NeuropadiatriePub Date : 1979-02-01DOI: 10.1055/s-0028-1085314
T Nakano, H Sakai, J Kinoshita, S Yagishita, Y Itoh
{"title":"The fine structure of blood cells in ceroid-lipofuscinosis (Spielmeyer-Vogt's disease).","authors":"T Nakano, H Sakai, J Kinoshita, S Yagishita, Y Itoh","doi":"10.1055/s-0028-1085314","DOIUrl":"https://doi.org/10.1055/s-0028-1085314","url":null,"abstract":"<p><p>Peripheral blood and bone marrow in a case of juvenile type of Spielmeyer-Vogt's disease were examined with the light and electron microscope for the occurrence of curvilinear profile (CLP), rectilinear profile (RLP), finger-print profile (FPP) and other inclusions. A large quantity of parallel tubular arrays (PTAs) and a few CLPs, RLPs and FPPs were present in the cytoplasm of the lymphocytes. In addition, many plasma cells in the bone marrow contained FPPs, RLPs and CLPs in the vacuoles of their cytoplasm. The other relevant inclusions were observed in the cytoplasm of the bone marrow cells. Moreover, amorphous or membranous inclusions with rectilinear or curvilinear profiles were seen in some vacuoles in the cytoplasm of many erythrocytes. The incidence of these characteristic inclusions in the plasma cells or the erythrocytes were not described nor the present. The correlation and the diagnostic significance of these characteristic inclusions were discussed.</p>","PeriodicalId":76211,"journal":{"name":"Neuropadiatrie","volume":"10 1","pages":"56-66"},"PeriodicalIF":0.0,"publicationDate":"1979-02-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1055/s-0028-1085314","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"11433956","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
NeuropadiatriePub Date : 1979-02-01DOI: 10.1055/s-0028-1085311
A Lundberg
{"title":"The drawing test -- a tool for assessment of arm-hand function in children of 1--3 years of age.","authors":"A Lundberg","doi":"10.1055/s-0028-1085311","DOIUrl":"https://doi.org/10.1055/s-0028-1085311","url":null,"abstract":"<p><p>The construction and evaluation of a simple drawing test for assessment of arm-hand function in children of 1--3 years of age are described. A thick crayon (1.2 x 10 cm) and a piece of white paper (20 x 30 cm) are the only equipment needed. The need, when assessing fine motor development, of a test for evaluation of arm-hand function and the advantages of the test described are discussed. It is concluded that the method is of diagnostic value in children with CNS and neuromuscular disorders and is a useful tool for clinical studies and for routine developmental examination.</p>","PeriodicalId":76211,"journal":{"name":"Neuropadiatrie","volume":"10 1","pages":"29-34"},"PeriodicalIF":0.0,"publicationDate":"1979-02-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1055/s-0028-1085311","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"11785471","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
NeuropadiatriePub Date : 1979-02-01DOI: 10.1055/s-0028-1085308
F G Jung
{"title":"Ad libitum food intake of newborns cumulatively registered by a food dispenser.","authors":"F G Jung","doi":"10.1055/s-0028-1085308","DOIUrl":"https://doi.org/10.1055/s-0028-1085308","url":null,"abstract":"newborns food dispenser cumulative intake curves Pudel disturbance in satiation and appetite control obesity","PeriodicalId":76211,"journal":{"name":"Neuropadiatrie","volume":"10 1","pages":"3-9"},"PeriodicalIF":0.0,"publicationDate":"1979-02-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1055/s-0028-1085308","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"11785472","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Abstracts of the 1979 Meeting of the European Federation of Child Neurology Societies in Brussels.","authors":"","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76211,"journal":{"name":"Neuropadiatrie","volume":"10 Suppl ","pages":"402-64"},"PeriodicalIF":0.0,"publicationDate":"1979-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"11266394","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
NeuropadiatriePub Date : 1978-11-01DOI: 10.1055/s-0028-1091491
J Hamer
{"title":"Removal of craniopharyngioma by subnasal-transsphenoidal operation.","authors":"J Hamer","doi":"10.1055/s-0028-1091491","DOIUrl":"https://doi.org/10.1055/s-0028-1091491","url":null,"abstract":"<p><p>Two children with transsphenoidal microneurosurgical extirpation of a craniopharyngioma are presented. The value of this relatively new surgical approach is demonstrated, and the indication for transsphenoidal microsurgery in selected cases of craniopharyngioma is discussed in relation to the hitherto few similar case reports in the pertinent literature. The subnasal-transsphenoidal approach is the operative method of choice in purely or mainly intrasellar craniopharyngioma. This operation is also indicated in combined intra- and suprasellar craniopharyngiomas where the solid portion of the tumor is located intrasellarly and where the cystic part extends suprasellarly. In addition, the transsphenoidal operation may be a safe procedure in emergency cases with rapid loss of vision provided that the craniopharyngioma does not have a purely supra- and parasellar expansion. The esseential prerequisite for transsphenoidal neurosurgery in craniopharyngioma is an enlarged sella turcica. The importance of computerized cranial tomography with regard to preoperative differential diagnosis of a predominantly solid or cystic lesion and to postoperative control of radical tumor excision is emphasized. It is assumed that 25% of all patients with craniopharyngioma could benefit from transsphenoidal operation.</p>","PeriodicalId":76211,"journal":{"name":"Neuropadiatrie","volume":"9 4","pages":"312-9"},"PeriodicalIF":0.0,"publicationDate":"1978-11-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1055/s-0028-1091491","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"11785211","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
NeuropadiatriePub Date : 1978-11-01DOI: 10.1055/s-0028-1091497
K Bergström, B Bille
{"title":"Computed tomography of the brain in children with minimal brain damage: a preliminary study of 46 children.","authors":"K Bergström, B Bille","doi":"10.1055/s-0028-1091497","DOIUrl":"https://doi.org/10.1055/s-0028-1091497","url":null,"abstract":"<p><p>Forty-six children aged 4 to 15 years with minimal brain damage (MBD) underwent computed cranial tomography (CT). The criteria used for a diagnosis of MDB was the presence of clinical features of a developmental disturbance of the central nervous system causing incoordination. CT revealed abnormalities in 15 cases (32.6%), consisting in cerebral atrophy, asymmetry or an anomaly.</p>","PeriodicalId":76211,"journal":{"name":"Neuropadiatrie","volume":"9 4","pages":"378-84"},"PeriodicalIF":0.0,"publicationDate":"1978-11-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1055/s-0028-1091497","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"11785214","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
NeuropadiatriePub Date : 1978-11-01DOI: 10.1055/s-0028-1091495
L von Wendt, S Similä, A Hirvasniemi, E Suvanto
{"title":"Altered levels of various amino acids in blood plasma and cerebrospinal fluid of patients with nonketotic hyperglycinemia.","authors":"L von Wendt, S Similä, A Hirvasniemi, E Suvanto","doi":"10.1055/s-0028-1091495","DOIUrl":"https://doi.org/10.1055/s-0028-1091495","url":null,"abstract":"Similä Visakorpi Seppäläinen Simila von Wendt","PeriodicalId":76211,"journal":{"name":"Neuropadiatrie","volume":"9 4","pages":"360-8"},"PeriodicalIF":0.0,"publicationDate":"1978-11-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1055/s-0028-1091495","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"11785213","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
NeuropadiatriePub Date : 1978-11-01DOI: 10.1055/s-0028-1091493
J A Luijten, W Straks, L F Blikkendaal-Lieftinck, G E Staal, J Willemse
{"title":"Metachromatic leukodystrophy: a comparative study of the ultrastructural findings in the peripheral nervous system of three cases, one of the late infantile, one of the juvenile and one of the adult form of the disease.","authors":"J A Luijten, W Straks, L F Blikkendaal-Lieftinck, G E Staal, J Willemse","doi":"10.1055/s-0028-1091493","DOIUrl":"https://doi.org/10.1055/s-0028-1091493","url":null,"abstract":"<p><p>The ultrastructural findings in the peripheral nerve of three cases of M. L. D., namely of the late infantile, the juvenile and the adult form are described. The pathological changes consist of two phenomena: segmental demyelination and lysosomal storage of sulfatides, both probably separate results of a deficiency of the enzyme Arylsulfatase A. Some differences are found in the degree of segmental demyelination and the type of lysosomal storage products. A possible relation between these differences and the supposed difference in the defect of the enzyme Arylsulfatase A, responsible for the different subtypes of the disease, is postulated.</p>","PeriodicalId":76211,"journal":{"name":"Neuropadiatrie","volume":"9 4","pages":"338-50"},"PeriodicalIF":0.0,"publicationDate":"1978-11-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1055/s-0028-1091493","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"11433239","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
NeuropadiatriePub Date : 1978-11-01DOI: 10.1055/s-0028-1091490
G Gross-Selbeck, W Ebell, H Doose
{"title":"Galvanic skin response in photosensitive children.","authors":"G Gross-Selbeck, W Ebell, H Doose","doi":"10.1055/s-0028-1091490","DOIUrl":"https://doi.org/10.1055/s-0028-1091490","url":null,"abstract":"<p><p>Investigations of galvanic skin response under stress by different stimuli were carried out in 65 photosensitive and 70 non-photosensitive subjects aged 11--17 years. Photosensitive individuals at the age of 12--15 years showed a more pronounced skin reaction than non-photosensitive ones. The emotional reagibility (expressed by IE = (SEE TEXT), Traxel 1960, Stocksmeier and Langosch 1973) shows significantly higher values than in nonphotosensitive children. In addition to this, photosensitive subjects demonstrate a delayed habituation. Together with further results (Gross-Selbeck et al. 1976) the findings indicate that photosensitivity is not the isolated symptom of a genetically determined increased cerebral excitability, which can represent a factor in the pathogenesis of epilepsy for instance, but must be understood as a special characteristic of a particular constitution.</p>","PeriodicalId":76211,"journal":{"name":"Neuropadiatrie","volume":"9 4","pages":"303-11"},"PeriodicalIF":0.0,"publicationDate":"1978-11-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1055/s-0028-1091490","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"11785210","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}