{"title":"Hereditary glomerulonephritis of non-Alport type.","authors":"C C Doherty, D T Middleton, C M Hill","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>In three unrelated kindreds, 21 subjects with hereditary renal disease were identified. The mode of inheritance was autosomal dominant and the main clinical features were asymptomatic proteinuria and/or haematuria. Three of the 16 females but none of the five males developed progressive renal failure. Renal biopsy carried out in six of the 21 patients showed varying degrees of mesangial change with glomerular deposition of IgM and C3 in some cases. Nerve deafness and renal ultrastructural changes typical of Alport's Syndrome were absent. The renal disease in these subjects does not conform with previously recognised types of familial nephropathy.</p>","PeriodicalId":76354,"journal":{"name":"Proceedings of the European Dialysis and Transplant Association. European Dialysis and Transplant Association","volume":"19 ","pages":"575-81"},"PeriodicalIF":0.0,"publicationDate":"1983-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17927666","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
N Gretz, F Manz, R Augustin, T M Barrat, C Bender-Götze, M Brandis, H J Bremer, J Brodehl, M Broyer, M Bulla, L Callis, C Chantler, L Diekmann, M J Dillon, F Egli, J H Ehrich, W Endres, A Fanconi, C Feldhoff, J Geisert, D Gekle, B Geschöll-Bauer, K Grote, R Grüttner, W Hagge, C B Haycock, H Hennemann, B Klare, D Leupold, H Löhr, D Michalk, A Oliveira, F Ott, K Pistor, J Rau, K Schärer, F Schindera, H Schmidt, H Schulte-Wissermann, K Verrier-Jones, H P Weber, U Willenbockel, H Wolf
{"title":"Survival time in cystinosis. A collaborative study.","authors":"N Gretz, F Manz, R Augustin, T M Barrat, C Bender-Götze, M Brandis, H J Bremer, J Brodehl, M Broyer, M Bulla, L Callis, C Chantler, L Diekmann, M J Dillon, F Egli, J H Ehrich, W Endres, A Fanconi, C Feldhoff, J Geisert, D Gekle, B Geschöll-Bauer, K Grote, R Grüttner, W Hagge, C B Haycock, H Hennemann, B Klare, D Leupold, H Löhr, D Michalk, A Oliveira, F Ott, K Pistor, J Rau, K Schärer, F Schindera, H Schmidt, H Schulte-Wissermann, K Verrier-Jones, H P Weber, U Willenbockel, H Wolf","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>In a retrospective study the overall survival time of 205 cystinotic patients of six countries was determined. The median survival time was 8.5 years. The median time for 'renal death' (age at death due to uraemia or age at starting renal replacement therapy) was 9.2 years. The youngest patient dying of renal death was 5.2 years. No sex difference in survival time was noticed. Furthermore no difference in survival time was noted between the different countries. The analysis of the overall survival curve indicates no clear differences between the infantile and adolescent types of cystinosis.</p>","PeriodicalId":76354,"journal":{"name":"Proceedings of the European Dialysis and Transplant Association. European Dialysis and Transplant Association","volume":"19 ","pages":"582-9"},"PeriodicalIF":0.0,"publicationDate":"1983-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17927667","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
K Andrassy, P J Oertel, O Mehls, W Kreusser, J Koderisch, E Ritz
{"title":"Thromboembolic complications and haemostasis in the nephrotic syndrome--is there a difference between children and adults?","authors":"K Andrassy, P J Oertel, O Mehls, W Kreusser, J Koderisch, E Ritz","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76354,"journal":{"name":"Proceedings of the European Dialysis and Transplant Association. European Dialysis and Transplant Association","volume":"19 ","pages":"597-601"},"PeriodicalIF":0.0,"publicationDate":"1983-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17927668","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
A Dal Canton, G Fuiano, G Conte, M Terribile, M Sabbatini, B Cianciaruso, V E Andreucci
{"title":"Why diuretic treatment increases azotaemia in patients with chronic glomerulonephritis.","authors":"A Dal Canton, G Fuiano, G Conte, M Terribile, M Sabbatini, B Cianciaruso, V E Andreucci","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76354,"journal":{"name":"Proceedings of the European Dialysis and Transplant Association. European Dialysis and Transplant Association","volume":"19 ","pages":"744-8"},"PeriodicalIF":0.0,"publicationDate":"1983-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17927672","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
J Rottembourg, B Issad, J L Gallego, P Degoulet, F Aime, B Gueffaf, M Legrain
{"title":"Evolution of residual renal function in patients undergoing maintenance haemodialysis or continuous ambulatory peritoneal dialysis.","authors":"J Rottembourg, B Issad, J L Gallego, P Degoulet, F Aime, B Gueffaf, M Legrain","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>A study has been carried out to compare over an 18 month period the residual glomerular filtration rate (GFR) measured by the creatinine clearance in two matched groups of 25 patients with end-stage renal disease. One group was treated by continuous ambulatory peritoneal dialysis, the other one by maintenance haemodialysis. GFR was similar in both groups immediately before starting dialysis therapy, respectively 4.3 +/- 2.3 and 4.4 +/- 2.4 ml/min. From the beginning of the dialysis treatment to the eighteenth month there was a significant and progressive decrease of GFR in the group of patients treated by haemodialysis, while in the peritoneal dialysis group GFR and peritoneal clearances remained stable.</p>","PeriodicalId":76354,"journal":{"name":"Proceedings of the European Dialysis and Transplant Association. European Dialysis and Transplant Association","volume":"19 ","pages":"397-403"},"PeriodicalIF":0.0,"publicationDate":"1983-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17927745","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
K Ota, H Kawaguchi, S Nakagawa, S Koshikawa, K Maeda, N Matsui, Y Hirasawa, T Sasaoka
{"title":"Clinical evaluation of a new thrombin inhibitor available for haemodialysis.","authors":"K Ota, H Kawaguchi, S Nakagawa, S Koshikawa, K Maeda, N Matsui, Y Hirasawa, T Sasaoka","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76354,"journal":{"name":"Proceedings of the European Dialysis and Transplant Association. European Dialysis and Transplant Association","volume":"20 ","pages":"144-9"},"PeriodicalIF":0.0,"publicationDate":"1983-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17711806","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Effects of parathyroidectomy on blood pressure development in eucalcaemic, spontaneously hypertensive rats.","authors":"J F Mann, E Ritz","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76354,"journal":{"name":"Proceedings of the European Dialysis and Transplant Association. European Dialysis and Transplant Association","volume":"20 ","pages":"220-2"},"PeriodicalIF":0.0,"publicationDate":"1983-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17713586","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
M Wauthier, P Vereerstraeten, Y Pirson, C Toussaint, G P Alexandre, P Kinnaert, H Van Geertruyden, C van Ypersele de Strihou
{"title":"Prevalence and causes of hypertension late after renal transplantation.","authors":"M Wauthier, P Vereerstraeten, Y Pirson, C Toussaint, G P Alexandre, P Kinnaert, H Van Geertruyden, C van Ypersele de Strihou","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>We analysed the prevalence and causes of hypertension in 77 patients followed greater than or equal to 7 years after renal transplantation. Prevalence of hypertension remains stable, around 55 per cent, up to 11 years post-transplant. Age, sex, type of original nephropathy, graft source or prednisolone dosage are not related to hypertension; body weight is greater in hypertensive patients. Presence of native kidneys is responsible for hypertension in about one-quarter of non-nephrectomised patients. No renal artery stenosis was observed in this group. At seven years, serum creatinine is greater in hypertensive patients, suggesting that graft dysfunction is an important cause of hypertension in long term survivors.</p>","PeriodicalId":76354,"journal":{"name":"Proceedings of the European Dialysis and Transplant Association. European Dialysis and Transplant Association","volume":"19 ","pages":"566-71"},"PeriodicalIF":0.0,"publicationDate":"1983-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17408637","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
P Kramer, M Broyer, F P Brunner, H Brynger, R A Donckerwolcke, C Jacobs, N H Selwood, A J Wing
{"title":"Combined report on regular dialysis and transplantation in Europe, XII, 1981.","authors":"P Kramer, M Broyer, F P Brunner, H Brynger, R A Donckerwolcke, C Jacobs, N H Selwood, A J Wing","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76354,"journal":{"name":"Proceedings of the European Dialysis and Transplant Association. European Dialysis and Transplant Association","volume":"19 ","pages":"4-59"},"PeriodicalIF":0.0,"publicationDate":"1983-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17408808","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Minimal change glomerulonephritis and focal glomerulosclerosis markers and 'in vitro' activity of peripheral blood mononuclear cell.","authors":"P Dall'Aglio, C Chizzolini, C Brigati","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Serum concentrations of IgG, IgA and IgM and PBMC were investigated in 11 prevalently adult patients with idiopathic glomerulonephritis, five minimal change glomerulonephritis (MCGN) and six focal glomerulosclerosis (FGS) and nephrotic syndrome. Among the peripheral blood mononuclear cells (PBMC) E rosette forming cells (T-cells), surface immunoglobulin bearing cells (B-cells), and T-cells with IgG Fc receptor (T gamma) were determined. In the culture supernatants of PBMC stimulated with PWM, the concentration of secreted IgG, IgA and IgM was determined by a solid phase immunofluorescence assay. After stimulation with PWM and PHA, the 3H-TdR uptake from PBMC was evaluated. In patients only the serum values of IgG were found significantly decreased. No difference was observed between patients and healthy age and sex matched controls, in percentage and absolute number of T and B-cells, whereas an increased number of T gamma was present in patients. In these patients after stimulation with PWM the production of IgG and IgA, but not IgM, and the 3H-TdR incorporation, were significantly lower than in healthy controls. These results suggest an imbalance in the cellular co-operation or an intrinsic B-cell defect in the synthesis or secretion of Ig in MCGN and FGS.</p>","PeriodicalId":76354,"journal":{"name":"Proceedings of the European Dialysis and Transplant Association. European Dialysis and Transplant Association","volume":"19 ","pages":"673-8"},"PeriodicalIF":0.0,"publicationDate":"1983-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17409387","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
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