European Journal of Pediatric Surgery Reports最新文献_第3页

Upper Ureteral Reconstruction with a Tapered Descending Colon after Failed Pyeloplasties in a 13-Year-Old Boy. 13岁男孩肾盂成形术失败后输尿管上段以锥形降结肠重建一例。

IF 0.6

European Journal of Pediatric Surgery Reports Pub Date : 2023-01-01 DOI: 10.1055/a-2035-4637

Hideaki Nakajima, Hiroyuki Koga, Seitaro Kosaka, Mao Ikari, Geoffrey J Lane, Atsuyuki Yamataka

{"title":"Upper Ureteral Reconstruction with a Tapered Descending Colon after Failed Pyeloplasties in a 13-Year-Old Boy.","authors":"Hideaki Nakajima, Hiroyuki Koga, Seitaro Kosaka, Mao Ikari, Geoffrey J Lane, Atsuyuki Yamataka","doi":"10.1055/a-2035-4637","DOIUrl":"https://doi.org/10.1055/a-2035-4637","url":null,"abstract":"An 11-year-old boy was referred for further management of a 6-cm-long grossly stenosed ureter following two failed left ureteropelvic junction (UPJ) obstruction repairs elsewhere. A tapered segment of the descending colon (TDC) was used successfully for ureteral reconstruction. The UPJ was exposed through a left flank incision. The stenosed segment was excised; both ends appeared severely inflamed and thickened. Tissue interposition was required and ureteroplasty with a TDC was performed by incising the peritoneum adjacent to the excised ureter to mobilize the descending colon to the retroperitoneal space. To prepare the TDC, an 8-cm segment of the colon with intact blood vessels was isolated, tapered, and sutured into a funnel shape using a 14-Fr catheter as a temporary stent. After colocolostomy, the colon was returned to the abdominal cavity, the peritoneum was closed carefully to prevent vascular compromise, and the TDC was anastomosed to the ureter and renal calyx with interrupted absorbable sutures. A double J stent (DJS) and percutaneous nephrostomy tube were placed. Postoperative recovery was uneventful. The DJS was removed on day 50 after confirming smooth urine flow through both the ureter-TDC and calyx-TDC anastomoses. Diuretic renography performed 68 days postoperatively was unobstructed. The patient is currently well after 12 months follow-up. This would appear to be the first report of a TDC being used to create a funnel-shaped segment to reconstruct a long, grossly stenosed ureter. The TDC is simpler than the re-tubularizing colon but requires monitoring for postoperative mucus-related complications and malignant transformation.","PeriodicalId":43204,"journal":{"name":"European Journal of Pediatric Surgery Reports","volume":null,"pages":null},"PeriodicalIF":0.6,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10085642/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"9304516","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Congenital Internal Jugular Phlebectasia: An Anomaly Still Poorly Recognized. 先天性颈内静脉扩张:一种仍未被充分认识的异常。

IF 0.6

European Journal of Pediatric Surgery Reports Pub Date : 2023-01-01 DOI: 10.1055/a-2130-3269

Alessandro Raffaele, Marta Gazzaneo, Piero Romano, Maria Sole Prevedoni Gorone, Luigi Avolio

{"title":"Congenital Internal Jugular Phlebectasia: An Anomaly Still Poorly Recognized.","authors":"Alessandro Raffaele, Marta Gazzaneo, Piero Romano, Maria Sole Prevedoni Gorone, Luigi Avolio","doi":"10.1055/a-2130-3269","DOIUrl":"https://doi.org/10.1055/a-2130-3269","url":null,"abstract":"Congenital internal jugular phlebectasia (CIJP) is a rare condition characterized by congenital dilatation of the vein without tortuosity that becomes more evident during straining as a lateral neck mass. CIJP often remains undiagnosed from a few months to several years after the onset of the swelling. It is frequently asymptomatic although symptomatic cases have been occasionally reported. We present the case of a healthy 7-year-old boy with a lateral neck mass, triggered by the Valsalva maneuver. Neck ultrasound (US) showed right internal jugular axial ectasia, increasing during the Valsalva maneuver; contrast computed tomography (CT) scan confirmed a fusiform dilatation of the right internal jugular vein. Due to the lack of symptoms, we treated our patient conservatively. At 5 years of follow-up, the patient is still asymptomatic, with no evidence of complications or thrombosis. Due to its self-limiting nature, treatment for asymptomatic cases of CIJP should be conservative, providing a follow-up with both clinical and US annual evaluations.","PeriodicalId":43204,"journal":{"name":"European Journal of Pediatric Surgery Reports","volume":null,"pages":null},"PeriodicalIF":0.6,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10471426/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"10142883","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Combined Pre- and Postnatal Minimally Invasive Approach to a Complex Symptomatic Congenital Pulmonary Airway Malformation. 产前产后联合微创治疗复杂症状性先天性肺气道畸形。

IF 0.6

European Journal of Pediatric Surgery Reports Pub Date : 2023-01-01 DOI: 10.1055/a-2107-0409

Francesco Macchini, Stefano Mazzoleni, Giacomo Cavallaro, Nicola Persico, Irene Borzani, Ernesto Leva

{"title":"Combined Pre- and Postnatal Minimally Invasive Approach to a Complex Symptomatic Congenital Pulmonary Airway Malformation.","authors":"Francesco Macchini, Stefano Mazzoleni, Giacomo Cavallaro, Nicola Persico, Irene Borzani, Ernesto Leva","doi":"10.1055/a-2107-0409","DOIUrl":"https://doi.org/10.1055/a-2107-0409","url":null,"abstract":"Congenital pulmonary airway malformation (CPAM) is a rare congenital lung lesion that usually remains asymptomatic during the fetal and neonatal period. However, it can occasionally cause prenatal cardiocirculatory failure and fetal hydrops, requiring a thoraco-amniotic shunt (TAS) placement. In other cases, it can also cause symptoms at birth (such as respiratory distress) and may require urgent surgical intervention. Thoracoscopic lobectomy for neonates is rarely reported. Here, we report a case of right macrocystic CPAM causing fetal hydrops at 27 weeks of gestation. The fetus was treated with a TAS placement that successfully resolved the hydrops. At 39 weeks of gestation, a male neonate was born (weight 2,850 g). The TAS spontaneously displaced during delivery, causing an open pneumothorax (PNX), initially treated with a drainage. His condition gradually worsened, requiring ventilatory support. Computed tomography (CT) scan showed different giant cysts in the context of the right lower lobe, left mediastinal shift, and compression of the rest of the lung. An urgent surgical management was required. A thoracoscopic right lower lobectomy was performed at 10 days of life (weight 2,840 g). The postoperative course was uneventful; the child remained totally asymptomatic and showed a good recovery. To the best of our knowledge, this is the first reported case of open iatrogenic PNX following TAS positioning and the second of neonatal thoracoscopic lobectomy in a newborn weighting less than 3 kg. The purpose of this report is to indicate that minimally invasive surgery is feasible, safe, and effective for the resection of CPAM, even in small newborns.","PeriodicalId":43204,"journal":{"name":"European Journal of Pediatric Surgery Reports","volume":null,"pages":null},"PeriodicalIF":0.6,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10370641/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"10263729","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Successful Sirolimus Treatment for Recurrent Pericardial Effusion in a Large Cervicomediastinal Provisionally Unclassified Vascular Anomaly: A Case Report. 西罗莫司成功治疗颈纵隔大血管异常复发性心包积液1例。

IF 0.6

European Journal of Pediatric Surgery Reports Pub Date : 2023-01-01 DOI: 10.1055/a-2057-7177

Julio César Moreno-Alfonso, María San Basilio Berenguer, María Del Carmen Sarmiento Caldas, Jesús González Cayón, Santiago de la Puente, Paloma Triana, Juan Carlos López-Gutiérrez

{"title":"Successful Sirolimus Treatment for Recurrent Pericardial Effusion in a Large Cervicomediastinal Provisionally Unclassified Vascular Anomaly: A Case Report.","authors":"Julio César Moreno-Alfonso, María San Basilio Berenguer, María Del Carmen Sarmiento Caldas, Jesús González Cayón, Santiago de la Puente, Paloma Triana, Juan Carlos López-Gutiérrez","doi":"10.1055/a-2057-7177","DOIUrl":"https://doi.org/10.1055/a-2057-7177","url":null,"abstract":"Provisionally unclassified vascular anomalies (PUVA) are a group of diseases with unique characteristics that make them unclassifiable within vascular tumors or malformations. We describe a PUVA as the cause of recurrent pericardial effusion and its response to sirolimus. A 6-year-old girl was referred with a cervicothoracic vascular anomaly, a violaceous, and irregular lesion in the neck and upper chest, diagnosed as \"hemangioma\". She had pericardial effusion at the neonatal age that required pericardiocentesis, propranolol, and corticosteroids. She remained stable for 5 years, when she presented with a severe pericardial effusion. A magnetic resonance visualized a diffuse vascular image in the cervical and thoracic region with mediastinal extension. The pathological study showed a vascular proliferation in the dermis and hypodermis with positive staining for Wilms' Tumor 1 Protein (WT1) and negative for Glut-1. Genetic testing found a variant in GNA14 , for which the diagnosis of PUVA was established. When a pericardial drain was placed without response, treatment with sirolimus was started with resolution of the effusion. Sixteen months later, the malformation is stable and there has been no recurrence of pericardial effusion. In a significant group of patients, definitive diagnosis is not possible despite pathological and genetic analysis. Mammalian target of rapamycin inhibitors may become a therapeutic option if symptoms are severe enough, with a low rate of reported side effects.","PeriodicalId":43204,"journal":{"name":"European Journal of Pediatric Surgery Reports","volume":null,"pages":null},"PeriodicalIF":0.6,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10191730/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"9868952","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Hyperspectral Imaging-A Novel Tool to Assess Tissue Perfusion and Oxygenation in Esophageal Anastomoses. 高光谱成像-一种评估食管吻合口组织灌注和氧合的新工具。

IF 0.6

European Journal of Pediatric Surgery Reports Pub Date : 2023-01-01 DOI: 10.1055/s-0043-1769106

Duarte Vaz Pimentel, Larissa Merten, Jan-Hendrik Gosemann, Ines Gockel, Boris Jansen-Winkeln, Steffi Mayer, Martin Lacher

引用次数: 0

Cloacal Malformation with Associated Urethral Atresia. 阴腔畸形伴尿道闭锁。

IF 0.6

European Journal of Pediatric Surgery Reports Pub Date : 2023-01-01 DOI: 10.1055/s-0043-1761206

Tamador Al-Shamaileh, Laura Tiusaba, Shimon Eric Jacobs, Teresa Lynn Russell, Elizaveta Bokova, Hans G Pohl, Briony K Varda, Christina Ho, Christina Feng, Andrea Badillo, Marc A Levitt

{"title":"Cloacal Malformation with Associated Urethral Atresia.","authors":"Tamador Al-Shamaileh, Laura Tiusaba, Shimon Eric Jacobs, Teresa Lynn Russell, Elizaveta Bokova, Hans G Pohl, Briony K Varda, Christina Ho, Christina Feng, Andrea Badillo, Marc A Levitt","doi":"10.1055/s-0043-1761206","DOIUrl":"https://doi.org/10.1055/s-0043-1761206","url":null,"abstract":"Introduction Cloacal malformations comprise a heterogeneous group of anomalies that are considered the most complex anorectal malformations (ARMs) in females. Precise evaluation to identify the unique anatomy prior to reconstruction with collaboration between colorectal surgeons, urologists, and gynecologists is vital. Here, we present a rare anatomical variation in a patient with a cloacal malformation which affected operative and postoperative management. Case description A 6-year-old female with cloaca who underwent colostomy, vaginostomy, and vesicostomy as a newborn presented for reconstruction. Her VACTERL workup was negative except for an atretic right kidney. Her ARM index included the cloaca, a normal spine, and sacrum with a lateral sacral ratio of 0.7, predicting good potential for bowel continence. Cystoscopy through the vesicostomy showed a small bladder with normal ureteral orifices, and a closed bladder neck, with no identifiable urethra. A cloacagram showed an atretic common channel, a single small vagina, and a rectum below the pubococcygeal line. The patient underwent a posterior sagittal anorectovaginourethroplasty, vaginal patch using rectum, rectoplasty, and perineal body reconstruction. The urethra was not amenable to reconstruction, so the vesicostomy was preserved and a future Mitrofanoff was planned. Conclusion Urethral atresia is a rare and challenging finding in cloaca patients, and a vesicostomy is needed to drain urine in the newborn period. Preoperative examination under anesthesia, cystoscopy, vaginoscopy, and cloacagram are crucial to identify the precise anatomy and to plan accordingly.","PeriodicalId":43204,"journal":{"name":"European Journal of Pediatric Surgery Reports","volume":null,"pages":null},"PeriodicalIF":0.6,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9904968/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"10678814","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Successful on-ECLS Repair of CDH and Omphalocele in a Newborn. 新生儿CDH和脐膨出的ecls成功修复。

IF 0.6

European Journal of Pediatric Surgery Reports Pub Date : 2023-01-01 DOI: 10.1055/s-0043-1767734

Frank Fideler, Migdad Mustafi, Hans-Joachim Kirschner, Ines Gerbig, Jörg Fuchs, Michael Hofbeck, Matthias Kumpf, Oliver Kagan, Jörg Michel, Walter Jost, Felix Neunhoeffer

{"title":"Successful on-ECLS Repair of CDH and Omphalocele in a Newborn.","authors":"Frank Fideler, Migdad Mustafi, Hans-Joachim Kirschner, Ines Gerbig, Jörg Fuchs, Michael Hofbeck, Matthias Kumpf, Oliver Kagan, Jörg Michel, Walter Jost, Felix Neunhoeffer","doi":"10.1055/s-0043-1767734","DOIUrl":"https://doi.org/10.1055/s-0043-1767734","url":null,"abstract":"Both congenital diaphragmatic hernias (CDHs) and omphaloceles show relevant overall mortality rates as individual findings. The combination of the two has been described only sparsely in the literature and almost always with a fatal course. Here, we describe a term neonate with a rare high-risk constellation of left-sided CDH and a large omphalocele who was successfully treated on extracorporeal life support (ECLS). Prenatally, the patient was diagnosed with a large omphalocele and a left CDH with a lung volume of ∼27% and an observed to expected lung-to-head ratio of 30%. Due to respiratory insufficiency, an ECLS device was implanted. As weaning from ECLS was not foreseeable, the female infant underwent successful surgery on ECLS on the ninth day of life. Perioperative high-frequency oscillatory ventilation and circulatory and coagulation management under point-of-care monitoring were the main anesthesiological challenges. Over the following 3 days, ECLS weaning was successful, and the patient was extubated after another 43 days. Surgical treatment on ECLS can expand the spectrum of therapy in high-risk constellations if potential risks are minimized and there is close interdisciplinary cooperation.","PeriodicalId":43204,"journal":{"name":"European Journal of Pediatric Surgery Reports","volume":null,"pages":null},"PeriodicalIF":0.6,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10085641/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"9304519","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Dirofilaria repens in a Pediatric Patient-First Case Report from Switzerland. Dirofilaria再次出现在一份来自瑞士的儿科患者优先病例报告中。

IF 0.6

European Journal of Pediatric Surgery Reports Pub Date : 2023-01-01 DOI: 10.1055/s-0043-1768706

Rebekka Rose, Kai-Uwe Kleitsch, Diana Born, Pascal Heye

引用次数: 0

A Deeper Curse: A Hirschsprung Patient's Evaluation Unmasks a Rare Association with Congenital Central Hypoventilation Syndrome and Neuroblastoma. 更深的诅咒:一名巨结肠患者的评估揭示了先天性中枢性低通气综合征和神经母细胞瘤的罕见关联。

IF 0.6

European Journal of Pediatric Surgery Reports Pub Date : 2022-11-29 eCollection Date: 2022-01-01 DOI: 10.1055/s-0042-1758826

Shimon Eric Jacobs, Laura Tiusaba, Elizaveta Bokova, Tamador Al-Shamaileh, Teresa Lynn Russell, Emily C Rutan, Harutyun Haroyan, Yong Wang, Christina Feng, Andrea Badillo, Marc A Levitt

引用次数: 0

Successful Treatment of a Single Giant Renal Cyst in a Newborn with Drainage and Sclerotherapy. 引流和硬化疗法成功治疗新生儿单个巨大肾囊肿。

IF 0.6

European Journal of Pediatric Surgery Reports Pub Date : 2022-11-11 eCollection Date: 2022-01-01 DOI: 10.1055/a-1939-4031

Adriana Koenig, Anika Ménétrey, Tobias Jhala, Vincent Uerlings, Philipp O Szavay

引用次数: 0