{"title":"Bronze Baby Syndrome","authors":"F. Cneude, A. Bourlet, G. Vittu, J. Cousin","doi":"10.1007/springerreference_40509","DOIUrl":"https://doi.org/10.1007/springerreference_40509","url":null,"abstract":"","PeriodicalId":75405,"journal":{"name":"Acta paediatrica Academiae Scientiarum Hungaricae","volume":"4 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"1998-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"52963433","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Dynamics of adrenal steroidogenesis in childhood: steroid excretion in prepubertal and pubertal girls.","authors":"L Kecskés, Z Juricskay, Z Tatai, M Szécsényi","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>C19-C21O2-3 steroid spectrum and C21O5 corticoids have been studied in the urine collected from 29 girls aged 2-14 years. A total of 34 investigations was carried out by means of simultaneous two-column gas chromatography. The values of steroid excretion have been expressed in terms related to body weight and body surface, respectively. Before the age of seven the excretion of C19O2 steroids representing adrenal androgens and their metabolites did not exceed 7 micrograms/kg/day or 170 micrograms/m2/day (\"infantile type androgen excretion\"). Then it began to increase between the 7th and 9th years of life and preceded the appearance of the physical signs of adrenarche. The increase was accelerated during puberty and no value under 18 micrograms/kg/day, or 600 micrograms/m2/day, respectively, was found when the physical signs of adrenarche were present (\"puberty type androgen excretion\"). Excretion of 11-oxygenated C19 steroids, C21O5 corticoids and pregnenediol was also augmented during puberty; however, when compared with the increase in C19O2 excretion this augmentation was moderate. As a consequence of the marked elevation in C19O2 excretion, the ratio of C19O2 to C21O5, too, increased during puberty, indicating that the cortisol-androgen dissociation, otherwise characteristic of childhood, had ceased. It is concluded that the most plausible explanation of the increased androgen production is the gradual development of the zona reticularis during puberty.</p>","PeriodicalId":75405,"journal":{"name":"Acta paediatrica Academiae Scientiarum Hungaricae","volume":"23 2","pages":"151-65"},"PeriodicalIF":0.0,"publicationDate":"1982-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"18152270","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Haemodialysis treatment of acute renal failure in hypertonic dehydration.","authors":"I Marosvári, S Köves","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":75405,"journal":{"name":"Acta paediatrica Academiae Scientiarum Hungaricae","volume":"23 2","pages":"145-50"},"PeriodicalIF":0.0,"publicationDate":"1982-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17865755","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Energy metabolism, substrate utilization, metabolite and hormone levels in infants fed various parenteral solutions.","authors":"I Rubecz","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Previous observations on the effects of various types of parenteral nutrition on changes in oxygen consumption, respiratory quotient, total heat production, distribution of nutrient utilization, metabolic and hormonal levels in infants during the neonatal and postneonatal periods are reviewed. The relevant findings obtained in fifty-two newborn infants infused with different types of metabolic solutions were as follows. Oxygen consumption increased during Aminosol-glucose and Intralipid-glucose infusion. The respiratory quotient varied according to the oxidation of the nutrients. A significant elevation was observed during Aminosol-glucose infusion, which tended to fall in response to Intralipid. Total heat production was increased during all types of parenteral nutrition, and substrate utilization depended on the quality and amount of nutrient intake. The magnitude of the changes in concentrations of metabolites (glucose, free fatty acids, alpha-amino-nitrogen) and insulin and growth hormone were smallest when the parenteral nutrition consisted of glucose, amino acids and lipid and the total caloric intake did not exceed the maintenance energy expenditure. On the basis of the results, during the neonatal period it seems advisable to administer as parenteral nutrition, about 70--75 kcal/kg/day in the form of 7.0--8.0 g/kg/day glucose, 1.7--2.0 g/kg/day amino acids and 3.0--4.0 g/kg/day lipid.</p>","PeriodicalId":75405,"journal":{"name":"Acta paediatrica Academiae Scientiarum Hungaricae","volume":"23 1","pages":"59-68"},"PeriodicalIF":0.0,"publicationDate":"1982-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17859212","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Fatal infectious mononucleosis. Report of a case with a review of the literature.","authors":"P Kajtár, S Molnár, M Várbiró","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":75405,"journal":{"name":"Acta paediatrica Academiae Scientiarum Hungaricae","volume":" ","pages":"17-25"},"PeriodicalIF":0.0,"publicationDate":"1982-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"35266287","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"A diagnostic survey of patients referred for chromosome analysis.","authors":"G Kosztolányi","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Out of 692 patients referred for chromosome analysis because of abnormal clinical features, 199 (28.7%) had chromosomal abnormalities. In addition, assessment of the abnormal phenotypic features and the data of other (laboratory, X-ray, etc.) examinations revealed 25 (3.6%) single gene disorders, 25 (3.6%) recognizable syndromes or associations of unknown aetiology, and in 4 cases (0.6%) environmental agents were established as possible aetiological factors. Altogether, of the 692 cases, 253 (36.5%) had a definitive diagnosis, while the remainder 439 were undiagnosed. These results suggest that (i) chromosome analysis is worthwhile if the patient has significant clinical abnormalities, and (ii) a request for chromosome analysis should be viewed as one step in syndrome identification, so that a normal karyotype should stimulate the physician to further efforts to establish a diagnosis.</p>","PeriodicalId":75405,"journal":{"name":"Acta paediatrica Academiae Scientiarum Hungaricae","volume":" ","pages":"35-40"},"PeriodicalIF":0.0,"publicationDate":"1982-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"35266289","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Relationship between metabolic control and plasma lipoprotein level in diabetic children.","authors":"G Soltész, D Molnár, L Klujber, M Kardos","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>All lipid and lipoprotein fractions except for total cholesterol were found to be high in diabetic children under long-term treatment. There was a positive correlation between HDL-cholesterol, HbA1a-c and the insulin dose. In untreated diabetic children, plasma triglyceride and its subfractions were also high, but phospholipids were normal. Total plasma cholesterol was normal, but its VLDL + LDL subfraction was increased and HDL-cholesterol low. After two months of insulin-treatment, parallel with the decrease of HbA1a-c, the HDL-cholesterol increased and there was a drop in the level of triglycerides. It is concluded that HDL-cholesterol is a good parameter of metabolic control during the initial therapy of diabetes. In patients under long-term treatment there is no such a simple relationship between control and HDL-cholesterol and the daily insulin-dose seems to play an important role in the regulation of plasma HDL-cholesterol.</p>","PeriodicalId":75405,"journal":{"name":"Acta paediatrica Academiae Scientiarum Hungaricae","volume":"23 1","pages":"75-83"},"PeriodicalIF":0.0,"publicationDate":"1982-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"18093193","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Intrauterine weight retardation and the concomitant length retardation: a statistical analysis of anthropometric data.","authors":"I Járai","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>In 237 low birth weight for gestational age term infants (birth weight less than or equal to 10th percentile; gestational age less than or equal to 37 wk) percentage deviations of birth weight and crown-heel length for gestational age were correlated (a) in a series of linear regressions of three subsequent groups formed according to the magnitude of weight retardation (b) in the pooled material by non-liner regression. Linear regressions yielded equivocal results as to the existence of concomitant length retardation (no correlation in group 1, significant correlation in group 2 and 3). The significant non-linear correlation (i = 0.66 ; p less than 0.001) and the exponential type regression curve (Y) % length deficit = 2.45 1.04 X' % weight deficit) gave an explanation of the controversial findings. If mild to moderate weight retardation is included in studies comparing weight and length, a greater variability and, possibly, a conclusion of non-existence of concomitant retardation will result while, if severe or extreme weight retardation are screened out using stricter criteria, (e.g. 5th, 3rd percentiles, -2 SD) one would find more infants with significant length retardation, and the conclusions would be the opposite, i.e. an obligatory length retardation following malnutrition. In anthropometric-statistical studies the results should never be generalized and extrapolated below, or beyond the cut-off points chosen.</p>","PeriodicalId":75405,"journal":{"name":"Acta paediatrica Academiae Scientiarum Hungaricae","volume":"23 1","pages":"9-16"},"PeriodicalIF":0.0,"publicationDate":"1982-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"18216170","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"The cerebrospinal fluid of newborn infants with perinatal hypoxia.","authors":"M Fekete, G Soltész, M Horváth","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":75405,"journal":{"name":"Acta paediatrica Academiae Scientiarum Hungaricae","volume":"23 2","pages":"179-87"},"PeriodicalIF":0.0,"publicationDate":"1982-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"18152272","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Cardiomegaly in hypoglycaemic small-for-gestational-age infants.","authors":"K Schultz, J Weisenbach","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>The chest X-rays of 15 hypoglycaemic small-for-gestational-age infants showed cardiomegaly in 10 infants, 4 had heart failure. None of the infants had respiratory distress syndrome, congenital heart disease, septicaemia, anaemia or polycythaemia; infants of diabetic mothers were excluded. Cardiomegaly disappeared with the normalization of blood glucose in most of the cases. The cause of the cardiomegaly and heart failure might be related to insufficient cardiac energy substrates in small-for-gestational-age infants. This condition should also be considered in the differential diagnosis of cardiomegaly and heart failure.</p>","PeriodicalId":75405,"journal":{"name":"Acta paediatrica Academiae Scientiarum Hungaricae","volume":"23 1","pages":"69-73"},"PeriodicalIF":0.0,"publicationDate":"1982-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"17277105","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}