Journal of Indian Association of Pediatric Surgeons最新文献

{"title":"Value of Dynamic Renal Scintigraphy in Suggesting Congenital Midureteral Stricture: A Case Series and Literature Review.","authors":"Mohamed Oulad Saiad, Driss Tahiri","doi":"10.4103/jiaps.jiaps_168_25","DOIUrl":"https://doi.org/10.4103/jiaps.jiaps_168_25","url":null,"abstract":"<p><p>This study aims to discuss the role of dynamic renal scintigraphy (DRS) in diagnosing congenital midureteral stricture (CMUS) as a rare and challenging condition in children, often confused with ureteropelvic junction obstruction (UPJO), leading to inadequate management. We retrospectively analyzed DRS data from 133 cases of hydronephrosis from 2015 to 2023, including 3 CMUS and 15 UPJO by Crossing Vessels (CV). Preoperative protocol involved ultrasound and DRS. We adhered to the paediatric protocol of the European Association of Nuclear Medicine, only radiotracer selection depended on availability. Surgery was indicated based on symptoms, obstruction on DRS, and reduced renal function. Ureteral stricture was considered congenital if no extrinsic compression was found. We excluded non operated patients and those with missing data. Proximal ureteral retention on DRS was observed in one case with complete stricture in lumbar ureter (case1), absent in a case with ipsilateral UPJO (case 2), and equivocal findings were noted with incomplete stricture in the pelvic ureter (case 3). Ureteral stasis was consistently absent in all 130 cases of PUJO including 15 cas of CV. CMUS diagnosis was confirmed intraoperatively in all 3 cases. Lumbotomy allowed surgical access in 2 cases but was unsuitable in one. Outcomes were favorable in 3 patients. Often requested for hydronephrosis, DRS can provide additional information suggesting CMUS. However, ureteral retention on DRS may not always be present, particularly in cases of incomplete stenosis or associated uropathies.</p>","PeriodicalId":16069,"journal":{"name":"Journal of Indian Association of Pediatric Surgeons","volume":"31 2","pages":"270-274"},"PeriodicalIF":0.0,"publicationDate":"2026-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13061483/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147645378","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Hyaline Vascular Castleman Disease Presenting as Occipital Scalp Swelling in a Child.","authors":"Sumona Bose, Abanti Das, Tummidi Santosh, Rama Saha","doi":"10.4103/jiaps.jiaps_332_25","DOIUrl":"https://doi.org/10.4103/jiaps.jiaps_332_25","url":null,"abstract":"<p><p>Castleman disease (CD) is rare in children, especially with occipital scalp involvement. We report a 9-year-old girl with a long-standing, asymptomatic occipital swelling diagnosed as hyaline vascular Castleman disease post-excision. This case highlights the need to consider Castleman's disease in atypical pediatric scalp masses for accurate diagnosis and management.</p>","PeriodicalId":16069,"journal":{"name":"Journal of Indian Association of Pediatric Surgeons","volume":"31 2","pages":"313-315"},"PeriodicalIF":0.0,"publicationDate":"2026-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13061479/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147645525","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Laparoscopic Management of Median Arcuate Ligament Syndrome in an Adolescent Girl.","authors":"Edamakanti Swetha Soni, T K Jayakumar, Harshal Madavi, Nilesh Nagdeve, Amitkumar Jadhav, Kiran Khedkar, Ketki Kedar, Siddhi Chawla","doi":"10.4103/jiaps.jiaps_162_25","DOIUrl":"https://doi.org/10.4103/jiaps.jiaps_162_25","url":null,"abstract":"<p><p>This case report highlights successful laparoscopic decompression of median arcuate ligament syndrome (MALS) in a 13-year-old girl, demonstrating the effectiveness of the minimally invasive approach in resolving vascular compression. Postoperative imaging confirmed the celiac artery decompression. This case supports laparoscopy as a safe and effective surgical option in pediatric MALS.</p>","PeriodicalId":16069,"journal":{"name":"Journal of Indian Association of Pediatric Surgeons","volume":"31 2","pages":"261-263"},"PeriodicalIF":0.0,"publicationDate":"2026-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13061476/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147645530","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Extragonadal Primary Mixed Germ Cell Tumor of the Stomach.","authors":"Basharat Mubeen, Roopa Rachel Paulose, Anoop Koshy, Mohan K Abraham, Anju Farsana, Keechilat Pavithran","doi":"10.4103/jiaps.jiaps_343_25","DOIUrl":"https://doi.org/10.4103/jiaps.jiaps_343_25","url":null,"abstract":"<p><p>Germ cell tumors (GCT) are most commonly observed in the gonads. Extragonadal GCTs (EGCT) are uncommon and are considered metastatic or primary tumors. Histologically and immunophenotypically, EGCTs resemble gonadal GCT. EGCTs in the gastrointestinal tract are extremely rare and are seen more frequently as metastases than primary tumors. Here, we discuss a case of primary mixed GCT of the stomach in a 4-year-old boy to highlight the fact that GCT should be considered in the differential diagnosis of any poorly differentiated epithelioid neoplasm in the pediatric population. The site should not hinder one from thinking of it. Histomorphological appearances, supporting immunohistochemistry, and tumor markers can help in establishing the correct diagnosis and ensuring the appropriate management of patients.</p>","PeriodicalId":16069,"journal":{"name":"Journal of Indian Association of Pediatric Surgeons","volume":"31 2","pages":"307-309"},"PeriodicalIF":0.0,"publicationDate":"2026-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13061492/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147645532","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Specialized Diagnostics are Required for the Management of an Intraparotid Facial Nerve Schwannoma.","authors":"Josef Finsterer","doi":"10.4103/jiaps.jiaps_400_25","DOIUrl":"https://doi.org/10.4103/jiaps.jiaps_400_25","url":null,"abstract":"","PeriodicalId":16069,"journal":{"name":"Journal of Indian Association of Pediatric Surgeons","volume":"31 2","pages":"319-320"},"PeriodicalIF":0.0,"publicationDate":"2026-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13061463/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147645307","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"A Comparative Study on the Uroflowmetry Parameters between Single-stage and Staged Hypospadias Repair.","authors":"C Ashwin Kumar, Nitinkumar B Borkar, Charu Tiwari, Revanth Kalla, T Narasimha Murty, Rahul Giri","doi":"10.4103/jiaps.jiaps_226_25","DOIUrl":"https://doi.org/10.4103/jiaps.jiaps_226_25","url":null,"abstract":"<p><strong>Objective: </strong>Uroflowmetry documents functional outcome after hypospadias surgery. We aim to compare the uroflowmetry parameters between single-stage and staged hypospadias repair and determine any statistical difference.</p><p><strong>Materials and methods: </strong>This was a prospective cohort study conducted from July 2022 to July 2024. We compared the uroflowmetry parameters between single-stage and staged hypospadias repair on postoperative Day 10, Day 30, and Day 60. Quantitative variables were described as mean ± standard deviation and median with range and assessed using a paired <i>t</i>-test. Qualitative data were assessed using the Chi-square test or Fisher's exact test. A <i>P</i> < 0.05 was taken as statistical significance.</p><p><strong>Results: </strong>An Increase in mean flow rate and total voided volume was noted in both groups. The max flow rate was noted to decrease with time in both groups from day 10 to Day 60. Max flow rate increased with time in the single-stage repair and decreased with time in the staged repair group, but the values of max flow rate were statistically significant only for Day 60 with <i>P</i> = 0.08 (<0.05).</p><p><strong>Conclusions: </strong>Uroflowmetry is a good tool to assess the functional outcome after hypospadias surgery. There was a statistically significant difference only in maximum flow rate (Qmax) between single-stage and staged repair groups on Day 60, indicating urinary outflow obstruction in the staged repair group in our study.</p>","PeriodicalId":16069,"journal":{"name":"Journal of Indian Association of Pediatric Surgeons","volume":"31 2","pages":"173-179"},"PeriodicalIF":0.0,"publicationDate":"2026-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13061503/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147645422","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Erratum: Urachal Rhabdomyosarcoma in Children: A Rare Malignancy with Review of Literature.","authors":"","doi":"10.4103/jiaps.jiaps_71_26","DOIUrl":"10.4103/jiaps.jiaps_71_26","url":null,"abstract":"<p><p>[This corrects the article on p. 119 in vol. 31.].</p>","PeriodicalId":16069,"journal":{"name":"Journal of Indian Association of Pediatric Surgeons","volume":"31 2","pages":"322"},"PeriodicalIF":0.0,"publicationDate":"2026-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13061464/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147645515","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Chronic Pancreatitis with Portal Venous Thrombosis in a Child: Difficult Scenario for Surgery.","authors":"Basant Kumar, Rajneesh Kumar Singh, Rohit Kapoor, Nishant Agarwal","doi":"10.4103/jiaps.jiaps_303_25","DOIUrl":"https://doi.org/10.4103/jiaps.jiaps_303_25","url":null,"abstract":"<p><p>Chronic pancreatitis in children is uncommon but may be complicated by portal vein (PV) thrombosis and extrahepatic portal hypertension (EPH). This association poses significant diagnostic and therapeutic challenges. We report a 12-year-old boy with chronic calcific pancreatitis complicated by EPH secondary to PV thrombosis. He presented with recurrent abdominal pain, nonbilious vomiting, hypersplenism, and variceal bleeding. Imaging revealed a portal cavernoma with thrombosed PV, dilated splenic vein, atrophic pancreas, and ductal calculi. The patient underwent splenectomy with proximal splenorenal shunt and lateral pancreaticojejunostomy in a single sitting. Postoperative recovery was uneventful. At 8 months follow-up, the shunt remained patent, and the patient was asymptomatic apart from one self-limiting pain episode. Recurrent pancreatitis with EPH in children is rare. A multidisciplinary, individualized approach with careful preoperative optimization and tailored surgery can achieve good outcomes.</p>","PeriodicalId":16069,"journal":{"name":"Journal of Indian Association of Pediatric Surgeons","volume":"31 2","pages":"301-303"},"PeriodicalIF":0.0,"publicationDate":"2026-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13061493/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147645393","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Clinical Spectrum and Surgical Outcomes of Parasitic Twins in Early Infancy: Case Series and Experience from a Tertiary Care Center.","authors":"Ashish Chhabra, Saalim Nazki, Shipra Galhotra, Lubna Samad, Saswati Behera","doi":"10.4103/jiaps.jiaps_170_25","DOIUrl":"https://doi.org/10.4103/jiaps.jiaps_170_25","url":null,"abstract":"<p><strong>Background: </strong>Parasitic or heteropagus conjoined twins are an exceptionally rare congenital anomaly, with an estimated incidence of 1 in 1-2 million live births. These anomalies pose complex clinical and surgical challenges due to their varied anatomical presentations. Multidisciplinary evaluation and timely intervention are essential for favorable outcomes. The study aimed at clinical presentation, anatomical description, management, and outcomes of various heteropagus twins that were managed in a single tertiary care center.</p><p><strong>Methods: </strong>This retrospective study included six patients diagnosed with heteropagus twinning. Antenatal ultrasonography (USG) findings were reviewed where available. Postnatal investigations included USG, magnetic resonance imaging, and two-dimensional echocardiography for anatomical delineation and cardiac evaluation. Surgical intervention was performed based on the anatomical site and complexity of attachment. Resected specimens were sent for histopathological examination.</p><p><strong>Results: </strong>All patients presented in early infancy. Presentations were diverse: one had a sacral mass mimicking a myelomeningocele (rachipagus) containing intestinal loops; another had a limb, phallus, and testis with lipomeningocele; the third baby had an extra lower limb attached to the pelvis; the fourth baby had an accessory digit on the back; the fifth baby had rudimentary parasitic tissue near the perineum, and the last baby had a mandibular outgrowth resembling a distorted ill-formed face. All cases underwent successful surgical separation with good postoperative recovery. One of the babies succumbed to neonatal sepsis. All the patients are under a strict surveillance protocol with a minimum follow-up period of 3 years and longest being 8 years.</p><p><strong>Conclusion: </strong>Heteropagus twins exhibit a wide range of anatomical variations. Early antenatal diagnosis, detailed imaging, and prompt surgical management are key to achieving favorable outcomes. In addition, preoperative planning must include a detailed anatomical survey through the radiological scans and also cardiac evaluation. Surgical procedure to separate the parasitic twin varies from a simple to a more complex approach, so a multidisciplinary approach ensures comprehensive care and minimizes morbidity.</p>","PeriodicalId":16069,"journal":{"name":"Journal of Indian Association of Pediatric Surgeons","volume":"31 2","pages":"180-186"},"PeriodicalIF":0.0,"publicationDate":"2026-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13061470/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147645481","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Early Colon Feeding in Santulli Procedure in Neonates: A Single-center Prospective Study.","authors":"Hinglaj Saha, Saswata Barenya, Soumyajit Banerjee, Pankaj Kumar Halder","doi":"10.4103/jiaps.jiaps_273_25","DOIUrl":"https://doi.org/10.4103/jiaps.jiaps_273_25","url":null,"abstract":"<p><strong>Aim: </strong>The aim of this study was to assure a cost-effective method maintaining a progressive weight gain and providing early nutrition in the form of colon feed through a feeding tube in Santulli procedure to the neonate.</p><p><strong>Materials and methods: </strong>An observational study over 7 years in a single center. Out of 52 patients who underwent Santulli procedure for congenital intestinal atresia or refractory meconium ileus, 12 were excluded and the remaining were divided into 2 groups; Case 1 included 20 patients with colon feeding tube; Case 2 included 20 patients without colon feeding tube. A control group of 20 patients was formed and compared with Case 1 and Case 2. Progressive weight gain was assessed in all the three groups. Human breast milk (HBM) was used for feeding in addition to oral rehydration solution replacement per grams to weight of stoma output and zinc 1 ml/kg, iron 1 ml, and medium chain triglyceride oil 1-2 mg/kg per day.Results: Statistical significance was found on day 4/5 (<i>p</i> = 0.0174). Statistical differences were consistent from day 35 onward. All the group showed statistically highly significant values (<i>p</i> < 0.0001) from Day 2 onwards. Case 2 showed lower mean values as compared to Case 1 and control while Case 1 maintained higher values than control. Institutional ethical committee approval was taken.</p><p><strong>Conclusion: </strong>Colon enteral feeding is a cost-effective method with the use of HBM, enhancing both early adaptation of neonatal intestine, promoting catch-up growth and immunity.</p>","PeriodicalId":16069,"journal":{"name":"Journal of Indian Association of Pediatric Surgeons","volume":"31 2","pages":"161-167"},"PeriodicalIF":0.0,"publicationDate":"2026-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13061458/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"147645487","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}