World Journal for Pediatric and Congenital Heart Surgery最新文献_第9页

Isolated Vascular Rings Are Common Cardiovascular Malformations. 孤立的血管环是常见的心血管畸形。

IF 0.9

World Journal for Pediatric and Congenital Heart Surgery Pub Date : 2023-01-01 DOI: 10.1177/21501351221122972

William N Evans, Ruben J Acherman, Michael L Ciccolo, Juan Lehoux, Dean Berthoty, Arthur Montes, Gary A Mayman, Humberto Restrepo

{"title":"Isolated Vascular Rings Are Common Cardiovascular Malformations.","authors":"William N Evans, Ruben J Acherman, Michael L Ciccolo, Juan Lehoux, Dean Berthoty, Arthur Montes, Gary A Mayman, Humberto Restrepo","doi":"10.1177/21501351221122972","DOIUrl":"https://doi.org/10.1177/21501351221122972","url":null,"abstract":"Objective: We investigated the prevalence of isolated vascular rings in the general population of Southern Nevada.Methods: We identified those prenatally and postnatally diagnosed with an isolated vascular ring between January 2014 and December 2021. We included only those with vascular or ligamentous structures completely encircling the trachea and esophagus. To investigate the prevalence of isolated vascular rings, we included only those with situs solitus, levocardia, and no significant intracardiac malformations.Results: We identified 112 patients. Of the 112, 66 (59%) were female. There were approximately 211,000 total live births in Southern Nevada for the study period, for an overall prevalence of 5.3 isolated vascular rings per 10 000 live births. However, for the years 2014 to 2017, the average prevalence figure was 3.5 per 10 000 live births, and for the years 2018 to 2021, the average prevalence figure was 7.1 (range 6.5-8.0) per 10 000 live births. Simultaneously, the prenatal detection rate rose from 66% to 86%.Conclusions: Isolated vascular rings are common cardiovascular malformations. As prenatal detection rates in the Southern Nevada general population approach 90%, the prevalence figures for isolated vascular rings appear to asymptote at about 7 per 10 000 live births.","PeriodicalId":23974,"journal":{"name":"World Journal for Pediatric and Congenital Heart Surgery","volume":"14 1","pages":"21-23"},"PeriodicalIF":0.9,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"9387561","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 2

Safety and Efficacy of Right Axillary Thoracotomy for Repair of Congenital Heart Defects in Children. 右腋窝开胸术治疗儿童先天性心脏缺损的安全性和有效性。

IF 0.9

World Journal for Pediatric and Congenital Heart Surgery Pub Date : 2023-01-01 DOI: 10.1177/21501351221127283

Sameh M Said, Kristin C Greathouse, Christina M McCarthy, Nicholas Brown, Sacha Kumar, Mahmoud I Salem, Benjamin Kloesel, Sandeep Sainathan

{"title":"Safety and Efficacy of Right Axillary Thoracotomy for Repair of Congenital Heart Defects in Children.","authors":"Sameh M Said, Kristin C Greathouse, Christina M McCarthy, Nicholas Brown, Sacha Kumar, Mahmoud I Salem, Benjamin Kloesel, Sandeep Sainathan","doi":"10.1177/21501351221127283","DOIUrl":"https://doi.org/10.1177/21501351221127283","url":null,"abstract":"Background: Minimally invasive repair of congenital heart defects in children has not gained wide popularity yet compared to minimally invasive approaches in adults. We sought to review our experience with this approach in children.Methods: This study included a total of 37 children (24 girls, 64.9%) with a mean age of 6.5 ± 5.1 years, who underwent vertical axillary right minithoracotomy for repair of a variety of congenital heart defects between May 2020 and June 2022.Results: The mean weight of these children was 25.66 ± 18.3 kg. Trisomy 21 syndrome was present in 3 patients (8.1%). The most common congenital heart defects that were repaired via this approach were atrial septal defects (secundum in 11 patients, 29.7%; primum in 5, 13.5%; and unroofed coronary sinus in 1, 2.7%). Twelve patients (32.4%) underwent repair of partial anomalous pulmonary venous connections with or without sinus venosus defects, while 4 patients (10.8%) underwent closure of membranous ventricular septal defects. Mitral valve repair, resection of cor triatriatum dexter, epicardial pacemaker placement, and myxoma resection occurred in 1 patient (2.7%) each. No early mortality or reoperations. All patients were extubated in the operating room, and the mean length of hospital stay was 3.3 ± 2.04 days. Follow-up was complete (mean 7 ± 5 months). No late mortality or reoperations. One patient required epicardial pacemaker placement due to sinus node dysfunction 5 months after surgery.Conclusions: Vertical axillary right thoracotomy is a cosmetically superior approach that is safe and effective for repair of a variety of congenital heart defects in children.","PeriodicalId":23974,"journal":{"name":"World Journal for Pediatric and Congenital Heart Surgery","volume":"14 1","pages":"47-54"},"PeriodicalIF":0.9,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"10869493","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Influence of Body Mass Index in Donor-Recipient Size Mismatch in Pediatric Heart Transplantation. 体质量指数对儿童心脏移植供体-受体尺寸不匹配的影响。

IF 1

World Journal for Pediatric and Congenital Heart Surgery Pub Date : 2023-01-01 DOI: 10.1177/21501351221127284

Laura K Lowrey, Jaimin Trivedi, Karthik Ramakrishnan, Pranava Sinha, Shriprasad R Deshpande

{"title":"Influence of Body Mass Index in Donor-Recipient Size Mismatch in Pediatric Heart Transplantation.","authors":"Laura K Lowrey, Jaimin Trivedi, Karthik Ramakrishnan, Pranava Sinha, Shriprasad R Deshpande","doi":"10.1177/21501351221127284","DOIUrl":"10.1177/21501351221127284","url":null,"abstract":"Background: Body weight is the traditional metric for matching donor and recipient size for pediatric heart transplantation (pHT). We hypothesized that mismatch in body mass index (BMI) or body surface area (BSA) rather than weight is better associated with outcomes of transplantation and therefore should be used for donor-recipient size matching.Methods: Analysis of the United Network for Organ Sharing database limited to pHT recipients was performed. Donor and recipient mismatch groups were created for weight, BMI, and BSA ratios. Differences in recipient characteristics between each cohort and the impact of mismatch on outcomes were statistically analyzed.Results: A total of 4,465 patients were included in the analysis of which 43% had congenital heart disease (CHD). There were significant differences in patient characteristics by matching, independent of the matching parameter. Multivariable regression analysis showed that a low donor-recipient BMI ratio (compared to normal) (CHD OR 1.70; non-CHD 2.78) was a predictor of one-year mortality (all P < .001) in both CHD and non-CHD cohorts. Low BMI ratio was also associated with worse long-term survival in non-CHD groups, but not in the CHD cohort. Weight and BSA ratio did not predict one year or long-term survival.Conclusion: The use of low BMI donors compared to recipient may predict poor early and long-term survival and therefore should be avoided in pHT. The use of BMI matching may improve donor-recipient matching in pHT.","PeriodicalId":23974,"journal":{"name":"World Journal for Pediatric and Congenital Heart Surgery","volume":"14 1","pages":"31-39"},"PeriodicalIF":1.0,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"9387562","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

How do Adults With Congenital Heart Disease Evaluate Their Clinical Care? 成人先天性心脏病患者如何评价其临床护理?

IF 0.9

World Journal for Pediatric and Congenital Heart Surgery Pub Date : 2023-01-01 DOI: 10.1177/21501351221127895

Pasangi M Wijayarathne, Alexandrea Ng, Samuel Menahem

{"title":"How do Adults With Congenital Heart Disease Evaluate Their Clinical Care?","authors":"Pasangi M Wijayarathne, Alexandrea Ng, Samuel Menahem","doi":"10.1177/21501351221127895","DOIUrl":"https://doi.org/10.1177/21501351221127895","url":null,"abstract":"Background: Almost 90% of patients with congenital heart disease (CHD) now reach adulthood. How do they evaluate the care they received?Methods: Adults with CHD (ACHD) recruited for an international multi-center study (APPROACH-IS II) were posed 3 additional \"questions\" to determine their perceptions of the positive, negative, and areas for improvement of their clinical care. The findings underwent a thematic analysis.Results: Of the 210 recruited, 183 completed the questionnaire, 147 answered the 3 \"questions.\" Most appreciated open communication and support, a holistic approach, continuity of and readily accessible care conducted by experts, and with good outcomes. Less than half reported negative concerns which included loss of autonomy, distress from multiple and/or painful investigations, restricted lifestyles, medication side-effects, and anxiety about their CHD. Others found their reviews time-consuming with long travel times. Some complained of limited support, poor accessibility to services in rural areas, shortage of ACHD specialists, absence of tailored rehabilitation programs, and at times their own as well as their clinicians' limited understanding of their CHD. Suggestions for improvement included better communication, further education about their CHD, availability of simplified written information, mental health and support services, support groups, seamless transition to adult care and providing better prognostications, financial assistance, flexible appointments, telehealth reviews, and greater access to rural specialist care.Conclusions: In addition to providing optimal medical and surgical care for ACHD, clinicians need to be cognizant of their patients' concerns and proactive in addressing them.","PeriodicalId":23974,"journal":{"name":"World Journal for Pediatric and Congenital Heart Surgery","volume":"14 1","pages":"55-62"},"PeriodicalIF":0.9,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"9387565","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 3

Whole-Chest Three-Dimensional Modeling Aids Hybrid Pulmonary Valve Replacement Following Double Switch Operation. 全胸部三维建模辅助双开关手术后混合式肺动脉瓣置换术。

IF 0.9

World Journal for Pediatric and Congenital Heart Surgery Pub Date : 2023-01-01 DOI: 10.1177/21501351221132161

Philip Carmon, Gregory A Fleming, Piers C A Barker, Gregory M Sturgeon, Joseph W Turek, Reid C Chamberlain

引用次数: 0

Implementation of Virtual Fontan Heart Camps During a Pandemic. 流行病期间虚拟Fontan心脏营地的实施。

IF 0.9

World Journal for Pediatric and Congenital Heart Surgery Pub Date : 2023-01-01 DOI: 10.1177/21501351221127289

Edythe B Tham, Danielle E Harake, Lily Q Lin, Katie J Du, Lucy E Harris, Elina Williams, Alanna L Ash, Carolina A Escudero

{"title":"Implementation of Virtual Fontan Heart Camps During a Pandemic.","authors":"Edythe B Tham, Danielle E Harake, Lily Q Lin, Katie J Du, Lucy E Harris, Elina Williams, Alanna L Ash, Carolina A Escudero","doi":"10.1177/21501351221127289","DOIUrl":"https://doi.org/10.1177/21501351221127289","url":null,"abstract":"Background: Children with a Fontan operation represent a unique form of congenital heart disease (CHD) that requires multiple cardiac surgeries and procedures with an uncertain long-term outcome. Given the rarity of the types of CHD that require this procedure, many children with a Fontan do not know any others like them.Methods: With the cancelation of medically supervised heart camps due to the COVID-19 pandemic, we have organized several physician-led virtual day camps for children with a Fontan operation to connect with others in their province and across Canada. The aim of this study was to describe the implementation and evaluation of these camps via the use of an anonymous online survey immediately after the event and reminders on days 2 and 4 postevent.Results: Fifty-one children have participated in at least 1 of our camps. Registration data showed that 70% of participants did not know anyone else with a Fontan. Postcamp evaluations showed that 86% to 94% learned something new about their heart and 95% to 100% felt more connected to other children like them.Conclusion: We have demonstrated the implementation of a virtual heart camp to expand the support network for children with a Fontan. These experiences may help to promote healthy psychosocial adjustments through inclusion and relatedness.","PeriodicalId":23974,"journal":{"name":"World Journal for Pediatric and Congenital Heart Surgery","volume":"14 1","pages":"63-69"},"PeriodicalIF":0.9,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9975293/pdf/10.1177_21501351221127289.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"9371343","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Outcomes After Anatomic Versus Physiologic Repair of Congenitally Corrected Transposition of the Great Arteries: A Systematic Review and Meta-Analysis. 先天性大动脉转位解剖与生理性修复后的结果：系统回顾和荟萃分析。

IF 1.1

World Journal for Pediatric and Congenital Heart Surgery Pub Date : 2023-01-01 DOI: 10.1177/21501351221127894

Isao Anzai, Yanling Zhao, Arnaldo Dimagli, Christian Pearsall, Marian LaForest, Emile Bacha, David Kalfa

{"title":"Outcomes After Anatomic Versus Physiologic Repair of Congenitally Corrected Transposition of the Great Arteries: A Systematic Review and Meta-Analysis.","authors":"Isao Anzai, Yanling Zhao, Arnaldo Dimagli, Christian Pearsall, Marian LaForest, Emile Bacha, David Kalfa","doi":"10.1177/21501351221127894","DOIUrl":"10.1177/21501351221127894","url":null,"abstract":"Surgical treatment for congenitally corrected transposition of the great arteries is widely debated, with both physiologic repair and anatomic repair holding advantages and disadvantages. This meta-analysis, which includes 44 total studies consisting of 1857 patients, compares mortality at different time points (operative, in-hospital, and post-discharge), reoperation rates, and postoperative ventricular dysfunction between these two categories of procedures. Although anatomic and physiologic repair had similar operative and in-hospital mortality, anatomic repair patients had significantly less post-discharge mortality (6.1% vs 9.7%; P = .006), lower reoperation rates (17.9% vs 20.6%; P < .001), and less postoperative ventricular dysfunction (16% vs 43%; P < .001). When anatomic repair patients were subdivided into those who had atrial and arterial switch versus those who had atrial switch with Rastelli, the double switch group had significantly lower in-hospital mortality (4.3% vs 7.6%; P = .026) and reoperation rates (15.6% vs 25.9%; P < .001). The results of this meta-analysis suggest a protective benefit of favoring anatomic repair over physiologic repair.","PeriodicalId":23974,"journal":{"name":"World Journal for Pediatric and Congenital Heart Surgery","volume":"14 1","pages":"70-76"},"PeriodicalIF":1.1,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"9387567","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Novel Insights into the Etiology, Genetics, and Embryology of Hypoplastic Left Heart Syndrome. 左心发育不全综合征病因学、遗传学和胚胎学的新见解。

IF 0.9

World Journal for Pediatric and Congenital Heart Surgery Pub Date : 2022-09-01 DOI: 10.1177/21501351221102961

George C Gabriel, Hisato Yagi, Xinxiu Xu, Cecilia W Lo

{"title":"Novel Insights into the Etiology, Genetics, and Embryology of Hypoplastic Left Heart Syndrome.","authors":"George C Gabriel, Hisato Yagi, Xinxiu Xu, Cecilia W Lo","doi":"10.1177/21501351221102961","DOIUrl":"10.1177/21501351221102961","url":null,"abstract":"Hypoplastic left heart syndrome (HLHS) is a relatively rare severe congenital heart defect (CHD) closely linked to other left ventricular outflow tract (LVOT) lesions including bicuspid aortic valve (BAV), one of the most common heart defects. While HLHS, BAV, and other LVOT lesions have a strong genetic underpinning, their genetic etiology remains poorly understood. Findings from a large-scale mouse mutagenesis screen showed HLHS has a multigenic etiology and is genetically heterogenous, explaining difficulties in identifying the genetic causes of HLHS. In Ohia mice, HLHS shows incomplete penetrance. Some mice exhibited small LV with normal aorta, and others a normal LV with hypoplastic aorta, indicating the LV hypoplasia is not hemodynamically driven. In Ohia mutants, HLHS was found to have a digenic modular construction, with mutation in a chromatin modifier causing the small LV phenotype and mutation in Pcdha9 causing the aorta/aortic valve hypoplasia. The Pcdha9 mutation alone can cause BAV, and in the human genome two common deletion copy number variants spanning PCDHA7-10 are associated with BAV. Hence the digenic etiology of HLHS can account for the close association of HLHS, a rare CHD, with BAV, one of the most common CHD. Functional analysis of Ohia HLHS heart tissue showed severe mitochondrial dysfunction in the small LV, while the normal size RV is also affected but milder, suggesting possible role in vulnerability of surgically palliated HLHS patients to heart failure. These findings suggest insights into the genetics of HLHS may yield new therapies for improving outcome for patients with HLHS.","PeriodicalId":23974,"journal":{"name":"World Journal for Pediatric and Congenital Heart Surgery","volume":"13 5","pages":"565-570"},"PeriodicalIF":0.9,"publicationDate":"2022-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10010598/pdf/nihms-1874347.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"9092883","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Transposition With Hypertrophic Cardiomyopathy and Persistent Pulmonary Hypertension of the Newborn 新生儿转位合并肥厚性心肌病和持续性肺动脉高压

IF 0.9

World Journal for Pediatric and Congenital Heart Surgery Pub Date : 2022-05-23 DOI: 10.1177/21501351221098135

B. Brooks, A. Krishnan, Y. D'udekem, Gregory K. Yurasek

引用次数: 0

Valve-Sparing Aortic Root Replacement in a Patient With an FLNA Variant FLNA变异患者保留瓣膜的主动脉根置换术

IF 0.9

World Journal for Pediatric and Congenital Heart Surgery Pub Date : 2022-05-18 DOI: 10.1177/21501351221099272

A. Lobbestael, Caleb P. Bupp, M. Haw

引用次数: 0