No To Hattatsu最新文献_第8页

[A 6-month-old female patient who suffered clustering of afebrile seizures (part 2)]. [一例6个月大的女性患者出现聚集性发热性癫痫发作(第二部分)]。

No To Hattatsu Pub Date : 2016-05-01

Toshiyuki Yamamoto

引用次数: 0

[Deployment and problems after the "Joint recommendations on sedation during MRI examination"]. 【“MRI检查中镇静联合建议”后的部署及问题】。

No To Hattatsu Pub Date : 2016-03-01

Seigo Korematsu, Hideo Yamanouchi

引用次数: 0

[Future challenges and children's situation after the Great East Japan Earthquake]. [东日本大地震后未来的挑战和儿童的处境]。

No To Hattatsu Pub Date : 2016-03-01

Soichiro Tanaka, Atsushi Kamei

引用次数: 0

[A case of prolonged paroxysmal sympathetic hyperactivity]. [长时间阵发性交感神经亢进一例]。

No To Hattatsu Pub Date : 2016-03-01

Akiko Yamamoto, Shuhei Ide, Yuji Iwasaki, Makiko Kaga, Masataka Arima

{"title":"[A case of prolonged paroxysmal sympathetic hyperactivity].","authors":"Akiko Yamamoto, Shuhei Ide, Yuji Iwasaki, Makiko Kaga, Masataka Arima","doi":"","DOIUrl":"","url":null,"abstract":"We report the case of a 4-year-old girl who presented with paroxysmal sympathetic hyperactivity (PSH), after developing severe hypoxic-ischemic-encephalopathy because of cardiopulmonary arrest. She showed dramatic paroxysmal sympathetic activity with dystonia. She was treated with wide variety of medications against PSH, which were found to be effective in previous studies. Among them, morphine, bromocriptine, propranolol, and clonidine were effective in reducing the frequency of her attacks while gabapentin, baclofen, dantrolene, and benzodiazepine were ineffective. Though the paroxysms decreased markedly after the treatment, they could not be completely controlled beyond 500 days. Following the treatment, levels of plasma catecholamines and their urinary metabolites decreased to normal during inter- paroxysms. However, once a paroxysm had recurred, these levels were again very high. This case study is considered significant for two rea- sons. One is that PSH among children have been rarely reported, and the other is that this case of prolonged PSH delineated the transition of plasma catecholamines during the treatment. The excitatory: inhibitory ratio (EIR) model proposed by Baguley was considered while dis- cussing drug sensitivity in this case. Accumulation of similar case studies will help establish more effective treatment strategies and elucidate the pathophysiology of PSH.","PeriodicalId":39367,"journal":{"name":"No To Hattatsu","volume":"48 2","pages":"127-31"},"PeriodicalIF":0.0,"publicationDate":"2016-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34459737","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

[Meet the experts: therapy of myasthenia gravis in childhood]. 【认识专家:小儿重症肌无力的治疗方法】。

No To Hattatsu Pub Date : 2016-03-01

Masafumi Morimoto, Kazuhiro Haginoya

引用次数: 0

[Recent state of Japan obstetric compensation system and its 2015 revision]. [日本产科赔偿制度近况及其2015年修订版]。

No To Hattatsu Pub Date : 2016-03-01

Atsuo Nezu, Yasuhiro Suzuki

引用次数: 0

[Promote further progresses in child neurology based on a global partnership of health professionals and scientists, bring joy to all children with neurological disorders]. [在卫生专业人员和科学家的全球伙伴关系基础上促进儿童神经病学的进一步进展，为所有患有神经系统疾病的儿童带来欢乐]。

No To Hattatsu Pub Date : 2016-03-01

Toshisaburo Nagai

引用次数: 0

[The reports of the collaborative studies supported by the Japanese Society of Child Neurology]. [日本儿童神经病学学会支持的合作研究报告]。

No To Hattatsu Pub Date : 2016-03-01

引用次数: 0

[Niemann-Pick type C disease: pathophysiology, diagnosis and treatment]. [Niemann-Pick C型病:病理生理、诊断与治疗]。

No To Hattatsu Pub Date : 2016-03-01

Kousaku Ohno

引用次数: 0

[Characteristic asymmetric abnormal eye movement and dystonic posture as the first symptoms of alternating hemiplegia of childhood]. [儿童交替性偏瘫的首发症状:不对称异常眼动和张力障碍]。

No To Hattatsu Pub Date : 2016-03-01

Takahiro Motoki, Masayuki Sasaki, Atsushi Ishii, Shinichi Hirose

{"title":"[Characteristic asymmetric abnormal eye movement and dystonic posture as the first symptoms of alternating hemiplegia of childhood].","authors":"Takahiro Motoki, Masayuki Sasaki, Atsushi Ishii, Shinichi Hirose","doi":"","DOIUrl":"","url":null,"abstract":"A 3-month-old girl exhibited asymmetric abnormal eye movement and unilateral dystonic posture intermittently after the first few days of life. Unilateral ocular deviation or nystagmus were the main signs of abnormal eye movements. She was suspected to have alternating hemiplegia of childhood (AHC) despite the absence of apparent alternating hemiplegic episodes. Gene analysis revealed a de-novo missense mutation (Asp801Asn) of ATP1A3. AHC is a rare neurodevelopmental disorder characterized by recurrent transient attacks of hemiplegia affecting the unilateral or bilateral side of the body; in most cases, these attacks begin in the first 6 months of life. Initial symptoms of AHC are not alternating hemiplegic episodes, but rather asymmetric abnormal eye movement, dystonic posture, or seizures. It is difficult to diagnose AHC early because no specific findings are observed in the diagnostic laboratory or neuroradiological examinations. Early diagnosis is important because flunarizine may have a protective effect on the severe motor deterioration associated with AHC. Asymmetric abnormal eye movement could be an important clinical symptom for the diagnosis of AHC in early infancy.","PeriodicalId":39367,"journal":{"name":"No To Hattatsu","volume":"48 2","pages":"133-6"},"PeriodicalIF":0.0,"publicationDate":"2016-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34459738","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0