E. De Mattia , M. Iatomasi , B. Garabelli , C. Lunetta , V.A. Sansone , F. Rao
{"title":"Use of the Intermittent Abdominal Pressure Ventilation to guarantee speech in a tracheostomized Amyotrophic Lateral Sclerosis patient","authors":"E. De Mattia , M. Iatomasi , B. Garabelli , C. Lunetta , V.A. Sansone , F. Rao","doi":"10.1016/j.rppnen.2017.03.002","DOIUrl":"10.1016/j.rppnen.2017.03.002","url":null,"abstract":"","PeriodicalId":101122,"journal":{"name":"Revista Portuguesa de Pneumologia (English Edition)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2017-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1016/j.rppnen.2017.03.002","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"35058191","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
C. Ribeiro , D. Ferreira , S. Conde , P. Oliveira , W. Windisch
{"title":"Validation of the Portuguese Severe Respiratory Insufficiency Questionnaire for home mechanically ventilated patients","authors":"C. Ribeiro , D. Ferreira , S. Conde , P. Oliveira , W. Windisch","doi":"10.1016/j.rppnen.2017.01.001","DOIUrl":"10.1016/j.rppnen.2017.01.001","url":null,"abstract":"<div><p>The aim of this study was to develop and validate the professional translation and cultural adaptation of the Portuguese Severe Respiratory Insufficiency (SRI) Questionnaire.</p><p>The sample was composed of 93 patients (50 male patients, 53.8%) with a mean age of 66.3 years. The most frequent diagnostic groups were chronic obstructive pulmonary disease, obesity hypoventilation syndrome and restrictive chest wall disorders.</p><p>The patients were asked to fill in both the SRI and SF-36 questionnaires. Factor analysis of the SRI questionnaire was performed leading to an explained variance of 73%, and resulted in 13 components. When analyzing the reliability, we obtained values for Cronbach's alpha above 0.70 for most subscales with the reliability of the summary scale being even higher (0.84).</p><p>This professional translation and cultural adaptation of the Portuguese SRI Questionnaire has good psychometric properties which are similar, not only to the original, but also to other translations. These characteristics make this questionnaire applicable to the Portuguese population receiving home mechanical ventilation for severe respiratory insufficiency.</p></div>","PeriodicalId":101122,"journal":{"name":"Revista Portuguesa de Pneumologia (English Edition)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2017-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1016/j.rppnen.2017.01.001","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34765533","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"The impact of anaemia and iron deficiency in chronic obstructive pulmonary disease: A clinical overview","authors":"A. Robalo Nunes , M. Tátá","doi":"10.1016/j.rppnen.2016.12.005","DOIUrl":"10.1016/j.rppnen.2016.12.005","url":null,"abstract":"<div><h3>Introduction</h3><p>Anaemia is increasingly recognised as an important comorbidity in the context of chronic obstructive pulmonary disease (COPD), but remains undervalued in clinical practice. This review aims to characterise the impact of anaemia and iron deficiency in COPD.</p></div><div><h3>Methods</h3><p>Literature review of studies exploring the relationship between anaemia/iron deficiency and COPD, based on targeted MEDLINE and Google Scholar queries.</p></div><div><h3>Results</h3><p>The reported prevalence of anaemia in COPD patients, ranging from 4.9% to 38.0%, has been highly variable, due to different characteristics of study populations and lack of a consensus on the definition of anaemia. Inflammatory processes seem to play an important role in the development of anaemia, but other causes (including nutritional deficiencies) should not be excluded from consideration. Anaemia in COPD has been associated with increased morbidity, mortality, and overall reduced quality of life. The impact of iron deficiency, irrespective of anaemia, is not as well studied, but it might have important implications, since it impacts production of red blood cells and respiratory enzymes. Treatment of anaemia/iron deficiency in COPD remains poorly studied, but it appears reasonable to assume that COPD patients should at least receive the same type of treatment as other patients.</p></div><div><h3>Conclusions</h3><p>Anaemia and iron deficiency continue to be undervalued in most COPD clinical settings, despite affecting up to one-third of patients and having negative impact on prognosis. Special efforts should be made to improve clinical management of anaemia and iron deficiency in COPD patients as a means of achieving better patient care.</p></div>","PeriodicalId":101122,"journal":{"name":"Revista Portuguesa de Pneumologia (English Edition)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2017-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1016/j.rppnen.2016.12.005","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34761070","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
G. Rocha , F. Flôr-de-Lima , I. Azevedo , H. Guimarães
{"title":"Severe bronchopulmonary dysplasia with large pneumatoceles in an extreme preterm newborn","authors":"G. Rocha , F. Flôr-de-Lima , I. Azevedo , H. Guimarães","doi":"10.1016/j.rppnen.2017.02.001","DOIUrl":"10.1016/j.rppnen.2017.02.001","url":null,"abstract":"","PeriodicalId":101122,"journal":{"name":"Revista Portuguesa de Pneumologia (English Edition)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2017-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1016/j.rppnen.2017.02.001","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34830948","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
A.A.D. Sasso , G. Zanetti , C.A. Souza , D.L. Escuissato , K.L. Irion , M.D. Guimarães , A. Soares Souza Jr , D. Penha , E. Marchiori
{"title":"High resolution computed tomography of the chest in the evaluation of patients with Birt–Hogg–Dubé syndrome","authors":"A.A.D. Sasso , G. Zanetti , C.A. Souza , D.L. Escuissato , K.L. Irion , M.D. Guimarães , A. Soares Souza Jr , D. Penha , E. Marchiori","doi":"10.1016/j.rppnen.2017.02.003","DOIUrl":"10.1016/j.rppnen.2017.02.003","url":null,"abstract":"","PeriodicalId":101122,"journal":{"name":"Revista Portuguesa de Pneumologia (English Edition)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2017-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1016/j.rppnen.2017.02.003","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34844841","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
B.R.A. Silva , R. Rufino , C.H. Costa , V.S. Vilela , R.A. Levy , A.J. Lopes
{"title":"Ventilation distribution and small airway function in patients with systemic sclerosis","authors":"B.R.A. Silva , R. Rufino , C.H. Costa , V.S. Vilela , R.A. Levy , A.J. Lopes","doi":"10.1016/j.rppnen.2017.01.004","DOIUrl":"10.1016/j.rppnen.2017.01.004","url":null,"abstract":"<div><h3>Background</h3><p>Despite the importance of traditional pulmonary function tests (PFTs) in managing systemic sclerosis (SSc), many patients with pulmonary disease diagnosed by computed tomography (CT) present with normal PFTs.</p></div><div><h3>Objective</h3><p>To evaluate the efficacy of the nitrogen single-breath washout (N<sub>2</sub>SBW) test in diagnosing SSc and to correlate N<sub>2</sub>SBW parameters with the PFT indexes used in the follow-up of these patients, clinical data, and CT findings.</p></div><div><h3>Methods</h3><p>Cross-sectional study in which 52 consecutive SSc patients were subjected to spirometry, body plethysmography, analysis of the diffusing capacity for carbon monoxide (DLCO), analysis of respiratory muscle strength, N<sub>2</sub>SBW testing, and CT analysis.</p></div><div><h3>Results</h3><p>Twenty-eight patients had a forced vital capacity (FVC) that was <70% of the predicted value. In the N<sub>2</sub>SBW test, 44 patients had a phase III slope (Phase III slope<sub>N2SBW</sub>) that was >120% of the predicted value, while 15 patients had a closing volume/vital capacity (CV/VC) that was >120% of the predicted value. A significant difference in Phase III slope<sub>N2SBW</sub> was observed when the patients with predominant traction bronchiectasis and honeycombing were compared to the patients with other CT patterns (<em>p</em> <!--><<!--> <!-->0.0001). The Phase III slope<sub>N2SBW</sub> was correlated with FVC (<em>r</em><sub>s</sub> <!-->=<!--> <!-->−0.845, <em>p</em> <!--><<!--> <!-->0.0001) and DLCO (<em>r</em><sub>s</sub> <!-->=<!--> <!-->−0.600, <em>p</em> <!--><<!--> <!-->0.0001), and the CV/VC was correlated with FVC (<em>r</em><sub>s</sub> <!-->=<!--> <!-->−0.460, <em>p</em> <!-->=<!--> <!-->0.0006) and residual volume/total lung capacity (<em>r</em><sub>s</sub> <!-->=<!--> <!-->0.328, <em>p</em> <!-->=<!--> <!-->0.017).</p></div><div><h3>Conclusion</h3><p>Ventilation heterogeneity is a frequent finding in SSc patients that is associated with restrictive damage, changes in pulmonary diffusion, and CT patterns. In addition, approximately one-third of the patients presented with findings that were compatible with small airway disease.</p></div>","PeriodicalId":101122,"journal":{"name":"Revista Portuguesa de Pneumologia (English Edition)","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2017-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1016/j.rppnen.2017.01.004","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34782282","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}