{"title":"Left atrial filling index and left atrial strain - novel predictors of left ventricular diastolic dysfunction in adolescents with acute myocarditis.","authors":"Monika Jarecka, Radosław Pietrzak, Bożena Werner","doi":"10.33963/v.phj.107210","DOIUrl":"https://doi.org/10.33963/v.phj.107210","url":null,"abstract":"","PeriodicalId":17784,"journal":{"name":"Kardiologia polska","volume":" ","pages":""},"PeriodicalIF":3.7,"publicationDate":"2025-07-11","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144608708","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":3,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Katarzyna Holcman, Paweł Rubiś, Piotr Podolec, Monika Ostrowska, Agnieszka Stępień-Wroniecka, Katarzyna Graczyk, Krystian Mróz, Andrzej Ząbek, Krzysztof Boczar, Ewa Dziewięcka, Mateusz Winiarczyk, Bogdan Ćmiel, Maria Kurek, Magdalena Kostkiewicz
{"title":"Transthyretin-related amyloid cardiomyopathy: A single-center experience in southern Poland, an endemic area.","authors":"Katarzyna Holcman, Paweł Rubiś, Piotr Podolec, Monika Ostrowska, Agnieszka Stępień-Wroniecka, Katarzyna Graczyk, Krystian Mróz, Andrzej Ząbek, Krzysztof Boczar, Ewa Dziewięcka, Mateusz Winiarczyk, Bogdan Ćmiel, Maria Kurek, Magdalena Kostkiewicz","doi":"10.33963/v.phj.107207","DOIUrl":"https://doi.org/10.33963/v.phj.107207","url":null,"abstract":"<p><strong>Background: </strong>Transthyretin amyloid cardiomyopathy (ATTR CA) is a rare, fatal disease characterised by the deposition of amyloid fibrils derived from misfolded transthyretin (TTR) protein. This single-center study investigated the clinical characteristics, genetic profile, and geographic distribution of ATTR CA patients in southern Poland, a suspected endemic area.</p><p><strong>Material and methods: </strong>This prospective study was conducted between 2020 and 2025 involving 100 adults, including a cohort of consecutive index patients with confirmed ATTR CA. Furthermore, all consenting first-degree relatives were invited to undergo targeted assessment through a familial cascade screening approach. The study incorporated clinical data, echocardiography, scintigraphy, genetic testing, and prospective follow-up for five years to assess all-cause mortality.</p><p><strong>Results: </strong>Among 100 participants (27 index patients and 73 relatives), 6 relatives were diagnosed with ATTR CA and 15 were identified as carriers of a pathogenic TTR variant. The most frequently identified TTR variant was Phe53Leu, suggesting a high regional prevalence in southern Poland, alongside Glu109Lys, Glu122Lys, and Glu82Lys. The presence of hereditary ATTR CA was significantly associated with increased risk of all-cause mortality (HR, 7.67; 95% CI, 2.33-25.26; P < 0.001). All 33 patients with ATTR CA were eligible for tafamidis; moreover, two patients in this cohort with polyneuropathy were treated with inotersen, representing the first applications of these therapies in Poland.</p><p><strong>Conclusion: </strong>A comprehensive diagnostic approach is crucial for timely initiation of disease-modifying therapies. Our study suggests that, in this region, there is a high rate of the Phe53Leu TTR variant; however, further research is needed to validate these findings (NCT05814380).</p>","PeriodicalId":17784,"journal":{"name":"Kardiologia polska","volume":" ","pages":""},"PeriodicalIF":3.7,"publicationDate":"2025-07-11","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144608712","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":3,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Carlos Romero-Carrete, Aitor Alquézar-Arbé, Julio Núñez, Víctor Gil, Javier Jacob, Alfons Aguirre, Ana Villarejo Jimenez, Maria Borja-Cano, Rafael de la Espriella, Enrique Santas, Carolina Sánchez, Daniel Repullo, Lidia Fuentes, Sara Anaya Bustos, Gema Miñana, Pere Llorens, Òscar Miró
{"title":"Predictors of long-term survival in patients with a first episode of acute heart failure.","authors":"Carlos Romero-Carrete, Aitor Alquézar-Arbé, Julio Núñez, Víctor Gil, Javier Jacob, Alfons Aguirre, Ana Villarejo Jimenez, Maria Borja-Cano, Rafael de la Espriella, Enrique Santas, Carolina Sánchez, Daniel Repullo, Lidia Fuentes, Sara Anaya Bustos, Gema Miñana, Pere Llorens, Òscar Miró","doi":"10.33963/v.phj.107033","DOIUrl":"10.33963/v.phj.107033","url":null,"abstract":"<p><strong>Introduction: </strong>Acute heart failure (AHF) represents a critical event in heart failure progression, yet data on long-term outcomes after first hospitalization, remain scarce. The aim is to describe long-term survival and evaluate its predictors after the first episode of AHF.</p><p><strong>Material and methods: </strong>Patients from five Spanish hospitals with a confirmed first diagnosis of AHF were categorized based on survival (≥5 or RESULTS: A total of 1986 patients were included, median age 76 years (range: 68-82), 50% women, and 57% with preserved LVEF. Five-year mortality was 52%. Adjusted analysis showed that age (OR, 0.470 per 10-year increment; 95% CI, 0.421-0.525), New York Heart Association class III-IV vs. I (OR, 0.476; 95% CI, 0.341-0.666) and II vs. I (OR, 0.780; 95% CI, 0.627-0.969), chronic kidney disease (OR, 0.609; 95% CI, 0.452-0.820), coronary artery disease (OR, 0.657; 95% CI, 0.523-0.824), diabetes mellitus (OR, 0.658; 95% CI, 0.534-0.811), and male sex (OR, 0.774; 95% CI, 0.625-0.958) were associated with death within 5 years. LVEF at inclusion was not related to 5-year survival.</p><p><strong>Conclusions: </strong>Survival after a first AHF episode is poor, with age, New York Heart Association class, kidney function, coronary artery disease, diabetes, and sex being key predictors of long-term mortality.</p>","PeriodicalId":17784,"journal":{"name":"Kardiologia polska","volume":" ","pages":""},"PeriodicalIF":3.7,"publicationDate":"2025-07-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144560498","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":3,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Gerasimos Filippatos, Grigoris V Karamasis, Stavros G Drakos
{"title":"Shock Team and Shock Centers for the care of cardiogenic shock.","authors":"Gerasimos Filippatos, Grigoris V Karamasis, Stavros G Drakos","doi":"10.33963/v.phj.107059","DOIUrl":"10.33963/v.phj.107059","url":null,"abstract":"","PeriodicalId":17784,"journal":{"name":"Kardiologia polska","volume":" ","pages":""},"PeriodicalIF":3.7,"publicationDate":"2025-07-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144560499","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":3,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Daniel Rzeźnik, Anna Kabłak-Ziembicka, Mateusz Kozioł, Katarzyna Chwaleba, Krzysztof Krawczyk, Maciej Krupiński, Karolina Golińska-Grzybała, Paweł Kleczyński, Jacek Legutko
{"title":"Chronic coronary artery occlusion in a patient with coronary-pulmonary fistulas. Intervene, or not to intervene?","authors":"Daniel Rzeźnik, Anna Kabłak-Ziembicka, Mateusz Kozioł, Katarzyna Chwaleba, Krzysztof Krawczyk, Maciej Krupiński, Karolina Golińska-Grzybała, Paweł Kleczyński, Jacek Legutko","doi":"10.33963/v.phj.107029","DOIUrl":"10.33963/v.phj.107029","url":null,"abstract":"","PeriodicalId":17784,"journal":{"name":"Kardiologia polska","volume":" ","pages":""},"PeriodicalIF":3.7,"publicationDate":"2025-07-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144560495","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":3,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Sonia Alicja Nartowicz, Magdalena Janus, Artur Cieślewicz, Katarzyna Malesza, Agnieszka Bartczak-Rutkowska, Aleksandra Ciepłucha, Małgorzata Pyda, Maciej Lesiak, Olga Trojnarska
{"title":"Galectin-3 concentrations and exercise capacity assessment in adult patients with cyanosis due to congenital heart disease.","authors":"Sonia Alicja Nartowicz, Magdalena Janus, Artur Cieślewicz, Katarzyna Malesza, Agnieszka Bartczak-Rutkowska, Aleksandra Ciepłucha, Małgorzata Pyda, Maciej Lesiak, Olga Trojnarska","doi":"10.33963/v.phj.107036","DOIUrl":"10.33963/v.phj.107036","url":null,"abstract":"","PeriodicalId":17784,"journal":{"name":"Kardiologia polska","volume":" ","pages":""},"PeriodicalIF":3.7,"publicationDate":"2025-07-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144560497","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":3,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Łukasz Nowotka, Anna Drohomirecka, Jakub Malinowski, Joanna Zakrzewska-Koperska, Paula Połaska, Joanna Wiśniewska, Anna Simoniuksztis, Maciej Pronicki, Magdalena Marczak, Piotr Kołsut, Anna Konopka, Ewa Sitkowska, Tomasz Zieliński, Łukasz Szumowski, Maciej Sterliński
{"title":"From mononucleosis to heart transplantation: An uncommon course of Epstein-Barr virus-associated myocarditis.","authors":"Łukasz Nowotka, Anna Drohomirecka, Jakub Malinowski, Joanna Zakrzewska-Koperska, Paula Połaska, Joanna Wiśniewska, Anna Simoniuksztis, Maciej Pronicki, Magdalena Marczak, Piotr Kołsut, Anna Konopka, Ewa Sitkowska, Tomasz Zieliński, Łukasz Szumowski, Maciej Sterliński","doi":"10.33963/v.phj.107057","DOIUrl":"10.33963/v.phj.107057","url":null,"abstract":"","PeriodicalId":17784,"journal":{"name":"Kardiologia polska","volume":" ","pages":""},"PeriodicalIF":3.7,"publicationDate":"2025-07-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144560496","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":3,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Maryla Kocowska-Trytko, Aleksandra Banaś, Wiktoria Wojciechowska, Michał Terlecki, Agnieszka Olszanecka, Marek Rajzer
{"title":"Takotsubo syndrome and flash pulmonary edema in a patient with critical renal artery stenosis.","authors":"Maryla Kocowska-Trytko, Aleksandra Banaś, Wiktoria Wojciechowska, Michał Terlecki, Agnieszka Olszanecka, Marek Rajzer","doi":"10.33963/v.phj.106941","DOIUrl":"https://doi.org/10.33963/v.phj.106941","url":null,"abstract":"","PeriodicalId":17784,"journal":{"name":"Kardiologia polska","volume":" ","pages":""},"PeriodicalIF":3.7,"publicationDate":"2025-06-27","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144506146","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":3,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Armin Pietruczuk, Michał Gałeczka, Sławomir Pluta, Mateusz Knop, Adam Sokal, Roland Fiszer, Oskar Kowalski
{"title":"Complicated course of a supraventricular arrhythmia treatment in a single-ventricle patients: Case series.","authors":"Armin Pietruczuk, Michał Gałeczka, Sławomir Pluta, Mateusz Knop, Adam Sokal, Roland Fiszer, Oskar Kowalski","doi":"10.33963/v.phj.106942","DOIUrl":"https://doi.org/10.33963/v.phj.106942","url":null,"abstract":"","PeriodicalId":17784,"journal":{"name":"Kardiologia polska","volume":" ","pages":""},"PeriodicalIF":3.7,"publicationDate":"2025-06-27","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"144506143","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":3,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}