{"title":"Radiation exposure to the ocular lens during CT scanning.","authors":"B B Storrs, S E Byrd","doi":"10.1159/000120399","DOIUrl":"https://doi.org/10.1159/000120399","url":null,"abstract":"<p><p>Measurements of radiation exposure during routine CT scanning were found to average 4.2 R at the level of the ocular lens. This data was combined with CT scanning rate data from a sample of 100 patients followed in the myelomeningocele clinic. The number of scans averaged 7.75/patient with a range of 0-34 scans. Cumulative radiation exposure to date ranged from 0 to 143 R. Radiation dosage nomenclature and acceptable limits are discussed and recommendations for reduction of dosage are presented.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 5","pages":"254-7"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120399","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14394202","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Management of craniopharyngiomas in children.","authors":"T Tomita","doi":"10.1159/000120390","DOIUrl":"https://doi.org/10.1159/000120390","url":null,"abstract":"<p><p>Craniopharyngiomas are histologically benign neoplasms occurring in the intra- and suprasellar region. Their location and close relation with visual pathways, hypothalamus and major basal vessels may cause difficulty in resecting these tumors without surgical complications. Radiotherapy after limited resection of craniopharyngiomas has been advocated by some investigators while others contend radical resections by means of advanced surgical techniques afford better outcome of patients. Although optimal treatment is yet to be defined, the review of our institutional experience and the critical analysis of the literature show that radiation therapy may be effective but not curative. It is recommended that surgeons should make every effort to effect total excision at the initial operation.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 4","pages":"204-11"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120390","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14209819","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Role of magnetic resonance imaging and three-dimensional computerized tomography in craniovertebral junction anomalies.","authors":"C T Pappas, H L Rekate","doi":"10.1159/000120357","DOIUrl":"https://doi.org/10.1159/000120357","url":null,"abstract":"<p><p>The surgical management of craniovertebral junction abnormalities depends on accurate radiological identification of the static and dynamic relationships. Four cases are presented to show the importance of flexion/extension magnetic resonance imaging and three-dimensional computerized tomography scanning in the evaluation of these relationships. With these techniques, anterior and/or posterior decompressive procedures can be appropriately planned to reduce and stabilize craniovertebral abnormalities. Long-term neural deficits can be reversed by these procedures.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 1","pages":"18-22"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120357","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14346226","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Heterogeneity of nemaline myopathy. A follow-up study of 13 cases.","authors":"E Shahar, R C Tervo, E G Murphy","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>The marked heterogeneity of nemaline myopathy is again shown in the present series of 13 patients. Most children have a long-standing, mild, and slowly progressing proximal myopathy. Two brothers with extreme weakness died during the neonatal period of respiratory failure representing the X-linked variant. One adult with proximal weakness was also diagnosed as having nemaline myopathy. An unusual course was observed in 2 infants who initially had moderate weakness but subsequently developed severe generalized weakness including respiratory muscles. This led to irreversible respiratory failure requiring continuous ventilatory support for as long as 9 and 15 years, respectively. Although uncommon, the possibility of an imminent respiratory failure in initially weak infants should also be taken into account within the clinical spectrum of nemaline myopathy.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 5","pages":"236-40"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14394201","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Use of the 'H' reflex recovery curve in selective posterior rhizotomy.","authors":"B B Storrs, T Nishida","doi":"10.1159/000120376","DOIUrl":"https://doi.org/10.1159/000120376","url":null,"abstract":"<p><p>Selective posterior rhizotomy is a safe and effective treatment in carefully selected patients. It produces objective and lasting changes in muscle tone and function without serious sensory complications. The 'H' reflex recovery curve technique allows objective evaluation of sensory rootlets and a physiologic rationale for the selection of abnormal rootlets. In 95 patients this technique has provided good results without significant sensory compromise.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 3","pages":"120-3"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120376","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14381111","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Temporal-lobe abnormalities in thanatophoric dysplasia.","authors":"A S Knisely, M W Ambler","doi":"10.1159/000120384","DOIUrl":"https://doi.org/10.1159/000120384","url":null,"abstract":"<p><p>We identified distinctive and characteristic abnormalities in the hippocampal formations of 4 individuals with thanatophoric dysplasia (TD), one of whom was a fetus of 19 weeks gestational age. Primitive medial fissures in this subject could be identified, but development of the dentate gyrus and organization of the pyramidal layer in the hippocampal formation were abnormal. We infer that temporal-lobe dysmorphogenesis in TD begins between 11.5 weeks gestational age, when hippocampal and fimbriodentate fissure formation takes place, and 13.5 weeks gestational age, when differential proliferation and migration of the cells that form the pyramidal layer and the dentate gyrus takes place. Any etiology proposed for TD must not only account for disordered endochondral and endomembranous bone formation but also explain the origins of early temporal-lobe dysplasia.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 4","pages":"169-76"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120384","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14396020","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Sylvian fissure meningioma in a child: case report and review of the literature.","authors":"D Silbergeld, M Berger, B Griffin","doi":"10.1159/000120362","DOIUrl":"https://doi.org/10.1159/000120362","url":null,"abstract":"<p><p>A case report of a Sylvian fissure meningioma in a 4-year-old female is presented. Childhood meningiomas are discussed, and the literature is reviewed with respect to the location of the lesion in the Sylvian fissure. The role of radiotherapy following subtotal resection of meningiomas is also described.</p>","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 1","pages":"50-3"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120362","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14347114","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Edward J. Zampella, Patricia A. Aronin, G. T. Odrezin, Ernest R. Duvall
{"title":"Conservative management of thrombosed vein of Galen malformations. Report of two cases and a review of the literature.","authors":"Edward J. Zampella, Patricia A. Aronin, G. T. Odrezin, Ernest R. Duvall","doi":"10.1159/000120402","DOIUrl":"https://doi.org/10.1159/000120402","url":null,"abstract":"Spontaneously thrombosed vein of Galen malformations are rare congenital vascular malformations. Surgical treatment of these lesions based on experience with the management of patent malformations has yielded less than satisfactory results. This report reviews the literature concerning these lesions and details our experience with nonoperative management in 2 patients.","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 5 1","pages":"264-71"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120402","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"64570927","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Dementia, rigidity and seizures in an adolescent boy.","authors":"I J Butler, E Rouah, P Pearl","doi":"10.1159/000120410","DOIUrl":"https://doi.org/10.1159/000120410","url":null,"abstract":"","PeriodicalId":77766,"journal":{"name":"Pediatric neuroscience","volume":"14 6","pages":"307-14"},"PeriodicalIF":0.0,"publicationDate":"1988-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1159/000120410","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14397559","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}