{"title":"Successful percutaneous intervention of a symptomatic right isolated subclavian artery – A rare case report","authors":"Vinothkumar S.P. , Abhishek Mallick , Anuja Sanjay Gadre , Ira Dhawan , Shyam K.S. Thingnam , Manoj Kumar Rohit","doi":"10.1016/j.ppedcard.2023.101676","DOIUrl":"10.1016/j.ppedcard.2023.101676","url":null,"abstract":"<div><p>We report a rare case of symptomatic late presenter with complete isolation of the right subclavian artery<span> in the form of inadequate right upper limb perfusion<span> and growth due to pulmonary steal phenomenon that was managed successfully by less invasive percutaneous ductal closure with a vascular plug.</span></span></p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-08-25","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"43092546","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Aortic stiffness in patients with childhood essential hypertension: Is obesity a risk factor or not?","authors":"Gunes Isik , Celal Varan","doi":"10.1016/j.ppedcard.2023.101669","DOIUrl":"10.1016/j.ppedcard.2023.101669","url":null,"abstract":"<div><h3>Background</h3><p>Hypertension (HTN) is a global health problem with a rising prevalence that affects both children and adults.</p></div><div><h3>Objectives</h3><p><span><span>We aim to assess aortic stiffness in children with </span>essential HTN using </span>echocardiography and evaluate the parameters that influence the development of aortic stiffness.</p></div><div><h3>Methods</h3><p><span><span>Included in the prospective study were patients who were newly diagnosed with essential HTN and who were admitted to the Pediatric Nephrology and </span>Pediatric Cardiology<span> outpatient clinics of Adiyaman University between June 1 and December 31, 2022. All patient groups underwent 24-hour ambulatory blood pressure monitoring<span> (ABPM) for a definitive diagnosis of essential HTN. The echocardiographic examinations of all participants were carried out by the same pediatric cardiologist. Aortic stiffness parameters and Epicardial </span></span></span>Adipose Tissue (EAT) thickness were measured by routine echocardiography. Patients under the age of 18 years were included in the study. Demographic data, serum biochemical parameters, echocardiography findings, and 24-hour ABPM data were noted.</p></div><div><h3>Results</h3><p>A total of 76 children were enrolled in the study, including 31 patients (9 female; 22 male) and 45 controls (14 female; 31 male). The control and patient groups had similar overall sex and age distributions. Systolic and diastolic blood pressure and pulse pressure were higher in the hypertensive group than in the control group (p < 0.01). Considering the effects of obesity and HTN, three groups were formed. A significant reduction in aortic distensibility was noted in the non-obese hypertensive group when compared to the control group (p = 0.047).</p></div><div><h3>Conclusion</h3><p>Non-obese hypertensive children showed significantly reduced aortic distensibility than the control group, suggesting that the etiology of HTN in the non-obese hypertensive group may involve mechanisms beyond obesity-related factors. Seeking preventative care is more common in obese patients than non-obese patients.</p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-08-22","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"48217733","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Ajitkumar Jadhav, Digvijay D. Nalawade, Pratik S. Wadhokar, Anishkumar Khan
{"title":"Pediatric ectopic atrial tachycardia: Successful management with beta blocker and Ivabradine in a 7-year-old girl - A case report","authors":"Ajitkumar Jadhav, Digvijay D. Nalawade, Pratik S. Wadhokar, Anishkumar Khan","doi":"10.1016/j.ppedcard.2023.101667","DOIUrl":"https://doi.org/10.1016/j.ppedcard.2023.101667","url":null,"abstract":"<div><p><span>Ectopic atrial tachycardia<span> (EAT) is a supraventricular tachycardia commonly found in younger children, which can lead to tachycardia-induced cardiomyopathy. While </span></span>radiofrequency ablation<span><span> is often recommended for older children, limited studies exist on the use of Ivabradine, a medication that </span>lowers heart rate, in children with EAT.</span></p><p><span><span><span>A 7-year-old girl presented with exertional palpitations and </span>dizziness<span> upon sudden changes in posture. Physical examination, 12-lead ECG, and 2D-ECHO were unremarkable. A 24-hour Holter monitor revealed atrial high-rate episodes with distinct P waves, abnormal axis, longer RP interval, and QRS </span></span>alternans, confirming a diagnosis of EAT. The patient was treated with </span>Metoprolol<span><span> initially, resulting in partial symptom relief. However, repeat Holter monitoring<span><span> showed persistent ectopic atrial rhythm episodes. Based on literature review, Ivabradine was added to the treatment regimen after one week. With the addition of Ivabradine, heart rate reduction was observed, accompanied by alternating periods of restored </span>sinus rhythm and ectopic atrial rhythm. Although ectopic atrial rhythm episodes persisted, the patient's symptoms improved compared to earlier. This case report provides additional evidence for the successful use of Ivabradine as an adjunctive therapy, along with </span></span>beta blockers<span>, in the management of resistant atrial ectopic tachycardia in children. While research on its use in younger children is scarce, this case highlights the potential effectiveness of Ivabradine in treating EAT, warranting further clinical studies to evaluate its safety and efficacy compared to standard treatment protocols for pediatric ectopic atrial tachycardia.</span></span></p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-08-19","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49763154","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Liwei Yu , Allison K. Cabalka , Frank Cetta , Nathaniel W. Taggart , Donald J. Hagler , Joseph Chan , Jason H. Anderson
{"title":"Staged transcatheter therapy of coarctation of the aorta in children utilizing balloon-expandable covered stent grafts","authors":"Liwei Yu , Allison K. Cabalka , Frank Cetta , Nathaniel W. Taggart , Donald J. Hagler , Joseph Chan , Jason H. Anderson","doi":"10.1016/j.ppedcard.2023.101666","DOIUrl":"10.1016/j.ppedcard.2023.101666","url":null,"abstract":"<div><p><span><span>We present a series of three children with coarctation of the aorta (CoA); native CoA, recurrent CoA, and CoA with a </span>patent ductus arteriosus<span>. Each patient underwent transcatheter implantation of a Viabahn VBX stent with post implant high pressure </span></span>balloon dilation<span>. All cases demonstrated resolution of the CoA with no residual gradient from the ascending to descending thoracic aorta. All procedures were free of complications which allowed for hospital discharge on the same day. The small delivery profile, re-dilation capacity, and frame design of this stent make it uniquely advantageous for treating CoA in children.</span></p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-08-12","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"45781744","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
AjitkumarJadhav, Digvijay D. Nalawade, Pratik Wadhokar, Anishkumar Khan
{"title":"Paediatric ectopic atrial tachycardia: Successful management with beta blocker and Ivabradine in a 7-year-old girl - A case report","authors":"AjitkumarJadhav, Digvijay D. Nalawade, Pratik Wadhokar, Anishkumar Khan","doi":"10.1016/j.ppedcard.2023.101667","DOIUrl":"https://doi.org/10.1016/j.ppedcard.2023.101667","url":null,"abstract":"","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"48931030","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Richard Emmett Frye , Benjamin Ittleman , Veronika Shabanova , Lissa Sugeng , Jeremy Steele , Dina Ferdman , Ruchika Karnik
{"title":"Left ventricular strain in pediatric patients with bicuspid aortic valves and aortopathy","authors":"Richard Emmett Frye , Benjamin Ittleman , Veronika Shabanova , Lissa Sugeng , Jeremy Steele , Dina Ferdman , Ruchika Karnik","doi":"10.1016/j.ppedcard.2023.101636","DOIUrl":"10.1016/j.ppedcard.2023.101636","url":null,"abstract":"<div><h3>Background</h3><p><span><span>Bicuspid aortic valve is the most common congenital cardiac defect. Left ventricular strain has been shown to be lower in adults with bicuspid aortic valve and preserved </span>ejection fraction. Additionally, left ventricular strain has been independently associated with </span>aortic valve replacement<span> and all-cause mortality in adults. In pediatric patients, left ventricular strain in patients<span> with bicuspid aortic valve with and without aortopathy has not been evaluated.</span></span></p></div><div><h3>Objectives</h3><p>We aimed to evaluate the effect of clinical aortopathy on left ventricular strain in pediatric patients with well-functioning bicuspid aortic valve compared to normal controls.</p></div><div><h3>Methods</h3><p>This is a single-center retrospective study in patients <21 years of age with normal ejection fraction and no prior cardiac interventions. Patients were divided into three groups: 1) healthy controls with normal transthoracic echocardiograms<span> 2) well-functioning BAV without clinical aortopathy 3) well-functioning BAV with isolated clinical aortopathy. TTE images were analyzed to obtain left ventricle global longitudinal strain and left ventricle global circumferential strain, respectively. Strain values were compared across the three groups.</span></p></div><div><h3>Results</h3><p>The mean values and 95 % confidence intervals (95%CIs) for LVGLS were −23.1 (−24.3, −22.0), −22.5 (−23.8, −21.1), and −21.2 (−22.5, −20.0) for groups 1, 2 and 3 respectively. There was a statistically significant difference in Left ventricular global longitudinal strain in group 3 compared to group 1(<em>p</em> = 0.033). There was no significant difference in global circumferential strain between the three groups.</p></div><div><h3>Conclusion</h3><p>Our study demonstrates lower left ventricular strain in patients with a well-functioning bicuspid aortic valve and clinical aortopathy compared to controls. This is suggestive of an early effect on the left ventricular myocardium caused by a change in loading conditions from alteration in aortic elasticity. Left ventricular strain is a potential early marker for this and can be utilized for further correlation with clinical outcomes.</p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"48138931","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
John F. Keaney III , M. Abigail Simmons , Robert W. Elder , Cheyenne M. Beach
{"title":"Fontan-related morbidity and paced QRS duration: A case series","authors":"John F. Keaney III , M. Abigail Simmons , Robert W. Elder , Cheyenne M. Beach","doi":"10.1016/j.ppedcard.2023.101641","DOIUrl":"10.1016/j.ppedcard.2023.101641","url":null,"abstract":"<div><p>Permanent pacemakers have been associated with Fontan-related morbidity and mortality. Longer QRS duration and QRS prolongation over time may be associated with poorer outcomes in Fontans patients. We present a series of eleven Fontan patients with ventricular pacing on serial electrocardiograms (ECGs), including seven with Fontan-related morbidity. Paced QRS duration increased over time in nearly all patients, with several having extremely long QRS durations at the end of the follow-up period. We explore the role that paced QRS duration may play in Fontan-related morbidity and mortality and its potential as a therapeutic target for patient management.</p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"45505690","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Modified technique of percutaneous fenestrated Fontan completion without custom made stent or prior surgical preparation - A case report","authors":"Rajaguru Ganesan , Chinnasamy Sivaprakasam Muthukumaran , Sangeetha Viswanathan , Zeeshan Lakhani","doi":"10.1016/j.ppedcard.2023.101617","DOIUrl":"10.1016/j.ppedcard.2023.101617","url":null,"abstract":"<div><p><span>We describe a technique of percutaneous Fontan completion without presurgical preparation by perforating the right atrial roof through the main pulmonary artery. In our case, we used uncovered stents to create a framework to hold the fenestrated covered stent graft in position and finally completed a fenestrated cavo-caval </span>anastomosis without obstructing hepatic venous drainage.</p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"48333958","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Congenital right pulmonary artery to left atrial fistula: Successful transcatheter closure with the cocoon duct occluder","authors":"Amit Kumar Singh, Ashish Tiwari, Ayush Shukla, Abhishek Singh, Sharad Chandra, Gaurav Chaudhary","doi":"10.1016/j.ppedcard.2023.101637","DOIUrl":"10.1016/j.ppedcard.2023.101637","url":null,"abstract":"<div><p><span>A fistula between the </span>right pulmonary artery<span> (RPA) and left atrium (LA) is a rare cardiac entity. Several cases have documented surgical closure, yet only a few describe transcatheter device closure. A 14-year-old adolescent male with a history of sporting activity developed exertional dyspnea. Over a 2-year duration, the dyspnea progressed from New York Heart Association (NYHA) class II to III at the time of admission. We describe transcatheter closure of a RPA–LA fistula using a 16/18 mm Cocoon Duct Occluder (Vascular Innovations Co. Ltd., Nonthaburi, Thailand).</span></p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"42231394","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Denis J. Donovan , Namrata G. Jain , Valeriya M. Feygina , Hilda E. Fernandez , Warren A. Zuckerman
{"title":"A novel approach to pediatric cardiorenal syndrome","authors":"Denis J. Donovan , Namrata G. Jain , Valeriya M. Feygina , Hilda E. Fernandez , Warren A. Zuckerman","doi":"10.1016/j.ppedcard.2023.101635","DOIUrl":"10.1016/j.ppedcard.2023.101635","url":null,"abstract":"<div><p><span>Cardiorenal syndrome describes the complex interplay between the heart and the kidney, where failure of one organ can lead to dysfunction and failure in the other. We describe an adolescent who presented with advanced </span>kidney disease<span> necessitating dialysis, who was found to have severe systolic and diastolic heart failure. Consideration was initially given for joint kidney and heart transplant over concerns about the severity of his cardiac dysfunction.</span></p><p><span><span>During transplant evaluation, he was treated with a strategy of intermittent hemodialysis in combination with </span>peritoneal dialysis. His </span>hemodynamics<span> improved to the point that he was able to undergo kidney transplant alone. In the days immediately following kidney transplant, his cardiac function rapidly improved, completely normalized within 6 weeks of transplant, and has remained normal.</span></p><p>This case describes the improvement of severe systolic and diastolic heart failure from cardiorenal syndrome with combined hemodialysis and peritoneal dialysis in a pediatric patient whose fluid management had previously been suboptimal on nightly peritoneal dialysis. This strategy led to better fluid management and significant improvement in cardiac function and hemodynamics, which allowed for successful kidney transplant alone, and avoidance of heart transplant. Following successful kidney transplant, cardiac function rapidly and completely normalized. Combined dialysis is an uncommon strategy that has not previously been reported for the purpose of cardiac rehabilitation and avoidance of multiorgan transplant in pediatric patients.</p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"46142966","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}