Clinical Neurology最新文献_第10页

[A case of propriospinal myoclonus at sleep onset in which video-polysomnography with additional surface electromyogram was useful for diagnosis]. [一例睡眠开始时出现本体脊髓肌阵挛的病例，其视频多导睡眠图和附加的表面肌电图有助于诊断]。

Clinical Neurology Pub Date : 2024-11-22 Epub Date: 2024-10-19 DOI: 10.5692/clinicalneurol.cn-001951

Yoko Fujii, Mutsumi Okura, Yaeko Kashiwai, Mitsutaka Taniguchi, Motoharu Ohi

{"title":"[A case of propriospinal myoclonus at sleep onset in which video-polysomnography with additional surface electromyogram was useful for diagnosis].","authors":"Yoko Fujii, Mutsumi Okura, Yaeko Kashiwai, Mitsutaka Taniguchi, Motoharu Ohi","doi":"10.5692/clinicalneurol.cn-001951","DOIUrl":"10.5692/clinicalneurol.cn-001951","url":null,"abstract":"Propriospinal myoclonus at sleep onset (PSM-S) is a sudden myoclonic jerk that occurs during the transition from wakefulness to sleep. It is a sleep-related movement disorder that causes difficulty falling asleep due to involuntary movements that spread caudally and rostrally through the propriospinal tract. Diagnosis requires observation of movements and polysomnography (PSG), and there are few reports. An 80-year-old man was referred to our center for insomnia due to abdominal movements at sleep onset. During the EEG test, we observed the caudal and rostral propagation of movements emanating from the abdomen. Attended video-PSG with additional surface electromyography revealed that myoclonic jerks occurred during the transition from wake to stage N1 and disappeared during sleep stage N2. EMG activity originated from the rectus abdominis muscle, followed by rostral and caudal propagation. Here, we report a case demonstrating that PSG with additional surface electromyography is important and useful for the diagnosis of PMS at sleep onset.","PeriodicalId":39292,"journal":{"name":"Clinical Neurology","volume":" ","pages":"813-817"},"PeriodicalIF":0.0,"publicationDate":"2024-11-22","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142476977","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

[A case of T1 radiculopathy caused by intervertebral disc herniation with cervical angina]. [椎间盘突出症引起的 T1 根神经病伴颈部心绞痛病例]。

Clinical Neurology Pub Date : 2024-10-29 Epub Date: 2024-10-26 DOI: 10.5692/clinicalneurol.cn-001989

Kazuki Sogawa, Tetsuo Ando, Yasuo Kanamori, Syunsuke Koga, Masahiro Sonoo, Toshio Fukutake

引用次数: 0

[Proposals for the early diagnosis of late-onset hereditary ATTR amyloidosis in ‍nonendemic areas in Japan]. [关于在日本非流行区早期诊断晚发型遗传性 ATTR 淀粉样变性病的建议]。

Clinical Neurology Pub Date : 2024-10-29 Epub Date: 2024-10-26 DOI: 10.5692/clinicalneurol.cn-002002

Keiko Maruyama Saladini, Haruki Koike, Mitsuharu Ueda, Yoshiki Sekijima, Yukio Ando

引用次数: 0

[A case of hypertrophic pachymeningitis as a systemic autoimmune/inflammatory disorder (SAID) associated with chronic myelomonocytic leukemia]. [与慢性粒单核细胞白血病相关的肥厚性咽鼓管炎作为系统性自身免疫/炎症性疾病（SAID）的一个病例]。

Clinical Neurology Pub Date : 2024-10-29 Epub Date: 2024-10-21 DOI: 10.5692/clinicalneurol.cn-002007

Tatsuya Sato, Tomoyuki Inoue, Satoshi Kubo, Kota Sato, Takahiro Himeno, Yuka Terasawa

{"title":"[A case of hypertrophic pachymeningitis as a systemic autoimmune/inflammatory disorder (SAID) associated with chronic myelomonocytic leukemia].","authors":"Tatsuya Sato, Tomoyuki Inoue, Satoshi Kubo, Kota Sato, Takahiro Himeno, Yuka Terasawa","doi":"10.5692/clinicalneurol.cn-002007","DOIUrl":"10.5692/clinicalneurol.cn-002007","url":null,"abstract":"A 67-year-old woman with past medical history of chronic myelomonocytic leukemia (CMML) presented with a chief complaint of headache, diplopia, and hearing impairment in the right ear. Examination revealed impaired ocular movement in the left eye and sensorineural hearing loss in the right ear. Cerebrospinal fluid analysis showed increased cell count and protein, and MRI showed contrast enhancement of hypertrophic dura mater. Since there were no other abnormalities which would have been a cause of hypertrophic pachymeningitis, it was considered as systemic autoimmune/inflammatory disorder (SAID) associated with CMML. Treatment with steroid, cyclophosphamide, and methotrexate led to improvement of the symptoms. SAIDs develop in up to 25% of patients with myelodysplastic syndromes (MDS) or CMML, which may be the only symptoms of MDS/CMML. As a phenotype of SAIDs, systemic vasculitis, connective tissue diseases, and neutrophilic diseases are frequently reported; however, isolated involvement of central nerve system is rarely reported. To our knowledge, this is the first report of hypertrophic pachymeningitis as SAID associated with CMML. To clarify the pathogenesis of neurologic involvement of SAIDs, accumulation of cases is necessary.","PeriodicalId":39292,"journal":{"name":"Clinical Neurology","volume":" ","pages":"742-745"},"PeriodicalIF":0.0,"publicationDate":"2024-10-29","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142308725","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

[Amaurosis fugax in Marfan syndrome with myxomatous degeneration]. [马凡综合征伴肌瘤变性的大眼病]。

Clinical Neurology Pub Date : 2024-10-29 Epub Date: 2024-10-21 DOI: 10.5692/clinicalneurol.cn-001987

Takeo Sato, Mari Satake, Hiroki Iitsuka, Masahiro Mimori, Tadashi Umehara, Chisen Takeuchi, Yasuyuki Iguchi

引用次数: 0

[Acute internal carotid artery occlusion following administration of Andexanet alfa for the reversal of direct factor Xa inhibitors in patients with cerebral hemorrhage]. [脑出血患者使用安达赛酮α逆转直接 Xa 因子抑制剂后出现急性颈内动脉闭塞]。

Clinical Neurology Pub Date : 2024-10-29 Epub Date: 2024-10-21 DOI: 10.5692/clinicalneurol.cn-001997

Sota Uemura, Junji Takasugi, Nobuyuki Ohara, Masamori Koyanagi, Tsuyoshi Ohta, Michi Kawamoto

{"title":"[Acute internal carotid artery occlusion following administration of Andexanet alfa for the reversal of direct factor Xa inhibitors in patients with cerebral hemorrhage].","authors":"Sota Uemura, Junji Takasugi, Nobuyuki Ohara, Masamori Koyanagi, Tsuyoshi Ohta, Michi Kawamoto","doi":"10.5692/clinicalneurol.cn-001997","DOIUrl":"10.5692/clinicalneurol.cn-001997","url":null,"abstract":"An 87-year-old woman receiving aspirin and apixaban with a history of large artery atherosclerotic stroke, and pulmonary embolism presented to the hospital for aphasia and right hemiplegia. A head CT scan showed 18-ml hematoma in the left thalamus. Low-dose Andexanet alfa was administered 84 minutes after the onset of stroke, and 10 hours and 24 minutes after the last dose of apixaban. Three hours later after admission, she had flaccid hemiplegia and became comatose. CT and CT angiography revealed occlusion of left internal carotid artery (ICA) and no evidence of hematoma expansion. Although repetitive mechanical thrombectomy resulted in recanalization (modified TICI 2b), carotid ultrasound revealed the occlusion of left ICA on next day. On day 7, she died of brain herniation following extensive cerebral infarction. It has been reported that some patients did experience thrombotic events after administration of Andexanet alfa. Our case illustrates that even large vessel occlusion might occur after intravenous injection of Andexanet alfa. Thus, careful follow-up, including cerebrovascular imaging, is required immediately after administration of Andexanet alfa.","PeriodicalId":39292,"journal":{"name":"Clinical Neurology","volume":" ","pages":"730-735"},"PeriodicalIF":0.0,"publicationDate":"2024-10-29","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142308727","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

[Clinical features of five Japanese cases with leucine-rich glioma inactivated-1 (LGI1) antibody-positive encephalitis]. [富亮氨酸胶质瘤灭活-1（LGI1）抗体阳性脑炎五例日本病例的临床特征]。

Clinical Neurology Pub Date : 2024-10-29 Epub Date: 2024-10-26 DOI: 10.5692/clinicalneurol.cn-001977

Naoki Moro, Masanori Nakajima, Hidenobu Shozawa, Kentaro Nagai, Ayumi Uchibori, Yaeko Ichikawa

{"title":"[Clinical features of five Japanese cases with leucine-rich glioma inactivated-1 (LGI1) antibody-positive encephalitis].","authors":"Naoki Moro, Masanori Nakajima, Hidenobu Shozawa, Kentaro Nagai, Ayumi Uchibori, Yaeko Ichikawa","doi":"10.5692/clinicalneurol.cn-001977","DOIUrl":"10.5692/clinicalneurol.cn-001977","url":null,"abstract":"We studied the clinical features of five Japanese cases with leucine-rich glioma inactivated-1 (LGI1) antibody-positive encephalitis. Their symptoms included seizures, hallucinations, memory impairment, apathy, anxiety, agitation, faciobrachial dystonic seizure (FBDS), and ictal piloerection. All five patients showed hippocampal fluid attenuated inversion recovery (FLAIR) hyperintensity on brain MRI even though their cell counts of cerebrospinal fluid (CSF) were normal range. Four patients had syndrome of inappropriate secretion of antidiuretic hormone. One patient with FBDS also showed basal ganglia lesion on her brain MRI. Sodium channel blockers apparently lowered the frequency of FBDS. One patient had a thyroid cancer and underwent thyroidectomy. Substantial response to immunotherapy was seen in four out of five cases. At follow-up ≥2 years, all five patients had never relapsed. In cases of limbic encephalitis with normal CSF cell counts and hyponatremia, we should consider LGI1 antibody-positive encephalitis and conduct immunotherapy immediately.","PeriodicalId":39292,"journal":{"name":"Clinical Neurology","volume":" ","pages":"714-718"},"PeriodicalIF":0.0,"publicationDate":"2024-10-29","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142355939","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

[Utility of EEG in neurological emergencies and critical care]. [脑电图在神经系统急症和重症监护中的作用]。

Clinical Neurology Pub Date : 2024-10-29 Epub Date: 2024-10-26 DOI: 10.5692/clinicalneurol.cn-001928

Hajime Yoshimura

引用次数: 0

[A case of young onset cerebral amyloid angiopathy associated with dural grafting]. [一例与硬脑膜移植有关的年轻发病脑淀粉样血管病]。

Clinical Neurology Pub Date : 2024-10-29 Epub Date: 2024-10-21 DOI: 10.5692/clinicalneurol.cn-002006

Kengo Furutsuka, Aya Murakami, Haruka Iwamura, Kosuke Miyake, Akio Asai, Yusuke Yakushiji

{"title":"[A case of young onset cerebral amyloid angiopathy associated with dural grafting].","authors":"Kengo Furutsuka, Aya Murakami, Haruka Iwamura, Kosuke Miyake, Akio Asai, Yusuke Yakushiji","doi":"10.5692/clinicalneurol.cn-002006","DOIUrl":"10.5692/clinicalneurol.cn-002006","url":null,"abstract":"A 47-year-old man was admitted to our hospital because of sudden-onset motor aphasia and right hemiplegia. His past medical history was notable for left craniotomy and hematoma evacuation following a traumatic brain hemorrhage approximately 40 years earlier, for which dural grafting was performed. He also had a history of three lobar hemorrhages in the left hemisphere since the age of 42 years. Brain CT imaging revealed an acute left frontal lobar hemorrhage. His initial brain MRI conducted at our hospital demonstrated hemorrhagic findings with left hemisphere dominance, including acute and old lobar hemorrhage, cortical superficial siderosis, and cerebral microbleeds. Cerebrospinal fluid analyses demonstrated reduced levels of cerebral amyloid-β 42, and elevated total tau. His apolipoprotein E genotype was ε3/ε3. Whole-exome sequencing did not detect mutations in genes associated with Alzheimer's disease, including presenilin 1, presenilin 2, and amyloid precursor protein. These findings led to a clinical diagnosis of iatrogenic cerebral amyloid angiopathy (CAA) using recently proposed diagnostic criteria, which do not require pathological evaluation of the brain. Iatrogenic CAA should be considered as a cause of lobar hemorrhage in young patients, especially those with a past history of neurosurgery.","PeriodicalId":39292,"journal":{"name":"Clinical Neurology","volume":" ","pages":"736-741"},"PeriodicalIF":0.0,"publicationDate":"2024-10-29","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142308726","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

[Primary intramedullary spinal cord lymphoma with long spinal cord lesion]. [原发性髓内脊髓淋巴瘤伴脊髓长段病变]。

Clinical Neurology Pub Date : 2024-10-29 Epub Date: 2024-10-21 DOI: 10.5692/clinicalneurol.cn-002008

Atsushi Hara, Hideo Aihara, Hiroaki Hirata, Tokiko Nakai, Toshiyuki Uehara

引用次数: 0