Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica最新文献

{"title":"Eponyms for Hirschsprung's disease.","authors":"Ó Girón-Vallejo","doi":"10.54847/cp.2025.03.11","DOIUrl":"https://doi.org/10.54847/cp.2025.03.11","url":null,"abstract":"","PeriodicalId":94306,"journal":{"name":"Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica","volume":"38 3","pages":"85-90"},"PeriodicalIF":0.0,"publicationDate":"2025-07-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144692938","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Transcultural adaptation and validation of the Pectus Carinatum Body Image Quality of Life Questionnaire (PeCBI-QOL) into Spanish.","authors":"J V Redondo Sedano, A Gómez Sánchez, V A García-Tabernero Hernández, C Martín-Arriscado Arroba, A Gómez Fraile, M D Delgado Muñoz","doi":"10.54847/cp.2025.03.12","DOIUrl":"https://doi.org/10.54847/cp.2025.03.12","url":null,"abstract":"<p><strong>Introduction: </strong>The primary objective was to conduct the translation and subsequent transcultural adaptation into Spanish of the Pectus Carinatum Body Image Quality of Life questionnaire (PeCBI-QOL), designed to assess Pectus Carinatum (PC)'s quality of life impact.</p><p><strong>Material and methods: </strong>A translation and transcultural adaptation process was carried out according to WHO guidelines. The process consisted of the following steps: direct translation, Delphi pilot study, retro-translation, cognitive survey to patients, and analysis/validation.</p><p><strong>Results: </strong>42 patients and their respective caregivers replied to the validation questionnaire. Principal component factor analysis of the patient questionnaire showed a 4-factor solution, whereas in the caregiver questionnaire, it showed a 3-factor one. The questionnaires demonstrated good reliability, with internal consistency alpha coefficients of 0.78 and 0.85, respectively. The subscale-based concordance analysis also revealed good results in terms of reliability, except for the Motivation/treatment adhesion subscale in the patient questionnaire.</p><p><strong>Conclusion: </strong>The Spanish version of the PeCBI-QOL questionnaire is valid and reliable for assessing PC's impact on patients' body image and quality of life.</p>","PeriodicalId":94306,"journal":{"name":"Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica","volume":"38 3","pages":"91-99"},"PeriodicalIF":0.0,"publicationDate":"2025-07-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144692943","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Laparoscopic approach of anorectal malformations: Have we learnt anything in the past 10 years?","authors":"J C de Agustín Asensio","doi":"10.54847/cp.2025.03.10","DOIUrl":"https://doi.org/10.54847/cp.2025.03.10","url":null,"abstract":"","PeriodicalId":94306,"journal":{"name":"Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica","volume":"38 3","pages":"83-84"},"PeriodicalIF":0.0,"publicationDate":"2025-07-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144692941","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Intraoperative radiotherapy in the local control of chest wall Ewing sarcoma.","authors":"S Monje Fuente, A Del Cañizo López, J Ordóñez Pereira, M A García-Casillas, L Pérez Egido, I Bada Bosch, J Bueno Romero, J Cerdá Berrocal, M De La Torre Macías, E Cela De Julián, C González San Segundo, J C De Agustín Asensio","doi":"10.54847/cp.2025.03.13","DOIUrl":"https://doi.org/10.54847/cp.2025.03.13","url":null,"abstract":"<p><strong>Introduction: </strong>Ewing sarcoma is a rare malignant tumor with an incidence of 3 cases per 1 million inhabitants annually. Cross-disciplinary management is key to improve survival rates. The role played by intraoperative radiotherapy in terms of treatment is still to be defined.</p><p><strong>Material and methods: </strong>A retrospective study of pediatric patients (up to 16 years of age) with chest wall Ewing sarcoma undergoing tumor resection surgery, intraoperative radiotherapy, and chest wall reconstruction in our institution from 2011 to 2024 was carried out. Variables such as age at surgery, sex, neoadjuvant treatment, resection type, characteristics of intraoperative radiotherapy, reconstruction type, complications, local control rate, relapses, survival, and reconstruction's functional result were collected.</p><p><strong>Results: </strong>8 patients were included. Mean age at diagnosis was 12.5 years. Full tumor mass removal with free margins (R0) was achieved in 100% of the cases. Reconstructive techniques with flexible patches, titanium plates, and muscle flaps were used. None of the flaps was lost. Overall survival was 87.5%, with a mean follow-up period of 6 years. 3- and 5-year overall survival rates were 100% and 80%, respectively. Local control of the disease was achieved in 100% of the cases.</p><p><strong>Conclusions: </strong>This paper discusses the role of intraoperative radiotherapy as a good treatment alternative to achieve the local control of Ewing sarcoma associated with large surgical resections.</p>","PeriodicalId":94306,"journal":{"name":"Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica","volume":"38 3","pages":"100-105"},"PeriodicalIF":0.0,"publicationDate":"2025-07-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144692940","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Non-invasive follicular thyroid neoplasm with papillary-like nuclear features (NIFTP) in pediatrics.","authors":"D Del Gordo Caballero, J Mancera Morales, C E Villamil Giraldo, S Ruiz Gutiérrez, A F Siabatto Cleves, J P Luengas Monroy","doi":"10.54847/cp.2025.03.15","DOIUrl":"10.54847/cp.2025.03.15","url":null,"abstract":"<p><strong>Introduction: </strong>Non-invasive follicular thyroid neoplasm with papillary-like nuclear features (NIFTP) has a low malignancy potential. First acknowledged by the WHO in 2017, this tumor is rare in the pediatric population, with less than 25 cases reported. Accurate diagnosis is key to avoid overtreatment and complications.</p><p><strong>Clinical observation: </strong>Two cases of adolescents with solid thyroid nodules assessed by fine-needle aspiration biopsy are presented. Hemithyroidectomy was decided upon. Both surgical specimens were reported as NIFTP. Both cases were presented before a cross-disciplinary board, and since malignancy potential was low, treatment was regarded as completed.</p><p><strong>Discussion: </strong>NIFTP identification is key to avoid unnecessary treatments such as total thyroidectomy or iodine therapy, which may bring about serious consequences in children. A high level of diagnostic suspicion and a cross-disciplinary approach are required to optimize management and clinical results in these patients.</p>","PeriodicalId":94306,"journal":{"name":"Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica","volume":"38 3","pages":"112-115"},"PeriodicalIF":0.0,"publicationDate":"2025-07-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144692942","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Efficacy and safety of the conservative management of appendiceal phlegmon during childhood.","authors":"N Sanz Villa, D Peláez Mata, L Pérez Egido, P Aguado Roncero, J Ordóñez Pereira, J C De Agustín Asensio, J C Ollero Fresno","doi":"10.54847/cp.2025.03.14","DOIUrl":"https://doi.org/10.54847/cp.2025.03.14","url":null,"abstract":"<p><strong>Objective: </strong>To assess the efficacy and safety of conservative management with interval appendectomy vs. baseline surgery in the treatment of appendiceal phlegmon.</p><p><strong>Material and methods: </strong>A retrospective study of the 76 phlegmons treated from July 2016 to June 2024 was carried out. Two treatment groups were created -the baseline surgery (G1: 46 children) group and the conservative with interval appendectomy (G2: 30 children) group. Clinical and progression characteristics of both groups were collected and compared.</p><p><strong>Results: </strong>No significant differences were found in terms of age, progression time, presence of appendicolith, or mean hospital stay. The number of intra-abdominal collections at diagnosis was greater in G2 (21.7% vs. 56.6%; p< 0.05), and the percentage of complications was significantly higher in G1 (54.34% vs. 20%; p< 0.002). In G2, 3 collection drainage procedures were carried out, and 4 children underwent surgery in an acute stage as a result of treatment failure. Following discharge, 2 patients from G2 underwent emergency surgery, 4 refused surgery, and 20 underwent surgery after 184 ± 55 days. Of the latter, 2 had complications. 89.47% of the appendices removed had histological disorders.</p><p><strong>Conclusions: </strong>Conservative treatment of appendiceal phlegmon is safe and effective. It significantly reduces morbidity, and it is not contraindicated by age, presence of appendicolith, or intra-abdominal collections. However, large collection drainage procedures may be required. We believe interval appendectomy is indicated in a period of 3-6 months.</p>","PeriodicalId":94306,"journal":{"name":"Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica","volume":"38 3","pages":"106-111"},"PeriodicalIF":0.0,"publicationDate":"2025-07-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144692937","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Acquired interstitial emphysema in a premature patient. Treatment with unilateral angioplasty balloon pulmonary blockage.","authors":"D Crehuet Gramatyka, L Sánchez Pulido, C Pérez Costoya, E Enríquez Zarabozo, C Granell Suárez, V Álvarez Muñoz","doi":"10.54847/cp.2025.03.16","DOIUrl":"10.54847/cp.2025.03.16","url":null,"abstract":"<p><strong>Introduction: </strong>Pulmonary interstitial emphysema is a severe rare complication associated with mechanical ventilation in pre-term patients. It induces alterations both in ventilation and pulmonary perfusion, and it may cause progressive overdistension of the side involved and atelectasis of the contralateral lung. Management is uneasy and requires changing ventilation strategies, with invasive procedures such as blockage and selective pulmonary ventilation being potentially necessary.</p><p><strong>Clinical case: </strong>Premature female patient born at gestation week 26+0, with an initially good clinical progression and baseline chest X-rays showing no signs of congenital pulmonary injury. On day 20 of life, progressive respiratory deterioration was noted. In the series X-rays and chest CT-scan, a right-sided pulmonary interstitial emphysema with mediastinal displacement and left-sided pulmonary atelectasis, associated with hemodynamic and respiratory instability, was observed. On day 26 of life, in light of the poor clinical progression and the immediate threat of death, decision was made to place a right-sided bronchial blocker with a 3x20 mm angioplasty balloon, after the bronchus had been measured through CT-scan. Following placement, respiratory and ventilation parameters improved immediately. The device was kept inflated for 3 days. 10 days after removing the bronchial blocker, the patient was successfully extubated, and she was discharged after 100 days in hospital, with no respiratory symptoms, and the pre-discharge CT-scan showing no signs of emphysema. After 50 months of follow-up, the patient remains asymptomatic from a respiratory standpoint, and psychomotor development is normal.</p><p><strong>Discussion: </strong>Selective angioplasty balloon pulmonary blockage has been supported by scientific evidence in extremely premature patients with acquired interstitial emphysema associated with compromised ventilation and atelectasis of the contralateral lung. In our case, it helped save the patient's life with not sequelae being caused.</p>","PeriodicalId":94306,"journal":{"name":"Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica","volume":"38 3","pages":"116-121"},"PeriodicalIF":0.0,"publicationDate":"2025-07-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144692936","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"In memoriam: Álex Urbistondo.","authors":"G Guillén, J A Molino, J L Ramos, I Eizaguirre","doi":"10.54847/cp.2025.03.09","DOIUrl":"https://doi.org/10.54847/cp.2025.03.09","url":null,"abstract":"","PeriodicalId":94306,"journal":{"name":"Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica","volume":"38 3","pages":"81-82"},"PeriodicalIF":0.0,"publicationDate":"2025-07-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144692939","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"In memoriam: Enrique Jaureguizar Monereo (1948 - 2025).","authors":"","doi":"10.54847/cp.2025.02.10","DOIUrl":"https://doi.org/10.54847/cp.2025.02.10","url":null,"abstract":"","PeriodicalId":94306,"journal":{"name":"Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica","volume":"38 2","pages":"37"},"PeriodicalIF":0.0,"publicationDate":"2025-04-07","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143805114","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"The role of ERCP in the treatment of recurrent acute pancreatitis.","authors":"C Fedrigo Loyola Batista, M Possenti Frizzarin, F C Ribeiro Godoy, I Carrapato Assis, N Estorino da Costa, M Azevedo Maciel, R A Bertachi Uvo, R Forti Maschietto","doi":"10.54847/cp.2025.02.18","DOIUrl":"10.54847/cp.2025.02.18","url":null,"abstract":"<p><strong>Introduction: </strong>The incidence of acute pancreatitis is increasing in the pediatric population. Up to 35% of children have recurrence secondary to anatomical variations of the pancreatic duct. In this context, endoscopic retrograde cholangiopancreatography (ERCP) stands as a key diagnostic and therapeutic tool.</p><p><strong>Clinical case: </strong>We present two cases of recurrent acute pancreatitis (RAP) in 2 adolescents aged 14 and 15 years old. Apart from small gallstones in the gallbladder in one of them, bile duct or pancreatic duct disorders were not identified at either ultrasonography or nuclear magnetic resonance cholangiopancreatography (NMRCP). In both cases, diagnosis was established through ERCP, with two ERCPs required in each case before accurate diagnosis was achieved. ERCP had to be repeated as a result of technical issues in one case, and due to lack of relevant findings in the other. RAP episodes ceased after plastic prostheses had been placed in the pancreatic duct.</p><p><strong>Discussion: </strong>TAnatomical variations of the pancreatic duct are a cause of RAP in the pediatric population. ERCP allows diagnosis to be established even when regular imaging studies are not conclusive.</p>","PeriodicalId":94306,"journal":{"name":"Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica","volume":"38 2","pages":"77-80"},"PeriodicalIF":0.0,"publicationDate":"2025-04-07","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143805223","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}