Zeitschrift fur Rheumatologie最新文献_第9页

IF 0.9 4区医学

Zeitschrift fur Rheumatologie Pub Date : 2024-06-01 Epub Date: 2024-04-29 DOI: 10.1007/s00393-024-01503-0

Stefan Schmiedel

引用次数: 0

[Hemophagocytic lymphohistiocytosis and macrophage activation syndrome : A multidisciplinary challenge]. [嗜血细胞淋巴组织细胞增多症和巨噬细胞活化综合征：多学科挑战]。

IF 1 4区医学

Zeitschrift fur Rheumatologie Pub Date : 2024-06-01 Epub Date: 2024-01-24 DOI: 10.1007/s00393-023-01472-w

Nikolas Ruffer, Ricardo Kosch, Katja Weisel, Ina Kötter, Martin Krusche

{"title":"[Hemophagocytic lymphohistiocytosis and macrophage activation syndrome : A multidisciplinary challenge].","authors":"Nikolas Ruffer, Ricardo Kosch, Katja Weisel, Ina Kötter, Martin Krusche","doi":"10.1007/s00393-023-01472-w","DOIUrl":"10.1007/s00393-023-01472-w","url":null,"abstract":"Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening hyperinflammatory syndrome that is characterized by hyperferritinemia, cytopenia, disseminated intravascular coagulopathy and functional disorders of the liver and the central nervous system. The term macrophage activation syndrome is predominantly used for secondary HLH in the context of autoimmune diseases (e.g., systemic juvenile idiopathic arthritis). In addition, malignancies and genetic inborn errors of immunity can predispose to the development of HLH. Infections (e.g., Epstein-Barr virus) in turn represent possible triggers of an acute episode. Due to the unspecific manifestation of the disease, a systematic evaluation of the organ systems is recommended in the clinical and laboratory analytical clarification of hyperinflammatory syndromes. In general, the treatment should be carried out by a multidisciplinary team with expertise in rheumatology, hematological oncology, infectious diseases and intensive care medicine. The primary treatment of HLH usually consists of glucocorticoids and in cases of a rapid deterioration of the condition anakinra (interleukin 1 block) and intravenous immunoglobulins can be employed. Treatment of the underlying disease should be consequently carried out in parallel, together with antimicrobial treatment.","PeriodicalId":23834,"journal":{"name":"Zeitschrift fur Rheumatologie","volume":" ","pages":"376-386"},"PeriodicalIF":1.0,"publicationDate":"2024-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139546792","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Mitteilungen der DGRh. DGRh 的通信。

IF 1 4区医学

Zeitschrift fur Rheumatologie Pub Date : 2024-06-01 DOI: 10.1007/s00393-024-01528-5

引用次数: 0

Mitteilungen der DGRh - Veranstaltungen der Rheumaakademie. DGRh 的公告 - 风湿病研究院的活动。

IF 1 4区医学

Zeitschrift fur Rheumatologie Pub Date : 2024-06-01 DOI: 10.1007/s00393-024-01525-8

引用次数: 0

[Fever in rheumatology : A (differential) diagnostic challenge]. [风湿病学中的发热：（鉴别）诊断难题]。

IF 1 4区医学

Zeitschrift fur Rheumatologie Pub Date : 2024-06-01 Epub Date: 2024-06-03 DOI: 10.1007/s00393-024-01513-y

Ina Kötter, Martin Krusche

引用次数: 0

[Importance of lysosomal storage diseases in rheumatology]. [溶酶体贮积症在风湿病学中的重要性]。

IF 1 4区医学

Zeitschrift fur Rheumatologie Pub Date : 2024-06-01 Epub Date: 2024-05-27 DOI: 10.1007/s00393-024-01521-y

Charlotte Aries, Cornelia Rudolph, Nicole Muschol

引用次数: 0

[Patient-reported outcomes in German vasculitis patients-Data from the KOBRA quality project]. [德国血管炎患者的患者报告结果来自KOBRA质量项目的数据]。

IF 1 4区医学

Zeitschrift fur Rheumatologie Pub Date : 2024-06-01 Epub Date: 2023-10-13 DOI: 10.1007/s00393-023-01437-z

Christian Löffler, Martin Rudwaleit, Heinz-Jürgen Lakomek, Carina Stammann, Bernhard Hellmich

{"title":"[Patient-reported outcomes in German vasculitis patients-Data from the KOBRA quality project].","authors":"Christian Löffler, Martin Rudwaleit, Heinz-Jürgen Lakomek, Carina Stammann, Bernhard Hellmich","doi":"10.1007/s00393-023-01437-z","DOIUrl":"10.1007/s00393-023-01437-z","url":null,"abstract":"Background/objectives: Current data on the care of patients with vasculitis in Germany are scarce. Patient-reported outcome (PRO) questionnaires can capture aspects of the disease that escape conventional scores for disease activity, remission, and damage. For this reason, the Association of Rheumatological Acute Care Clinics (VRA) initiated a data analysis as part of the KOBRA quality project, the results of which are presented here.Patients and methods: Patients with vasculitis of vessels of any size or with polymyalgia rheumatica were included. The prospective survey included data on demographics, disease, pain, treatment, follow-up and satisfaction at the time of inpatient admission, discharge and follow-up after 2.5 months. All patients completed the AAV-PRO and EQ-5D-3L questionnaires on admission and follow-up.Results: In this study 420 patients were recruited and follow-up data were available from 302. On average, improvements were documented in all 5 dimensions of the EQ-5D, with the strongest effects in self-care and coping with activities of daily living. In the AAV-PRO, highly significant differences were seen in the domains systemic symptoms and physical functioning. Satisfaction with medical and nursing treatment was very high and did not correlate with pain level or with the AAV-PRO measures.Discussion: Under zreatment patient-reported outcomes improve at least partially in vasculitis patients. Satisfaction with medical treatment quality is independent of these outcomes.","PeriodicalId":23834,"journal":{"name":"Zeitschrift fur Rheumatologie","volume":" ","pages":"416-424"},"PeriodicalIF":1.0,"publicationDate":"2024-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"41214418","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Mitteilungen der DRL. DRL 的通信。

IF 1 4区医学

Zeitschrift fur Rheumatologie Pub Date : 2024-06-01 DOI: 10.1007/s00393-024-01530-x

引用次数: 0

[The most frequent febrile syndromes and autoinflammatory diseases in adulthood]. [成年期最常见的发热综合征和自身炎症]。

IF 1 4区医学

Zeitschrift fur Rheumatologie Pub Date : 2024-06-01 Epub Date: 2024-05-27 DOI: 10.1007/s00393-024-01522-x

Anne Pankow, Martin Krusche

引用次数: 0

[Patient-oriented optimization of the quality of care in a specialized outpatient clinic in a tertiary rheumatology center : A qualitative study]. [以患者为导向优化三级风湿病中心专科门诊的护理质量：一项定性研究]。

IF 1 4区医学

Zeitschrift fur Rheumatologie Pub Date : 2024-05-28 DOI: 10.1007/s00393-024-01520-z

Vlora Ibishi, Uta Kiltz, Styliani Tsiami, Michael Wessels, Xenofon Baraliakos

{"title":"[Patient-oriented optimization of the quality of care in a specialized outpatient clinic in a tertiary rheumatology center : A qualitative study].","authors":"Vlora Ibishi, Uta Kiltz, Styliani Tsiami, Michael Wessels, Xenofon Baraliakos","doi":"10.1007/s00393-024-01520-z","DOIUrl":"https://doi.org/10.1007/s00393-024-01520-z","url":null,"abstract":"Background: The adaptation of structures and processes in treatment procedures can contribute to increasing patient satisfaction and is the focus of patient-oriented quality assurance.Objective: To identify patient satisfaction as well as needs, expectations and preferences with respect to care and, based on this, to formulate recommendations for action to optimize the quality of care at a large tertiary rheumatology center.Material and methods: As part of a qualitative research approach, semi-structured patient interviews and a focus group interview consisting of physicians in rheumatology training in outpatient specialist care were conducted. The quality dimensions of Donabedian were recorded. The data material was evaluated and analyzed using the content-structuring qualitative content analysis according to Kuckartz with the MAXQDA evaluation software.Results: Using 12 patient interviews and a focus group of 3 future rheumatologists, recommendations for action to optimize the quality of care were derived on the basis of the structural, process and outcome quality. There was a need for optimization in the areas of personnel management, internal practice processes, practice equipment and treatment processes in the outpatient clinic.Conclusion: The results from the patient interviews and the focus group revealed the aspects in need of optimization. The methodology and results of this study can serve as a reference point for analyses of other rheumatology clinics in order to improve the quality of care within the framework of patient-oriented quality management and continuous further development.","PeriodicalId":23834,"journal":{"name":"Zeitschrift fur Rheumatologie","volume":" ","pages":""},"PeriodicalIF":1.0,"publicationDate":"2024-05-28","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"141161470","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0