Andrew P. Morgan , Joseph S. DeRaddo , Christopher Atkins , Michael Jay Campbell
{"title":"Streptococcal endarteritis associated with severe aortic coarctation","authors":"Andrew P. Morgan , Joseph S. DeRaddo , Christopher Atkins , Michael Jay Campbell","doi":"10.1016/j.ppedcard.2023.101657","DOIUrl":"https://doi.org/10.1016/j.ppedcard.2023.101657","url":null,"abstract":"<div><p><span>Bicuspid aortic valve and coarctation of the aorta are risk factors for infective endocarditis and endarteritis<span>. We describe a case of a 4-year-old boy whose severe aortic coarctation was diagnosed only when he presented with endarteritis due to </span></span><span><em>Streptococcus pneumoniae</em></span><span>, which evolved into a mycotic pseudoaneurysm requiring urgent repair.</span></p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49746687","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
David Soeliongan Waworuntu , Hans Natanael , Erling David Kaunang , Stefanus Gunawan , Jose Meky Mandei , Fima Lanra Fredrik Gerald Langi , Fahrul Nurkolis
{"title":"Comparison of the effectiveness of USCOM and echocardiography in assessing cardiac output on pediatric patients with shock","authors":"David Soeliongan Waworuntu , Hans Natanael , Erling David Kaunang , Stefanus Gunawan , Jose Meky Mandei , Fima Lanra Fredrik Gerald Langi , Fahrul Nurkolis","doi":"10.1016/j.ppedcard.2023.101658","DOIUrl":"10.1016/j.ppedcard.2023.101658","url":null,"abstract":"<div><h3>Background</h3><p>Shock<span><span><span> is a circulatory failure, and its clinical manifestations result in decreased cardiac output. </span>Hemodynamic monitoring is important in shock patients to determine further management. Demand for noninvasive examination methods, such as ultrasound cardiac output monitoring (USCOM) and </span>echocardiography, is increasing because of their practicality and lower risks.</span></p></div><div><h3>Objectives</h3><p>The aim of this study is to compare cardiac output determined using USCOM and echocardiography in pediatric patients with shock.</p></div><div><h3>Methods</h3><p><span>This prospective observational study used a cross-sectional data collection approach. It collected data on 48 pediatric shock patients in the Pediatric Intensive Care Unit at Kandou General Hospital (Manado, Indonesia) between March and June 2022. The instruments used were USCOM and echocardiography. The regression analysis results are presented as odds ratios (ORs) with 95 % confidence intervals and </span><em>p</em> < 0.05.</p></div><div><h3>Results</h3><p>The mean cardiac output of pediatric patients with shock was 2.50 (standard deviation [SD] = 2.28) with USCOM and 2.45 (SD = 0.77) with echocardiography. Echocardiographic and USCOM cardiac output values were significantly correlated, with a coefficient of determination (<em>R</em><sup>2</sup>) of 0.832 (83.2 %), indicating a near-perfect linear correlation.</p></div><div><h3>Conclusion</h3><p>This study's results show that USCOM is as effective as echocardiography in assessing cardiac output in children with shock.</p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"45782217","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Comparison of venous approach and conventional approach in children undergoing percutaneous patent ductus arteriosus closure","authors":"Shilpa Aryal, Manish Shrestha, Poonam Sharma, Subash Chandra Shah, Amshu Shakya, Kul Ratna Thapa, Vidhata K.C. Bhandari, Urmila Shakya","doi":"10.1016/j.ppedcard.2023.101660","DOIUrl":"10.1016/j.ppedcard.2023.101660","url":null,"abstract":"<div><h3>Background</h3><p>The standard method for the closure of PDA is the conventional method, where both arterial and venous access are obtained. Patent ductus arteriosus can be closed successfully via venous-only approach.</p></div><div><h3>Objectives</h3><p>To compare the outcomes of the venous approach and combined arterial and venous approach (conventional approach) among children undergoing percutaneous patent ductus arteriosus device closure at Sahid Gangalal National heart center, Kathmandu, Nepal.</p></div><div><h3>Methods</h3><p>A total of 248 children <15 years of age with a diagnosis of PDA were included in this retrospective observational study. Echocardiography was used for the selection of patients. We compared the venous approach and combined arterial and venous approach (conventional approach) of PDA device closure in these patients.</p></div><div><h3>Results</h3><p>A total of 248 children with age groups of 6 months to 14 years were enrolled during the study period. The venous-only approach (group B) was used in 96 patients, and the conventional approach (group A) was used in 152 patients. Baseline characteristics, clinical characteristics, and clinical outcomes in terms of success rate, complications, procedure time, fluoroscopic time, and contrast used were compared between the two groups.</p><p>The rate of successful closure in group A and group B patient groups were 96.7 % and 100 %, respectively. The mean procedure time was significantly lesser in group B as compared to group A (25 ± 6.6 min in group B vs. 52 ± 10.4 min in group B, <em>p</em><span> value ≤ 0.001). The mean fluoroscopy time was also significantly lesser in group B as compared to group A (5 min ± 1.728 in group B vs. 6.5 min ± 2.3 in group A, </span><em>p</em>-value <0.001). Similarly, the total amount of contrast used was also significantly lesser in group B as compared to group A (24.2 ml ± 11.8 in group B vs. 30ml ± 14.45, <em>p</em> value = 0.001). The complication rate was 11.2 % (<em>n</em> = 17) in group A vs 11 % (<em>n</em> = 11) in group B patient groups.</p></div><div><h3>Conclusion</h3><p>The venous-only approach can be used as a method of closing PDA as it has lesser procedure time, fluoroscopic time, and lesser amount of contrast used. However, proper patient selection is important prior to performing device closure.</p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"43751037","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Jennifer H. Huang, Zach Hutchinson, Grant H. Burch, Brendan P. Kelly, Erin J. Madriago
{"title":"Echocardiographically-derived septal positional angle (EDSPA) as a measure of elevated right ventricular systolic pressure","authors":"Jennifer H. Huang, Zach Hutchinson, Grant H. Burch, Brendan P. Kelly, Erin J. Madriago","doi":"10.1016/j.ppedcard.2023.101659","DOIUrl":"https://doi.org/10.1016/j.ppedcard.2023.101659","url":null,"abstract":"<div><h3>Background</h3><p>Pulmonary hypertension is a significant yet rare disease that can have many long-term consequences, including death. Cardiac catheterization is the gold standard for measuring pulmonary artery mean pressures (PAMP), but is invasive and risks potentially serious complications. This study hypothesizes that a semi-quantitative, non-invasive echocardiographic measure of septal positioning can be used to assess PAMP.</p></div><div><h3>Objective</h3><p>To assess an alternative echocardiographic measure of right ventricular systolic pressure.</p></div><div><h3>Methods</h3><p><span>This study was a retrospective study of patients with and without pulmonary hypertension who had a transthoracic echocardiogram<span> and cardiac catheterization. Patients undergoing </span></span>atrial septal defect<span> closure represented controls. Two blinded readers calculated the “Echocardiographically-Derived Septal Positional Angle (EDSPA),” which was compared to corresponding catheterization data, including mean pulmonary artery pressures.</span></p></div><div><h3>Results</h3><p>A total of 159 children were included, of which 150 had interpretable echocardiographic data based on image quality or axis of imaging plane. 39 children were identified as having pulmonary hypertension while 111 children had an atrial septal defect. Patient age ranged from a minimum of 54 days and maximum of 19 years [mean 7.1 years (SD = 5.30)]. Inter-observer variability between two readers [Pearson correlation coefficient of 0.939 (p < .001)] and intra-observer variability were low [intraclass correlation coefficient (ICC) of 0.95 and 0.96 for each observer, respectively]. An EDSPA of ≤39° predicted a PAMP>20 mm Hg (as measured by cardiac catheterization) with a 76 % sensitivity and 76 % specificity (AUC 0.846).</p></div><div><h3>Conclusions</h3><p>EDSPA is a useful, non-invasive, and reproducible echocardiographic measure of PAMP that is easy to perform. With a sensitivity and specificity near 80 %, it has significant utility in screening for pulmonary hypertension and determining which patients should undergo further invasive diagnostic testing.</p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49746303","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Fumiya Yoneyama , Michiaki Imamura , Manish Bansal , Athar M. Qureshi , Jeffery S. Heinle
{"title":"Patent ductus arteriosus banding for pulmonary hypertension","authors":"Fumiya Yoneyama , Michiaki Imamura , Manish Bansal , Athar M. Qureshi , Jeffery S. Heinle","doi":"10.1016/j.ppedcard.2023.101655","DOIUrl":"10.1016/j.ppedcard.2023.101655","url":null,"abstract":"<div><p>Treating large patent ductus arteriosus (PDA) in the setting of pulmonary hypertension (PHTN) is challenging. Comprehensive management is essential for assessing pulmonary vascular reactivity and timing of PDA closure. We present a case of severe PHTN associated with pulmonary venous stenosis, which was treated with PDA banding as a staged procedure for the eventual PDA occlusion.</p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"45373888","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Univentricular heart palliation with clipped right ventricle-to-pulmonary artery shunt at 1.6 kg: A case report","authors":"Toshi Maeda , Hisao Nagato , Kotaro Inaguma , Kosuke Yoshizawa , Otohime Mori","doi":"10.1016/j.ppedcard.2023.101656","DOIUrl":"https://doi.org/10.1016/j.ppedcard.2023.101656","url":null,"abstract":"<div><p><span><span>A female infant with low body weight was diagnosed with double outlet right ventricle, </span>pulmonary atresia<span>, hypoplastic left ventricle<span>, and patent ductus arteriosus. We performed a right ventricle-to-pulmonary artery shunt with a ringed expanded </span></span></span>polytetrafluoroethylene<span><span> graft (5 mm) using the Dunk technique at the age of 39 days (1622 g). The shunt was clipped to regulate the pulmonary blood flow<span>. The clips were dislodged using balloon angioplasty 4 months postoperatively. Afterward, the patient underwent a </span></span>Fontan procedure<span><span> without fenestration during the third operation at the age of 3 years. She did not require pulmonary </span>artery plasty or balloon angioplasty for the pulmonary artery during her course.</span></span></p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49746304","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Transcatheter tricuspid valve-in-valve replacement with the off-label Edwards SAPIEN 3 Ultra valve in mixed tricuspid valve disease: Two case description and literature review","authors":"Daniel Sew, Atul Kalantre, Marinos Kantzis","doi":"10.1016/j.ppedcard.2023.101678","DOIUrl":"10.1016/j.ppedcard.2023.101678","url":null,"abstract":"<div><p>We report successful off-label usage of the Edwards SAPIEN 3<span> Ultra valve in two cases of transcatheter tricuspid valve-in-valve implantation. Patients had previous tricuspid valve replacements for different conditions and became progressively symptomatic in recent years. Deployment was performed with Edwards eSheath and GORE DrySeal sheath, resulting in no major complications or valvular leaks during short-term follow-up.</span></p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"43189948","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Denis J. Donovan , Matthew Theoharakis , Anna Rose , Rebecca Epstein , Adam M. Butensky , Michael A. Fremed , Sophia Chrisomalis-Dring , Anne Ferris
{"title":"Parental perceptions of the effect of the COVID-19 pandemic on outpatient services for patients with single ventricle congenital heart disease","authors":"Denis J. Donovan , Matthew Theoharakis , Anna Rose , Rebecca Epstein , Adam M. Butensky , Michael A. Fremed , Sophia Chrisomalis-Dring , Anne Ferris","doi":"10.1016/j.ppedcard.2023.101665","DOIUrl":"https://doi.org/10.1016/j.ppedcard.2023.101665","url":null,"abstract":"<div><h3>Background</h3><p>Patients with congenital heart disease<span> (CHD), particularly single ventricle<span> CHD, may experience neurodevelopmental delays. The COVID-19 pandemic created numerous challenges surrounding access to care. This study evaluates the effect of the pandemic on delivery of outpatient therapies to this high-risk group and satisfaction with services.</span></span></p></div><div><h3>Objectives</h3><p>To determine the effect of the pandemic on the delivery of outpatient therapies to patients with SV-CHD at our center, as well as parental satisfaction, at various time points.</p></div><div><h3>Methods</h3><p>A survey was administered to parents of patients with single ventricle CHD regarding services at various stages of the pandemic. Patients were eligible if they had a bidirectional Glenn operation between 1/1/2010–3/1/2020. The survey assessed the services received and parental satisfaction pre-pandemic, mid-pandemic, and at the time of survey administration (7/2022–2/2023).</p></div><div><h3>Results</h3><p>Of 228 eligible patients, 133 were contacted, and 36 (27 %) completed the survey. Nineteen (52.8 %) had a child with developmental delay. During the pandemic, 84 % (<em>n</em> = 16/19) of patients who qualified for services were receiving them. Services were largely virtual or hybrid (<em>n</em> = 12/16, 75 %), compared to 100 % in-person pre-pandemic and at the time of survey completion. Satisfaction with services during the pandemic was low, with 12.5 % (<em>n</em> = 2/16) stating they were “extremely satisfied,” compared with 93.3 % (<em>n</em> = 14/15) pre-pandemic and 46.7 % (<em>n</em> = 7/15) at the time of survey completion.</p></div><div><h3>Conclusion</h3><p>In our study, patients with single ventricle CHD continued to receive outpatient services during the pandemic; however, these services were largely virtual, and satisfaction was low. By the time of survey completion, services had returned in person with improvement in satisfaction. More studies are needed to elucidate if changes in the delivery of services during the pandemic may have affected neurodevelopmental status in this high-risk group.</p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49746463","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Streptococcal endarteritis associated with severe aortic coarctation","authors":"A. Morgan, J. Deraddo, C. Atkins, M. J. Campbell","doi":"10.1016/j.ppedcard.2023.101657","DOIUrl":"https://doi.org/10.1016/j.ppedcard.2023.101657","url":null,"abstract":"","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"54928431","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Fernanda Maria Correia Ferreira Lemos, Mário Luiz Ribeiro, Wolney de Andrade Martins
{"title":"Biventricular systolic and diastolic function in adolescents with sickle cell anemia and sickle cell traits – Systematic review","authors":"Fernanda Maria Correia Ferreira Lemos, Mário Luiz Ribeiro, Wolney de Andrade Martins","doi":"10.1016/j.ppedcard.2023.101677","DOIUrl":"10.1016/j.ppedcard.2023.101677","url":null,"abstract":"<div><h3>Background</h3><p><span><span><span>Sickle cell anemia is the most prevalent hereditary </span>hematological disease with high morbidity and mortality rates worldwide. Cardiac involvement and cardiomyopathy are frequent manifestations of sickle cell anemia. Echocardiographic analysis using </span>tissue Doppler and </span><em>speckle tracking</em> is an important tool for assessing cardiac functions.</p></div><div><h3>Aim of Review</h3><p><span><span>This study aimed to determine cardiac function alterations in patients with sickle cell anemia and </span>sickle cell traits<span> to assess the usefulness of new echocardiographic techniques for the early detection of myocardial dysfunction in this disease. A systematic review was carried out using PubMed, Scientific Electronic Library Online, and Latin American and Caribbean Health Sciences Literature databases based on the </span></span><em>Preferred Reporting Items for Systematic Reviews and Meta-Analyses</em> methodology and Population, Intervention, Control, and Outcomes criteria. Original cohort, case-control, cross-sectional, and case series articles published between December 1999 and March 2023 were analyzed.</p></div><div><h3>Key Scientific Concepts of Review</h3><p>Echocardiographic studies have focused on identifying the impact of ventricular systolic and diastolic performance on this disease. The studies analyzed in the current systematic review suggest intrinsic myocardial abnormalities in patients with sickle cell anemia, which may indicate early signs of cardiac involvement in young individuals.</p></div>","PeriodicalId":46028,"journal":{"name":"PROGRESS IN PEDIATRIC CARDIOLOGY","volume":null,"pages":null},"PeriodicalIF":0.9,"publicationDate":"2023-08-25","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49639833","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}