International journal of cardiology. Congenital heart disease最新文献_第9页

QRS fragmentation versus QRS prolongation in predicting right ventricular enlargement and dysfunction in children and adults with repaired Tetralogy of Fallot QRS碎裂与QRS延长预测法洛四联症修复儿童和成人右心室增大和功能障碍

International journal of cardiology. Congenital heart disease Pub Date : 2023-09-01 DOI: 10.1016/j.ijcchd.2022.100408

Stephanie Gaydos , Anthony Hlavacek , Susan Evenhouse , Jacob Strelow , Shahryar Chowdhury , Lanier Jackson

{"title":"QRS fragmentation versus QRS prolongation in predicting right ventricular enlargement and dysfunction in children and adults with repaired Tetralogy of Fallot","authors":"Stephanie Gaydos , Anthony Hlavacek , Susan Evenhouse , Jacob Strelow , Shahryar Chowdhury , Lanier Jackson","doi":"10.1016/j.ijcchd.2022.100408","DOIUrl":"10.1016/j.ijcchd.2022.100408","url":null,"abstract":"<div><p>Patients with repaired Tetralogy of Fallot (rTOF) have risks of late life-threatening sequelae, including right ventricular (RV) dilation and failure, arrhythmias, and sudden death. QRS prolongation is a well-known ECG predictor of these outcomes but has poor sensitivity for mortality. Growing evidence demonstrates QRS fragmentation (fQRS) as a better prognostic marker for mortality in adults with rTOF, though the two markers have not been directly compared as correlates for CMR abnormalities. Additionally, fQRS has never been studied in pediatric TOF. This single institution retrospectively reviewed 138 CMRs in rTOF patients (median age 21.7 years) who had a corresponding 12-lead ECG within 1 year. fQRS was defined as ≥3 R-waves/notches in the R/S complex (>2 in right bundle branch block) in ≥2 contiguous leads. QRS prolongation was defined as QRS ≥160 ms. Nearly half (46%) the sample had fQRS (42.1% of pediatric subgroup), and 26% had QRS prolongation. Both markers were significantly associated with reduced RV ejection fraction (EF%) (p < 0.01) and larger RV end-diastolic volumes (p < 0.01). QRS prolongation alone predicted lower LV EF% (p = 0.02). Regression analyses showed both QRS prolongation (p < 0.01) and fQRS (p < 0.01) independently associated with reduced RV EF%; QRS prolongation alone predicted RV dilation (p < 0.01). We concluded that both QRS prolongation and fQRS are equivalent as significant markers of RV dysfunction in rTOF patients. QRS prolongation may be a better surrogate for RV dilation specifically. fQRS was frequently seen in children with rTOF and was significantly associated with similar late structural sequelae.</p></div>","PeriodicalId":73429,"journal":{"name":"International journal of cardiology. Congenital heart disease","volume":"13 ","pages":"Article 100408"},"PeriodicalIF":0.0,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"45776258","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 2

Gynaecological health in adult congenital heart disease women: Addressing menorrhagia, infertility, contraception, menopause 成年先天性心脏病妇女的妇科健康：解决月经过多、不孕、避孕、更年期

International journal of cardiology. Congenital heart disease Pub Date : 2023-09-01 DOI: 10.1016/j.ijcchd.2023.100470

Gurleen Wander, Mark R. Johnson, Roshni R. Patel

{"title":"Gynaecological health in adult congenital heart disease women: Addressing menorrhagia, infertility, contraception, menopause","authors":"Gurleen Wander, Mark R. Johnson, Roshni R. Patel","doi":"10.1016/j.ijcchd.2023.100470","DOIUrl":"10.1016/j.ijcchd.2023.100470","url":null,"abstract":"<div><p>Developments in medical and surgical techniques have improved survival in women with congenital heart disease (CHD) with most now surviving well into adulthood. Reproductive health amongst these women is underexplored and needs more attention. Women with CHD are known to have more menstrual dysfunction than the general population and have higher maternal and fetal risks when they become pregnant. Adequate and timely preconception counselling, including contraception within a multidisciplinary team (MDT) are essential to optimise pre pregnancy cardiac status and improve pregnancy outcomes. Counselling regarding fertility, sexuality, contraception and menopause is necessary and should start early, around 12–13 years, and as they transition into adult services. Fertility seems to be reduced in women with complex CHD and consideration for assisted reproduction technique (ART) should be assessed by the MDT as risks associated with ART including ovarian hyperstimulation syndrome, bleeding, thrombosis and infection can have profound effects on women with complex cyanotic CHD.</p></div>","PeriodicalId":73429,"journal":{"name":"International journal of cardiology. Congenital heart disease","volume":"13 ","pages":"Article 100470"},"PeriodicalIF":0.0,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"46861264","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 1

Thyroid dysfunction in pediatric Fontan patients is associated with unfavorable hemodynamic status and severity of protein-losing enteropathy: A report from the Fontan care network 儿童Fontan患者的甲状腺功能障碍与不良的血液动力学状态和蛋白质丢失肠病的严重程度有关：Fontan护理网络的一份报告

International journal of cardiology. Congenital heart disease Pub Date : 2023-09-01 DOI: 10.1016/j.ijcchd.2023.100475

Joszi Sweer , Ingo Germund , Markus Khalil , Christian Apitz , Kim ten Dam , Stefanie Wendt , Narayanswami Sreeram , Floris E.A. Udink ten Cate , Fontan Care Network

{"title":"Thyroid dysfunction in pediatric Fontan patients is associated with unfavorable hemodynamic status and severity of protein-losing enteropathy: A report from the Fontan care network","authors":"Joszi Sweer , Ingo Germund , Markus Khalil , Christian Apitz , Kim ten Dam , Stefanie Wendt , Narayanswami Sreeram , Floris E.A. Udink ten Cate , Fontan Care Network","doi":"10.1016/j.ijcchd.2023.100475","DOIUrl":"https://doi.org/10.1016/j.ijcchd.2023.100475","url":null,"abstract":"<div><h3>Background</h3><p>Thyroid dysfunction may have adverse effects on Fontan hemodynamics. Data on thyroid function in pediatric Fontan patients with or without protein-losing enteropathy (PLE) are limited.</p></div><div><h3>Methods</h3><p>This retrospective multicenter study included 67 Fontan patients (median age 10.9 years; 35.8% female; 28.4% PLE) in whom thyroid function testing was performed.</p></div><div><h3>Results</h3><p>Subclinical hypothyroidism (SHT) was present in 16 (23.9%) patients. Subjects with SHT had significantly lower systolic blood pressure (p = 0.014) and body weight z-score (p = 0.006), were in a worse New York Heart Association (NYHA) functional class (p = 0.004), were more often pacing dependent (p = 0.007), and were more likely to have PLE (p = 0.033, 8/19 (42.1%) patients). Serum thyroid stimulating hormone (TSH) levels were significantly higher in patients with NYHA class ≥ II (p = 0.005), significant atrioventricular valve regurgitation (p = 0.023), elevated serum natriuretic peptides (p = 0.031), and in those with PLE (p = 0.002). Patients with active PLE had significantly higher TSH levels than those in remission (p = 0.003). A strong inverse relationship was found between lower free triiodothyronine (fT3) levels and natriuretic peptides (r: −0.599, p = 0.040). Using binary logistic regression analysis we found that worse NYHA class was an independent predictor of SHT (OR 4.2; 95% CI 1.1–16.1, p = 0.036).</p></div><div><h3>Conclusions</h3><p>Subclinical thyroid dysfunction is common in Fontan, particularly in patients with hemodynamic derangements and PLE. Future studies are needed to address the prognostic implications of thyroid dysfunction in the Fontan population.</p></div>","PeriodicalId":73429,"journal":{"name":"International journal of cardiology. Congenital heart disease","volume":"13 ","pages":"Article 100475"},"PeriodicalIF":0.0,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49802363","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Palliating the unpalliated adult single ventricle patient – Options and review of literature 缓解未配对的成年单心室患者——选择和文献综述

International journal of cardiology. Congenital heart disease Pub Date : 2023-09-01 DOI: 10.1016/j.ijcchd.2023.100464

Kelsey McLean , Tacy Downing , Anitha John , Pranava Sinha , Seiji Ito

引用次数: 0

Exercise, prescription and training in ACHD ACHD的锻炼、处方和训练

International journal of cardiology. Congenital heart disease Pub Date : 2023-09-01 DOI: 10.1016/j.ijcchd.2023.100467

Guido Pieles , Michael Papadakis , Werner Budts

{"title":"Exercise, prescription and training in ACHD","authors":"Guido Pieles , Michael Papadakis , Werner Budts","doi":"10.1016/j.ijcchd.2023.100467","DOIUrl":"10.1016/j.ijcchd.2023.100467","url":null,"abstract":"<div><p>The number of adult patients with congenital heart disease (CHD) is steadily increasing and exceeds nowadays the number of children with CHD. This is due to significant advances in therapeutic possibilities that became available over the last four decades. As such, this aging population survives the CHD complications and is exposed to the traditional cardiovascular risk factors for atherosclerotic disease such as high blood pressure, elevated cholesterol levels, long-standing exposure to smoking, overweight and obesity, and a sedentary lifestyle. Consequently, it becomes important to put more emphasis on all these risk factors. A preventive strategy is central, and early encouragement of physical activity is part of this approach. A minimum of physical activity has a beneficial effect both physically and mentally. With this overview, we mainly want to emphasize the importance of preventive measures. We would like to emphasize that all individuals should receive an exercise prescription which adheres to the minimum recommendations by WHO/NICE and this advice should form the baseline. Moreover, we intend to show that physical activity can be done safely in patients with CHD and that recreational and competitive sports are feasible in many circumstances.</p></div>","PeriodicalId":73429,"journal":{"name":"International journal of cardiology. Congenital heart disease","volume":"13 ","pages":"Article 100467"},"PeriodicalIF":0.0,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"47310533","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 1

Criss-cross pulmonary arteries in common arterial trunk – Implications to management and outcome 总动脉主干中的交叉肺动脉Cris——对治疗和结果的影响

International journal of cardiology. Congenital heart disease Pub Date : 2023-09-01 DOI: 10.1016/j.ijcchd.2023.100471

Magdi H. Yacoub , Mohamed Nagy , Hatem Hosny , Ahmed Afifi , Amr El Sawy , Ahmed Mahgoub , Hedaia Abdullah , Soha Romeih , Mahmoud Shehata , Abdelrahman Elafifi

{"title":"Criss-cross pulmonary arteries in common arterial trunk – Implications to management and outcome","authors":"Magdi H. Yacoub , Mohamed Nagy , Hatem Hosny , Ahmed Afifi , Amr El Sawy , Ahmed Mahgoub , Hedaia Abdullah , Soha Romeih , Mahmoud Shehata , Abdelrahman Elafifi","doi":"10.1016/j.ijcchd.2023.100471","DOIUrl":"https://doi.org/10.1016/j.ijcchd.2023.100471","url":null,"abstract":"<div><h3>Objectives</h3><p>To investigate the incidence, types and pathophysiology of criss-cross pattern of the proximal pulmonary arteries in common arterial trunk and its influence on management and outcomes.</p></div><div><h3>Methods</h3><p>Retrospective review of all patients with common arterial trunk who underwent Aswan Truncus Operation with regard to the origin and course of the proximal pulmonary artery branches as defined by 3D segmented models pre, immediately and 1 and 2 years after operation.</p></div><div><h3>Results</h3><p>Between January 2019 and September 2022, 39 patients (19 males, aged 1–12 months) underwent the Aswan Truncus Operation. 18 patients (46%) had criss-cross arrangement of the proximal pulmonary artery. The mortality, ICU and hospital stay were not affected by the presence or absence of the criss-cross pattern. However, following operation in the criss-cross group, there was evidence of different degrees of kinking and twisting of the right pulmonary artery. This resulted in severe narrowing which required stenting or reoperation at different stages (1 during ICU stay and another after 1 year). Separate origin of the left pulmonary artery (Criss-cross Type 2) from a long stenotic ductus arteriosus required resection of the stenotic segment followed by anastomosis to the right pulmonary artery recreating a 60° angle of bifurcation.</p></div><div><h3>Conclusion</h3><p>Criss-cross pattern of proximal pulmonary arteries is common in patients with common arterial trunk. Pre-operative diagnosis and tailored approaches of repair are required to prevent late complications.</p></div>","PeriodicalId":73429,"journal":{"name":"International journal of cardiology. Congenital heart disease","volume":"13 ","pages":"Article 100471"},"PeriodicalIF":0.0,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49802362","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Psychologically informed medicine: A call for a holistic approach to improve mental health and wellbeing for those of us living with congenital heart disease 心理知情医学：呼吁采取全面的方法来改善我们这些先天性心脏病患者的心理健康和福祉

International journal of cardiology. Congenital heart disease Pub Date : 2023-09-01 DOI: 10.1016/j.ijcchd.2023.100468

Liza Morton

引用次数: 0

Position statement for the development of adult congenital heart disease units in Latin America and the Caribbean: Recommendations by the adult congenital heart disease chapter and pediatric cardiology council of the interamerican society of cardiology … 拉丁美洲和加勒比地区成人先天性心脏病单位发展的立场声明：美洲心脏病学会成人先天性心病分会和儿科心脏病委员会的建议…

International journal of cardiology. Congenital heart disease Pub Date : 2023-09-01 DOI: 10.1016/j.ijcchd.2023.100461

John J. Araujo , Carla P. Rodríguez-Monserrate , Amalia Elizari , Lucelli Yáñez-Gutiérrez , Mariela Mouratian , Fernando Amaral , Manuel Huertas-Quiñonez , Mónica Rosario , Mauricio O'Connell , Oscar N. Aguirre-Zurita , Carlos Fernández , Marcelo Callau-Briceño , María M. Lorente- Coppola , Nancy Garay

{"title":"Position statement for the development of adult congenital heart disease units in Latin America and the Caribbean: Recommendations by the adult congenital heart disease chapter and pediatric cardiology council of the interamerican society of cardiology …","authors":"John J. Araujo , Carla P. Rodríguez-Monserrate , Amalia Elizari , Lucelli Yáñez-Gutiérrez , Mariela Mouratian , Fernando Amaral , Manuel Huertas-Quiñonez , Mónica Rosario , Mauricio O'Connell , Oscar N. Aguirre-Zurita , Carlos Fernández , Marcelo Callau-Briceño , María M. Lorente- Coppola , Nancy Garay","doi":"10.1016/j.ijcchd.2023.100461","DOIUrl":"https://doi.org/10.1016/j.ijcchd.2023.100461","url":null,"abstract":"<div><p>In 2020, there was an estimated prevalence of more than 1.8 million adults with congenital heart disease (ACHDs) living in South America, and 677,000 in Central America and the Caribbean. The ACHD mortality is higher in developing countries, compared with developed countries, and it has been shown that concentrating this population in specialized ACHD units improves their survival and prognosis. Currently, Latin American (LATAM) and Caribbean countries have an insufficient number of specialists and specialized ACHD units. Analyzing this situation, the Inter-American Society of Cardiology's (IASC) ACHD chapter and Pediatric Cardiology Council have prepared the first recommendations for developing ACHD units in LATAM and Caribbean countries. This article is the first collaborative work between South American, Central American and Caribbean countries. It describes the main points for organizing and developing ACHD units adapted to our own reality. Each point has been discussed in terms of barriers and challenges, followed by specific recommendations for improving and developing ACHD care. They have been reviewed and endorsed by the International Society for Adult Congenital Heart Disease (ISACHD), and the goal of their implementation is for each ACHD unit in the region to have the standards of quality and efficiency to improve the prognosis and survival of ACHDs in the region.</p></div>","PeriodicalId":73429,"journal":{"name":"International journal of cardiology. Congenital heart disease","volume":"13 ","pages":"Article 100461"},"PeriodicalIF":0.0,"publicationDate":"2023-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49802361","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Psychologically informed medicine: A call for a holistic approach to improve mental health and wellbeing for those of us living with congenital heart disease. 心理知情医学:改善先天性心脏病患者心理健康的整体方法

IF 0.8

International journal of cardiology. Congenital heart disease Pub Date : 2023-07-11 eCollection Date: 2023-09-01 DOI: 10.1016/j.ijcchd.2023.100468

Liza Morton

引用次数: 0

Transcatheter secundum atrial septal defect closure using intracardiac echocardiography in adult patient with azygos/hemiazygos continuation of the inferior vena cava 经导管二次房间隔缺损闭合术在成人奇偶静脉/半奇偶静脉下腔静脉延续中的应用

International journal of cardiology. Congenital heart disease Pub Date : 2023-06-01 DOI: 10.1016/j.ijcchd.2023.100443

Leonardo Varotto, Alberto Dotto, Luca Spigolon, Gian Luca Spadaro, Francesco Caprioglio

引用次数: 0