C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE最新文献

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Chest CT Analysis for Features of Fibrosis in Children with SpC Genetic Mutations SpC基因突变儿童纤维化特征的胸部CT分析
C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4379
E. DeBoer, S. Humphries, J. Weinman, D. Lynch, R. Deterding
{"title":"Chest CT Analysis for Features of Fibrosis in Children with SpC Genetic Mutations","authors":"E. DeBoer, S. Humphries, J. Weinman, D. Lynch, R. Deterding","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4379","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4379","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"13 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123609285","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Pulmonary Function During and After the School-Age in Patients with Swyer-James-Macleod Syndrome: A Single Center Experience 斯威-詹姆斯-麦克劳德综合征患者学龄期间和学龄后的肺功能:单中心经验
C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4377
Jooho Park, Eun-Mi Kim, Boram Lee
{"title":"Pulmonary Function During and After the School-Age in Patients with Swyer-James-Macleod Syndrome: A Single Center Experience","authors":"Jooho Park, Eun-Mi Kim, Boram Lee","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4377","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4377","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"101 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122036718","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Primary Ciliary Dyskinesia (PCD) Diagnostic Testing Before and After Establishment as a PCD Clinical Center 原发性纤毛运动障碍(PCD)临床中心建立前后的诊断测试
C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4381
M. O'Connor, T. J. Hochstetler, N. Vanderbilt, L. R. Young
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引用次数: 0
Evaluation of Inter-Observer Variation for CT Identification of Childhood Interstitial Lung Disease 评价儿童间质性肺疾病CT诊断的观察者间变异
C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4380
Joseph Jacob, C. Owens, A. Brody, T. Semple, T. Watson, A. Calder, P. Garcia-Pena, P. Tomà, A. Devaraj, H. Walton, A. Moreno‐Galdó, P. Aurora, A. Rice, T. Vece, S. Cunningham, A. Wells, A. Nicholson, A. Bush
{"title":"Evaluation of Inter-Observer Variation for CT Identification of Childhood Interstitial Lung Disease","authors":"Joseph Jacob, C. Owens, A. Brody, T. Semple, T. Watson, A. Calder, P. Garcia-Pena, P. Tomà, A. Devaraj, H. Walton, A. Moreno‐Galdó, P. Aurora, A. Rice, T. Vece, S. Cunningham, A. Wells, A. Nicholson, A. Bush","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4380","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4380","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"85 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"132530629","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Ciliary Biopsy Quality Improvement: Before and After Establishment of a Primary Ciliary Dyskinesia (PCD) Clinical Center 睫状体运动障碍(PCD)临床中心建立前后睫状体活检质量的改善
C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4382
T. Curry, J. Atkinson, V. Prasad, L. R. Young, M. O'Connor
{"title":"Ciliary Biopsy Quality Improvement: Before and After Establishment of a Primary Ciliary Dyskinesia (PCD) Clinical Center","authors":"T. Curry, J. Atkinson, V. Prasad, L. R. Young, M. O'Connor","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4382","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4382","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"26 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"131839103","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Pulmonary Manifestations and Outcomes in ANCA Associated Vasculitides: A Single Center Experience ANCA相关血管粥样硬化的肺部表现和预后:单中心经验
C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4378
E. Sayad, D. M. McNeill, D. Spielberg, M. D. Guzman, M. Carmona
{"title":"Pulmonary Manifestations and Outcomes in ANCA Associated Vasculitides: A Single Center Experience","authors":"E. Sayad, D. M. McNeill, D. Spielberg, M. D. Guzman, M. Carmona","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4378","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4378","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"12 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"121611905","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Airway and Airspace Morphometry in Human Pediatric Lung by UltraHRCT and Thick Section Fluorescence Microscopy 应用超hrct和厚层荧光显微镜观察儿童肺部气道和空域形态
C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4372
G. Pryhuber, C. Poole, Daria Krenitsky, T. Baran, T. Foster, H. Huyck, G. Bandyopadhyay, A. Howell, M. Moreland, R. Lisa, J. Dutra, J. Holden-Wiltse, Ravi S. Misra, T. Mariani
{"title":"Airway and Airspace Morphometry in Human Pediatric Lung by UltraHRCT and Thick Section Fluorescence Microscopy","authors":"G. Pryhuber, C. Poole, Daria Krenitsky, T. Baran, T. Foster, H. Huyck, G. Bandyopadhyay, A. Howell, M. Moreland, R. Lisa, J. Dutra, J. Holden-Wiltse, Ravi S. Misra, T. Mariani","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4372","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4372","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"120 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"114331777","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Characterization of Pulmonary Function in Children with Hermansky-Pudlak Syndrome Hermansky-Pudlak综合征患儿肺功能特征分析
C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4375
W. De Jesús-Rojas, E. Rivera
{"title":"Characterization of Pulmonary Function in Children with Hermansky-Pudlak Syndrome","authors":"W. De Jesús-Rojas, E. Rivera","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4375","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4375","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"27 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123362806","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Abnormal Pulmonary Lymphatic Flow in Patients with Lymphatic Anomalies and Respiratory Compromise on MR Lymphangiogram MR淋巴管造影显示淋巴异常和呼吸损害患者的异常肺淋巴流
C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a7386
M. Itkin, D. Rabinowitz, G. Nadolski, P. Stafler, L. Mascarenhas, D. Adams
{"title":"Abnormal Pulmonary Lymphatic Flow in Patients with Lymphatic Anomalies and Respiratory Compromise on MR Lymphangiogram","authors":"M. Itkin, D. Rabinowitz, G. Nadolski, P. Stafler, L. Mascarenhas, D. Adams","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a7386","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a7386","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"23 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128525317","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Pediatric Hematopoietic Stem Cell Transplant Patients' Six-Minute Walk Test Distance Declines at Day 100 but Returns to Baseline by 1-Year Post Transplant 儿童造血干细胞移植患者的6分钟步行测试距离在第100天下降,但在移植后1年恢复到基线
C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4373
C. Towe, A. Chhabra, N. Gloude, K. Foster, L. Walkup, J. Woods, Leann Mount, M. Grimley, S. Davies, K. Myers
{"title":"Pediatric Hematopoietic Stem Cell Transplant Patients' Six-Minute Walk Test Distance Declines at Day 100 but Returns to Baseline by 1-Year Post Transplant","authors":"C. Towe, A. Chhabra, N. Gloude, K. Foster, L. Walkup, J. Woods, Leann Mount, M. Grimley, S. Davies, K. Myers","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4373","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4373","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"68 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"131048349","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 1
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