D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES最新文献

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Increased NADPH in Human PCD Airway Epithelial Cells: Does the Reducing Environment in Cells with Ciliary Dysfunction Lead to Decreased NO Evolution? 人PCD气道上皮细胞NADPH升高:纤毛功能障碍细胞的还原环境是否导致NO进化减少?
D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6184
N. Marozkina, Laura Smith, C. Cotton, B. Gaston
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引用次数: 0
Airway Stem Cell Heterogeneity in Advanced Cystic Fibrosis 晚期囊性纤维化的气道干细胞异质性
D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6189
W. Xian, S. Niroula, F. McKeon
{"title":"Airway Stem Cell Heterogeneity in Advanced Cystic Fibrosis","authors":"W. Xian, S. Niroula, F. McKeon","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6189","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6189","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"16 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123040145","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
The Structure the Calcium Activated Chloride Channel Regulator 1 (CLCA1) VWA Domain and Its Translation Application to Potentiate TMEM16A Anion Channel Activity in Primary CF Airway Cells 钙活化氯离子通道调节因子1 (CLCA1) VWA结构域的结构及其在原代CF气道细胞中增强TMEM16A阴离子通道活性的翻译应用
D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6194
T. Brett, K. Berry, M. Sala-Rabanal, D. Byers, E. Katz, C. Nichols, J. Alexander-Brett
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引用次数: 0
Evaluating Peripheral Blood Eosinophilia and Health Outcomes in Hospitalized Cystic Fibrosis Patients with Pulmonary Exacerbations 评估住院囊性纤维化合并肺加重患者外周血嗜酸性粒细胞和健康结局
D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6177
A. Siedlecki, B. Quon, S. Tebbutt, D. Dorscheid
{"title":"Evaluating Peripheral Blood Eosinophilia and Health Outcomes in Hospitalized Cystic Fibrosis Patients with Pulmonary Exacerbations","authors":"A. Siedlecki, B. Quon, S. Tebbutt, D. Dorscheid","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6177","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6177","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"53 7","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"121008691","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 2
Neutrophil Function May Impact Sex Based Differences in Disease Outcomes in Cystic Fibrosis 中性粒细胞功能可能影响囊性纤维化患者疾病结局的性别差异
D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6185
Moumita Bose, S. Abid, A. Keller, L. Fernandez, L. Schumacher, O. Cavazos, R. Jain
{"title":"Neutrophil Function May Impact Sex Based Differences in Disease Outcomes in Cystic Fibrosis","authors":"Moumita Bose, S. Abid, A. Keller, L. Fernandez, L. Schumacher, O. Cavazos, R. Jain","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6185","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6185","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"18 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123429529","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
eNose Technology for Detection of Pseudomonas Aeruginosa Infection in Cystic Fibrosis Patients 囊性纤维化患者铜绿假单胞菌感染的eNose检测技术
D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6181
A. Lammers, R. Kos, R. D. Vries, P. Brinkman, J. W. F. Dagelet, Niels W. Rutjes, C. Majoor, S. Terheggen-Lagro, E. Weersink, L. Bos, P. Sterk, A. M. Zee, A. Neerincx
{"title":"eNose Technology for Detection of Pseudomonas Aeruginosa Infection in Cystic Fibrosis Patients","authors":"A. Lammers, R. Kos, R. D. Vries, P. Brinkman, J. W. F. Dagelet, Niels W. Rutjes, C. Majoor, S. Terheggen-Lagro, E. Weersink, L. Bos, P. Sterk, A. M. Zee, A. Neerincx","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6181","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6181","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"62 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128733487","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 2
Cystic Fibrosis Disease Severity Correlates with Biomarkers of Elastin Degradation 囊性纤维化疾病严重程度与弹性蛋白降解生物标志物相关
D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6179
A. Dabo, Shuren Ma, P. Geraghty, C. McCarthy, G. Mcelvaney, G. Turino
{"title":"Cystic Fibrosis Disease Severity Correlates with Biomarkers of Elastin Degradation","authors":"A. Dabo, Shuren Ma, P. Geraghty, C. McCarthy, G. Mcelvaney, G. Turino","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6179","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6179","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"31 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133066295","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Effect of Bicarbonate on Cathelicidin and Neutrophil Killing of Pseudomonas Aeruginosa 碳酸氢盐对铜绿假单胞菌抗菌素和中性粒细胞杀伤的影响
D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6182
R. Siew, K. Akong, V. Nizet
{"title":"Effect of Bicarbonate on Cathelicidin and Neutrophil Killing of Pseudomonas Aeruginosa","authors":"R. Siew, K. Akong, V. Nizet","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6182","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6182","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"36 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116136390","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
A Precision Approach to Analyzing Inflammatory-Induced Glycogene Changes in Cystic Fibrosis 一种精确分析囊性纤维化中炎症诱导的糖基因变化的方法
D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6193
J. Barnes, C. Sesler, E. Helton, M. Mazur, R. Denson, R. Zaharias, A. Adewale, S. Rowe, S. Krick
{"title":"A Precision Approach to Analyzing Inflammatory-Induced Glycogene Changes in Cystic Fibrosis","authors":"J. Barnes, C. Sesler, E. Helton, M. Mazur, R. Denson, R. Zaharias, A. Adewale, S. Rowe, S. Krick","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6193","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6193","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"24 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125989443","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Oligotherapeutics to Improve CFTR Correction 少药改善CFTR矫正
D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6196
F. Kabir, S. Sasaki, S. Guo, N. Ambalavanan, S. Rowe, W. Harris
{"title":"Oligotherapeutics to Improve CFTR Correction","authors":"F. Kabir, S. Sasaki, S. Guo, N. Ambalavanan, S. Rowe, W. Harris","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6196","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a6196","url":null,"abstract":"","PeriodicalId":291196,"journal":{"name":"D34. CYSTIC FIBROSIS AND BRONCHIECTASIS: CLINICAL AND MECHANISTIC STUDIES","volume":"92 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115674256","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
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