发布求助
文献互助 智能选刊 最新文献

Journal of Cystic Fibrosis最新文献

筛选
英文 中文
22 The changing face of cystic fibrosis research: challenges of multi-centre microbiology cohort studies 囊性纤维化研究的变化：多中心微生物队列研究的挑战
IF 6 2区 医学
Journal of Cystic Fibrosis Pub Date : 2025-10-01 DOI: 10.1016/S1569-1993(25)01642-X
I. Evans, C. Duplancic, T. Kidd, E. Ballard, R. Thomson, C. Wainwright, S. Bell, O. NTM in CF Investigators
{"title":"22 The changing face of cystic fibrosis research: challenges of multi-centre microbiology cohort studies","authors":"I. Evans, C. Duplancic, T. Kidd, E. Ballard, R. Thomson, C. Wainwright, S. Bell, O. NTM in CF Investigators","doi":"10.1016/S1569-1993(25)01642-X","DOIUrl":"10.1016/S1569-1993(25)01642-X","url":null,"abstract":"","PeriodicalId":15452,"journal":{"name":"Journal of Cystic Fibrosis","volume":"24 ","pages":"Page S12"},"PeriodicalIF":6.0,"publicationDate":"2025-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145190087","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":2,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
24 Determinants of Staphylococcus aureus persistence in the CF rat lung following highly effective modulator therapy 高效调节剂治疗后CF大鼠肺中金黄色葡萄球菌持久性的决定因素
IF 6 2区 医学
Journal of Cystic Fibrosis Pub Date : 2025-10-01 DOI: 10.1016/S1569-1993(25)01644-3
K. Shaffer, J. Kieth, S. Combs, A. Oden, L. Wilson, S. Barnes, S. Birket
{"title":"24 Determinants of Staphylococcus aureus persistence in the CF rat lung following highly effective modulator therapy","authors":"K. Shaffer, J. Kieth, S. Combs, A. Oden, L. Wilson, S. Barnes, S. Birket","doi":"10.1016/S1569-1993(25)01644-3","DOIUrl":"10.1016/S1569-1993(25)01644-3","url":null,"abstract":"","PeriodicalId":15452,"journal":{"name":"Journal of Cystic Fibrosis","volume":"24 ","pages":"Page S13"},"PeriodicalIF":6.0,"publicationDate":"2025-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145190089","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":2,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
51 Evaluating the clinical utility of oropharyngeal swabs from children with cystic fibrosis on elexacaftor/tezacaftor/ivacaftor using shotgun metagenomics 51 .使用散弹枪宏基因组学评估囊性纤维化儿童口咽拭子对elexaftor /tezacaftor/ivacaftor的临床应用价值
IF 6 2区 医学
Journal of Cystic Fibrosis Pub Date : 2025-10-01 DOI: 10.1016/S1569-1993(25)01670-4
D. Bouzek, C. Pope, A. Dutta, H. Hayden, A. Verster, D. Wolter, J. Pittman, F. Ratjen, M. Rosenfeld, L. Hoffman
{"title":"51 Evaluating the clinical utility of oropharyngeal swabs from children with cystic fibrosis on elexacaftor/tezacaftor/ivacaftor using shotgun metagenomics","authors":"D. Bouzek, C. Pope, A. Dutta, H. Hayden, A. Verster, D. Wolter, J. Pittman, F. Ratjen, M. Rosenfeld, L. Hoffman","doi":"10.1016/S1569-1993(25)01670-4","DOIUrl":"10.1016/S1569-1993(25)01670-4","url":null,"abstract":"","PeriodicalId":15452,"journal":{"name":"Journal of Cystic Fibrosis","volume":"24 ","pages":"Page S25"},"PeriodicalIF":6.0,"publicationDate":"2025-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145189676","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":2,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
75 Alginate scavenging by Achromobacter xylosoxidans mediates competitive interactions with mucoid Pseudomonas aeruginosa during polymicrobial infection 在多微生物感染过程中，木氧化无色杆菌清除海藻酸盐介导了与粘液样铜绿假单胞菌的竞争性相互作用
IF 6 2区 医学
Journal of Cystic Fibrosis Pub Date : 2025-10-01 DOI: 10.1016/S1569-1993(25)01694-7
W. Swords
{"title":"75 Alginate scavenging by Achromobacter xylosoxidans mediates competitive interactions with mucoid Pseudomonas aeruginosa during polymicrobial infection","authors":"W. Swords","doi":"10.1016/S1569-1993(25)01694-7","DOIUrl":"10.1016/S1569-1993(25)01694-7","url":null,"abstract":"","PeriodicalId":15452,"journal":{"name":"Journal of Cystic Fibrosis","volume":"24 ","pages":"Page S39"},"PeriodicalIF":6.0,"publicationDate":"2025-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145189693","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":2,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
35 The aetiology and epidemiology of nontuberculous mycobacteria (NTM) in Australians with cystic fibrosis 澳大利亚囊性纤维化患者非结核分枝杆菌（NTM）的病原学和流行病学
IF 6 2区 医学
Journal of Cystic Fibrosis Pub Date : 2025-10-01 DOI: 10.1016/S1569-1993(25)01654-6
C. Duplancic, K. Alene, E. Ballard, R. Thomson, C. Wainwright, G. Rogers, A. Clements, A. Floto, S. Bell, O. NTM in CF Investigators
{"title":"35 The aetiology and epidemiology of nontuberculous mycobacteria (NTM) in Australians with cystic fibrosis","authors":"C. Duplancic, K. Alene, E. Ballard, R. Thomson, C. Wainwright, G. Rogers, A. Clements, A. Floto, S. Bell, O. NTM in CF Investigators","doi":"10.1016/S1569-1993(25)01654-6","DOIUrl":"10.1016/S1569-1993(25)01654-6","url":null,"abstract":"","PeriodicalId":15452,"journal":{"name":"Journal of Cystic Fibrosis","volume":"24 ","pages":"Page S18"},"PeriodicalIF":6.0,"publicationDate":"2025-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145189769","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":2,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
39 Lessons learned characterizing non-tuberculous mycobacteria infection progression in a cystic fibrosis and non-cystic fibrosis bronchiectasis population 39囊性纤维化和非囊性纤维化支气管扩张人群非结核分枝杆菌感染进展特征的经验教训
IF 6 2区 医学
Journal of Cystic Fibrosis Pub Date : 2025-10-01 DOI: 10.1016/S1569-1993(25)01658-3
J. Hurley, J. Stark, R. Klingsberg
{"title":"39 Lessons learned characterizing non-tuberculous mycobacteria infection progression in a cystic fibrosis and non-cystic fibrosis bronchiectasis population","authors":"J. Hurley, J. Stark, R. Klingsberg","doi":"10.1016/S1569-1993(25)01658-3","DOIUrl":"10.1016/S1569-1993(25)01658-3","url":null,"abstract":"","PeriodicalId":15452,"journal":{"name":"Journal of Cystic Fibrosis","volume":"24 ","pages":"Page S20"},"PeriodicalIF":6.0,"publicationDate":"2025-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145189859","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":2,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
47 Disruptions in mannitol metabolism lead to diagnostic evasive Staphylococcus aureus in cystic fibrosis patients 47甘露醇代谢紊乱导致囊性纤维化患者出现诊断性金黄色葡萄球菌
IF 6 2区 医学
Journal of Cystic Fibrosis Pub Date : 2025-10-01 DOI: 10.1016/S1569-1993(25)01666-2
T. Zaputil, J. Zapata, A. Rozen, A. Fischer
{"title":"47 Disruptions in mannitol metabolism lead to diagnostic evasive Staphylococcus aureus in cystic fibrosis patients","authors":"T. Zaputil, J. Zapata, A. Rozen, A. Fischer","doi":"10.1016/S1569-1993(25)01666-2","DOIUrl":"10.1016/S1569-1993(25)01666-2","url":null,"abstract":"","PeriodicalId":15452,"journal":{"name":"Journal of Cystic Fibrosis","volume":"24 ","pages":"Page S23"},"PeriodicalIF":6.0,"publicationDate":"2025-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145189935","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":2,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
23 Mycobacteria acquisition from potable water across the drinking water system in Australia 澳大利亚饮用水系统中分枝杆菌的获取
IF 6 2区 医学
Journal of Cystic Fibrosis Pub Date : 2025-10-01 DOI: 10.1016/S1569-1993(25)01643-1
K. Ramsay, K. Smith, C. Duplancic, S. Taylor, G. Rogers, C. Wainwright, R. Thomson, S. Bell
{"title":"23 Mycobacteria acquisition from potable water across the drinking water system in Australia","authors":"K. Ramsay, K. Smith, C. Duplancic, S. Taylor, G. Rogers, C. Wainwright, R. Thomson, S. Bell","doi":"10.1016/S1569-1993(25)01643-1","DOIUrl":"10.1016/S1569-1993(25)01643-1","url":null,"abstract":"","PeriodicalId":15452,"journal":{"name":"Journal of Cystic Fibrosis","volume":"24 ","pages":"Pages S12a-S13"},"PeriodicalIF":6.0,"publicationDate":"2025-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145190088","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":2,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Letter to the editor: Semaglutide-associated recurrent distal intestinal obstruction in cystic fibrosis. 致编辑的信：囊性纤维化患者与塞马格鲁肽相关的复发性远端肠梗阻。
IF 6 2区 医学
Journal of Cystic Fibrosis Pub Date : 2025-09-29 DOI: 10.1016/j.jcf.2025.09.007
Rita Kamoua, Kristen Paradine, Luke McCoy
{"title":"Letter to the editor: Semaglutide-associated recurrent distal intestinal obstruction in cystic fibrosis.","authors":"Rita Kamoua, Kristen Paradine, Luke McCoy","doi":"10.1016/j.jcf.2025.09.007","DOIUrl":"https://doi.org/10.1016/j.jcf.2025.09.007","url":null,"abstract":"","PeriodicalId":15452,"journal":{"name":"Journal of Cystic Fibrosis","volume":" ","pages":""},"PeriodicalIF":6.0,"publicationDate":"2025-09-29","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145199468","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":2,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Cystic fibrosis-related liver disease in children- A vascular or a biliary disease? 儿童囊性纤维化相关性肝病——是血管疾病还是胆道疾病？
IF 6 2区 医学
Journal of Cystic Fibrosis Pub Date : 2025-09-28 DOI: 10.1016/j.jcf.2025.09.005
Amit Saha, Michael Stormon, Peter Lewindon, Nicole Graf, Guy Lampe, Mark Oliver
{"title":"Cystic fibrosis-related liver disease in children- A vascular or a biliary disease?","authors":"Amit Saha, Michael Stormon, Peter Lewindon, Nicole Graf, Guy Lampe, Mark Oliver","doi":"10.1016/j.jcf.2025.09.005","DOIUrl":"https://doi.org/10.1016/j.jcf.2025.09.005","url":null,"abstract":"<p><strong>Background: </strong>Cystic fibrosis-related liver disease(CFLD) has long been thought to be secondary to CFTR dysfunction in the biliary epithelial cells causing hepatobiliary complications,eventually progressing to cirrhosis. However, in more recent studies, non-cirrhotic portal hypertension(NCPH) has been postulated as a possible alternative mechanism contributing to CFLD.</p><p><strong>Methods: </strong>We collected clinical information pertaining to the status of their liver disease from children with CFLD who underwent liver transplant at the 3 paediatric liver transplant centres in Australia- Melbourne, Sydney and Brisbane. Explant histopathology slides were independently reviewed by 2 experienced pathologists based at two different anatomical pathology centres.</p><p><strong>Results: </strong>Data was collected from 18 children (including 10 females, median age 13 years) making this the largest paediatric series reported. Pre-transplant, all had evidence of portal hypertension with splenomegaly and thrombocytopenia. Median bilirubin, ALT, ALP, GGT levels and PELD/MELD, aspartate aminotransferase to platelet ratio index (APRI) and fibrosis-4 (FIB-4) scores were recorded to ascertain pre-transplant status. All explanted livers had evidence of variable degree of biliary cholestasis/cirrhosis as the predominant histopathological feature, whereas 11 out of the 18 explants (61%) also had patchy/focal areas of NCPH, mostly within the less fibrous or macro nodular areas.</p><p><strong>Conclusions: </strong>Data from this series reinstates the longstanding observation that focal biliary fibrosis/biliary cirrhosis seems to be the predominant pathophysiology in this condition, and NCPH, if present, is mostly focal, representing overlap features in a percentage of these patients. As such, NCPH may represent an early feature in CFLD before progressing to biliary stasis and cirrhosis.</p>","PeriodicalId":15452,"journal":{"name":"Journal of Cystic Fibrosis","volume":" ","pages":""},"PeriodicalIF":6.0,"publicationDate":"2025-09-28","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145191705","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":2,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
首页 上一页
0
×
引用
GB/T 7714-2015
复制
MLA
复制
APA
复制
导出至
BibTeX EndNote RefMan NoteFirst NoteExpress
×
提示
您的信息不完整，为了账户安全，请先补充。
现在去补充
×
提示
您因"违规操作"
具体请查看互助需知
我知道了
×
提示
现在去查看 取消
×
提示
确定
请完成安全验证×
相关产品
×
本文献相关产品
联系我们：info@booksci.cn Book学术提供免费学术资源搜索服务，方便国内外学者检索中英文文献。致力于提供最便捷和优质的服务体验。 Copyright © 2023 布克学术 All rights reserved.
京ICP备2023020795号-1
ghs 京公网安备 11010802042870号
Book学术文献互助
Book学术文献互助群
群 号：604180095
Book学术官方微信