{"title":"Increased NADPH in Human PCD Airway Epithelial Cells: Does the Reducing Environment in Cells with Ciliary Dysfunction Lead to Decreased NO Evolution?","authors":"N. Marozkina, Laura Smith, C. Cotton, B. Gaston","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6184","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6184","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129293497","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Airway Stem Cell Heterogeneity in Advanced Cystic Fibrosis","authors":"W. Xian, S. Niroula, F. McKeon","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6189","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6189","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"16 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123040145","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
T. Brett, K. Berry, M. Sala-Rabanal, D. Byers, E. Katz, C. Nichols, J. Alexander-Brett
{"title":"The Structure the Calcium Activated Chloride Channel Regulator 1 (CLCA1) VWA Domain and Its Translation Application to Potentiate TMEM16A Anion Channel Activity in Primary CF Airway Cells","authors":"T. Brett, K. Berry, M. Sala-Rabanal, D. Byers, E. Katz, C. Nichols, J. Alexander-Brett","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6194","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6194","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"3 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"127892197","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Evaluating Peripheral Blood Eosinophilia and Health Outcomes in Hospitalized Cystic Fibrosis Patients with Pulmonary Exacerbations","authors":"A. Siedlecki, B. Quon, S. Tebbutt, D. Dorscheid","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6177","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6177","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"53 7","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"121008691","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Moumita Bose, S. Abid, A. Keller, L. Fernandez, L. Schumacher, O. Cavazos, R. Jain
{"title":"Neutrophil Function May Impact Sex Based Differences in Disease Outcomes in Cystic Fibrosis","authors":"Moumita Bose, S. Abid, A. Keller, L. Fernandez, L. Schumacher, O. Cavazos, R. Jain","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6185","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6185","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"18 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123429529","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
A. Lammers, R. Kos, R. D. Vries, P. Brinkman, J. W. F. Dagelet, Niels W. Rutjes, C. Majoor, S. Terheggen-Lagro, E. Weersink, L. Bos, P. Sterk, A. M. Zee, A. Neerincx
{"title":"eNose Technology for Detection of Pseudomonas Aeruginosa Infection in Cystic Fibrosis Patients","authors":"A. Lammers, R. Kos, R. D. Vries, P. Brinkman, J. W. F. Dagelet, Niels W. Rutjes, C. Majoor, S. Terheggen-Lagro, E. Weersink, L. Bos, P. Sterk, A. M. Zee, A. Neerincx","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6181","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6181","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"62 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128733487","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
A. Dabo, Shuren Ma, P. Geraghty, C. McCarthy, G. Mcelvaney, G. Turino
{"title":"Cystic Fibrosis Disease Severity Correlates with Biomarkers of Elastin Degradation","authors":"A. Dabo, Shuren Ma, P. Geraghty, C. McCarthy, G. Mcelvaney, G. Turino","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6179","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6179","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"31 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133066295","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Effect of Bicarbonate on Cathelicidin and Neutrophil Killing of Pseudomonas Aeruginosa","authors":"R. Siew, K. Akong, V. Nizet","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6182","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6182","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"36 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116136390","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
J. Barnes, C. Sesler, E. Helton, M. Mazur, R. Denson, R. Zaharias, A. Adewale, S. Rowe, S. Krick
{"title":"A Precision Approach to Analyzing Inflammatory-Induced Glycogene Changes in Cystic Fibrosis","authors":"J. Barnes, C. Sesler, E. Helton, M. Mazur, R. Denson, R. Zaharias, A. Adewale, S. Rowe, S. Krick","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6193","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6193","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"24 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125989443","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
F. Kabir, S. Sasaki, S. Guo, N. Ambalavanan, S. Rowe, W. Harris
{"title":"Oligotherapeutics to Improve CFTR Correction","authors":"F. Kabir, S. Sasaki, S. Guo, N. Ambalavanan, S. Rowe, W. Harris","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6196","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6196","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"92 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115674256","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}