JPGN reports最新文献

JPGN Reports 2024 Reviewer Acknowledgment.

JPGN reports Pub Date : 2025-02-10 eCollection Date: 2025-02-01 DOI: 10.1002/jpr3.12150

引用次数: 0

Exclusive enteral nutrition for induction of remission in pediatric Crohn's disease: Short- and long-term tolerance and acceptance.

JPGN reports Pub Date : 2024-12-30 eCollection Date: 2025-02-01 DOI: 10.1002/jpr3.12163

Catto Sandrine, Dugelay Emmanuelle, Viala Jérôme, Martinez-Vinson Christine

{"title":"Exclusive enteral nutrition for induction of remission in pediatric Crohn's disease: Short- and long-term tolerance and acceptance.","authors":"Catto Sandrine, Dugelay Emmanuelle, Viala Jérôme, Martinez-Vinson Christine","doi":"10.1002/jpr3.12163","DOIUrl":"10.1002/jpr3.12163","url":null,"abstract":"Objectives: In children with mild to moderate Crohn's disease (CD), exclusive enteral nutrition (EEN) is the first-line treatment. However, adherence to this therapeutic strategy remains challenging because of numerous psychosocial factors. This study aimed to evaluate the short-term acceptability and long-term tolerance of EEN.Methods: A single-center retrospective study involving a pediatric population with CD was conducted at Robert-Debré Hospital in Paris between December 2023 and March 2024.Results: Thirty-two patients responded to the questionnaire. developed specifically for this study. It included detailed sections on the EEN received, duration, observed consequences, difficulties encountered by patients and their families, and sociodemographic information. Twenty patients (62%) received oral treatment, while 12 (38%) required a nasogastric tube (NGT). Thirty-eight percent of the patients prematurely discontinued treatment. Most children reported difficulties related to taste, vomiting, and discomfort caused by the NGT. Fifty-nine percent of children would recommend treatment due to its rapid effectiveness, despite the challenges posed by the taste and exclusive nature of the diet. Thirty-two percent of patients reported persistent eating disorders (EDs) long after treatment discontinuation, and 12.5% reported social disorders. Despite strict treatment constraints, children managed to adapt and maintain their daily activities.Conclusion: EEN has significant benefits for children with CD; however, its acceptability is mixed owing to dietary and social constraints. Adequate dietary and psychological support is crucial for improving adherence to treatment and preventing EDs in one third of our patients after treatment.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"6 1","pages":"11-18"},"PeriodicalIF":0.0,"publicationDate":"2024-12-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11810808/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143412192","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Salmonella splenic abscess.

JPGN reports Pub Date : 2024-12-25 eCollection Date: 2025-02-01 DOI: 10.1002/jpr3.12145

Arun Ajmera, Joanne Thio, Sharef Al-Mulaabed, Jeffrey A Bornstein

引用次数: 0

Successful use of transcutaneous parasacral stimulation in a patient with myelomeningocele and fecal incontinence: A case report.

JPGN reports Pub Date : 2024-12-20 eCollection Date: 2025-02-01 DOI: 10.1002/jpr3.12152

Roman Bigliardi, Claudia Riera-Canales, Adriana Oviedo, Gonzalo Ortiz, Julian Fernández, Santiago Meduri, Patricio Birsa, Gabriela Messere, Miguel Saps

{"title":"Successful use of transcutaneous parasacral stimulation in a patient with myelomeningocele and fecal incontinence: A case report.","authors":"Roman Bigliardi, Claudia Riera-Canales, Adriana Oviedo, Gonzalo Ortiz, Julian Fernández, Santiago Meduri, Patricio Birsa, Gabriela Messere, Miguel Saps","doi":"10.1002/jpr3.12152","DOIUrl":"10.1002/jpr3.12152","url":null,"abstract":"Myelomeningocele is a complex congenital defect that affects the spinal cord and structures associated with it. These patients often have neurogenic bowel and bladder dysfunction with constipation, fecal and urinary incontinence. In addition to dietary modifications, laxatives, and enemas, therapies such as biofeedback and neurostimulation (invasive and noninvasive) are sometimes used. These techniques are rarely available, may require surgical procedures, and are not devoid of complications. We present the case of a 13-year-old boy with myelomeningocele at the L4 level, with constipation, dyssynergic defecation, and fecal incontinence (FI). He was treated with biofeedback achieving partial improvement of FI, and then with transcutaneous electrical neurostimulation (TENS) with subsequent resolution of constipation and FI. To our knowledge, this is the first case report using neurostimulation with TENS applied to the S2-S4 dermatomes in a patient with myelomeningocele. This represents a safe, noninvasive, and low-cost treatment for these patients.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"6 1","pages":"48-51"},"PeriodicalIF":0.0,"publicationDate":"2024-12-20","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11810818/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143412203","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Persistent abdominal distension, bilious emesis, and feeding intolerance in an infant without anatomical bowel obstruction.

JPGN reports Pub Date : 2024-12-18 eCollection Date: 2025-02-01 DOI: 10.1002/jpr3.12151

Muhammad Rehan Khan, Anshu Maheshwari, Daniel J Robertson, Julie Khlevner, Raj P Kapur, Manu R Sood

引用次数: 0

Drug-induced liver injury from Deferasirox in a pediatric patient with hereditary spherocytosis: A case report.

JPGN reports Pub Date : 2024-12-16 eCollection Date: 2025-02-01 DOI: 10.1002/jpr3.12155

Siddhant Talwar, Blake Rosenthal, Madhav Vissa, Kayla Cort, Joshua Byers, Sabina Ali

引用次数: 0

Left-sided gallbladder and Chilaiditi syndrome in an infant. 婴儿左侧胆囊和奇莱蒂综合征。

JPGN reports Pub Date : 2024-12-16 eCollection Date: 2025-02-01 DOI: 10.1002/jpr3.12153

Laura J Bradstreet, Teresa Chapman, Jonathan O Swanson, Katryn N Furuya

引用次数: 0

A rare case of pancreatic mucinous cystic neoplasm in a pediatric patient.

JPGN reports Pub Date : 2024-12-13 eCollection Date: 2025-02-01 DOI: 10.1002/jpr3.12156

Muhammed Ali Colak, A Jay Freeman, Christie Heinzman, Muhammad A Khan, Shamlal Mangray, Carol J Potter, Sara K Rasmussen, Mitchell A Rees, Jaimie D Nathan

{"title":"A rare case of pancreatic mucinous cystic neoplasm in a pediatric patient.","authors":"Muhammed Ali Colak, A Jay Freeman, Christie Heinzman, Muhammad A Khan, Shamlal Mangray, Carol J Potter, Sara K Rasmussen, Mitchell A Rees, Jaimie D Nathan","doi":"10.1002/jpr3.12156","DOIUrl":"10.1002/jpr3.12156","url":null,"abstract":"Pancreatic mucinous cystic neoplasms (MCNs) are rare tumors predominantly identified in middle-aged females. Occurrences are extremely rare in children. We report a rare case of pancreatic MCN in an adolescent. A 14-year-old female with Smith-Magenis syndrome and steatotic liver disease (SLD) presented with abdominal discomfort. Magnetic resonance elastography obtained for SLD revealed cholelithiasis and a 0.5-cm cyst in the distal pancreas. Observation was recommended by her pediatric surgery provider. At 18 years old, contrast-enhanced abdominal magnetic resonance imaging showed a 2.4-cm mildly complex, septate, cystic lesion along the distal pancreas with no soft tissue component, pancreatic atrophy, or ductal dilation. Endoscopic ultrasound with cyst fluid cytology showed no definitive neoplasm. Carcinoembryonic antigen level of cyst fluid was markedly elevated at 11,207 ng/mL, concerning an MCN. She was referred to Hepatopancreatobiliary Surgery for evaluation and underwent robotic-assisted distal pancreatectomy. Final pathology revealed a 2.8-cm low-grade MCN with intermediate-grade dysplasia.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"6 1","pages":"60-64"},"PeriodicalIF":0.0,"publicationDate":"2024-12-13","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11810804/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143412186","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

A 13-year-old with dual pancreatic rests.

JPGN reports Pub Date : 2024-12-13 eCollection Date: 2025-02-01 DOI: 10.1002/jpr3.12154

Christian Hochhalter, Cyrus Edelson, Sabina Mir

引用次数: 0

A Canadian multicenter pediatric eosinophilic esophagitis cohort: Evidence for a nondilation approach to esophageal narrowing.

JPGN reports Pub Date : 2024-12-09 eCollection Date: 2025-02-01 DOI: 10.1002/jpr3.12149

David Burnett, Vishal Avinashi, Thomas Hoang, Anthony Otley, Rabin Persad, Mary Sherlock, Hien Q Huynh

{"title":"A Canadian multicenter pediatric eosinophilic esophagitis cohort: Evidence for a nondilation approach to esophageal narrowing.","authors":"David Burnett, Vishal Avinashi, Thomas Hoang, Anthony Otley, Rabin Persad, Mary Sherlock, Hien Q Huynh","doi":"10.1002/jpr3.12149","DOIUrl":"10.1002/jpr3.12149","url":null,"abstract":"Objectives: Improving characterization of the narrowing phenotype in pediatric eosinophilic esophagitis (EoE).Methods: New pediatric EoE diagnoses from 2015 to 2018 were retrospectively identified in Vancouver (BC), Northern Alberta (AB), Hamilton (ON), and Nova Scotia (NS). Incidence rates were calculated using 2016 Federal census data. Clinical, endoscopic, and histologic data were gathered from diagnosis until the end of the follow-up period (fall 2019).Results: The incidence of EoE in patients less than 15 years old was 5.4 per 100,000 person-years. Of the 332 new diagnoses, 40 (12.0%) had endoscopically identified esophageal narrowing at diagnosis or during the follow-up period, with a subset of 11 (27.5% of narrowed cohort) patients undergoing mechanical esophageal dilation. The median age at diagnosis and median duration of symptoms were higher in the cohort with narrowing than those without. Patient-reported food bolus impaction and dysphagia were associated with esophageal narrowing. Trachealization was the endoscopic finding most commonly associated with esophageal narrowing. Of the 65 esophagogastroduodenoscopies performed in the follow-up of a known esophageal narrowing, 4 of the 31 (13%) had resolution of this finding post mechanical dilation, and 19 of the 39 (49%) had resolution of the narrowing after initiation of new medical or dietary treatments (without dilation).Conclusions: EoE is common in Canadian children, with esophageal narrowing being present within a few years of diagnosis in 12% of cases. Interestingly, a large portion of narrowing resolved without mechanical dilation.","PeriodicalId":501015,"journal":{"name":"JPGN reports","volume":"6 1","pages":"19-26"},"PeriodicalIF":0.0,"publicationDate":"2024-12-09","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11810807/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143412185","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0