{"title":"Acute Measles Encephalitis: Primary Encephalitis or Postinfectious Encephalomyelitis","authors":"B. John, Mrigank Choubey, J. Debnath","doi":"10.1055/s-0036-1583523","DOIUrl":"https://doi.org/10.1055/s-0036-1583523","url":null,"abstract":"Abstract Measles remains an important vaccine-preventable disease, particularly in the developing countries. The disease at times is accompanied by numerous complications in the backdrop of malnutrition. Of these, the neurologic complications are the most devastating. The neurological involvement in measles encompasses at least four distinct conditions, namely, primary measles encephalitis (PME), acute postinfectious measles encephalomyelitis (APME), measles inclusion body encephalitis, and subacute sclerosing panencephalitis. The pathogenesis of PME or APME continues to be enigmatic with both immune mechanism and direct viral invasion being variously incriminated. We report a fatal case of measles encephalitis in a 3.5-year-old child, with a slow and indolent course over a 1-month period with laboratory evidence of acute measles infection without any demonstrable virus in the body fluid at the time of the encephalitis with typical magnetic resonance imaging features.","PeriodicalId":89989,"journal":{"name":"Journal of pediatric neuroradiology","volume":"35 1","pages":"060 - 063"},"PeriodicalIF":0.0,"publicationDate":"2015-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"84029732","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Pfeiffer Syndrome Type II: Cloverleaf Skull and Hydrocephalus Discovered on Fetal MRI","authors":"Mamta Gupta, C. Singh, S. Byrd","doi":"10.1055/s-0036-1583313","DOIUrl":"https://doi.org/10.1055/s-0036-1583313","url":null,"abstract":"Abstract Pfeiffer syndrome (PS) is a rare hereditary condition with predominantly complicated craniofacial anomalies due to osteochondrodysplasia with craniosynostosis. Based on the clinical findings, it is divided into three subtypes. We report a case of PS type II, discovered on the antenatal ultrasonography and confirmed on the fetal magnetic resonance imaging (MRI). We shall discuss the clinical and radiological features and the advantage of fetal MRI to confirm and evaluate the fetus for other associated anomalies. According to the MEDLINE search, only one case so far has been reported with in utero fetal MRI findings of PS II.","PeriodicalId":89989,"journal":{"name":"Journal of pediatric neuroradiology","volume":"28 1","pages":"064 - 067"},"PeriodicalIF":0.0,"publicationDate":"2015-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"77814506","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Spontaneous Resolution of a High-Flow Congenital Spinal Epidural Arteriovenous Fistula in a Pediatric Patient","authors":"N. Majeed, P. Gailloud","doi":"10.1055/s-0036-1579684","DOIUrl":"https://doi.org/10.1055/s-0036-1579684","url":null,"abstract":"Abstract The spontaneous resolution of a spinal vascular malformation is a rare phenomenon. We report the case of a 19-month-old male infant with a high-flow congenital spinal epidural arteriovenous fistula that completely regressed between the time of diagnostic angiography and planned endovascular treatment. Prior reported instances, potential underlying mechanisms, and implications for management timing and necessity are discussed.","PeriodicalId":89989,"journal":{"name":"Journal of pediatric neuroradiology","volume":"47 1","pages":"029 - 031"},"PeriodicalIF":0.0,"publicationDate":"2015-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"86008830","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Nonsedated Magnetic Resonance Imaging for Congenital Sensorineural Hearing Loss","authors":"Jeffrey Cheng, V. Nguyen","doi":"10.1055/s-0036-1579622","DOIUrl":"https://doi.org/10.1055/s-0036-1579622","url":null,"abstract":"Abstract Hearing loss is the most common congenital condition in the United States. Magnetic resonance imaging (MRI) may be used in evaluation. Imaging in infants and children often requires sedation or general anesthesia to acquire images not degraded by motion artifact. Avoidance of sedation may decrease resource utilization and potentially avoid not yet understood possible cognitive deficits from early anesthetic exposure.Given that the membranous labyrinth, cochlea, and internal auditory canal are normally high in fluid concentration, an MRI focused on T2 imaging at the beginning of the study may provide an alternative imaging strategy with avoidance of anesthesia and radiation.","PeriodicalId":89989,"journal":{"name":"Journal of pediatric neuroradiology","volume":"65 1","pages":"025 - 028"},"PeriodicalIF":0.0,"publicationDate":"2015-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"83942231","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Vikram Bhise, K. Buyukturkoglu, M. Inglese, J. Wollack, K. Balashov
{"title":"Severe Progressive Brain Atrophy in Pediatric Multiple Sclerosis","authors":"Vikram Bhise, K. Buyukturkoglu, M. Inglese, J. Wollack, K. Balashov","doi":"10.1055/s-0036-1579645","DOIUrl":"https://doi.org/10.1055/s-0036-1579645","url":null,"abstract":"Abstract Background Multiple sclerosis (MS) is an immune-mediated disease of the central nervous system. Progressive brain atrophy is a known marker of patient disability and cognitive impairment in MS patient, but limited information is available about the clinical and cognitive consequences in the pediatric population. Case Report We present a case of aggressive pediatric-onset MS with severe rapidly progressive brain atrophy, neurological disability, and cognitive deterioration. Serial brain magnetic resonance imaging studies demonstrate ongoing cerebral atrophy correlating with severe deficits on serial neuropsychological testing. Conclusion A subset of pediatric MS patient may be vulnerable to severe cognitive deterioration associated with marked brain atrophy.","PeriodicalId":89989,"journal":{"name":"Journal of pediatric neuroradiology","volume":"70 1","pages":"032 - 035"},"PeriodicalIF":0.0,"publicationDate":"2015-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"79789220","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"A Case Report of a Cervical Exostosis and Spinal Cord Compression in a Child with Trichorhinophalangeal Syndrome II","authors":"S. Farook, A. Mistry, M. Hussain, D. Crimmins","doi":"10.1055/s-0036-1579623","DOIUrl":"https://doi.org/10.1055/s-0036-1579623","url":null,"abstract":"Abstract Trichorhinophalangeal syndrome (TRPS) is an extremely rare complex genetic disorder with autosomal dominant inheritance. This case report discusses the management of a 4-year-old child with TRPS II (previously known as Langer–Giedion syndrome), who presented with right-sided hemiparesis and a limping gait secondary to spinal cord compression at the level of C1. Here, we document a child who underwent a successful decompressive laminectomy, highlighting the importance of a multidisciplinary team approach in managing rare and complex cases.","PeriodicalId":89989,"journal":{"name":"Journal of pediatric neuroradiology","volume":"60 1","pages":"041 - 044"},"PeriodicalIF":0.0,"publicationDate":"2015-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"78870107","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
T. Onal, Guven Onur Afacan, B. Muezzınoğlu, Y. Anık, G. Akansel
{"title":"Giant Neck Hemangiopericytoma Detected on Fetal Magnetic Resonance Imaging","authors":"T. Onal, Guven Onur Afacan, B. Muezzınoğlu, Y. Anık, G. Akansel","doi":"10.1055/s-0036-1579620","DOIUrl":"https://doi.org/10.1055/s-0036-1579620","url":null,"abstract":"Abstract We present the fetal and postnatal magnetic resonance imaging findings in a case of fetal hemangiopericytoma.","PeriodicalId":89989,"journal":{"name":"Journal of pediatric neuroradiology","volume":"61 1","pages":"045 - 048"},"PeriodicalIF":0.0,"publicationDate":"2015-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"84642927","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
E. Demirel, A. Subaşıoğlu, T. Kalayci, B. Birlik, U. Turhan, S. Kelekci
{"title":"Cavum Vergae: In the Differential Diagnosis of Fetal Midline Intracranial Cystic Lesions","authors":"E. Demirel, A. Subaşıoğlu, T. Kalayci, B. Birlik, U. Turhan, S. Kelekci","doi":"10.1055/s-0036-1579621","DOIUrl":"https://doi.org/10.1055/s-0036-1579621","url":null,"abstract":"Abstract Cavum vergae (CV) cysts are developmental cysts of the midline of the brain that is formed from the posterior extension of the cavum septum pellucidum. Several cases of enlarged CV have been reported previously, but prenatal diagnosis of this condition is very rare. We report a case of isolated dilated CV diagnosed prenatally. When midline intracranial cysts are determined prenatally, first physicians must pay attention to distinguish them from pathologic cyst and determine whether associated malformations are present or not. The sonography is a useful tool for both the differential diagnosis and identification of associated malformations. Although CV may be present as a normal variation without clinical findings, it has been also considered as a marker of impaired neurodevelopment. Although the relationship between the CV and the various clinical findings such as headache, papilla edema, cognitive and behavior disorders, and psychiatric problems has not been fully elucidated, an accurate evaluation will be helpful for estimation of prognosis, the assessment of the risk for the other related malformations, and for the follow-up of the patient. Also, it is important to identify these kinds of findings, to clarify their clinical importance and for genetic counseling.","PeriodicalId":89989,"journal":{"name":"Journal of pediatric neuroradiology","volume":"3 1","pages":"036 - 040"},"PeriodicalIF":0.0,"publicationDate":"2015-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"89543507","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Mega Corpus Callosum in a Patient with Macrocephaly and Focal Motor Delay","authors":"James S. Park, Kevin Khodabakhsh, G. Heller","doi":"10.1055/s-0035-1564664","DOIUrl":"https://doi.org/10.1055/s-0035-1564664","url":null,"abstract":"Abstract An enlarged corpus callosum is a rare entity, with extremely low rates documented in literature. When paired with macrocephaly, only a handful of cases without any other underlying systemic condition are known to exist. We present a novel case of a macrocephalic patient with magnetic resonance imaging findings of an enlarged (or mega) corpus callosum. Neurologic exam demonstrated right lower extremity hypertonicity without any other developmental disorder. It is important to be aware of an enlarged corpus callosum as it may be associated with an underlying motor disorder.","PeriodicalId":89989,"journal":{"name":"Journal of pediatric neuroradiology","volume":"35 4","pages":"011 - 013"},"PeriodicalIF":0.0,"publicationDate":"2015-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1055/s-0035-1564664","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"72545629","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
N. Altınbaş, G. Gural, A. Gunes, B. Deri̇nkuyu, H. Unlu
{"title":"Arrested Pneumatization in Pediatric Age Group: Computed Tomography and Magnetic Resonance Imaging Findings","authors":"N. Altınbaş, G. Gural, A. Gunes, B. Deri̇nkuyu, H. Unlu","doi":"10.1055/s-0035-1564665","DOIUrl":"https://doi.org/10.1055/s-0035-1564665","url":null,"abstract":"Abstract Objective Arrested pneumatization of the skull base is a developmental anatomical variant of the paranasal sinuses. Although it is an incidental finding, severe bone lesions can be confusing in the differential diagnosis. In this study, arrested pneumatization in the pediatric group is discussed with computed tomography (CT) and magnetic resonance imaging (MRI) findings. Methods Cranial scanning findings of 550 patients who underwent imaging in the Radiology Department of our hospital with various diagnoses between 2012 and 2013 were examined. CT and MRI findings of arrested pneumatization in six patients were evaluated and recorded. Results The patients ranged in age from 7 to 14 years. The indications for scanning included neurofibromatosis type 1 (n = 1), papilledema (n = 2), epilepsy (n = 1), sixth nerve palsy (n = 1), and headache (n = 1). Arrested pneumatization was detected incidentally in all patients. Four patients had arrested pneumatization of the sphenoid bone, and two had arrested pneumatization of the temporal bone (petrous apex). Conclusion Arrested pneumatization of the skull base is an incidental finding most commonly detected in association with the sphenoid bone. It is a benign imaging finding that can be observed in the pediatric group and may cause diagnostic confusion. Therefore, CT and MRI findings are of great importance for the final diagnosis.","PeriodicalId":89989,"journal":{"name":"Journal of pediatric neuroradiology","volume":"1 1","pages":"007 - 010"},"PeriodicalIF":0.0,"publicationDate":"2015-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"89744492","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}