{"title":"Progressive neurological deterioration in a 14-year-old girl.","authors":"P H Berman, G S Davidson, L E Becker","doi":"10.1159/000120361","DOIUrl":"https://doi.org/10.1159/000120361","url":null,"abstract":"","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 1","pages":"42-9"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120361","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14196238","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Diastematomyelia--a 40-year experience.","authors":"D J Gower, O Del Curling, D L Kelly, E Alexander","doi":"10.1159/000120369","DOIUrl":"https://doi.org/10.1159/000120369","url":null,"abstract":"<p><p>Diastematomyelia is a rare but potentially devastating spinal dysraphism classically characterized as a bony or fibrous spur separating two hemispinal cords. This study reviews our experience with diastematomyelia over a 40-year period from 1947 through 1987, and suggests that the neurologic and orthopedic deficits of diastematomyelia remain stable during extended follow-up after surgery.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 2","pages":"90-6"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120369","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14380282","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"A technique for removal of an adherent ventricular catheter.","authors":"I Chambi, E B Hendrick","doi":"10.1159/000120392","DOIUrl":"https://doi.org/10.1159/000120392","url":null,"abstract":"<p><p>A method of freeing the attachment of the intraventricular catheter to the ventricular ependyma or chorioid plexus is described. A metal ventricular cannula is inserted into the lumen of the ventricular catheter and a cutting current from a unipolar diathermy is applied to the distal end. The cutting effect at the interventricular end of the metal cannula effectively lyses the adhesions and permits safe removal of the ventricular catheter without subsequent bleeding.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 4","pages":"216-7"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120392","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14399755","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Spinal cord injury in I-cell disease.","authors":"M L Goodman, D Pang","doi":"10.1159/000120411","DOIUrl":"https://doi.org/10.1159/000120411","url":null,"abstract":"<p><p>I-cell disease (ICD), mucolipidosis II, is an autosomal recessive syndrome resulting from defective phosphorylation of acid hydrolases. The diagnosis is made in early childhood and in most cases death occurs by age 5 as a result of cardiorespiratory complications. Pathologic changes are limited to mesenchymal tissues. We treated two children with ICD who developed atlantoaxial dislocation and myelopathy following minor injuries. The first child developed cardiovascular instability with manipulation of the C1 ring at operation, necessitating removal of the arch of C1 and fusion from occiput to C2. The second child was quadriplegic following anatomic reduction of the C1-C2 dislocation at operation during which somatosensory evoked potentials (SSEPs) showed no deleterious change. The atlantoaxial joint is unstable in ICD due to an incompetent transverse ligament infiltrated by storage cells. A cartilaginous, rather than calcified, odontoid process may contribute to the instability. The intraoperative neural injury occurred during attempts to effect anatomical reduction of the chronically dislocated C1-C2 joints and could have resulted from inadvertent trauma to the vertebral arteries and subsequent infarction of the cord. The lack of change in the intraoperative SSEPs was probably due to relative sparing of the posterior columns during the cord injury. We recommend that children with ICD and atlantoaxial instability undergo closed reduction of any existing malalignment followed by posterior C1-C2 fusion as long as the operative risk is not prohibitive. If preoperative closed reduction is not readily feasible and the cord is severely compromised, the C1 arch should be removed and the occiput fused to C2. Forceful attempts at anatomical reduction of the chronically dislocated C1-C2 segments should be avoided.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 6","pages":"315-8"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120411","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14397560","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Benign ependymomas of the posterior fossa in childhood.","authors":"T Tomita, D G McLone, L Das, W N Brand","doi":"10.1159/000120405","DOIUrl":"https://doi.org/10.1159/000120405","url":null,"abstract":"<p><p>A series of 22 infants and children with posterior fossa benign ependymomas treated surgically during the past 12 years is presented. All patients were operated on with posterior fossa craniotomy: visible total resection in 10, subtotal resection in 9, partial resection in 2 and biopsy only in 1. One patient (4.5%) died shortly after surgery. Only 5 patients had documented infiltration of the floor of the fourth ventricle. Postoperative radiotherapy was administered with variable radiation fields and doses. Two out of six patients who had total resection and postoperative radiation therapy did not show recurrence during at least 26 months follow-up period. However, patients with incomplete tumor resection almost invariably developed recurrence. An attempt should be made to remove posterior fossa ependymomas totally at the initial craniotomy. The risk periods for recurrence were between 1 and 2 years after subtotal resection and between 2 and 3 years after total resection. In our experience, gross recurrent tumors appear to be resistant to chemotherapy, and a combination of surgery and radiation therapy does not necessarily prevent recurrence. Newer agents or protocols of adjuvant chemotherapy are needed to explore.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 6","pages":"277-85"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120405","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14399081","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Neuronal migration abnormalities can still be diagnosed by computed tomography!","authors":"A R Buckley, O Flodmark, E H Roland, A Hill","doi":"10.1159/000120394","DOIUrl":"https://doi.org/10.1159/000120394","url":null,"abstract":"<p><p>Magnetic resonance imaging is presently the best modality for evaluating gray/white matter anatomy. However, this modality is expensive and not yet readily available in all countries. Most neuronal migration abnormalities can be accurately diagnosed by computed tomography (CT) provided excellent scanning technique is used. Abnormalities of neuronal migration were identified with CT brain scans in 68 children and were categorized as focal heterotopias (11 patients), multifocal heterotopias (19 patients) of diffuse migration disorders (38 patients). The principal indications for imaging were correlated to the radiological features. Neuropathological confirmation of the migration abnormality was obtained in 8 patients. An increased awareness by both clinicians and radiologists together with optimal CT technique are essential for the accurate diagnosis of migration disorders in children.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 5","pages":"222-9"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120394","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14396289","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Gait analysis of cerebral palsy children before and after rhizotomy.","authors":"C L Vaughan, B Berman, L A Staudt, W J Peacock","doi":"10.1159/000120408","DOIUrl":"https://doi.org/10.1159/000120408","url":null,"abstract":"<p><p>Over the past decade, selective posterior rhizotomy has been used successfully to reduce spasticity in patients with cerebral palsy. Although clinical evaluation of these patients revealed functional improvement following surgery, more objective analysis of the outcome of this surgery was sought. Kinematic gait analysis of 14 patients with spastic cerebral palsy was performed before and after selective posterior rhizotomy. Measurements of stride length, thigh range of motion, knee range of motion, average speed of walking, and cadence were made. Statistically significant increases in stride length, thigh range and knee range were found. Average speed was increased and cadence was virtually unchanged. These results corroborate clinical findings of improvement in gait of spastic patients with cerebral palsy following selective posterior rhizotomy.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 6","pages":"297-300"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120408","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14397557","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Neonatal cerebral venous thrombosis.","authors":"W C Hanigan, P T Tracy, W S Tadros, R M Wright","doi":"10.1159/000120385","DOIUrl":"https://doi.org/10.1159/000120385","url":null,"abstract":"<p><p>Five cases of neonatal cerebral venous thrombosis (NCVT) diagnosed by magnetic resonance imaging (MRI) are presented in this report. MRI was specific for the anatomic diagnosis, demonstrating involvement of the superior sagittal sinus in 3 infants or deep venous system in the remaining 2. Four cases were associated with perinatal hypoxia or cranial trauma. Three of these children show significant developmental delays. The increased use of MRI may add significant information on the association of cerebral venous thrombosis with the common systemic illnesses of newborns.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 4","pages":"177-83"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120385","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14396022","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
W C Olivero, H L Rekate, H J Chizeck, W Ko, J M McCormick
{"title":"Relationship between intracranial and sagittal sinus pressure in normal and hydrocephalic dogs.","authors":"W C Olivero, H L Rekate, H J Chizeck, W Ko, J M McCormick","doi":"10.1159/000120388","DOIUrl":"https://doi.org/10.1159/000120388","url":null,"abstract":"<p><p>The relationship between intracranial and sagittal sinus pressure in normal and kaolin-induced hydrocephalic greyhounds was examined. In normal dogs there was an average 14 mm Hg pressure difference between the ventricles and the sagittal sinus. Elevations of intraventricular pressure were accompanied by small but consistent elevations in sagittal sinus pressure. In hydrocephalic dogs the average pressure differential was only 2 mm Hg. Also elevations of intraventricular pressure were accompanied by greater elevations in sagittal sinus pressures than those seen in normal dogs. The volume-buffering capacity of the sagittal sinus was decreased, and sinography revealed filling of unusual venous collaterals in hydrocephalic dogs--both suggesting an increased resistance to outflow in the sagittal sinus.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 4","pages":"196-201"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120388","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14399749","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}