World journal for pediatric & congenital heart surgery最新文献

{"title":"Contemporary Practice of Native Coarctation in Children Greater Than One Year of Age: A Society of Thoracic Surgeons Analysis.","authors":"Awais Ashfaq, Edo Bedzra, Konrad T Rajab, Levi N Bonnell, Ashok Muralidaran, Mark Bleiweis, David L S Morales, Robert H Habib, Jeffrey Jacobs, James A Quintessenza","doi":"10.1177/21501351241311276","DOIUrl":"10.1177/21501351241311276","url":null,"abstract":"<p><p>ObjectiveLimited data exist on surgical repairs for native coarctation of the aorta (Native-CoA) after year-one of life. We sought to establish surgical outcomes benchmark of older Native-CoA repair patients.MethodsAll patients greater than one year of age who underwent off-pump Native-CoA repair were identified from the Society of Thoracic Surgeons Congenital Heart Surgery Database (STS-CHSD) between January 1998 and December 2022.ResultsA total of 2,898 patients older than one year (mean age: 6.1 years; mean weight: 23.7 kg) underwent Native-CoA repair through left thoracotomy at 131 STS-CHSD centers. Vascular syndromes including Turners, Williams, and Alagille, were relatively rare at 1.8%. The most common procedures were extended end-to-end (1,309/2898, 45.2%) end-to-end 1,107/2898, (38.2%), and patch aortoplasty ((239/2898, 8.2%). From 1998 to 2018, there was an overall increase in the number of patients (14 vs 156), explained largely by the increased number of hospitals (4 vs 70). However, after 2018, case counts declined by nearly 50%. Operative mortality was rare (n = 3). An average of 1.2 complications per patient (438 total) occurred in 365/2898 (12.6%) patients. The most common complications included chylothorax (101/2898, 3.5%), unplanned 30-day readmission (28/1917, 1.5%), and arrhythmia requiring drug therapy (17/1917, 0.9%). Median length of hospital stay was four days, with hospital stay >6 days in 248 patients (14.8%).ConclusionsFrequency of off-pump Native-CoA repairs (age >1 year) is decreasing despite no notable change in total participating hospitals and case counts. This is likely due to increased percutaneous interventions despite very low documented mortality and morbidity of off-pump surgical repairs.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"439-445"},"PeriodicalIF":0.0,"publicationDate":"2025-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143257704","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Native Tricuspid Valve Endocarditis Delayed Glenn Procedure: A Case Report.","authors":"Madison B Argo, Joshua L Hermsen, Luke Lamers, Mike Wilhelm, Charles Bergstrom, Petros V Anagnostopoulos","doi":"10.1177/21501351251316231","DOIUrl":"10.1177/21501351251316231","url":null,"abstract":"<p><p>Infective endocarditis in infants with congenital heart disease is exceedingly rare and thus, treatment guidelines and expected outcomes are understudied. We present a 3-month-old girl diagnosed with native tricuspid valve endocarditis at the time of her pre-Glenn cardiac catheterization. She had resultant tricuspid valve and right ventricular dysfunction. After initiating intravenous antibiotics, she underwent an operation including a bidirectional Glenn, Sano shunt extirpation, tricuspid valve repair, and central pulmonary artery stent insertion. At 9 months postoperatively, the patient continues to do well with good right ventricular and tricuspid valve function. Surgical treatment of infective endocarditis may be performed during a Glenn operation with satisfactory short-term results.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"546-548"},"PeriodicalIF":0.0,"publicationDate":"2025-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143461311","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"A Coronary Challenge: Management of Dextro-Transposition With Levo-Malposed Great Vessels.","authors":"Mark B Lewis, John D Cleveland, Julie Fenske, Luke M Wiggins","doi":"10.1177/21501351251322158","DOIUrl":"10.1177/21501351251322158","url":null,"abstract":"<p><p>A full-term neonate was transferred to our facility after a postnatal diagnosis of dextro (D)-transposition and a ventricular septal defect (VSD). Initial transthoracic echocardiogram revealed atrial situs solitus (S), D-looped ventricles, ventriculo-arterial discordance, and levo-malposition of the great arteries. A single coronary artery was found to be originating from the rightward and anterior sinus of the aortic root. Therefore, we discussed our operative plan as a multidisciplinary team given the atypical anatomy and ultimately decided upon a full repair with an arterial switch operation and VSD closure. We describe our operative technique employed to tackle this uncommon anatomy.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"549-551"},"PeriodicalIF":0.0,"publicationDate":"2025-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143733847","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Aortopexy With Plication of Kommerell Diverticulum Is an Effective Alternative to Diverticulum Resection and Reimplantation of the Aberrant Left Subclavian Artery for Surgical Management of Vascular Rings in Children.","authors":"Adegbemisola Aregbe Perkins, Ana-Lucia Tomescu, Christopher J Knott-Craig, Umar Boston, Thomas Spentzas, Karthik Vaidyanathan Ramakrishnan","doi":"10.1177/21501351251329912","DOIUrl":"10.1177/21501351251329912","url":null,"abstract":"<p><p>BackgroundRight aortic arch with an aberrant left subclavian artery arising from a Kommerell diverticulum is the most common form of vascular ring. We report the outcomes of plication and pexy of the diverticulum in addition to division of the left-sided ligamentum to treat this lesion in children.MethodsForty-four patients were included in the study; 22 patients underwent division of the ligamentum arteriosum alone, while the other half underwent plication and/or pexy of the Kommerell diverticulum in addition to division of the ligamentum. The primary outcome of interest was reintervention for persistent symptoms following the initial operation. The other outcome studied was symptom relief on follow-up.ResultsThe baseline characteristics were similar between the two groups. There was no difference in the ratio of the size of the Kommerell diverticulum to the size of the left subclavian artery between the groups (1.6 vs 1.8, <i>P</i> = .22). The incidence of reoperation was similar in both groups (5% in each group, <i>P</i> = 1); 7/22 (32%) had persistent symptoms after ligamentum division alone, while only 1/22 (5%) had persistent symptoms after plication and/or pexy (<i>P</i> = .05).ConclusionPlication of the Kommerell diverticulum with pexy along with division of the ligamentum arteriosum is an effective alternative for treatment of right aortic arch with an aberrant left subclavian artery arising from the diverticulum.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"446-449"},"PeriodicalIF":0.0,"publicationDate":"2025-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144061161","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Outcomes in Late Presenting Obstructed Infracardiac Total Anomalous Pulmonary Venous Connection-Single Centre Experience.","authors":"Kartik Patel, Deepti Kakkar, Himani Pandya, Shyam S Kothari, Megha Sheth, Herin Patel, Trushar Gajjar, Amit Mishra","doi":"10.1177/21501351241305133","DOIUrl":"10.1177/21501351241305133","url":null,"abstract":"<p><p>BackgroundSurvival beyond one month of age is rare in children born with obstructed infracardiac total anomalous pulmonary venous connection (TAPVC). There are limited data available on surgical outcomes of the same subset. We conducted this retrospective study to identify risk factors associated with surgical outcomes in this patient population.MethodWe present a retrospective study of patients presenting at our institute with obstructed infracardiac TAPVC surviving beyond one month of age during the period from January 2015 to August 2019 (n = 14). Data reviewed included demographic parameters, preoperative laboratory results, echocardiogram images, and computed tomography if performed. Intraoperative as well as postoperative data including type of surgery, use of deep hypothermic arrest, mortality, and morbidity were noted. Follow-up clinical data were also collected from institutional record or telephonically. We have also collected echocardiographic data on follow up.ResultsThe mean age of our study cohort was 2.14 ± 0.68 months. Out of 14 total patients 3 patients eventually died. Risk factors that were significantly associated with mortality were low weight (odds ratio [OR] = 7.8, <i>P</i> = .005), preoperative bilirubin level (OR = 7.4, <i>P</i> = .007), use of deep hypothermic circulatory arrest (OR = 4.6, <i>P</i> = .031), tricuspid regurgitation grade (OR = 3.8, <i>P</i> = .050), and pulmonary artery hypertension (OR = 10.5, <i>P</i> = .001). Mean follow up for the study cohort was 2189 ± 538 days. One patient has mild flow acceleration across the anastomosis with a gradient of 5/3 mm Hg without any symptoms. The remainder of the patients are alive with excellent clinical as well as echocardiographic outcome.ConclusionThe presentation of infants with obstructed infracardiac TAPVC beyond one month of age is very rare. However, timely intervention can provide acceptable early and excellent late outcomes in this rare patient cohort.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"462-468"},"PeriodicalIF":0.0,"publicationDate":"2025-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143049387","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Surgical Repair of the Aorta in a Neonate With Arterial Tortuosity Syndrome.","authors":"Yuriy Y Kulyabin, Dmitriy S Zemel, Nataliya R Nichay, Alexey N Arkhipov, Darya A Dulceva, Ilya A Soynov","doi":"10.1177/21501351251322161","DOIUrl":"10.1177/21501351251322161","url":null,"abstract":"<p><p>Arterial tortuosity syndrome (ATS) is an autosomal-recessive genetic connective tissue disorder that affects the aorta and medium-sized arterial vessels.¹ We report a case of successful surgical management of the descending aorta in a ten-day-old patient with ATS who presented with multiorganic failure. The aortic reconstruction with a pulmonary homograft patch was performed using full-flow body perfusion.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"551-553"},"PeriodicalIF":0.0,"publicationDate":"2025-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143702412","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Invited Commentary: Kommerell Diverticulum-The Definitive Alternative.","authors":"Carl L Backer","doi":"10.1177/21501351251335641","DOIUrl":"10.1177/21501351251335641","url":null,"abstract":"","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"450-451"},"PeriodicalIF":0.0,"publicationDate":"2025-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144113303","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Liposomal Bupivacaine Versus Plain Bupivacaine for Pain Control Following Congenital Cardiac Surgery.","authors":"Brandon M Tanner, Jeremy Herrmann, Riad Lutfi, Mouhammad Yabrodi, Rania K Abbasi","doi":"10.1177/21501351241293157","DOIUrl":"10.1177/21501351241293157","url":null,"abstract":"<p><p>BackgroundPain control following cardiac surgery can be challenging, and inadequate pain control is associated with postoperative complications. Liposomal bupivacaine can improve postoperative pain control due to its prolonged duration compared with plain bupivacaine. However, there is a paucity of data regarding its efficacy in congenital cardiac surgery. The primary outcome was to compare opioid requirements between liposomal bupivacaine and plain bupivacaine for local infiltration in pediatric patients undergoing cardiac surgical procedures via a median sternotomy approach. Secondary outcomes included antiemetic use, adjunct pain medication use, length of stay, and pain scores.MethodsThis single center retrospective study analyzed data from 2017 to 2022 involving patients who underwent congenital cardiac surgery via median sternotomy. Sixty-three patients who received liposomal bupivacaine were matched with 33 patients who received plain bupivacaine. Patient data were extracted from the electronic medical record and underwent statistical analysis using Wilcoxon, χ², and Fisher exact tests.ResultsThere were no demographic differences between the two groups. Postoperative opioid use did not differ significantly between the liposomal bupivacaine and plain bupivacaine groups. The liposomal bupivacaine group had increased acetaminophen and antiemetic use, while the plain bupivacaine group had increased ketorolac use. Otherwise, there were no significant differences in secondary outcomes, including length of stay.ConclusionLiposomal bupivacaine may not offer any advantage over plain bupivacaine in congenital cardiac postoperative pain control.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"478-482"},"PeriodicalIF":0.0,"publicationDate":"2025-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142635461","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Three-Dimensional Printed Cardiac Models Demonstrating Extensive Cardiac Calcification Assist in Preprocedural Planning.","authors":"Ross Foley, Kevin Walsh, Eoin O'Cearbhaill, Colin J McMahon","doi":"10.1177/21501351241313319","DOIUrl":"10.1177/21501351241313319","url":null,"abstract":"<p><p>Cardiac calcification is common in adults with congenital heart disease, typically affecting surgical sites and prosthetic material. Understanding the precise location and degree of calcification is important during the decision-making process prior to possible intervention but can be difficult to determine in different imaging modalities. Advances in three-dimensional (3D) modeling and printing have made it possible to distinguish different tissue types and accurately display them in different colors on printed models. We present two adult congenital heart disease patients where advanced 3D printing was used to demonstrate cardiac calcification and aided the preprocedural planning process.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"543-546"},"PeriodicalIF":0.0,"publicationDate":"2025-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143257715","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Right Atrial Rhabdomyosarcoma; 35-Year Disease-Free Survival Following Radical Resection With Right Internal Thoracic Artery Bypass.","authors":"Aeleia F Hughes, Genevieve Yedlicka, Gurion Lantz, Randall Caldwell, John W Brown","doi":"10.1177/21501351251318723","DOIUrl":"10.1177/21501351251318723","url":null,"abstract":"<p><p>Cardiac rhabdomyosarcomas (RMS) are rare malignant tumors of the heart with a poor prognosis, even when appropriate treatment regimens are initiated. We present the case of a 12-year-old male who underwent radical resection of a right atrial mass, which was confirmed to be a primary cardiac RMS. He has received regular follow-up for the last 35 years, representing what is to our knowledge the longest reported disease-free survival in a patient with a primary cardiac RMS.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"528-529"},"PeriodicalIF":0.0,"publicationDate":"2025-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"143525758","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}