L. Walkup, K. Myers, A. Nelson, M. Willmering, M. Grimley, S. Davies, C. Towe, J. Woods
{"title":"Longitudinal Hyperpolarized 129Xe MRI Detects Stabilization and Reversibility of Early Lung Ventilation Abnormalities in Pediatric HSCT","authors":"L. Walkup, K. Myers, A. Nelson, M. Willmering, M. Grimley, S. Davies, C. Towe, J. Woods","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4386","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4386","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"213 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"114210833","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
W. Wee, S. Dell, T. To, S. Shapera, P. Chiu, J. Fisher
{"title":"Mortality of Pediatric Surgical Lung Biopsy in Ontario, Canada","authors":"W. Wee, S. Dell, T. To, S. Shapera, P. Chiu, J. Fisher","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4371","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4371","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"36 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128059103","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
P. A. Nourani, M. Maddox, J. Lebensburger, B. Pernell, A. Alishlash
{"title":"Nocturnal Hypoxemia Measured by Polysomnogram Is Associated with Acute Chest Syndrome in a Pediatric Sickle Cell Disease Population","authors":"P. A. Nourani, M. Maddox, J. Lebensburger, B. Pernell, A. Alishlash","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4388","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4388","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"45 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129068236","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
H. Omran, I. Hoeben, T. Noethe-Menchen, L. Jelten, Diana Frank, C. Werner, J. Tebbe, R. Hjeij, B. Dwornicziak, P. Pennekamp, H. Olbrich, N. Loges
{"title":"Recessive DNAH9 Loss-of-Function Mutations Cause Absence of ODAs Type 2 and Only Subtle Respiratory Ciliary Beating Defects","authors":"H. Omran, I. Hoeben, T. Noethe-Menchen, L. Jelten, Diana Frank, C. Werner, J. Tebbe, R. Hjeij, B. Dwornicziak, P. Pennekamp, H. Olbrich, N. Loges","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a7385","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a7385","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"17 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133309186","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Primary Ciliary Dyskinesia (PCD) Registry in Alberta","authors":"R. H. Cohn, I. Amirav","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4383","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4383","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"63 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129809461","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
L. Chen, J. Gong, E. Matta, K. Morrone, D. Manwani, D. Rastogi, A. De
{"title":"Higher Pulmonary Disease Burden among Hispanic Children with Sickle Cell Disease","authors":"L. Chen, J. Gong, E. Matta, K. Morrone, D. Manwani, D. Rastogi, A. De","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4387","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4387","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"3 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"124489718","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
C. Towe, S. Yasin, N. Fall, B. Carey, B. Trapnell, J. Woods, L. Walkup, J. Huggins, E. Morgan, T. Ting, K. Wikenheiser-Brokamp, A. Grom, G. Schulert
{"title":"A Novel Interstitial Lung Disease Associated with Systemic Juvenile Idiopathic Arthritis: Characteristics and Risk Factors","authors":"C. Towe, S. Yasin, N. Fall, B. Carey, B. Trapnell, J. Woods, L. Walkup, J. Huggins, E. Morgan, T. Ting, K. Wikenheiser-Brokamp, A. Grom, G. Schulert","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4374","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4374","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"73 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"124764749","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
S. Saxena, J. Pappas, E. Bracey, K. Smith-Whitley, O. Afolabi‐Brown, J.L. Allen, A. Bhandari
{"title":"Retrospective Cohort Study of Asthma Management in Pediatric Patients with Sickle Cell Disease","authors":"S. Saxena, J. Pappas, E. Bracey, K. Smith-Whitley, O. Afolabi‐Brown, J.L. Allen, A. Bhandari","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4389","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4389","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"5 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"126837069","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
M. Carmona, T. Vogel, S. Marchal, M. Guesmi, J. Dubus, M. Baravalle, S. Leroy, C. Marquette, Alexandre Fabre, V. Barlogis, J. Leiding, L. Forbes, L. Giovannini-Chami
{"title":"Treatment of Interstitial Lung Disease in STAT3 Gain-of-Function Using JAK Inhibitors","authors":"M. Carmona, T. Vogel, S. Marchal, M. Guesmi, J. Dubus, M. Baravalle, S. Leroy, C. Marquette, Alexandre Fabre, V. Barlogis, J. Leiding, L. Forbes, L. Giovannini-Chami","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4376","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4376","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"45 4","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"114032875","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
A. Chhabra, L. Walkup, C. Towe, N. Gloude, K. Foster, Leann Mount, M. Grimley, S. Davies, K. Myers, J. Woods
{"title":"129Xe MRI and Six Minute Walk Test Correlations in Pediatric Patients After Hematopoietic Stem-Cell Transplantation","authors":"A. Chhabra, L. Walkup, C. Towe, N. Gloude, K. Foster, Leann Mount, M. Grimley, S. Davies, K. Myers, J. Woods","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4385","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a4385","url":null,"abstract":"","PeriodicalId":395290,"journal":{"name":"C25. CLINICAL AND TRANSLATIONAL STUDIES IN RARE LUNG DISEASE","volume":"32 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128707766","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}