World journal for pediatric & congenital heart surgery最新文献

{"title":"The Congenital Heart Surgeons' Society Center for Research and Quality 2025 Annual Report.","authors":"Jeffrey Phillip Jacobs, William M DeCampli, Hani K Najm, Osami Honjo, Bahaaldin Alsoufi, Tara Karamlou, Anusha Jegatheeswaran, James D St Louis, Linda M Lambert, Cedric Manlhiot, S Ram Kumar, Alison Howell, James K Kirklin, Christo I Tchervenkov, Erle H Austin, David M Overman, Joseph A Dearani, Jennifer C Romano, Lars G Svensson, William G Williams, Marshall Lewis Jacobs, Eugene H Blackstone, Robert D B Jaquiss","doi":"10.1177/21501351261477040","DOIUrl":"https://doi.org/10.1177/21501351261477040","url":null,"abstract":"<p><p>The Congenital Heart Surgeons' Society (CHSS) is viewed by many as one of the most prestigious professional societies dedicated to pediatric and congenital cardiac surgery. The CHSS Center for Research and Quality (CRQ) Fall 2025 Work Weekend was held in Chicago on Saturday, October 25, 2025. The purpose of this article is to summarize the proceedings of the CHSS CRQ Fall 2025 Work Weekend and to provide a 2025 Annual Report of the CHSS CRQ. At the CHSS CRQ Fall 2025 Work Weekend, multiple topics were discussed related to ongoing CHSS research and quality initiatives. The CHSS CRQ is evolving to keep pace with the rapid evolution of medical informatics and the ever-evolving regulatory issues of clinical research. This 2025 Annual Report of the CHSS CRQ summarizes some of the ongoing initiatives at CHSS CRQ designed to assure that the CHSS CRQ continues to lead innovative and collaborative clinical research to improve pediatric and congenital cardiac care.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351261477040"},"PeriodicalIF":0.0,"publicationDate":"2026-10-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"149187210","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"The Fontan Procedure in Patients with Single-Lung Physiology: Insights from a Case Report and Scoping Review.","authors":"Albert Franz Guerrero-Becerra, Andrés Felipe Rubio-Duarte, Estefania Alejandra Fontecha-Vargas, Diego Márquez-Bohorquez","doi":"10.1177/21501351261491199","DOIUrl":"https://doi.org/10.1177/21501351261491199","url":null,"abstract":"<p><p>The Fontan operation represents the third stage of single-ventricle palliation and requires optimal cardiovascular and pulmonary conditions to achieve success. We report a 6-year-old boy with tricuspid atresia, pulmonary atresia, and functional single-lung circulation secondary to severe left pulmonary artery (LPA) hypoplasia and disconnection after previous palliation. Following comprehensive clinical, hemodynamic, and anatomic evaluation, including unsuccessful attempts at LPA recruitment, the patient underwent an extracardiac fenestrated single-lung Fontan procedure. At 2 years of follow-up, he remained in good functional status without Fontan-related complications or the need for reintervention. Additionally, we present a scoping review of published case reports and case series of children with single-lung physiology undergoing the Fontan procedure, focusing on early and follow-up survival. This case, together with the available literature, suggests that single-lung Fontan completion may be feasible in carefully selected patients following meticulous multidisciplinary evaluation, although long-term outcomes remain uncertain.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351261491199"},"PeriodicalIF":0.0,"publicationDate":"2026-10-14","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"149187282","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Single-Ventricle Physiology as a Dominant Determinant of Mortality, Resource Utilization, and Pulmonary Vein Reintervention in Total Anomalous Pulmonary Venous Connection: A Large Multicenter Study.","authors":"Darren Turner, Amir Mehdizadeh-Shrifi, Blue Lee, Hosam F Ahmed, Grant Chappell, Sarosh Batlivala, David Lehenbauer, Awais Ashfaq, David L S Morales, Marco Ricci","doi":"10.1177/21501351261472486","DOIUrl":"https://doi.org/10.1177/21501351261472486","url":null,"abstract":"<p><p>BackgroundChildren with single ventricle (SV) physiology and total anomalous pulmonary venous connection (TAPVC) face high surgical risk. Despite advances in single ventricle care, survival in SV/TAPVC patients has plateaued. We investigated multicenter outcomes, reintervention rates, and healthcare burden in this complex population.MethodsThe Pediatric Health Information System was queried for TAPVC repairs (2015-2024). Infants were stratified by single-ventricle versus biventricular (BiV) anatomy.ResultsAmong 1258 infants undergoing TAPVC repair, 10% (N = 120) had SV and 90% (N = 1138) had BiV anatomy. SV/TAPVC patients showed higher prematurity (11% [13/120] vs 8% [91/1138], <i>P</i> < .001), low birthweight (14% [17/120] vs 9% [102/1138], <i>P</i> < .001), and neurologic abnormalities (13% [16/120] vs 5% [60/1138], <i>P</i> < .001). Postoperatively, SV/TAPVC had increased delayed sternal closure (11% [13/120] vs 4% [45/1138], <i>P</i> < .001) and ECMO use (7% [8/120] vs 3% [34/1138], <i>P</i> < .001). Healthcare burden was substantially higher in SV/TAPVC children: 5-fold longer hospitalizations (102 vs 29 days, <i>P</i> < .001), 6-fold more hospital visits (6 vs 1, <i>P</i> < .001), and 5-fold higher costs ($1,019,390 vs $259,303, <i>P</i> < .001). Survival at 1 year after repair was severely reduced (SV: 52% vs BiV: 88%, <i>P</i> < .001). Pulmonary vein reinterventions were substantially higher (12-month cumulative incidence: 32% vs 5%, <i>P</i> < .001). Single ventricle physiology was a strong mortality predictor (HR: 3.69, <i>P</i> < .001), particularly pulmonary atresia with intact septum (HR: 6.62, <i>P</i> < .001) and hypoplastic left heart syndrome (HR: 4.42, <i>P</i> < .001).ConclusionsSingle ventricle physiology remains a powerful predictor of adverse outcome in children with TAPVC, with 1-year survival rates approaching 50%. Children with SV/TAPVC face substantially longer hospitalizations, higher reintervention rates, higher hospital visits, and overall 5-fold greater healthcare costs.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351261472486"},"PeriodicalIF":0.0,"publicationDate":"2026-10-14","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"149187270","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Effect of Postoperative Arrhythmia in Children Less Than 18 Years of Age Following Congenital Cardiac Surgery: A Prospective Study.","authors":"Raheja D, Sahu Mk, Khan Ms, Singh Sp, Talwar S, Devagourou V","doi":"10.1177/21501351261472478","DOIUrl":"https://doi.org/10.1177/21501351261472478","url":null,"abstract":"<p><p>BackgroundPostoperative arrhythmias are common among children after congenital cardiac surgery, potentially compromising hemodynamic stability and postoperative recovery. This study aimed to assess the impact of arrhythmias on hemodynamics and clinical outcomes.Material and MethodsThree hundred and twenty-nine children under 18 years of age undergoing congenital cardiac surgery were studied prospectively. In addition to standard postoperative hemodynamic monitoring, electrical cardiometry (ICON^®) was used to assess hemodynamic parameters across time points (prearrhythmia, during arrhythmia, and postarrhythmia). Repeated measures were analyzed using Friedman test followed by Wilcoxon signed-rank test with Bonferroni correction for pairwise comparisons. Poisson regression with robust variance estimation was used to identify independent predictors and calculate incidence rate ratios (IRR).ResultsPostoperative arrhythmias occurred in 53/329 patients (16.1%). Junctional ectopic tachycardia (34%, [18/53]) and supraventricular tachycardia (30.2%, [16/53]) were the most common. Arrhythmias were associated with low cardiac output (IRR 3.43; 95% confidence interval [CI] 2.27-5.17; <i>P</i> < .001), ventricular dysfunction (IRR 2.55; <i>P</i> < .001), acute kidney injury (IRR 2.01; <i>P</i> = .006), and liver dysfunction (IRR 4.56; <i>P</i> = .002) on unadjusted analysis. However, these associations were attenuated after adjustment for prearrhythmia hemodynamic variables like central venous pressure (CVP) and vasoactive-inotropic score (VIS) on multivariable analysis. Elevated CVP, VIS, and hypokalemia were predictors of arrhythmia.ConclusionsArrhythmias occurred in approximately one-sixth of children following congenital cardiac surgery and were associated with adverse hemodynamic changes, organ function, and recovery. However, these associations were attenuated after adjustment for prearrhythmia hemodynamic variables (CVP and VIS), suggesting that arrhythmia may reflect underlying instability rather than a primary causal factor.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351261472478"},"PeriodicalIF":0.0,"publicationDate":"2026-10-12","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"149171672","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Comparative Outcomes of Single-Stage Fontan Procedure Versus Staged Fontan Following Glenn Procedure in Single-Ventricle Patients.","authors":"Panat Kittisit, Janewit Wanichwatphibun, Mueanthep Chomvilailuk, Chayatat Sirinawin, Jule Namchaisiri, Vichai Benjacholamas","doi":"10.1177/21501351261484590","DOIUrl":"https://doi.org/10.1177/21501351261484590","url":null,"abstract":"<p><p>ObjectivesThe role of single-stage Fontan completion, performed without a preceding bidirectional Glenn, remains controversial in late-presenting patients and resource-limited settings. We compared early and midterm outcomes of single-stage and staged Fontan.MethodsThis was a retrospective review of consecutive patients undergoing Fontan completion at a tertiary congenital cardiac center between January 2003 and December 2025. Cohorts were grouped by whether Fontan was direct (single-stage) or after prior bidirectional Glenn (staged). Primary endpoints were in-hospital mortality and 1-year survival; secondary endpoints included complications, intensive care unit (ICU) and hospital stay, and midterm survival.ResultsOf the 118 patients (single-stage n = 66; staged <i>n</i> = 52), single-stage patients were older (median age 11 vs 8 years; <i>P</i> = .002), with higher mean pulmonary artery pressure (14.9 ± 3.4 vs 12.1 ± 3.3 mm Hg; <i>P</i> < .001) and lower ventricular ejection fraction (60% vs 67.5%; <i>P</i> = .01). Despite this, in-hospital mortality (9.1% vs 5.8%; <i>P</i> = .729), Kaplan-Meier 1-year survival (87.6% vs 94.2%; <i>P</i> = .59) and 5-year survival (87.6% vs 92.0%) did not differ. ICU stay (median 4 days), hospital stay (14 vs 15 days), and complications were comparable. Fontan-associated liver disease occurred in 17 of 109 patients (15.6%; 20.3% vs 10.0%; <i>P</i> = .138).ConclusionDespite less favorable baseline hemodynamics, early and midterm outcomes after single-stage Fontan were comparable to staged Fontan. Single-stage Fontan is a reasonable option for appropriately evaluated late-presenting patients in resource-constrained settings; multicenter studies are required to refine selection criteria.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351261484590"},"PeriodicalIF":0.0,"publicationDate":"2026-09-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"149083519","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"A Rare Complete Vascular Ring: Right Aortic Arch, Large Left Sided Patent Ductus Arteriosus, and Isolated Left Subclavian and Vertebral Arteries Mimicking a Double Aortic Arch.","authors":"Hariharan Krishnamurthi, Vijayakumar Raju, Naveen Srinivasan, Kaushik Jothinath, Sridevi Sundarajan, Sanchitha Harini Guruchandrasekar, Antony Terance Benjamin, Vinothkumar Sankaranarayanan Padalingam","doi":"10.1177/21501351261477049","DOIUrl":"https://doi.org/10.1177/21501351261477049","url":null,"abstract":"<p><p>We present the case of a symptomatic 6 month old infant with a very rare form of complete vascular ring caused by a right aortic arch with abnormal branching pattern and a large left-sided patent ductus arteriosus (PDA). The large left sided PDA connected between the main pulmonary artery and the descending thoracic aorta. This configuration in combination with the right aortic arch caused tracheoesophageal compression. In addition, the left subclavian artery (LSA) and left vertebral artery (LVA) were originating from the PDA (Isolated left subclavian and left vertebral artery). This anomaly closely parallels the characteristics observed in a double aortic arch. Successful management was achieved by division of the PDA with re-implantation of the isolated LSA and LVA into the left common carotid artery.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351261477049"},"PeriodicalIF":0.0,"publicationDate":"2026-09-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"149083529","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Composite Hemangioendothelioma of the Right Atrium Presenting With Cardiac Tamponade in an Adolescent.","authors":"Ranjith Chandran, Balaji Srimurugan, Amit Kumar Pandey, Praveen Reddy Bayya, Brijesh P Kottayil","doi":"10.1177/21501351261479337","DOIUrl":"https://doi.org/10.1177/21501351261479337","url":null,"abstract":"<p><p>Primary cardiac vascular tumors are rare in children. We report a 14-year-old girl with hemorrhagic pericardial effusion, cardiac tamponade, and a large right atrial mass. Echocardiogram identified the lesion and tamponade physiology. Pericardial drainage and stabilization preceded computed tomography (CT) and cardiac magnetic resonance imaging. The mass was excised under cardiopulmonary bypass, and the atrial defect was reconstructed with an autologous pericardial patch. Histopathology and immunohistochemistry favored composite hemangioendothelioma of low malignant potential. Postoperative FDG PET-CT showed no residual or metastatic disease. Adjuvant gemcitabine/docetaxel-based chemotherapy was given after multidisciplinary review. Six-month echocardiogram showed no recurrence.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351261479337"},"PeriodicalIF":0.0,"publicationDate":"2026-09-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"149121309","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"A Conduction-Sparing Atrial Patch Placement Technique During Atrioventricular Septal Defect Repair.","authors":"Ahmed Aboelenen, Saif Awlad Thani, Mohammed Tharwat, Shihab Al Mawali, Walid Noureldeen Allithy, Abdullah Al Farqani, Madan Mohan Maddali, Hamood Al Kindi","doi":"10.1177/21501351261480007","DOIUrl":"https://doi.org/10.1177/21501351261480007","url":null,"abstract":"<p><p>BackgroundSurgical repair of atrioventricular septal defect (AVSD) carries a persistent risk of postoperative complete heart block due to the close proximity of the atrioventricular conduction system to the inferior atrial septum during atrial patch placement. We evaluated a modified atrial patch placement technique designed to minimize conduction system injury during AVSD repair.MethodsAll patients undergoing AVSD repair between January 2019 and December 2024 were retrospectively reviewed. Patients were stratified according to the atrial patch placement technique. We evaluated a standard approach involving suturing along the inferior atrial septum adjacent to the hinge of the inferior bridging leaflet to the left of the inferior insertion of the atrial septum within the common junction, versus a modified conduction-sparing approach routing the atrial patch along the right atrial wall and around the orifice of the coronary sinus. The primary outcome was the incidence of postoperative complete heart block requiring permanent pacemaker implantation.ResultsA total of 208 patients underwent AVSD repair. Standard atrial patch placement was used in 132/208 patients (63.5%), and the modified technique was used in 76/208 patients (36.5%). Postoperative complete heart block occurred in 11/132 patients (8.3%) in the standard group and in none of the patients in the modified group. On multivariate analysis, the <b>modified technique</b> remained independently protective (odds ratio 0.022, 95% confidence interval 0.0008-0.61, <i>P</i> = .024).ConclusionsA conduction-sparing atrial patch placement strategy during AVSD repair was associated with the elimination of postoperative complete heart block in this cohort.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351261480007"},"PeriodicalIF":0.0,"publicationDate":"2026-09-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"149121205","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"A Simplified Overview of the Mustard Atrial Switch Operation - Refining the Surgical Technique.","authors":"Vijayakumar Raju, Christopher W Baird","doi":"10.1177/21501351261484528","DOIUrl":"https://doi.org/10.1177/21501351261484528","url":null,"abstract":"<p><p>The Mustard atrial switch procedure has been well documented since the 1960s and is generally considered easier to perform than the Senning procedure. In the current era, the atrial switch operation is primarily indicated as part of the anatomic correction of congenitally corrected transposition of the great arteries or for children with D-Transposition of the great arteries and an intact ventricular septum who present late with a regressed left ventricle, especially in developing regions. There is a scarcity of literature detailing the specific operative steps of the Mustard atrial switch operation. In this article, we present our surgical technique in a clear, step-by-step format, to facilitate understanding and encourage broader adoption within the paediatric cardiac surgical community.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351261484528"},"PeriodicalIF":0.0,"publicationDate":"2026-09-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"149121295","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Pulmonary Hemorrhage Due to Major Aortopulmonary Collateral Arteries Following the Arterial Switch Operation.","authors":"Brooke I Bauman, Harold M Burkhart, Arshid Mir, Christine Allen, Neil M Venardos, Subhrajit Lahiri","doi":"10.1177/21501351261472485","DOIUrl":"https://doi.org/10.1177/21501351261472485","url":null,"abstract":"<p><p>Major aortopulmonary collateral arteries (MAPCAs) are atypical in patients with transposition of the great arteries, with hemoptysis being an exceedingly rare complication. We present 2 cases of neonates undergoing arterial switch operations with postoperative courses complicated by significant hemoptysis. Both were managed successfully with MAPCA occlusion via cardiac catheterization. In the setting of hemoptysis in patients with transposition of the great arteries, clinicians should consider major aortopulmonary collaterals as a contributing factor.</p>","PeriodicalId":94270,"journal":{"name":"World journal for pediatric & congenital heart surgery","volume":" ","pages":"21501351261472485"},"PeriodicalIF":0.0,"publicationDate":"2026-09-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"149083588","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}