Acta paediatrica Scandinavica最新文献_第7页

Children with craniopharyngioma. Early growth failure and rapid postoperative weight gain. 儿童颅咽管瘤。早期生长衰竭和术后体重迅速增加。

Acta paediatrica Scandinavica Pub Date : 1988-07-01 DOI: 10.1111/j.1651-2227.1988.tb10705.x

R Sorva

{"title":"Children with craniopharyngioma. Early growth failure and rapid postoperative weight gain.","authors":"R Sorva","doi":"10.1111/j.1651-2227.1988.tb10705.x","DOIUrl":"https://doi.org/10.1111/j.1651-2227.1988.tb10705.x","url":null,"abstract":"Pre- and postoperative growth was analyzed in 22 children with craniopharyngioma. In 19 children a growth failure preceded the diagnosis by a mean of 4 years. Six children were obese preoperatively. During the first 3 postoperative months relative weight increased greater than 10% in 14/21 children (there was one surgical death). One year after surgery 13/21 were obese. Neither the size of the tumor nor the mode of surgery was decisive in the development of the obesity. Serum insulin and insulin-like growth factor I (IGF-I) were assessed in four children with growth hormone deficiency (GHD) who, after surgery for craniopharyngioma, were growing normally without GH substitution. One of them was normal in weight and had normal insulin and IGF-I levels; the others were obese and had supranormal insulin and subnormal IGF-I levels. One of the four and two other children with unsubstituted GHD reached final height SDS -0.8, -2.0 and -2.4. One child with normal postoperative GH response reached final height SDS -0.7. Final height SDS greater than or equal to -2.5 was gained with GH substitution by 6/11 children. It was greater than 2.0 SD below the height SDS expected from the heights of the parents in 7/11. An adequate monitoring of children's growth would lead to earlier diagnosis and probably better outcome.","PeriodicalId":75407,"journal":{"name":"Acta paediatrica Scandinavica","volume":"77 4","pages":"587-92"},"PeriodicalIF":0.0,"publicationDate":"1988-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1111/j.1651-2227.1988.tb10705.x","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14519733","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 72

Increased IgG2 and IgG3 concentration is associated with advanced Pseudomonas aeruginosa infection and poor pulmonary function in cystic fibrosis. IgG2和IgG3浓度升高与囊性纤维化患者晚期铜绿假单胞菌感染和肺功能不良有关。

Acta paediatrica Scandinavica Pub Date : 1988-07-01 DOI: 10.1111/j.1651-2227.1988.tb10703.x

T Pressler, B Mansa, T Jensen, S S Pedersen, N Høiby, C Koch

{"title":"Increased IgG2 and IgG3 concentration is associated with advanced Pseudomonas aeruginosa infection and poor pulmonary function in cystic fibrosis.","authors":"T Pressler, B Mansa, T Jensen, S S Pedersen, N Høiby, C Koch","doi":"10.1111/j.1651-2227.1988.tb10703.x","DOIUrl":"https://doi.org/10.1111/j.1651-2227.1988.tb10703.x","url":null,"abstract":"The concentrations of IgG subclass immunoglobulins were determined by radial immunodiffusion in serum from 126 patients with cystic fibrosis (CF). The results were compared to values from age-matched healthy children and adults and correlated to patients age, duration of chronic Pseudomonas aeruginosa infection and lung function parameters. Fifty-two percent of the patients had an elevated concentration of at least one of the IgG subclasses; IgG1 28%, IgG2 16%, IgG3 18% and IgG4 48%. There was significant correlation between elevated serum levels of IgG2, and to a lesser extent IgG3, with decreased lung function (for FEV1; p = 0.0001, and p = 0.001 respectively) and high levels of antipseudomonas precipitins (p = 0.008, and p = 0.002). A similar correlation was not found for IgG1 and IgG4. IgG subclasses vary in their ability to promote phagocytosis and to activate complement and it is possible that individual differences in the IgG subclass pattern could explain the variable course of this disease.","PeriodicalId":75407,"journal":{"name":"Acta paediatrica Scandinavica","volume":"77 4","pages":"576-82"},"PeriodicalIF":0.0,"publicationDate":"1988-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1111/j.1651-2227.1988.tb10703.x","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14266575","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 41

Growth, growth hormone and sex steroid secretion in girls with central precocious puberty treated with a gonadotrophin releasing hormone (GnRH) analogue. 促性腺激素释放激素(GnRH)类似物治疗中枢性性早熟女孩的生长、生长激素和性类固醇分泌

Acta paediatrica Scandinavica Pub Date : 1988-07-01 DOI: 10.1111/j.1651-2227.1988.tb10694.x

R Stanhope, P J Pringle, C G Brook

引用次数: 52

Haemolytic uraemic syndrome associated with Salmonella dysentery. 与沙门氏菌痢疾相关的溶血性尿毒综合征。

Acta paediatrica Scandinavica Pub Date : 1988-07-01 DOI: 10.1111/j.1651-2227.1988.tb10711.x

V Khoshoo, A Moudgil, A S Vasudev, M K Bhan, R N Srivastava

引用次数: 5

In vitro hydrolysis with a beta-galactosidase for treatment of intolerance to human milk in very low birthweight infants. 用β -半乳糖苷酶体外水解治疗极低出生体重婴儿对母乳不耐受。

Acta paediatrica Scandinavica Pub Date : 1988-07-01 DOI: 10.1111/j.1651-2227.1988.tb10709.x

F Chew, J Villar, N W Solomons, R Figueroa

引用次数: 3

Compliance with a dietary manipulation programme in families with infants prone to atopy. 易发生特应性反应的婴儿家庭对饮食控制方案的依从性。

Acta paediatrica Scandinavica Pub Date : 1988-07-01 DOI: 10.1111/j.1651-2227.1988.tb10701.x

L Pöysä, K Remes, M Korppi, K Launiala

{"title":"Compliance with a dietary manipulation programme in families with infants prone to atopy.","authors":"L Pöysä, K Remes, M Korppi, K Launiala","doi":"10.1111/j.1651-2227.1988.tb10701.x","DOIUrl":"https://doi.org/10.1111/j.1651-2227.1988.tb10701.x","url":null,"abstract":"The success of familial compliance with a dietary manipulation programme was studied prospectively in 91 newborn babies from atopic families for up to 12 months. The control group consisted of 72 infants from non-atopic families. The percentages of infants breast-fed at the age of six months were 58% and 38% in the study group and control group, respectively. The introduction of cow's milk based formulas was postponed until the age of three months in 63% of the infants in the study group and 47% of the infants in the control group. Solid food was avoided during the first three months in 76% and 45% of the infants in the study group and control group, respectively. Maternal age, smoking and low social class were associated with poor compliance. The existence of atopic dermatitis in any member of the family was associated with good compliance. The main advantages of our programme were the increased number of children breast-fed until the age of six months, and the reduced number of infants introduced to cow's milk based formulas or solid food before three months of age.","PeriodicalId":75407,"journal":{"name":"Acta paediatrica Scandinavica","volume":"77 4","pages":"563-8"},"PeriodicalIF":0.0,"publicationDate":"1988-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1111/j.1651-2227.1988.tb10701.x","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14519751","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 22

Partial splenic embolization in hypersplenism. 脾功能亢进的部分脾栓塞。

Acta paediatrica Scandinavica Pub Date : 1988-07-01 DOI: 10.1111/j.1651-2227.1988.tb10706.x

J Vazquez Estévez, L Lassaletta, A Perez-Higueras, J Utrilla, J A Diez-Pardo

引用次数: 4

Efficacy of beclomethasone nasal drops, administered in the Moffat's position for nasal polyposis. 倍氯米松滴鼻液在莫法特体位治疗鼻息肉病的疗效。

Acta paediatrica Scandinavica Pub Date : 1988-07-01 DOI: 10.1111/j.1651-2227.1988.tb10715.x

M Canciani, G Mastella

引用次数: 11

Heparin cofactor II, antithrombin and protein C in plasma from term and preterm infants. 足月和早产儿血浆中肝素辅助因子II、抗凝血酶和蛋白C的含量。

Acta paediatrica Scandinavica Pub Date : 1988-07-01 DOI: 10.1111/j.1651-2227.1988.tb10688.x

T R Andersson, H Bangstad, M L Larsen

引用次数: 12

High stature in neonatal myotubular myopathy. 新生儿肌管性肌病的高身高。

Acta paediatrica Scandinavica Pub Date : 1988-07-01 DOI: 10.1111/j.1651-2227.1988.tb10714.x

J C LeGuennec, J P Bernier, J Lamarche

{"title":"High stature in neonatal myotubular myopathy.","authors":"J C LeGuennec, J P Bernier, J Lamarche","doi":"10.1111/j.1651-2227.1988.tb10714.x","DOIUrl":"https://doi.org/10.1111/j.1651-2227.1988.tb10714.x","url":null,"abstract":"A male baby was delivered at 40 weeks of gestation. His birthweight was 3300 g (50th percentile) and length 57 cm (over the 97th percentile). Parents measured 1.70 m and 1.83 m, respectively. The mother later gave birth to two healthy infants, a boy and a girl who measured 53 cm and 47 cm and weighed 3800 g and 2700 g at 40 weeks and 39 weeks of gestation, respectively. In our patients the chest X-ray at birth showed the characteristic thin ribs (Fig. 1). A diagnosis of neuromuscular disease was rapidly made on the basis of persistent generalized hypotonia, muscle atrophy, and feeble respiratory efforts. Muscle biopsies taken from the biceps on the 8th day revealed the characteristic features of myotubular myopathy with predominance of type I fibres and persistence of fetal myotubes in a large proportion of the muscle fibers (Fig. 2). The baby died at 2 months of age from respiratory insufficiency. His mother was clinically normal and her muscle biopsy did not show any abnormality. Because of the high stature observed in this patient, previously published cases of neonatal myotubular myopathy were reviewed and birth length parameters were plotted on Lubchenco growth curves. Only in 6 previously reported cases (14) the height had been recorded. In four of the 6 infants the height was over the 90th percentile, and all had a decreased weight for height (Fig. 3).","PeriodicalId":75407,"journal":{"name":"Acta paediatrica Scandinavica","volume":"77 4","pages":"610-1"},"PeriodicalIF":0.0,"publicationDate":"1988-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1111/j.1651-2227.1988.tb10714.x","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"14519739","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 10