Nishi Nihon Hifuka最新文献

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Congenital Erythropoietic Porphyria. 先天性红细胞生成性卟啉症。
Nishi Nihon Hifuka Pub Date : 1999-01-01 DOI: 10.2336/NISHINIHONHIFU.61.163
Y. Kameyoshi, Toshihiko Tanaka, S. Hihara, Akinobu Yanagida, Shoso Yamamoto, Masaya Kamiyasu, Masaharu Mizuno, M. Kondo
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引用次数: 0
Polyangiitis Overlap Syndrome 多血管炎重叠综合征
Nishi Nihon Hifuka Pub Date : 1994-04-01 DOI: 10.2336/NISHINIHONHIFU.56.219
清広 筒井, 孝衞 広根, 陽一 田丸
{"title":"Polyangiitis Overlap Syndrome","authors":"清広 筒井, 孝衞 広根, 陽一 田丸","doi":"10.2336/NISHINIHONHIFU.56.219","DOIUrl":"https://doi.org/10.2336/NISHINIHONHIFU.56.219","url":null,"abstract":"12歳の男児。9歳時にアレルギー性鼻炎, 副鼻腔炎に罹患。初診の1ヵ月前に38℃台の発熱, 湿性咳嗽, 血痰, 腹痛, 下痢, 関節痛に引き続き, 四肢に紫斑·水疱が出現した。臨床検査では, 血尿·蛋白尿·赤沈亢進·好酸球増多·RF高値と胸部X線写真で中下肺野に間質陰影が認められた。下肢の紫斑の生検でleukocytoclastic vasculitisがみられ, 免疫螢光染色直接法で真皮全層の血管壁にIgG·IgMの沈着が認められた。腎生検で壊死性糸球体腎炎が, 肺生検で肺出血と間質性肺炎がみられた。プレドニゾロン(PSL)1日45mg内服1ヵ月後, 血尿と蛋白尿は依然認められたが, その他の臨床症状は消退した。PSL 1日20mgまで漸減したとき, 38℃台の発熱, 湿性咳嗽, 体幹·四肢の紫斑が再発した。PSL 1日45mgとサイクロフォスファマイド1日100mgの併用1ヵ月後, 血尿と蛋白尿を除く臨床症状は消退し, 6ヵ月後寛解した。","PeriodicalId":19437,"journal":{"name":"Nishi Nihon Hifuka","volume":"13 1","pages":"219-223"},"PeriodicalIF":0.0,"publicationDate":"1994-04-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"74522712","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
そう痒性皮膚疾患に対する塩酸アゼラスチン(アゼプチン®)の臨床評価 盐酸艾泽拉斯汀(acetrastin®)治疗瘙痒性皮肤疾病的临床评价
Nishi Nihon Hifuka Pub Date : 1993-12-01 DOI: 10.2336/NISHINIHONHIFU.55.1145
山梨県アゼプチン研究班
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引用次数: 0
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