Ga-Young Kim, Young Sang Cho, Mini Jo, Hee Jung Yun, Megan Quilter, Dae Young Kim, Il Joon Moon
{"title":"Effects of Hearing Aids on Static and Subjective Balance in Patients With Hearing Loss: A Pilot Study.","authors":"Ga-Young Kim, Young Sang Cho, Mini Jo, Hee Jung Yun, Megan Quilter, Dae Young Kim, Il Joon Moon","doi":"10.7874/jao.2024.00150","DOIUrl":"10.7874/jao.2024.00150","url":null,"abstract":"<p><strong>Background and objectives: </strong>This study aimed to investigate the effects of hearing aids (HAs) on reducing symptoms of dizziness in patients with hearing loss (HL) and dizziness. Subjects and.</p><p><strong>Methods: </strong>A pre- and post-intervention study was conducted between February 2022 and July 2022 at the outpatient clinic of a tertiary hospital in Seoul, South Korea. Ten participants (four males and six females) with HL and dizziness were recruited. Participants were screened using pure-tone audiometry and visual analog scale scores at baseline. Selected participants underwent the Modified Clinical Test of Sensory Interaction on Balance (mCTSIB) and Korean Dizziness Handicap Inventory (K-DHI) in the unaided state. Thereafter, participants were provided HAs and instructed to use them for at least 6 hours every day. At the 1-month follow-up, all participants were assessed in the aided state using the same tests as at baseline. All tests were performed bilaterally.</p><p><strong>Results: </strong>In the mCTSIB, a significant difference was observed in the foam surface-eyes closed score before (median=2.35) and after (median=2.2) HA use (p=0.049). No significant differences were observed in the K-DHI scores before and after HA use.</p><p><strong>Conclusions: </strong>HA use may improve the static and subjective perception of balance in patients with HL and dizziness. Future research should explore the benefits of HAs under various balance conditions such as dynamic balance and gait.</p>","PeriodicalId":44886,"journal":{"name":"Journal of Audiology and Otology","volume":"29 1","pages":"8-12"},"PeriodicalIF":1.1,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11824520/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143366341","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Wan Qi Lim, Cherie Xinyi Seah, Kevin Chi Chuen Choy, Seng Beng Yeo, Jane Peiwen Lim
{"title":"Recurrent Meningitis Following Previous Repair of Congenital Oval Window Defect.","authors":"Wan Qi Lim, Cherie Xinyi Seah, Kevin Chi Chuen Choy, Seng Beng Yeo, Jane Peiwen Lim","doi":"10.7874/jao.2024.00325","DOIUrl":"10.7874/jao.2024.00325","url":null,"abstract":"<p><p>A 19-year-old male patient with a history of congenital left oval window defect has had recurrent admissions to a children's hospital for bacterial meningitis since the age of 7. Investigations revealed a left-sided type 1 incomplete partition deformity of the left ear with a congenital oval window defect, leading to communication between the cranium and the middle ear. The patient underwent a left canal wall down mastoidectomy and oval window defect repair, remaining well for 3 years. He experienced two more episodes of bacterial meningitis as he got older, prompting repeated exploratory tympanotomy and repair of the cerebrospinal fluid (CSF) leak after each episode. Recently, he was referred again for recurrent meningitis. Investigations showed a recurrent oval window defect. After undergoing left external ear canal transection, mastoid and middle ear obliteration, and left Eustachian tube obliteration, he remained well without further leaks or meningitis. Congenital oval window defect is rare and may present with recurrent bacterial meningitis secondary to spontaneous CSF leak via the oval window. Radiology plays a crucial role in identifying the source of the CSF leak, facilitating more precise preoperative counseling and surgical intervention.</p>","PeriodicalId":44886,"journal":{"name":"Journal of Audiology and Otology","volume":"29 1","pages":"75-78"},"PeriodicalIF":1.1,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11824527/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143365883","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"A 250-kb Microdeletion Identified in Chromosome 16 Is Associated With Non-Syndromic Sensorineural Hearing Loss in a South Indian Consanguineous Family.","authors":"Jayakumar Swetha, Arulmozhi Sakthignanavel, Aarthi Manoharan, Jayakumar Rangarajalu, Priyadharshini Arunagiri, Chandramohan Govindasamy, Sambandam Ravikumar","doi":"10.7874/jao.2024.00038","DOIUrl":"10.7874/jao.2024.00038","url":null,"abstract":"<p><strong>Background and objectives: </strong>Hereditary hearing loss is the most common genetic disorder in children. Nearly 120 genes associated with auditory impairment have been identified. Although the disease is clinically and genetically complex, the chances of identifying deafness-causing loci increase when studying consanguineous families. Materials and.</p><p><strong>Methods: </strong>Whole-exome sequencing was performed to identify genetic variants underlying sensorineural hearing loss in affected individuals from a family with third-degree consanguineous practices.</p><p><strong>Results: </strong>A homozygous deletion of 250.285 kb was identified in the 16p12.2 region encompassing three genes, METTL9, IGSF6, and OTOA, and a partial deletion of the NPIPB4 gene co-segregated within the family.</p><p><strong>Conclusions: </strong>This study highlighted the genetic heterogeneity of hearing loss in consanguineous families. Future research should focus on the OTOA mutational spectrum in South Indian populations with hearing loss.</p>","PeriodicalId":44886,"journal":{"name":"Journal of Audiology and Otology","volume":"29 1","pages":"31-37"},"PeriodicalIF":1.1,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11824526/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143366326","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"A Case of Bilateral Sudden Deafness Caused by Wernicke Encephalopathy.","authors":"Yujeong Hong, Hyojung Kim, Dong-Hee Lee","doi":"10.7874/jao.2024.00311","DOIUrl":"10.7874/jao.2024.00311","url":null,"abstract":"<p><p>Wernicke encephalopathy, also known as thiamine deficiency, is characterized by a triad of symptoms: ophthalmoplegia, ataxia, and confusion. However, additional symptoms may manifest depending on the area affected by the lesion. Although multiple cranial neuropathies are possible, sudden onset bilateral hearing loss has been described in rare situations as the first manifestation of Wernicke encephalopathy. Here, we present a case report detailing the clinical experience of a patient diagnosed with Wernicke encephalopathy, whose initial presentation included sudden bilateral deafness. The patient was a 57-year-old man with alcoholism who was successfully diagnosed with Wernicke encephalopathy, and his hearing improved after high-dose intravenous thiamine therapy. Our case study results and a literature review indicate that video findings and suppression head impulse tests can be used to evaluate Wernicke encephalopathy.</p>","PeriodicalId":44886,"journal":{"name":"Journal of Audiology and Otology","volume":"29 1","pages":"67-74"},"PeriodicalIF":1.1,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11824529/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143366373","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Update on Medical Management of Acute Peripheral Facial Palsy.","authors":"Sang Hoon Kim, Min Young Kwak","doi":"10.7874/jao.2024.00731","DOIUrl":"10.7874/jao.2024.00731","url":null,"abstract":"<p><p>Acute facial nerve palsy, particularly Bell's palsy, is a common neurological disorder with an annual incidence of 20-30 cases per 100,000 individuals. It is characterized by sudden or gradual facial muscle palsy and is caused by viral reactivation, inflammation, or ischemia of the facial nerve. Prognosis varies widely, depending on the severity of nerve damage and timeliness of the intervention. Steroid therapy remains the cornerstone of Bell's palsy treatment because it reduces inflammation and facilitates recovery. Early administration, preferably within 72 hours of symptom onset, considerably improves outcomes. However, the efficacy of combination therapy remains controversial. Current guidelines recommend oral steroids as the primary treatment for Bell's palsy and suggest the selective use of antiviral agents in severe cases or when viral involvement is strongly suspected. For severe facial palsy, such as Ramsay Hunt syndrome or varicella-zoster virus-induced cases, combination therapy may improve outcomes and reduce sequelae; however, high-quality evidence is limited. Steroid therapy is the main treatment of Bell's palsy and antiviral therapy can be added in severe cases to improve prognosis. Additional research is required to develop standardized guidelines, concerning the use of antiviral therapies in conjunction with steroids.</p>","PeriodicalId":44886,"journal":{"name":"Journal of Audiology and Otology","volume":"29 1","pages":"1-7"},"PeriodicalIF":1.1,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11824525/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143366031","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Young-Soo Chang, Jong Sei Kim, Suyeon Park, Sung Hwa Hong, Il Joon Moon
{"title":"Does Cognitive Function Affect Performance and Listening Effort During Bilateral Wireless Streaming in Hearing Aid Users?","authors":"Young-Soo Chang, Jong Sei Kim, Suyeon Park, Sung Hwa Hong, Il Joon Moon","doi":"10.7874/jao.2023.00619","DOIUrl":"10.7874/jao.2023.00619","url":null,"abstract":"<p><strong>Background and objectives: </strong>Wireless streaming technology (WT), designed to transmit sounds directly from a mobile phone to hearing aids, was developed to enhance the signal-to-noise ratio. However, the advantages of WT during phone use and the specific demographic that can fully benefit from this technology has not been thoroughly evaluated. We aimed to investigate the benefits and identify predictive factors associated with bilateral wireless streaming among hearing aid users.</p><p><strong>Subjects and methods: </strong>Eighteen adults with symmetrical, bilateral hearing loss participated in the study. To assess the benefits of wireless streaming during phone use, researchers assessed sentence/word recognition and listening effort in two scenarios: a noisy background with WT turned \"OFF\" or \"ON.\" Listening effort was evaluated through self-reported measurements. Cognitive function was also assessed using the Montreal Cognitive Assessment (MoCA) score.</p><p><strong>Results: </strong>Participant mean age was 57.3 years (range 27-70), and the mean MoCA score was 27.0 (23-30). The activation of WT demonstrated a significant improvement in the sentence/word recognition test and reduced listening effort. The MoCA score showed a significant correlation with WT (ρ=0.59, p=0.01), suggesting a positive association between cognitive function and the benefits of WT.</p><p><strong>Conclusions: </strong>Bilateral wireless streaming may enhance sentence/word recognition and reduce listening effort during phone use in hearing aid users, with these benefits potentially linked to cognitive function.</p>","PeriodicalId":44886,"journal":{"name":"Journal of Audiology and Otology","volume":" ","pages":"271-277"},"PeriodicalIF":1.1,"publicationDate":"2024-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11540966/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"141555666","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Noor Dina Hashim, Khairunnisak Misron, Seo Jin Moon, Hae Eun Noh, Jinna Kim, In Seok Moon
{"title":"Clinico-Radiological Manifestations of Cochlear Schwannomas.","authors":"Noor Dina Hashim, Khairunnisak Misron, Seo Jin Moon, Hae Eun Noh, Jinna Kim, In Seok Moon","doi":"10.7874/jao.2024.00115","DOIUrl":"10.7874/jao.2024.00115","url":null,"abstract":"<p><strong>Background and objectives: </strong>Cochlear schwannomas, which are categorized into intracochlear and intravestibulocochlear schwannomas (ICs and IVCs, respectively) are rare and may cause hearing loss (HL). The affected region is invariably correlated with tumor location, which can be detected on magnetic resonance imaging (MRI). We describe the cochleovestibular manifestations of ICs and IVCs.</p><p><strong>Subjects and methods: </strong>The study included 31 patients with ICs or IVCs. Tumor extent and exact locations were delineated using MRI. Types of HL were subcategorized into the low-to-mid frequency (250 Hz to 1 kHz), mid-to-high frequency (>1 kHz), and all-frequency (universal) HL groups.</p><p><strong>Results: </strong>The tumors involved the entire cochlear turn (two ICs) or extended beyond the cochleae (nine IVCs) in 11 patients, and 20 ICs were located in specific locations as follows: 14 in the basal, 3 in the middle, and 3 in the middle and apical turns. No patient showed tumor invasion of the internal auditory canal or middle ear. The pattern of HL usually reflects the location or extent of a tumor. We observed HL at all frequencies, at low-to-mid frequencies, and at mid-to-high frequencies in 13, 4, and 14 patients, respectively. Dizziness or tinnitus was observed in >50% of patients. Surgical tumor removal was performed in 10 patients, and the remaining patients are undergoing annual monitoring.</p><p><strong>Conclusions: </strong>Cochlear schwannomas may be associated with HL, which may worsen over time and reflect tumor location. Therefore, these lesions should be considered in the differential diagnosis in patients who present with idiopathic, fluctuating, progressive or sudden HL.</p>","PeriodicalId":44886,"journal":{"name":"Journal of Audiology and Otology","volume":"28 4","pages":"284-290"},"PeriodicalIF":1.1,"publicationDate":"2024-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11540968/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142584624","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"The Relationship Between Lower Vitamin D Levels and Hearing Loss in Older Adults.","authors":"Yun Ji Lee, Jun Ho Jung, Jong Woo Chung","doi":"10.7874/jao.2023.00458","DOIUrl":"10.7874/jao.2023.00458","url":null,"abstract":"<p><strong>Background and objectives: </strong>Age-related hearing loss (ARHL) is a sensorineural disease that is associated with a number of factors. In addition to age, sex, environment, lifestyle, and comorbidities are all known to be related to ARHL as well. The prevalence of ARHL can be reduced by controlling the adjustable factors that cause it. Vitamin D levels are strongly related to calcium metabolism, which can affect ARHL. This study aimed to investigate the association between vitamin D and ARHL.</p><p><strong>Subjects and methods: </strong>A total of 1,104 subjects aged >65 years were enrolled from the fifth Korean National Health and Nutrition Examination Survey, which was conducted from 2010-2012. Every participant received both an audiological assessment and a nutritional survey. The association between ARHL and serum vitamin D concentration was analyzed using logistic regression analyses with complex sampling adjusted for confounding factors such as alcohol consumption, smoking status, mobility, and bone mineral density.</p><p><strong>Results: </strong>Our multivariable analysis revealed that males in the group with lower serum levels of vitamin D (< 20 ng/mL) had a higher prevalence of ARHL (odds ratio, 1.638, 95% confidence interval, 1.058-2.538, p=0.027).</p><p><strong>Conclusions: </strong>This finding suggests that lower serum levels of vitamin D are associated with ARHL in the older male population.</p>","PeriodicalId":44886,"journal":{"name":"Journal of Audiology and Otology","volume":" ","pages":"252-259"},"PeriodicalIF":1.1,"publicationDate":"2024-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11540969/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"141555670","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Hearing Screening for Older Adults With Cognitive Impairment: A Systematic Review.","authors":"Patcharaorn Limkitisupasin, Piyawat Jongpradubgiat, Nattawan Utoomprurkporn","doi":"10.7874/jao.2023.00507","DOIUrl":"10.7874/jao.2023.00507","url":null,"abstract":"<p><strong>Background and objectives: </strong>Hearing loss is the largest potentially modifiable risk factor for dementia. Early evaluation and intervention are crucial for older adults with cognitive impairment. However, pure-tone audiometry (PTA), the gold standard, may have limitations. This study reviewed auditory tests for detecting hearing loss in this population, comparing to PTA.</p><p><strong>Materials and methods: </strong>Following the Preferred Reporting Items for Systematic Reviews and Meta-Analyses (PRISMA) guidelines, we conducted a systematic review in PubMed, Scopus, and Embase. Ten studies (1,071 participants) comparing auditory tests and PTA in patients with dementia and mild cognitive impairment were included.</p><p><strong>Results: </strong>Electrophysiological and behavioral tests demonstrated strong correlation and accurate hearing impairment detection compared to PTA. Conversely, self-reported assessment showed weaker correlations when aligned with hearing thresholds.</p><p><strong>Conclusions: </strong>This study highlights the potential of electrophysiological and behavioral auditory tests in detecting hearing impairment in older adults with cognitive impairment, emphasizing the need for further research to develop practical screening protocols for this vulnerable population.</p>","PeriodicalId":44886,"journal":{"name":"Journal of Audiology and Otology","volume":" ","pages":"260-270"},"PeriodicalIF":1.1,"publicationDate":"2024-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11540973/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"141555667","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Mohammad Al-Alawneh, Ra'ed Al-Ashqar, Yazan Kanaan, Maulla Alali, Haitham Odat
{"title":"Postauricular Myofibroma of the Facial Canal: A Case Report.","authors":"Mohammad Al-Alawneh, Ra'ed Al-Ashqar, Yazan Kanaan, Maulla Alali, Haitham Odat","doi":"10.7874/jao.2024.00059","DOIUrl":"10.7874/jao.2024.00059","url":null,"abstract":"<p><p>Myofibromatosis is a proliferative disorder characterized by the development of soft tissue neoplasms referred to as myofibromas that predominantly occur in infants and young children. These lesions have been described using varied terminologies since they were first reported in 1951. However, these neoplasms are histopathologically characterized by benign fibroblast and myofibroblast proliferation containing a biphasic presentation of spindle-shaped cells surrounding a central zone of less differentiated cells arranged in a hemangiopericytoma-like pattern in all cases. Usually, myofibromatosis occurs in children aged <2 years and is observed at birth in nearly 60% of cases. We report a rare case of myofibroma in an 8-year-old boy who presented with an approximately 6-month history of a left postauricular mass. Histopathological evaluation of the resected mass confirmed the diagnosis.</p>","PeriodicalId":44886,"journal":{"name":"Journal of Audiology and Otology","volume":" ","pages":"309-313"},"PeriodicalIF":1.1,"publicationDate":"2024-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11540975/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142141347","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}