{"title":"Evaluation of inpatient mortality in pediatric Non-Hodgkin lymphoma and lessons learnt at a tertiary care hospital in Pakistan","authors":"Mahwish Faizan, Saadia Anwar, Rahat Ul Ain Kashif","doi":"10.1016/j.ejcped.2025.100270","DOIUrl":"10.1016/j.ejcped.2025.100270","url":null,"abstract":"","PeriodicalId":94314,"journal":{"name":"EJC paediatric oncology","volume":"5 ","pages":"Article 100270"},"PeriodicalIF":0.0,"publicationDate":"2025-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144756741","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Mohammed Uvaise Sikkander Batcha , Soumendu Manna , C. Balloji
{"title":"Management and outcome of systemic hypertension in patients with primary oncological diagnosis in PICU","authors":"Mohammed Uvaise Sikkander Batcha , Soumendu Manna , C. Balloji","doi":"10.1016/j.ejcped.2025.100288","DOIUrl":"10.1016/j.ejcped.2025.100288","url":null,"abstract":"","PeriodicalId":94314,"journal":{"name":"EJC paediatric oncology","volume":"5 ","pages":"Article 100288"},"PeriodicalIF":0.0,"publicationDate":"2025-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144757335","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Andrea Spessoto, Paola Madureira, Kelly Astolpho, Regina Célia de Almeida Ribeiro, Fernanda Quelian Penna
{"title":"Postoperative management of pediatric head and neck rhabdomyosarcoma with microsurgical reconstruction: Report of two cases","authors":"Andrea Spessoto, Paola Madureira, Kelly Astolpho, Regina Célia de Almeida Ribeiro, Fernanda Quelian Penna","doi":"10.1016/j.ejcped.2025.100289","DOIUrl":"10.1016/j.ejcped.2025.100289","url":null,"abstract":"","PeriodicalId":94314,"journal":{"name":"EJC paediatric oncology","volume":"5 ","pages":"Article 100289"},"PeriodicalIF":0.0,"publicationDate":"2025-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144757336","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Bruno Sanchez Camargo, Orlei Ribeiro de Araujo, Dafne Cardoso Bourguignon da Silva
{"title":"Effect of crystalloid expansion on extravascular lung water volume in critically ill children with cancer","authors":"Bruno Sanchez Camargo, Orlei Ribeiro de Araujo, Dafne Cardoso Bourguignon da Silva","doi":"10.1016/j.ejcped.2025.100287","DOIUrl":"10.1016/j.ejcped.2025.100287","url":null,"abstract":"","PeriodicalId":94314,"journal":{"name":"EJC paediatric oncology","volume":"5 ","pages":"Article 100287"},"PeriodicalIF":0.0,"publicationDate":"2025-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144757334","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Valérie de Haas, Esmee Slot , Laura van den Berg , Rana Dandis, Hester de Groot-Kruseman, Rob Pieters
{"title":"Dexamethasone/vincristine pulses significantly reduce administered doses of 6MP/MTX during maintenance therapy in childhood acute lymphoblastic leukemia","authors":"Valérie de Haas, Esmee Slot , Laura van den Berg , Rana Dandis, Hester de Groot-Kruseman, Rob Pieters","doi":"10.1016/j.ejcped.2025.100243","DOIUrl":"10.1016/j.ejcped.2025.100243","url":null,"abstract":"<div><h3>Background</h3><div>Maintenance therapy with 6-Mercaptopurine (6MP) and Methotrexate (MTX) with or without dexamethasone (DEX) and vincristine (VCR) pulses, is crucial in childhood acute lymphoblastic leukaemia (ALL). Dosing adjustments are based on white blood cell (WBC) and neutrophil counts (ANC) to balance relapse and infection risks. We investigated if clinicians adjust doses for high versus low WBC/ANC and how pulses affect WBC/ANC and dose intensity.</div></div><div><h3>Methods</h3><div>Analyzing WBC/ANC and 6MP/MTX doses in DCOG-ALL11 (ALL11) and ALLtogether (A2G) patients, we assessed clinical compliance with dose-adjustment guidelines.</div></div><div><h3>Results</h3><div>Across 2901 WBC checkpoints in ALL11 and 3806 in A2G (validation cohort), clinicians were non-compliant with dose-adjustment guidelines in 44 % (ALL11) and 31 % (A2G) of cases.</div><div>At checkpoints where no-compliance was observed, WBC/ANC levels were most frequently above target (85.1 % in ALL11 and 87.7 % in A2G) and rarely below (6.4 % in ALL11 and 6.7 % in A2G, p < 0.001).Median WBC/ANC levels often exceeded recommendations (3.1 and 1.6 ×109/L, respectively) and patients receiving DEX/VCR pulses had a lower median dose 6MP / MTX (60 %) than those without pulses (100 % ALL11, 75 % A2G; P < 0.001), resulting in lower absolute doses.</div></div><div><h3>Conclusions</h3><div>In conclusion, clinicians are less likely to adjust doses properly when WBC/ANC levels exceed targets, reducing 6MP/MTX dose intensity. DEX/VCR pulses significantly lower 6MP/MTX doses, possibly influencing their benefit in ALL maintenance.</div></div>","PeriodicalId":94314,"journal":{"name":"EJC paediatric oncology","volume":"5 ","pages":"Article 100243"},"PeriodicalIF":0.0,"publicationDate":"2025-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144178757","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Sarita Depani , Alexandre Vasiljevic , Martin Mynarek , Christelle Dufour , Elke Pfaff , Ata Ur Maaz , Léa Guerrini-Rousseau , Francois Doz , Martin Hasselblatt , Thankamma Ajithkumar , Kristian Aquilina , Martin U. Schuhmann , Eelco Hoving , Anna Tietze , Ulrike Löbel , Barry Pizer , Katja von Hoff , On behalf of the SIOP-Europe Rare Embryonal and Sarcomatous Tumours (REST) group
{"title":"Corrigendum to “European clinical practice recommendations for the diagnosis and treatment of paediatric pineal tumours” [EJC Paediatr. Oncol. 5 (2025) 100217]","authors":"Sarita Depani , Alexandre Vasiljevic , Martin Mynarek , Christelle Dufour , Elke Pfaff , Ata Ur Maaz , Léa Guerrini-Rousseau , Francois Doz , Martin Hasselblatt , Thankamma Ajithkumar , Kristian Aquilina , Martin U. Schuhmann , Eelco Hoving , Anna Tietze , Ulrike Löbel , Barry Pizer , Katja von Hoff , On behalf of the SIOP-Europe Rare Embryonal and Sarcomatous Tumours (REST) group","doi":"10.1016/j.ejcped.2025.100241","DOIUrl":"10.1016/j.ejcped.2025.100241","url":null,"abstract":"","PeriodicalId":94314,"journal":{"name":"EJC paediatric oncology","volume":"5 ","pages":"Article 100241"},"PeriodicalIF":0.0,"publicationDate":"2025-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144298595","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Management of a critical airway emergency caused by large oral haematoma secondary to severe mucositis","authors":"Caris Coyle, Heather Storey, Ismail Elbeshlawi, Arnwald Choi, Gogan Dhotar, Jenny Woodruff","doi":"10.1016/j.ejcped.2025.100250","DOIUrl":"10.1016/j.ejcped.2025.100250","url":null,"abstract":"","PeriodicalId":94314,"journal":{"name":"EJC paediatric oncology","volume":"5 ","pages":"Article 100250"},"PeriodicalIF":0.0,"publicationDate":"2025-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144756693","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Establishing a collaborative network for critically ill pediatric cancer patients across Latin America","authors":"Alejandra Méndez-Aceituno , Himy Muniz-Talavera , Xiomara Gamboa-Vásquez","doi":"10.1016/j.ejcped.2025.100245","DOIUrl":"10.1016/j.ejcped.2025.100245","url":null,"abstract":"","PeriodicalId":94314,"journal":{"name":"EJC paediatric oncology","volume":"5 ","pages":"Article 100245"},"PeriodicalIF":0.0,"publicationDate":"2025-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144756796","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Andrea Zühlsdorf , Alexander Humberg , Christoph Zöller , Volker Müller , Andreas Groll , Katja Masjosthusmann , Jenny Potratz
{"title":"An open abdomen is not a contraindication for ECMO in children with cancer","authors":"Andrea Zühlsdorf , Alexander Humberg , Christoph Zöller , Volker Müller , Andreas Groll , Katja Masjosthusmann , Jenny Potratz","doi":"10.1016/j.ejcped.2025.100284","DOIUrl":"10.1016/j.ejcped.2025.100284","url":null,"abstract":"","PeriodicalId":94314,"journal":{"name":"EJC paediatric oncology","volume":"5 ","pages":"Article 100284"},"PeriodicalIF":0.0,"publicationDate":"2025-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144757404","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}