Pediatric Cardiology最新文献_第8页

Clarifying the Cardiovascular Morphology and Associated Abnormalities in Patients with Double Inlet Right Ventricle Using Multidetector CT Angiography. 利用多层螺旋CT血管造影研究双入口右心室患者的心血管形态及相关异常。

IF 1.5 4区医学

Pediatric Cardiology Pub Date : 2025-01-05 DOI: 10.1007/s00246-024-03766-5

Niraj Nirmal Pandey, Mansi Verma, Sheetal Sharma, Vineeta Ojha, Sanjeev Kumar, Sivasubramanian Ramakrishnan, Priya Jagia

{"title":"Clarifying the Cardiovascular Morphology and Associated Abnormalities in Patients with Double Inlet Right Ventricle Using Multidetector CT Angiography.","authors":"Niraj Nirmal Pandey, Mansi Verma, Sheetal Sharma, Vineeta Ojha, Sanjeev Kumar, Sivasubramanian Ramakrishnan, Priya Jagia","doi":"10.1007/s00246-024-03766-5","DOIUrl":"https://doi.org/10.1007/s00246-024-03766-5","url":null,"abstract":"We sought to evaluate the intracardiac morphology and associated cardiovascular anomalies in patients with double inlet right ventricle (DIRV) on multidetector CT angiography. A retrospective search of our departmental database was conducted from January 2014 to January 2023 to identify patients with a diagnosis of DIRV on CT angiography. The intracardiac anatomy and associated cardiovascular abnormalities were systematically evaluated. Patients with a common atrioventricular valve were excluded. DIRV was diagnosed in 41 patients (36 males, 5 females; mean age at imaging: 7.4 years [range: 4 months-30 years]). Mirror-imaged viscero-atrial arrangement was observed in 12/41 (29.3%) while right isomerism and left isomerism were seen in 6/41 (14.6%) and 2/41 (4.9%) patients respectively. Hypoplastic left ventricular cavity was seen in 39/41 (95.1%) patients. AV valve straddling was observed in 40/41 (97.6%) patients. Atrial septal defect was seen in 28/41 (68.3%) patients. All (100%) patients had presence of ventricular septal defect. Twisted atrioventricular connections were seen in 4/41 (9.8%) patients. The most common ventriculo-arterial morphology was presence of double outlet right ventricle (DORV) seen in 25/41 (61%) patients. Some degree of pulmonary outflow obstruction was seen in 24/41 (58.5%) patients. Systemic venous anomalies, pulmonary venous anomalies and coronary artery anomalies were observed in 13/41 (31.7%), 6/41 (14.6%) and 8/41 (19.5%) patients. DIRV is a type of single ventricle congenital heart disease associated with an array of cardiovascular abnormalities, most commonly DORV and pulmonary outflow tract obstruction. The knowledge of associated anomalies is imperative for preoperative planning. CT angiography allows for detailed anatomical evaluation of DIRV and associated cardiovascular anomalies which may positively impact surgical management in these patients.","PeriodicalId":19814,"journal":{"name":"Pediatric Cardiology","volume":" ","pages":""},"PeriodicalIF":1.5,"publicationDate":"2025-01-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142932353","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Medical & Socioeconomic Risk Factors Associated with Lack of Neurodevelopmental Evaluation Following Neonatal Cardiac Surgery. 新生儿心脏手术后缺乏神经发育评估的医疗和社会经济风险因素

IF 1.5 4区医学

Pediatric Cardiology Pub Date : 2025-01-04 DOI: 10.1007/s00246-024-03761-w

Luma Essaid, Kelly Haque, Amanda Shillingford, Lauren Zimmerman, Alisa Burnham, Lyla Hampton, Oluwatimilehin Okunowo, J William Gaynor, Nicholas S Abend, Maryam Y Naim, Monique M Gardner

{"title":"Medical & Socioeconomic Risk Factors Associated with Lack of Neurodevelopmental Evaluation Following Neonatal Cardiac Surgery.","authors":"Luma Essaid, Kelly Haque, Amanda Shillingford, Lauren Zimmerman, Alisa Burnham, Lyla Hampton, Oluwatimilehin Okunowo, J William Gaynor, Nicholas S Abend, Maryam Y Naim, Monique M Gardner","doi":"10.1007/s00246-024-03761-w","DOIUrl":"https://doi.org/10.1007/s00246-024-03761-w","url":null,"abstract":"Neonates with congenital heart disease (CHD) who undergo cardiopulmonary bypass (CPB) are at high-risk for unfavorable neurodevelopmental (ND) outcomes and are recommended for ND evaluation (NDE); however, poor rates have been reported. We aimed to identify risk factors associated with lack of NDE. This single-center retrospective observational study included neonates < 30 days old who underwent CPB and survived to discharge between 2012 and 2018. Primary outcome (NDE) was ≥ 1 appointment at our center's dedicated cardiac, neonatal, or general ND clinics before the 3rd birthday. Predictor variables included demographic, medical, and social factors. Social disorganization index (SDI) was obtained with geocoding based on address at time of discharge. Logistic regression identified risk factors associated with lack of NDE. The cohort included 594 patients, predominantly male (59%) and white (59%). A majority (63%) had NDE. Lack of NDE was more common in patients with postnatal CHD diagnosis, CHD without arch obstruction, absence of postoperative seizures, living below 100% poverty level, lack of insurance, younger parental age, and overall higher SDI (p < 0.03). In multivariable analysis, lack of NDE was associated with single-ventricle CHD without arch obstruction (OR 2.17; 95% CI 1.08-4.55), two ventricle CHD without arch obstruction (OR 2.56; 95% CI 1.59-4.17), and higher SDI (OR 1.25; 95% CI 1.05-1.49); all p < 0.05. This study identifies medical and neighborhood-level socioeconomic factors that may help address care gaps in this high-risk population. Patients with socioeconomic disparities may benefit from increased care coordination upon discharge.","PeriodicalId":19814,"journal":{"name":"Pediatric Cardiology","volume":" ","pages":""},"PeriodicalIF":1.5,"publicationDate":"2025-01-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142927660","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Correction: Short and Mid-term Outcomes of Ductal Graft with Bilateral Pulmonary Banding in Hypoplastic Left Heart Syndrome and Variants. 更正：左心发育不全综合征及变异型的导管移植与双侧肺束带术的短期和中期疗效。

IF 1.5 4区医学

Pediatric Cardiology Pub Date : 2025-01-01 DOI: 10.1007/s00246-024-03640-4

Ayla Oktay, Ahmet Arnaz, Canan Ayabakan, Tayyar Sarioglu, Yusuf Kenan Yalcinbas

引用次数: 0

Correction: Ewing's Sarcoma Metastazing from the Right Pelvis via the Inferior Vena Cava into the Heart: Diagnosis and Successful Surgical Treatment. 更正：从右骨盆经下腔静脉进入心脏的尤文肉瘤转移：诊断和成功的手术治疗。

IF 1.5 4区医学

Pediatric Cardiology Pub Date : 2025-01-01 DOI: 10.1007/s00246-024-03690-8

Joachim Peter Sturmberg, Hans Meyer, Reiner Körfer, Wolfgang Matthies, Wolf-Rüdiger Thies, Alfred Schauer, Peter Weinel

引用次数: 0

Correction: Screening for Life-Threatening Arrhythmia in Asymptomatic Patients After Paediatric Cardiac Surgery: A Single-Centre Retrospective Analysis of 790 Pre-hospital-discharge 24-h Holter Electocardiogram Recordings. 更正：筛查儿科心脏手术后无症状患者中危及生命的心律失常：对 790 份出院前 24 小时 Holter 心电图记录的单中心回顾性分析。

IF 1.5 4区医学

Pediatric Cardiology Pub Date : 2025-01-01 DOI: 10.1007/s00246-024-03709-0

Evangelia Blana, Matthias Gass, Florian Berger, Hitendu Dave, Christian Balmer

引用次数: 0

Left Atrial Phasic Function via Cardiac Magnetic Resonance Imaging in Patients with Duchenne Muscular Dystrophy. Duchenne肌营养不良患者的心脏磁共振成像左心房时相功能。

IF 1.5 4区医学

Pediatric Cardiology Pub Date : 2025-01-01 Epub Date: 2023-11-08 DOI: 10.1007/s00246-023-03327-2

Taylor M Trussell, Tyler Brown, Elisa Marcuccio, Anna Mullikin, Huaiyu Zang, Nicholas J Ollberding, Chet Villa, Sean M Lang

{"title":"Left Atrial Phasic Function via Cardiac Magnetic Resonance Imaging in Patients with Duchenne Muscular Dystrophy.","authors":"Taylor M Trussell, Tyler Brown, Elisa Marcuccio, Anna Mullikin, Huaiyu Zang, Nicholas J Ollberding, Chet Villa, Sean M Lang","doi":"10.1007/s00246-023-03327-2","DOIUrl":"10.1007/s00246-023-03327-2","url":null,"abstract":"Cardiac dysfunction is a leading cause of morbidity and mortality in Duchenne muscular dystrophy (DMD). Left atrial (LA) function is a poorly understood concept in this patient population, and research suggests underlying structural changes that could affect atrial function. Cardiac magnetic resonance (CMR) imaging may provide an important non-invasive approach to evaluating LA function. This study was a single center retrospective review of consecutive CMR studies over a 1 year period comparing LA phasic function within a cohort of DMD patients, and to those with structurally and functionally normal hearts. LA strain measurements including global reservoir, conduit, boost-pump strain, and LA volumes were obtained retrospectively. Spearman correlation analyses were performed on atrial strain measurements. 107 DMD and 79 normal CMR studies were included. The DMD cohort had worse systolic function (p < 0.001), smaller indexed max LA and left ventricular (LV) volumes (p < 0.001), and greater LA emptying fraction (p < 0.001). In the DMD cohort, emptying fraction decreased with advanced patient age (p < 0.001) and diminishing systolic function (p < 0.001). DMD patients with moderate or severe LV dysfunction demonstrated lower LA emptying fraction (p = 0.002), more impaired 2-chamber LA reservoir (p = 0.003), and LA pump (p = 0.006) and conduit strain (p = 0.018). DMD patients with preserved function have lower indexed LA volumes with higher LA emptying fractions than controls. Progression of disease and age is associated with decreased LA emptying fraction with early manifestations in reservoir and conduit strain. These findings suggest that strain markers of LA compliance and early left ventricular relaxation are associated with worsening cardiomyopathy in the DMD population.","PeriodicalId":19814,"journal":{"name":"Pediatric Cardiology","volume":" ","pages":"72-80"},"PeriodicalIF":1.5,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"71522321","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Maternal Diabetes and Cardiovascular Health in the Offspring. 母亲糖尿病与后代心血管健康。

IF 1.5 4区医学

Pediatric Cardiology Pub Date : 2025-01-01 Epub Date: 2023-11-06 DOI: 10.1007/s00246-023-03333-4

Riasoya Jodah, Alisa Arunamata, Alaina K Kipps, Sharon Chen, Katie Jo Stauffer, Elif Seda Selamet Tierney

{"title":"Maternal Diabetes and Cardiovascular Health in the Offspring.","authors":"Riasoya Jodah, Alisa Arunamata, Alaina K Kipps, Sharon Chen, Katie Jo Stauffer, Elif Seda Selamet Tierney","doi":"10.1007/s00246-023-03333-4","DOIUrl":"10.1007/s00246-023-03333-4","url":null,"abstract":"Pulse wave velocity (PWV) has been explored to predict cardiovascular health in adults. Less is known about neonatal PWV. We evaluated the association between arterial stiffness of neonates of mothers (NoM) with diabetes and childhood health. Neonatal brachial-femoral PWV (bfPWV) was measured after birth and neonates followed for a median of 5.2 years [1 month-6.6 years]. 36 pregnant women with pregestational diabetes mellitus PGDM (n = 12), gestational diabetes mellitus (GDM) (n = 13), and controls (n = 11) were enrolled. Neonates were similar in weight, gestational age, and delivery mode. 26 neonates had follow-up data including weight, height and blood pressure. More mothers with PGDM had poor glycemic control compared to mothers with GDM (83% vs. 8%; p = 0.0002). PWV was higher in NoM with PGDM than controls (3.4 ± 0.5 vs. 2.6 ± 0.8 m/s; p = 0.04). At follow-up, children of mothers with diabetes (n = 16) had higher weight percentile (78.5 ± 27.9 vs 49.5 ± 34.6%; p = 0.02) and diastolic blood pressure (DBP) (68 ± 13.6 vs 57.3 ± 4.3 mmHg; p = 0.01) than controls (n = 10). No correlation emerged between neonatal PWV and childhood body mass index (BMI) or maternal HbA1c. Results suggest maternal diabetes affect neonatal arterial stiffness and childhood blood pressure; however, the mechanism is unclear. The long-term implications of these findings warrant further investigation.","PeriodicalId":19814,"journal":{"name":"Pediatric Cardiology","volume":" ","pages":"89-97"},"PeriodicalIF":1.5,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"71484713","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Myocardial Work for Dynamic Monitoring of Myocardial Injury in Neonatal Asphyxia. 用于动态监测新生儿窒息时心肌损伤的心肌工作。

IF 1.5 4区医学

Pediatric Cardiology Pub Date : 2025-01-01 Epub Date: 2023-12-20 DOI: 10.1007/s00246-023-03357-w

Xin-Lu Hu, Cui Hou, Hui Wang, Hong Li, Tao Pan, Jun-Cheng Ni, Yue-Yue Ding, Xue-Ying Si, Xiao-Chen Li, Qiu-Qin Xu

{"title":"Myocardial Work for Dynamic Monitoring of Myocardial Injury in Neonatal Asphyxia.","authors":"Xin-Lu Hu, Cui Hou, Hui Wang, Hong Li, Tao Pan, Jun-Cheng Ni, Yue-Yue Ding, Xue-Ying Si, Xiao-Chen Li, Qiu-Qin Xu","doi":"10.1007/s00246-023-03357-w","DOIUrl":"10.1007/s00246-023-03357-w","url":null,"abstract":"To assess the value of parameters of myocardial work for dynamic monitoring of myocardial injury after neonatal asphyxia. Fifty-three neonates with asphyxia admitted within 24 h after delivery were divided into a mild asphyxia group (n = 40) and severe asphyxia group (n = 13). Echocardiography was performed within 24 h post-birth, within 72 h post-birth (48 h after first echo), and during recovery. The left ventricular ejection fraction on M-mode echocardiography and by Simpson's biplane method (LVEF and Bi-EF, respectively), stroke volume (SV), cardiac output (CO), cardiac index (CI), global longitudinal strain (GLS), global work index (GWI), global constructive work (GCW), and other parameters were measured. Echocardiographic indicators were compared between groups and over time. GWI was significantly increased at 72 h in the mild asphyxia group (P < 0.05) but showed no significant change over time in the severe asphyxia group (P > 0.05). While GCW increased significantly over time in both groups (P < 0.05), it increased earlier in the mild asphyxia group. Time and grouping factors had independent effects on GWI and GCW (P > 0.05). The characteristics of differences in GWI and GCW between the two groups were different from those for LVEF, Bi-EF, SV, CO, CI, and GLS and their change characteristics with improvement from treatment. GWI and GCW changed significantly during recovery from neonatal asphyxia, and their change characteristics differed between mild and severe asphyxia cases. Myocardial work parameters can be used as valuable supplements to traditional indicators of left ventricular function to dynamically monitor the recovery from myocardial injury after neonatal asphyxia.","PeriodicalId":19814,"journal":{"name":"Pediatric Cardiology","volume":" ","pages":"163-172"},"PeriodicalIF":1.5,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"138830904","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Using DaSilva Cone Operation to Establish 1.5 or 2 Ventricle Circulation After Initial Single Ventricle Palliation with Starnes Procedure. 采用DaSilva锥体手术在初始单心室Starnes手术后建立1.5或2个心室循环。

IF 1.5 4区医学

Pediatric Cardiology Pub Date : 2025-01-01 Epub Date: 2023-12-01 DOI: 10.1007/s00246-023-03336-1

Craig P Dobson, Adam B Christopher, Mario Castro-Medina, Melita L Viegas, Jose Pedro Da Silva, Luciana Da Fonseca Da Silva

{"title":"Using DaSilva Cone Operation to Establish 1.5 or 2 Ventricle Circulation After Initial Single Ventricle Palliation with Starnes Procedure.","authors":"Craig P Dobson, Adam B Christopher, Mario Castro-Medina, Melita L Viegas, Jose Pedro Da Silva, Luciana Da Fonseca Da Silva","doi":"10.1007/s00246-023-03336-1","DOIUrl":"10.1007/s00246-023-03336-1","url":null,"abstract":"Ebstein anomaly (EA) is a congenital dysplasia of the tricuspid valve resulting in reduced right ventricular (RV) volume and tricuspid regurgitation. Severe EA in the neonatal period is associated with high mortality. The Starnes procedure (fenestrated RV exclusion) is reserved for EA patients with cardiogenic shock and has previously committed patients to single ventricle (SV) palliation. In this report, we present the results of a strategy to redirect patients utilizing the Da Silva Cone operation to achieve a 2 or 1.5 ventricle circulation. Single-center retrospective study including all consecutive cases of Da Silva Cone operation after Starnes procedure. Between 2019 and 2023, six conversions from Starnes procedure to Cone reconstruction were performed. All were critically ill before their Starnes procedure; four on extracorporeal membrane oxygenation. Two patients were successfully rerouted to a two-ventricle repair; the remainder to 1.5 ventricle circulation. RV pressure estimates showed no correlation with success. Post-Cone intensive care and hospital stays were brief, median 5 and 6 days, respectively. All are between 2.5 and 6 years old, without indications for SV palliation. There were no deaths, with follow up ranging 1 month-4 years. No repeat interventions were performed on the tricuspid valves. One subject had a surgical pulmonary valve replacement. Tricuspid regurgitation was mild in all. The Da Silva Cone operation offers successful redirection of EA patients from a SV pathway to a 1.5 or 2 ventricle pathway after Starnes procedure. The approach is feasible and durable in midterm follow-up. The decision to initially proceed with Starnes need not be an irrevocable decision to continue down a SV palliation pathway.","PeriodicalId":19814,"journal":{"name":"Pediatric Cardiology","volume":" ","pages":"107-115"},"PeriodicalIF":1.5,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"138461509","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Long-Term Results Following Combined Repair of Atrioventricular Septal Defect with Tetralogy of Fallot. 房室间隔缺损合并法洛四联症联合修复的远期疗效。

IF 1.5 4区医学

Pediatric Cardiology Pub Date : 2025-01-01 Epub Date: 2023-11-27 DOI: 10.1007/s00246-023-03343-2

Katja Schumacher, Mateo Marin-Cuartas, Sabine Meier, Muhammad Ikbal Aydin, Michael A Borger, Ingo Dähnert, Martin Kostelka, Marcel Vollroth

{"title":"Long-Term Results Following Combined Repair of Atrioventricular Septal Defect with Tetralogy of Fallot.","authors":"Katja Schumacher, Mateo Marin-Cuartas, Sabine Meier, Muhammad Ikbal Aydin, Michael A Borger, Ingo Dähnert, Martin Kostelka, Marcel Vollroth","doi":"10.1007/s00246-023-03343-2","DOIUrl":"10.1007/s00246-023-03343-2","url":null,"abstract":"Atrioventricular septal defect (AVSD) in association with tetralogy of Fallot (TOF) is a rare and complex congenital cardiac malformation. We report our institutional experience and outcomes following surgical correction over a 20-year period. Patients who underwent combined surgical AVSD and TOF correction between October 2001 and February 2020 were included for analysis. All patients underwent primary repair. The study data were prospectively collected and retrospectively analyzed. Primary outcomes were in-hospital mortality and long-term freedom from reoperation. During the study period, a total of 10 consecutive patients underwent combined surgical AVSD and TOF correction. Median age at operation was 307 days (IQR 228-457) and median weight was 7.7 kg (IQR 6.7-9.5). Down Syndrome was present in six of the patients. In-hospital mortality was 0%. One patient required re-exploration due to bleeding. Median follow-up was 11 years (IQR 11 months -16 years). There was one case of reoperation due to significant residual ventricular septal defect after 2 months. None of the patients died during follow-up. Combined primary AVSD and TOF repair can be performed with low early mortality and morbidity, as well as a high long-term freedom from reoperation.","PeriodicalId":19814,"journal":{"name":"Pediatric Cardiology","volume":" ","pages":"134-138"},"PeriodicalIF":1.5,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11746969/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"138445719","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0