{"title":"The Indication of Genetic Testing for the Children with Long QT Intervals","authors":"G. Izumi","doi":"10.9794/JSPCCS.36.344","DOIUrl":"https://doi.org/10.9794/JSPCCS.36.344","url":null,"abstract":"","PeriodicalId":89701,"journal":{"name":"Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery","volume":"36 1","pages":"344-345"},"PeriodicalIF":0.0,"publicationDate":"2020-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"44860296","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Takuya Nishijima, H. Tatewaki, I. Sakamoto, A. Shiose
{"title":"Cardiac Resynchronization Therapy Pacemaker and Double Valve Replacements Improved Cardiac Function after Physiological Repair in a Patient with Congenitally Corrected Transposition of the Great Arteries","authors":"Takuya Nishijima, H. Tatewaki, I. Sakamoto, A. Shiose","doi":"10.9794/jspccs.36.241","DOIUrl":"https://doi.org/10.9794/jspccs.36.241","url":null,"abstract":"The morphological right ventricle supports systemic circulation following physiological repair of congenitally corrected transposition of the great arteries (ccTGA); however, complications such as failure of the right ventricle, tricuspid valve regurgitation, and arrhythmia can arise in adolescence and adulthood. Here, we report the case of a 26-year-old woman who underwent a 4th surgery after undergoing physiological repair for ccTGA. Previously, she underwent a shunt procedure at the age of 3, ccTGA repair at the age of 10, and replacement of the left ventricle to the pulmonary artery conduit when she was 20 years old. In recent years, she was frequently hospitalized due to acute heart failure and atrial tachyarrhythmia. After further examination, we performed aortic and tricuspid valve replacement, and upgraded her cardiac resynchronization therapy pacemaker (CRT-P). Her post-operative course was uneventful, although she was administered catecholamine for an extended duration. Electrocardiogram revealed a decreased duration of QRS from 204 ms to 112 ms, following the CRT-P upgrade, and her brain natriuretic peptide level also markedly improved. She is doing well 2 years and 9 months after the surgeries.","PeriodicalId":89701,"journal":{"name":"Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery","volume":" ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2020-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49451544","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Hikoro Matsui, H. Ota, Kaname Uchida, Kenichiro Hayashi, R. Inuzuka
{"title":"Issue of Specialist Registration for Intensive and Critical Care in Pediatric Cardiology in Japan","authors":"Hikoro Matsui, H. Ota, Kaname Uchida, Kenichiro Hayashi, R. Inuzuka","doi":"10.9794/jspccs.36.232","DOIUrl":"https://doi.org/10.9794/jspccs.36.232","url":null,"abstract":"Background: Role of specialist of pediatric critical care is signi cant, especially for management of congenital heart diseases because most critical cardiac patients have been cared by pediatric cardiologists or cardiovascular surgeons in Japan. Objects: To clarify future issues in the eld of critical care in pediatric cardiology by investigating current situation of board certi cation and medical insurance in Japan. Methods: In this study, we investigated relationship between board certi cation and situation of training centers for the board-certi ed intensivist with pediatric cardiologists, pediatric cardiac surgeons and pediatricians in Japan from databases of o cial registration in the website. Results: Only 0.6% of board-certi ed pediatricians and 1.1% of board-certi ed pediatric cardiologists obtained board-certi ed intensivist. Certi cation of training center is 56% in all pediatric cardiac hospitals and their training systems is not appropriate for pediatricians because of lack of pediatric intensive care units especially in most university hospitals or general hospitals. ere is a gap between cities and regional area in the number of board-certi ed pediatricians with board certi ed intensivists. Conclusions: Signi cant gaps of board certi cation and medical insurance are recognized among regional areas in Japan requiring improvement of system and current situation in the eld of critical care of pediatric cardiology.","PeriodicalId":89701,"journal":{"name":"Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery","volume":" ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2020-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"46706855","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Issues around Pediatric Cardiology and Critical Care Medicine in Japan, from Intensivist’s Perspective","authors":"M. Osaki","doi":"10.9794/jspccs.36.239","DOIUrl":"https://doi.org/10.9794/jspccs.36.239","url":null,"abstract":"","PeriodicalId":89701,"journal":{"name":"Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery","volume":"104 2","pages":"239-240"},"PeriodicalIF":0.0,"publicationDate":"2020-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"41288696","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Treatment Strategy for Severe Systemic Right Ventricular Failure in Patients with Congenitally Corrected Transposition of the Great Arteries","authors":"H. Ozawa","doi":"10.9794/jspccs.36.249","DOIUrl":"https://doi.org/10.9794/jspccs.36.249","url":null,"abstract":"","PeriodicalId":89701,"journal":{"name":"Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery","volume":"36 1","pages":"249-251"},"PeriodicalIF":0.0,"publicationDate":"2020-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"46082800","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
A. Shishido, T. Hasegawa, Naoya Kamei, Ken Hayashi, Hironori Matsuhisa, Y. Oshima, Toshikatsu Tanaka
{"title":"Symptomatic Portosystemic Shunt via the Unligated Vertical Vein Following Repair of a Mixed-Type Total Anomalous Pulmonary Venous Connection: A Case Report","authors":"A. Shishido, T. Hasegawa, Naoya Kamei, Ken Hayashi, Hironori Matsuhisa, Y. Oshima, Toshikatsu Tanaka","doi":"10.9794/jspccs.36.263","DOIUrl":"https://doi.org/10.9794/jspccs.36.263","url":null,"abstract":"Mixed-type total anomalous pulmonary venous connection (TAPVC) with univentricular circulation has a wide variation of pulmonary venous anatomy and drainage. Surgical intervention for mixed-type TAPVC, including management of the vertical vein, remains controversial. Herein, we report a rare case of symptomatic portosystemic shunt via the unligated vertical vein following repair of the mixed-type TAPVC. An 18-day-old male neonate with a mixed-type TAPVC and asplenia underwent surgical repair of the TAPVC. e right vertical vein draining to the superior vena cava, and the le vertical vein draining to the portal vein were le patent. Elevated liver enzymes, coagulation abnormalities, hyperammonemia, and hypoglycemia were detected following surgery. Echocardiography revealed a portosystemic shunt draining from the portal vein to the le -sided atrium via the le unligated vertical vein. Elevated atrial pressure was detected on cardiac catheterization, and as a result, we performed banding of the le unligated vertical vein. is case highlights the need to discuss the portosystemic shunt as a postoperative complications in mixed-type TAPVC with univentricular circulation when considering both the surgical procedure and postoperative management.","PeriodicalId":89701,"journal":{"name":"Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery","volume":"36 1","pages":"263-268"},"PeriodicalIF":0.0,"publicationDate":"2020-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"43803902","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Hemodynamic Analysis-Based Therapeutic Intervention for Circulatory Failure in Pediatric Patients","authors":"Hirofumi Saiki","doi":"10.9794/jspccs.36.192","DOIUrl":"https://doi.org/10.9794/jspccs.36.192","url":null,"abstract":"Circulatory failure is a life threating condition for which every pediatric cardiologist should be prepared to perform physiological analyses, make optimal therapeutic decisions, and secure the best outcome. The correct approach for determining the cause of circulatory failure can accelerate the patients ʼ recovery from a critical condition, as well as mitigate in allowing their outcome, whereas patients can rapidly deteriorate if their management is inadequate. The integrated concept of cardio-vascular interactions, the pressure-volume relationship, is not novel, but it is vital in allowing clinicians to understand the underlying physiology of circulatory failure. Furthermore, the pressure-volume relationship has the advantage of describing both cardiac function and its loading condition in the same dimension. Accordingly, the pressure-volume relationship can help clinicians to determine the best available therapeutic intervention. This review aimes to convey the initial steps involved in assessing hemodynamic issues in children with circulatory failure.","PeriodicalId":89701,"journal":{"name":"Nihon Shoni Junkanki Gakkai zasshi = Pediatric cardiology and cardiac surgery","volume":" ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2020-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"48991514","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}