed an adolescent therapeutic educational program (ATEP) specifically intended for adolescents on long‐term HPN. The aim of this study was to report on the first sessions of this program.The ATEP is designed in three sessions of five consecutive days, during school holidays over the year. It includes group sessions on catheter handling, disconnecting and connecting the PN and catheter dressing, dealing with unforeseen events (e.g., fever or catheter injury), but also sessions with psychologist, social worker, sports teacher, fashion specialist, meeting with adults who received HPN since childhood. Specific course for the accompanying parents were also provided. Six months after the last session, a 3‐day trip to the attraction park “le Futuroscope,” Poitiers, France, was organized without any parental presence.After 3 ATEP courses, a total of 16 adolescents have been enrolled. They were aged between 13 and 17 years (median 14 IQR: 14–16.25). All were on long term HPN started during the neonatal period except for four who started PN at a median age of 10 years old (IQR: 1–10). At the time of the ATEP, their median PNDI was 105% (IQR: 95.5–120.8) while receiving a median of six infusions per week (IQR: 5–7). Thirteen received Taurolidine lock procedure. After the ATEP, 11 adolescents could be considered as fully autonomous, 4 as partially autonomous and one failed to gain any autonomy. Course evaluation by adolescents or parents was good to excellent.Through the holistic and multiprofessional approach of this training and the group cohesion, the adolescents were not only able to handle catheter care and PN connections but were able to understand and accept better their illness and project themselves into their own future.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"92 6","pages":""},"PeriodicalIF":0.0,"publicationDate":"2024-01-25","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139596631","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
JPGN reportsPub Date : 2024-01-23DOI: 10.1002/jpr3.12024
Anna Kozłowska‐Jalowska, A. Stróżyk, Andrea Horvath, H. Szajewska
{"title":"Evaluating the impact of lactase supplementation on infant colic: Study protocol for a systematic review of randomized controlled trials","authors":"Anna Kozłowska‐Jalowska, A. Stróżyk, Andrea Horvath, H. Szajewska","doi":"10.1002/jpr3.12024","DOIUrl":"https://doi.org/10.1002/jpr3.12024","url":null,"abstract":"Infant colic is a common functional gastrointestinal disorder that affects infants during their first months of life. The etiology of this condition remains unclear. However, some studies suggest lactase deficiency may be a contributing factor. Currently, the evidence on dietary treatment and lactase supplementation for management of infant colic is limited. We aim to systematically review evidence on the efficacy and safety of using a lactase supplementation for managing infant colic. The Cochrane Central Register of Controlled Trials (CENTRAL, the Cochrane Library), MEDLINE, and EMBASE will be searched to identify randomized controlled trials comparing oral lactase supplementation with placebo or no intervention in infants aged less than 6‐month‐old with infant colic using any recognized definition. The risk of bias will be assessed using the second version of the Cochrane Collaboration's risk‐of‐bias tool. The main outcome will be the number of responders in each group after treatment, defined as infants who experienced a decrease in daily crying as reported by the study authors. Additional outcomes will include the duration and frequency of crying episodes, infant sleep duration, parental satisfaction, discomfort of infants, number of hospital admissions, family quality of life, and adverse events during the intervention. The study findings will be published in a peer‐reviewed journal and will be submitted to relevant conferences.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"105 19","pages":""},"PeriodicalIF":0.0,"publicationDate":"2024-01-23","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139605668","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
JPGN reportsPub Date : 2024-01-18DOI: 10.1002/jpr3.12040
Carolena Trocchia, H. Shieh, Isabella Dolan, Michael J Wilsey, C. J. Smithers
{"title":"Pulling instead of pushing: A case report of gastrostomy‐assisted pull technique as an alternative method for endoluminal sponge placement in EVAC therapy","authors":"Carolena Trocchia, H. Shieh, Isabella Dolan, Michael J Wilsey, C. J. Smithers","doi":"10.1002/jpr3.12040","DOIUrl":"https://doi.org/10.1002/jpr3.12040","url":null,"abstract":"Endoscopic vacuum‐assisted therapy offers an easier and safer alternative to thoracic surgery, self‐expanding stents, or esophageal clips and has been shown to be a promising technique for management of pediatric esophageal perforations. In this report, we present a novel application of a percutaneous endoscopic gastrostomy‐assisted pull technique, wherein a preexisting gastrostomy is reaccessed to allow safe placement of the vacuum sponge with a more comfortable and effective endoscopic vacuum‐assisted closure therapy compared to transnasal or transoral options. A 7‐year‐old male with a history of type C esophageal atresia with distal tracheoesophageal fistula complicated by leak and refractory esophageal stricture, severe tracheomalacia, and prior esophageal stricture resection presented for posterior tracheoplasty and tracheopexy complicated by esophageal perforation. A preexisting gastrostomy site was re‐accessed to allow for a novel approach for endoluminal sponge placement in endoscopic vacuum‐assisted closure (EVAC) therapy by gastrostomy‐assisted pull technique. The patient had appropriate healing without further leak 1 month after repair. This case highlights the use of EVAC as a minimally invasive option for repair of esophageal perforation using a pull‐through method at the percutaneous endoscopic gastrostomy tube site as gastric access. This method may improve control of placement and reduce sponge migration, reduce intraluminal distance of sponge placement, and reduce morbidity by avoiding thoracotomy.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"7 9","pages":""},"PeriodicalIF":0.0,"publicationDate":"2024-01-18","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139525871","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
JPGN reportsPub Date : 2024-01-15DOI: 10.1002/jpr3.12029
P. Korček, Zbyněk Straňák
{"title":"High protein intake can lead to serious hypophosphatemia and hypokalemia in growth restricted preterm newborns","authors":"P. Korček, Zbyněk Straňák","doi":"10.1002/jpr3.12029","DOIUrl":"https://doi.org/10.1002/jpr3.12029","url":null,"abstract":"High protein parenteral nutrition (HPPN) in the early postnatal period is a recommended strategy for very low birth weight (VLBW) infants. However, limited data is available on electrolyte changes when HPPN strategy is utilized. We investigated the impact of HPPN on the development of hypophosphatemia and hypokalemia in preterm VLBW newborns.A retrospective, single‐center study investigated the levels of phosphate and potassium in VLBW infants who received HPPN (amino acids intake up to 3.5 g/kg/day) during the first week of life. Preterm infants were divided into two subgroups: appropriate for gestational age (AGA) and small for gestational age (SGA) newborns. Clinical data were obtained from hospital database and medical records.Overall, 170 VLBW infants were included for the study analysis: 41 SGA (mean birth weight 752 ± 39 g) and 129 AGA infants (mean birth weight 994 ± 23 g). Phosphate and potassium levels were significantly lower in the SGA infants compared to AGA infants (Phosphate: 0.97 ± 0.07 mmol/l vs. 1.44 ± 0.04 mmol/l, p < 0.001; Potassium: 3.0 ± 0.1 mmol/l vs. 3.6 ± 0.1 mmol/l, p < 0.001).Repeated measurement of serum phosphate and potassium is recommended when HPPN strategy is utilized in preterm SGA infants where significant hypophosphatemia and hypokalemia might have serious clinical consequences.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":" 27","pages":""},"PeriodicalIF":0.0,"publicationDate":"2024-01-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139620638","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}