World journal for pediatric & congenital heart surgery最新文献

{"title":"Monomorphic Ventricular Tachycardia Secondary to an Epicardial Pacing Lead.","authors":"Mitchell I Cohen, Christopher Moalli, Rob Przybylski, Lucas Collazo","doi":"10.1177/21501351251333675","DOIUrl":"https://doi.org/10.1177/21501351251333675","url":null,"abstract":"<p><p>Epicardial pacing leads are frequently used in small children and in complex congenital heart disease that precludes transvenous lead placement. While lead failure is not uncommon from epicardial pacing leads, proarrhythmic events are rare. We present an eight-year-old patient who developed spontaneous nonsustained ventricular tachycardia from a chronic unipolar epicardial pacing lead. Removal of the epicardial lead with cryoablation around the lead body resolved the ventricular tachycardia. To our knowledge, this is the first case report of a suture on epicardial pacing lead causing late ventricular tachycardia.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351251333675"},"PeriodicalIF":0.0,"publicationDate":"2025-04-24","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144051161","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Unintended Consequences of Innominate Artery Cannulation in a Pediatric Patient: Infection of Innominate Artery Graft Stump With Subsequent Formation of Right Common Carotid Artery Pseudoaneurysm.","authors":"Andreas Polycarpou, Satoshi Miyairi, Pranava Sinha, Edward Martin-Chaffee, Syed Murfad Peer","doi":"10.1177/21501351251333657","DOIUrl":"https://doi.org/10.1177/21501351251333657","url":null,"abstract":"<p><p>Indirect arterial cannulation techniques, such as cannulation of the innominate artery (IA) using an end-to-side anastomosed vascular graft, are commonly used to establish cardiopulmonary bypass in congenital cardiac surgery. Although rare, unintended consequences, such as graft infection, may occur. We describe a case of IA graft infection with subsequent pseudoaneurysm formation in a 10-year-old child who underwent multiple procedures for Tetralogy of Fallot with absent pulmonary valve syndrome.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351251333657"},"PeriodicalIF":0.0,"publicationDate":"2025-04-24","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144061762","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Unexpected Finding of an Inflammatory Myofibroblastic Tumor of the Heart Causing Pulmonary Artery Obstruction in an Asymptomatic Toddler.","authors":"Sara B A Morel, Elie Fadel, Sophie W Gao, Dorothée Dal Soglio, Pierre-Luc Bernier","doi":"10.1177/21501351251322154","DOIUrl":"https://doi.org/10.1177/21501351251322154","url":null,"abstract":"<p><p>Inflammatory myofibroblastic tumor (IMT) of the heart is a very rare tumor, constituting less than 5% of primary heart tumors. This case report describes the unexpected finding of IMT of the heart causing pulmonary artery obstruction in an asymptomatic toddler.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351251322154"},"PeriodicalIF":0.0,"publicationDate":"2025-04-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144004551","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Surgical Management of a Patient With Non-Fallot-Type Absent Pulmonary Valve Syndrome.","authors":"Jason J Breithaupt, Charles Fraser, Ryan Leahy, Brian Mejak, Dale Burkett, Megan Albertz, John Kim, Matthew L Stone","doi":"10.1177/21501351251327214","DOIUrl":"https://doi.org/10.1177/21501351251327214","url":null,"abstract":"<p><p>We describe the presentation and management of an infant with the unique constellation of a massive patent ductus arteriosus, severely insufficient pulmonary valve, hypoplastic tricuspid valve, and a resultant profoundly dilated and hypertrophic right ventricle with intact interventricular septum. Surgery consisted of ductal ligation and division, homograft patch augmentation of the aortic arch, modified Blalock-Taussig-Thomas shunt placement, right ventricle-to-pulmonary artery homograft placement, and atrial septectomy.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351251327214"},"PeriodicalIF":0.0,"publicationDate":"2025-04-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144061760","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Management of a Paraganglioma in a Fontan Patient: A Complex Case of Adrenergic Imbalance and Perioperative Care.","authors":"Carlos A Carmona, Michael R Bykhovsky, Elizabeth D Sherwin, Gregory K Yurasek","doi":"10.1177/21501351251322164","DOIUrl":"https://doi.org/10.1177/21501351251322164","url":null,"abstract":"<p><p>Pheochromocytomas and paragangliomas (PPGLs) are neuroendocrine tumors that secrete catecholamines. They can induce severe hypertension and tachycardia; thus, complicating the health of patients with stabilized congenital heart disease. Chronic hypoxemia is a potential driver for tumor development as discovered by the role of hypoxia-inducible factors in tumorigenesis. This case report describes a 24-year-old woman with hypoplastic left heart syndrome and fenestrated Fontan palliation who developed an adrenergic crisis following adjustments to her medications. She was initially on metoprolol for ventricular ectopy and suspended it to initiate phenoxybenzamine, an alpha-blocker, in preparation for surgical removal of a hormonally active retroperitoneal paraganglioma. Six days after discontinuation of the metoprolol, she presented to the emergency department with severe abdominal pain, palpitations, and nausea. The evaluation revealed supraventricular tachycardia and elevated blood pressure, which did not respond to initial treatments. She was admitted to the cardiac intensive care unit where she experienced further deterioration, necessitating intubation and treatment with amiodarone for rhythm control of her identified ectopic atrial tachycardia. Following stabilization and successful extubation, the patient was discharged on a regimen including amiodarone, metoprolol, and doxazosin. She successfully had her surgery in the following months and was weaned off amiodarone and metoprolol while remaining free of arrhythmias. This case highlights the complexities of managing PPGLs in Fontan patients and emphasizes the importance of multidisciplinary care to prevent and manage adrenergic crises.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351251322164"},"PeriodicalIF":0.0,"publicationDate":"2025-04-13","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144063386","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Complete Atrioventricular Septal Defect Repair in Patients With Down Syndrome Presenting Beyond Six Months- A Single Center Experience.","authors":"Kartik Patel, Chandrasekaran Ananthanarayanan, Trushar Gajjar, Amit Mishra, Bhavik Champaneri, Jigar Surti, Himani Pandya","doi":"10.1177/21501351251322162","DOIUrl":"https://doi.org/10.1177/21501351251322162","url":null,"abstract":"<p><p>BackgroundComplete atrioventricular septal defect (cAVSD) is the most common cardiac lesions associated with Down syndrome (DS). In DS, cAVSD repair is ideally performed before six months of age to prevent irreversible pulmonary artery hypertension (PAH). However, in developing countries, delayed repair is often unavoidable. We retrospectively analyzed the outcomes of cAVSD repair in DS patients presenting beyond six months of age.MethodBetween 2015 and 2019, 60 DS patients with cAVSD who underwent biventricular repair were reviewed. During the same time period 42 DS patients under 6 months of age underwent cAVSD repair. Their laboratory parameters and echocardiographic data were analyzed. Clinical findings as well as echocardiographic results at last follow-up were recorded.ResultMedian age of the cohort was eight months. There were 7/60 (11.7%) early mortalities due to right ventricular dysfunction secondary to persistent PAH (n = 4) and sepsis (n = 3). We found that right atrioventricular valve regurgitation (AVVR) grade (OR = 5.7, <i>P</i> = .017), postoperative serum bilirubin (OR = 4.03, <i>P</i> = .04), postoperative creatinine (OR = 7.06, <i>P</i> = .008), and right AVVR Gmax (OR = 6.08, <i>P</i> = .009) were independent risk factors for mortality. Mean follow-up was 1658 ± 771 days with a survival rate of 85% at 1, 5, and 10 years. Late reoperation (5.6% vs 3.7%) as well as prevalence of more than mild regurgitation was higher for the right AV valve as compared with the left AV valve (11.5% vs 1.9%). We did not find any factors associated with reoperation. All patients were clinically asymptomatic and did not have residual severe PAH.ConclusionComplete Atrioventricular septal defect repair in late-presenting patients with DS is feasible and yields good long-term outcomes. However, close follow-up is necessary to monitor for the late development of right AVVR.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351251322162"},"PeriodicalIF":0.0,"publicationDate":"2025-04-03","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143782322","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"In Memoriam: Albert Starr (1926-2024).","authors":"Marshall L Jacobs, Carl L Backer","doi":"10.1177/21501351251322901","DOIUrl":"https://doi.org/10.1177/21501351251322901","url":null,"abstract":"","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351251322901"},"PeriodicalIF":0.0,"publicationDate":"2025-03-28","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143733848","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Fate of Residual Patch Leak After Surgical Closure of Congenital Perimembranous Ventricular Septal Defects.","authors":"Hani N Mufti, Ysmeen T Bucklain, Abdulaziz M Shaheen, Ahmed Qumsani, Arwa A Alrrzqi, Sereen M Kazim, Luis Acosta, Alfredo Gamboa","doi":"10.1177/21501351251314387","DOIUrl":"https://doi.org/10.1177/21501351251314387","url":null,"abstract":"<p><p>IntroductionVentricular septal defects (VSDs) account for 50% of congenital heart defects in children. Surgical closure of moderate to large VSDs using patch material is considered the standard treatment in children to prevent future complications.ObjectivesWe evaluated the fate of VSD patch leak and its impact on aortic and tricuspid valve regurgitation at one year after surgery.MethodsThis retrospective study consisted of patients with a perimembranous VSD who underwent surgery between January 2016 and July 2021. Demographic, echocardiographic, clinical, and operative data were retrospectively reviewed. All patients' echocardiographic images were analyzed at discharge, 6, and 12 months after surgery. Echocardiography assessment focused on the degree of residual VSD (rVSD) patch leak and aortic and tricuspid regurgitation grade compared with preoperative echocardiography.ResultsSeventy-one consecutive patients who underwent perimembranous VSD surgical closure were reviewed. No patient required reintervention. There was one early mortality during follow-up. Of the 70 patients with complete follow-up, 24 patients (34.33%) had a 1-2 mm rVSD patch leak and 4 patients (5.7%) had a 2-3 mm rVSD patch leak at the time of discharge. At 12-month follow-up echocardiography, 67 patients (95.7%) had no rVSD patch leak. Aortic and tricuspid valve regurgitation significantly improved from discharge to 12 months after surgery. The size of the patch leak did not affect patients' weight gain (<i>P</i> ≥ .05).ConclusionsWe demonstrated that a 2 mm or less rVSD patch leak is benign, has no impact on tricuspid or aortic valve function, no impact on weight gain, and almost always decreases in severity or disappears.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351251314387"},"PeriodicalIF":0.0,"publicationDate":"2025-03-25","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143702463","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Over 3,000 Minimally Invasive Thoracotomies From the European Congenital Heart Surgeons Association for Quality Repairs of the Most Common Congenital Heart Defects: Safe and Routine for Selected Repairs.","authors":"Ali Dodge-Khatami, Juan-Miguel Gil-Jaurena, Jürgen Hörer, Paul Philipp Heinisch, Julie Cleuziou, Sara C Arrigoni, Robert A Cesnjevar, Hitendu H Dave, Alessandro Giamberti, Mauro Lo Rito, Alexander Kadner, Matthias Siepe, Roman Sekelyk, Dmytro Kozhokar, Illya Yemets, Alain Poncelet, Geoffroy de Beco, Jean Rubay, Andre Rüffer, Vincent Kundt, Sameh M Said, Zdzislaw Tobota, Jeffrey P Jacobs, Massimo Padalino, Vladimiro Vida","doi":"10.1177/21501351251322155","DOIUrl":"https://doi.org/10.1177/21501351251322155","url":null,"abstract":"<p><p>BackgroundMinimally invasive thoracotomies to repair selected congenital heart defects are considered only a cosmetic alternative approach by many; however, they represent the routine alternative in centers of expertise.MethodsPooled institutional data from the European Congenital Heart Surgeons Association using mini-thoracotomy approaches were analyzed since the beginning of their respective experiences until an inclusion surgical date of January 31, 2024, allowing at least six months postoperative follow-up.ResultsFrom 1999 to 2024, 3,007 patients from 11 centers underwent surgery. Age and weight ranged from 4 days to 73 years and 3.1 to 106 kg, respectively. Repaired defects included atrial and ventricular septal defects, partial anomalous pulmonary venous return, partial and complete atrioventricular septal defects, double-chambered right ventricle, cor triatriatum, scimitar syndrome, subaortic stenosis, and total anomalous pulmonary venous return (TAPVR). There was no surgical mortality or intraoperative conversion to sternotomy. Complications included wound infections (0.59%), pacemaker requirement (0.23%), phrenic nerve injury (0.26%), bleeding requiring exploration (0.13%), and neurologic injury (0.29%). Early or late reoperations were needed in 0.73%.ConclusionMinimally invasive thoracotomies are the preferred approach for selected congenital heart defects in the participating pediatric heart centers. Mini-thoracotomy incisions allow safe access to an ever-expanding spectrum of quality repairs, low morbidity, superior cosmetics, and early return to functionality in infants, children, and adults.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351251322155"},"PeriodicalIF":0.0,"publicationDate":"2025-03-25","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143702468","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Long-Term Clinical and Echocardiographic Follow-Up After Aortic Valve Tricuspidization With Polytetrafluoroethylene in Children: 15-Year Experience at a Single Center.","authors":"Matej Nosáľ, Fadi Sabateen, Pavel Valentík, Michal Šagát, Aref Saif Nagi, Vladimír Soják","doi":"10.1177/21501351251322159","DOIUrl":"https://doi.org/10.1177/21501351251322159","url":null,"abstract":"<p><p>ObjectivesAortic valve repair by tricuspidization with leaflet extensions is utilized in the management of aortic valve disease in children and adolescents. The aim of this study is to evaluate the long-term outcomes following aortic valve tricuspidization using polytetrafluoroethylene (PTFE) leaflet extensions at a single center.MethodsWe conducted a retrospective single-center analysis of 50 patients who underwent aortic valvuloplasty by tricuspidization with PTFE leaflet extensions between 2008 and 2024.ResultsFifty patients (37/50, 74% female) underwent aortic valvuloplasty using PTFE. The median age was 13 (interquartile range [IQR]: 1.8-25) years. During the median follow-up duration of 8.5 years (IQR: 8 months-15.8 years), 18 patients required reoperation at a mean of 7.3 ± 4 years. The 15-year survival rate was 95.6% (95% confidence interval [CI], 88%-98.8%), and 2 late deaths occurred. The freedom from reoperation at 1, 5, and 12 years was 100% (95% CI, 100%-100%), 82.8% (95% CI, 66.6%-91.4%), and 44.2% (95% CI, 26.2%-61%), respectively. At discharge, the mean peak systolic aortic valve gradients (15 ± 10 mm Hg) were significantly lower than preoperative (72 ± 35 mm Hg) values (<i>P</i> < .001). Mean of left ventricular end-diastolic diameter/body surface area index decreased from 38 ± 13 mm preoperatively to 34.4 ± 10.5 mm postoperatively, then reduced to 32 ± 7 mm at the latest follow-up (<i>P</i> = .003). Aortic regurgitation improved in all patients, and none had more than mild aortic regurgitation at hospital discharge.ConclusionsAortic leaflet extension valvuloplasty using PTFE is effective, safe, with excellent survival and favorable long-term outcomes. It provides reliable palliation in patients with congenital aortic valve diseases until a more permanent replacement alternative is available.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351251322159"},"PeriodicalIF":0.0,"publicationDate":"2025-03-21","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143675138","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}