Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery最新文献_第5页

Advance Care Planning for Pediatric Cardiac Patients 儿科心脏病患者的预先护理计划

Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery Pub Date : 2021-11-01 DOI: 10.9794/jspccs.37.217

Ayami Gonnokami

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Multidisciplinary Management of a Very Low-Birth-Weight Neonate with Total Anomalous Pulmonary Venous Connection and Extracardiac Multiple Anomalies 1例极低出生体重新生儿全肺静脉连接异常和心外多发性异常的多学科治疗

Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery Pub Date : 2021-11-01 DOI: 10.9794/jspccs.37.233

Y. Nakayama, Y. Iwata, Toshihide Nishimori, T. Kuwahara, N. Kuwabara, H. Goto, K. Omoya, Tetsuya Yamamoto, Atsushi Terazawa, T. Masue, Sadahiro Kato, T. Takeuchi

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Palliative Care for Children with Heart Disease 儿童心脏病的姑息治疗

Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery Pub Date : 2021-11-01 DOI: 10.9794/jspccs.37.215

M. Taketazu

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Comprehensive Genetic Analysis in Congenital Heart Disease 先天性心脏病的综合遗传分析

Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery Pub Date : 2021-11-01 DOI: 10.9794/jspccs.37.193

Satoshi Hayano

{"title":"Comprehensive Genetic Analysis in Congenital Heart Disease","authors":"Satoshi Hayano","doi":"10.9794/jspccs.37.193","DOIUrl":"https://doi.org/10.9794/jspccs.37.193","url":null,"abstract":"Congenital heart disease (CHD) is considered to be caused by multifactorial inheritance. Genetic variants and environmental factors have a complex effect on its onset. Chromosomal defects and single-gene disorders can also cause CHD. By analyzing syndromic CHDs and Mendelian inherited familial CHDs, many CHD-related genes have been identified. On the other hand, a large number of CHD-related genes are estimated to be undis-covered. The genetic basis of sporadic CHD also has not been elucidated. Over the last decade, owing to the advances in comprehensive DNA analysis techniques, our understanding of the genetic architecture of CHD is expanding. These advances include next-generation sequencers for nucleotide sequences and chromosomal microarray analysis for copy number abnormalities. Novel CHD-related genes have been reported from comprehensive genetic analyses of rare families and syndromes. Comprehensive genetic analysis of large cohorts have provided new areas of research, such as the identification of genes involved in the development of sporadic CHD and the analysis of epigenetic regulation in CHD development. This article reviews the history and pros-pects of comprehensive genetic analysis of CHD.","PeriodicalId":89701,"journal":{"name":"Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery","volume":" ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-11-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"46523131","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

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A Case of Transposition of the Great Arteries that Led to the Development of Non-IgE-Mediated Gastrointestinal Food Allergy after a Neonatal Necrotizing Enterocolitis Complication 一例新生儿坏死性小肠结肠炎并发症后大动脉移位导致非IgE介导的胃肠道食物过敏的病例

Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery Pub Date : 2021-11-01 DOI: 10.9794/jspccs.37.239

M. Nagata, Hisako Wakatsuki, Kotoko Matsui, Keisuke Jimbo, Takeshi Furukawa, Hideo Fukunaga, T. Kudo, Ken Takahashi, M. Kishiro, Toshiaki Shimizu

{"title":"A Case of Transposition of the Great Arteries that Led to the Development of Non-IgE-Mediated Gastrointestinal Food Allergy after a Neonatal Necrotizing Enterocolitis Complication","authors":"M. Nagata, Hisako Wakatsuki, Kotoko Matsui, Keisuke Jimbo, Takeshi Furukawa, Hideo Fukunaga, T. Kudo, Ken Takahashi, M. Kishiro, Toshiaki Shimizu","doi":"10.9794/jspccs.37.239","DOIUrl":"https://doi.org/10.9794/jspccs.37.239","url":null,"abstract":"Neonatal necrotizing enterocolitis (NEC) is a serious complication associated with congenital heart disease (CHD). Non-IgE-mediated gastrointestinal food allergy (non-IgE-GI-FA) in neonates and infants manifests as digestive symptoms, including emesis, diarrhea, melena, and abdominal distension, with occasional intestinal perforation and NEC. Previous studies showed the relationship between CHD and non-IgE-GI-FA, which suggests that a decrease in intestinal blood ow can be a risk factor of non-IgE-GI-FA in neonates and infants with CHD. We report the case of a neonate with transposition of the great arteries who developed NEC before an arterial switch operation (ASO) and non-IgE-GI-FA a er the operation. e patient presented with bloody stools a er the start of formula feeding and was diagnosed with NEC on the basis of abdominal radiography ndings. A er recovery from NEC, the patient underwent ASO. However, the patient presented with abdominal distension a er formula feeding was restarted and was diagnosed with non-IgE-GI-FA on the basis of the ndings of eosinophilia and positivity in an allergen-speci c lymphocyte stimulation test. is demonstrates that postoperative digestive symptoms impose the possibility of non-IgE-GI-FA in neonates with CHD, especially in those with an NEC complication. erefore, we infer that if gastrointestinal complications occur in patients with severe CHD, the possibility of non-IgE-GI-FA should be considered.","PeriodicalId":89701,"journal":{"name":"Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery","volume":" ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-11-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"47672192","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

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A Pragmatic Approach to the Asymptomatic Patient with a WPW Pattern ECG: Based on the Latest Evidence 对无症状WPW型心电图患者的实用方法:基于最新证据

Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery Pub Date : 2021-11-01 DOI: 10.9794/jspccs.37.165

Y. Yoshida

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Pediatric CV Surgeon Training System in the United States 美国儿科CV外科医生培训系统

Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery Pub Date : 2021-11-01 DOI: 10.9794/jspccs.37.246

T. Shinkawa

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A Case of Vascular Endothelial Dysfunction Detected Using Reactive Hyperemia-Peripheral Arterial Tonometry Contributed to the Development of Coronary Spastic Angina in a 10-Year-Old Boy 一例反应性充血-外周动脉张力计检测血管内皮功能障碍导致10岁男孩冠状动脉痉挛性心绞痛

Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery Pub Date : 2021-11-01 DOI: 10.9794/jspccs.37.220

S. Ikeda, Taku Ishii, Susumu Hosokawa, Tomohiro Nomura, Ayako Nagashima, Tomohiro Watanabe, Shozaburo Doi

引用次数: 1

Message to Next Generation 给下一代的信息

Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery Pub Date : 2021-11-01 DOI: 10.9794/jspccs.37.251

Y. Oshima

{"title":"Message to Next Generation","authors":"Y. Oshima","doi":"10.9794/jspccs.37.251","DOIUrl":"https://doi.org/10.9794/jspccs.37.251","url":null,"abstract":"2. 模倣から独創へ新たな術式のイメージ化 a. DKS吻合 DKS吻合は当初,上行大動脈をドアオープンにして,肺動脈断端と吻合する方法が行われていました.大動脈が前方の症例に対する DKSの第 1助手をしていた時,大動脈の後方を切開するイメージが描けませんでした.この際,両血管を離断すれば,視野も良く,前後での側々吻合の後,大動脈遠位端を後方に吻合,前方にパッチを補填することを思いつき,術者に提言,採用されました.これは,新しい方法だと喜び勇んで文献を調べると,既に報告済みでした.この術式は,その後,どのタイプにも応用できる,最も一般的な術式となりました. とても悔しい思いをしましたが,勉強不足と反省し,以後,症例報告やHow toを熱心に読むようにしました.助手の時代に,術者の立場を想定して手術を俯瞰してみると色々なアイデアが浮かんできます. b. Slide PA plasty, PA translocation 分岐角度が比較的急な左 PAのパッチ形成は,屈曲した形態になることが多く,悩ましいものでした.右の BTシャント後に左開胸で PA形成する機会があり,弓部形成と同じイメージで,slide plastyを行いました.正中アプローチでも応用し,その後,補填物を用いない形成として,PA本幹を用いた PA形成(PA translocation)へと進みました.EAAも当初,側開胸での報告であり,似通った視野で行ったことが既存術式の応用につながったと思います. c. 大動脈弁弁尖延長メルボルン時代に学んだ,大動脈の弁尖延長は,2001年頃,まだ国内では誰も導入していませんでしたが比較的模倣しやすく,数例に行いました.ただ,成績は思うほど芳しくなく,2尖弁や 1弁のみの形成例でしか,10年以上の再手術回避がありません.Rossまでの姑息術だと教えられましたが,安易に模倣しても,理論的な裏打ちがないと良好な成績は挙げられないことを再認識しました. d. Sutureless法 TAPVRを後方アプローチで修復する方法は,毎回,心房切開が難しく,縫合軸が合っていないためか,術後 PVOを経験し,何とかやさしい方法はないかと模索していました.そのなかで,肺静脈切開部を周囲の心膜に縫合すれば,多少,心房切開の軸がずれても,心膜に縫合すれば,縫合部の捻じれが回避できるのではと想像していました.しかし,縫合が二重となり,心膜と縫合した肺静脈吻合の肉芽形成がないとは言えず,実","PeriodicalId":89701,"journal":{"name":"Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery","volume":"1 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-11-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"41334798","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

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The Road to Pediatric Cardiovascular Surgeon 通往儿科心血管外科医生之路

Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery Pub Date : 2021-08-01 DOI: 10.9794/jspccs.37.159

M. Yamagishi

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