经导管关闭先天性肝外门静脉分流至右心房导致重度肺动脉高压的患儿：病例报告

IF 0.6 Q4 PEDIATRICS

PROGRESS IN PEDIATRIC CARDIOLOGY Pub Date : 2024-05-30 DOI:10.1016/j.ppedcard.2024.101729

Samir Shakya , Dinesh Chataut , Sharma Paudel , Ratna Mani Gajurel

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引用次数: 0

摘要

先天性肝外门静脉分流是指门静脉（在其分支之前）与全身静脉之一之间的异常连接。它是肺动脉高压的罕见病因。我们报告了一名两岁患儿的病例，该患儿患有严重的肺动脉高压和一种直接排入右心房的独特形式的先天性肝外门静脉分流。经皮成功关闭了分流道，随访时肺动脉压力从重度肺动脉高压降至中度肺动脉高压。

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Transcatheter closure of congenital extrahepatic portosystemic shunt to right atrium causing severe pulmonary hypertension in a child: A case report

Congenital extrahepatic portosystemic shunt is an abnormal connection between portal vein (prior to its branching) and one of the systemic veins. It is a rare cause of pulmonary hypertension. We report a 2-year-old child who presented with severe pulmonary artery hypertension and a unique form of congenital extrahepatic portosystemic shunt draining directly into right atrium. The shunt was successfully closed percutaneously, and pulmonary artery pressure fell from severe pulmonary artery hypertension to moderate pulmonary artery hypertension on follow up.

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来源期刊

PROGRESS IN PEDIATRIC CARDIOLOGY PEDIATRICS-

CiteScore

0.90

自引率

11.10%

发文量

审稿时长

75 days

期刊介绍： Progress in Pediatric Cardiology is an international journal of review presenting information and experienced opinion of importance in the understanding and management of cardiovascular diseases in children. Each issue is prepared by one or more Guest Editors and reviews a single subject, allowing for comprehensive presentations of complex, multifaceted or rapidly changing topics of clinical and investigative interest.