A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS最新文献

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Analysis of Th2 Biomarkers to Identify a Th2-High Subgroup of Cystic Fibrosis Patients 分析Th2生物标志物识别囊性纤维化患者的Th2高亚群
A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS Pub Date : 2022-05-01 DOI: 10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1995
J. Barry, P. Akuthota, D. Conrad
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引用次数: 0
Sexually Dimorphic Innate Immune Programs of Airway Monocytes in Cystic Fibrosis 囊性纤维化中气道单核细胞性异形先天免疫程序
A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS Pub Date : 2022-05-01 DOI: 10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1984
H. Yin, N. Li, N. Shiner, S. Khanal, J. Schupp, G. Chupp, J. L. Gómez, C. Britto-Leon
{"title":"Sexually Dimorphic Innate Immune Programs of Airway Monocytes in Cystic Fibrosis","authors":"H. Yin, N. Li, N. Shiner, S. Khanal, J. Schupp, G. Chupp, J. L. Gómez, C. Britto-Leon","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1984","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1984","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"8 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"114781568","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
An mRNA-Based Therapy to Treat Primary Ciliary Dyskinesia: Aerosol Delivery, Biodistribution and Tolerability 一种基于mrna的治疗原发性纤毛运动障碍的方法:气溶胶输送、生物分布和耐受性
A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS Pub Date : 2022-05-01 DOI: 10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2002
D. Liston, M. Hennig, D. Ishimaru, J. Eby, Salman Khalid Ahmed, X. Yu, A. Alfaifi, H. Lister, M. Sidhu, S. Comini, P. Gao, A. Ashworth, O.M. Mousa, M.J. Torres, D. Siegwart, V. Kharitonov, D. J. Lockhart, B. Wustman
{"title":"An mRNA-Based Therapy to Treat Primary Ciliary Dyskinesia: Aerosol Delivery, Biodistribution and Tolerability","authors":"D. Liston, M. Hennig, D. Ishimaru, J. Eby, Salman Khalid Ahmed, X. Yu, A. Alfaifi, H. Lister, M. Sidhu, S. Comini, P. Gao, A. Ashworth, O.M. Mousa, M.J. Torres, D. Siegwart, V. Kharitonov, D. J. Lockhart, B. Wustman","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2002","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2002","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"17 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"124493104","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Decline in Vitamin D Levels During Hospitalization for CF Pulmonary Exacerbations CF肺恶化住院期间维生素D水平下降
A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS Pub Date : 2022-05-01 DOI: 10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1994
A. Lennox, E. Brutsaert, H. Weber, M. Gorgy, D. Lindsay-Adler, Z. Messer, J. Welter, S. Krishnan, A. Dozor
{"title":"Decline in Vitamin D Levels During Hospitalization for CF Pulmonary Exacerbations","authors":"A. Lennox, E. Brutsaert, H. Weber, M. Gorgy, D. Lindsay-Adler, Z. Messer, J. Welter, S. Krishnan, A. Dozor","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1994","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1994","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"130308432","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
IL-22 Binding Protein (IL-22RA2) Is Associated with Chronic Sinopulmonary Infections in Cystic Fibrosis IL-22结合蛋白(IL-22RA2)与囊性纤维化患者慢性肺感染相关
A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS Pub Date : 2022-05-01 DOI: 10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1991
C. Bojanowski, K. Choi, J. Bodnar, S. Lee, G. Trevejo-Nuñez, G. Kurland, J. Bomberger, R. Schleimer, J. Kolls
{"title":"IL-22 Binding Protein (IL-22RA2) Is Associated with Chronic Sinopulmonary Infections in Cystic Fibrosis","authors":"C. Bojanowski, K. Choi, J. Bodnar, S. Lee, G. Trevejo-Nuñez, G. Kurland, J. Bomberger, R. Schleimer, J. Kolls","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1991","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1991","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"14 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"126611634","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Characterization of Ciliary Function in Bronchiectasis (EMBARC-BRIDGE Study) 支气管扩张患者纤毛功能的表征(EMBARC-BRIDGE研究)
A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS Pub Date : 2022-05-01 DOI: 10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2000
M. Bottier, L. Delgado, M. Shuttleworth, D. Cassidy, M. Crichton, S. Gallant, L. Perrea, S. Aliberti, J. Altenburg, M. Shteinberg, T. Welte, F. Blasi, P. Goeminne, O. Sibila, E. Polverino, C. Hogg, S. Ollosson, M. Loebinger, N. Lorent, J. Chalmers, A. Shoemark
{"title":"Characterization of Ciliary Function in Bronchiectasis (EMBARC-BRIDGE Study)","authors":"M. Bottier, L. Delgado, M. Shuttleworth, D. Cassidy, M. Crichton, S. Gallant, L. Perrea, S. Aliberti, J. Altenburg, M. Shteinberg, T. Welte, F. Blasi, P. Goeminne, O. Sibila, E. Polverino, C. Hogg, S. Ollosson, M. Loebinger, N. Lorent, J. Chalmers, A. Shoemark","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2000","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2000","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"116 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"117229672","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 1
Loss of Small Pulmonary Blood Vessels in Cystic Fibrosis 囊性纤维化患者肺小血管的丧失
A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS Pub Date : 2022-05-01 DOI: 10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1985
J. Amoakon, J. Lee, A. Naren
{"title":"Loss of Small Pulmonary Blood Vessels in Cystic Fibrosis","authors":"J. Amoakon, J. Lee, A. Naren","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1985","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1985","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"161 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122092926","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
MUC5B-Dominated Mucus Hyperproduction in the Bronchiolectatic Airway of Non-Cystic Fibrosis Bronchiectasis (NCFB) 非囊性纤维化支气管扩张症(NCFB)细支气管扩张气道muc5b主导的粘液分泌增多
A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS Pub Date : 2022-05-01 DOI: 10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2003
T. Asakura, K. Okuda, G. Chen, T. Kato, Y. Mikami, G.C. Rodney, S. M. Barbosa Cardenas, M. Chua, Y. Masugi, P. Noone, C. Ribeiro, C. Doerschuk, K. Olivier, N. Hasegawa, S. Randell, W. O'Neal, R. C. Boucher
{"title":"MUC5B-Dominated Mucus Hyperproduction in the Bronchiolectatic Airway of Non-Cystic Fibrosis Bronchiectasis (NCFB)","authors":"T. Asakura, K. Okuda, G. Chen, T. Kato, Y. Mikami, G.C. Rodney, S. M. Barbosa Cardenas, M. Chua, Y. Masugi, P. Noone, C. Ribeiro, C. Doerschuk, K. Olivier, N. Hasegawa, S. Randell, W. O'Neal, R. C. Boucher","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2003","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2003","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"63 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"127593713","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Collagen Neoepitope Biomarkers Are Increased in Allergic Broncho-Pulmonary Aspergillosis in Cystic Fibrosis 胶原新表位生物标志物在囊性纤维化变应性支气管-肺曲霉病中升高
A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS Pub Date : 2022-05-01 DOI: 10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1989
M. Weckmann, G. Nissen, J. Sand, H. Jessen, D. Leeming, B. Tümmler, M. Kopp, G. Hansen, E. von Mutius, K. Rabe, T. Bahmer, A. Möller, A. Jung, A. Dittrich, and the ALLIANCE Study Group as part of the German
{"title":"Collagen Neoepitope Biomarkers Are Increased in Allergic Broncho-Pulmonary Aspergillosis in Cystic Fibrosis","authors":"M. Weckmann, G. Nissen, J. Sand, H. Jessen, D. Leeming, B. Tümmler, M. Kopp, G. Hansen, E. von Mutius, K. Rabe, T. Bahmer, A. Möller, A. Jung, A. Dittrich, and the ALLIANCE Study Group as part of the German","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1989","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1989","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"262 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"132866159","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Select Amino Acids Increased Anion Secretion in Primary F508del/F508del HBEC by Activating CFTR and Alternative Anion Secretory Pathways 通过激活CFTR和其他阴离子分泌途径,选择性氨基酸增加原发性F508del/F508del HBEC阴离子分泌
A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS Pub Date : 2022-05-01 DOI: 10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1990
A. Grosche, X. Xu, D. Angoli, J. Guo, S. Prabhakaran, S. Vidyasagar
{"title":"Select Amino Acids Increased Anion Secretion in Primary F508del/F508del HBEC by Activating CFTR and Alternative Anion Secretory Pathways","authors":"A. Grosche, X. Xu, D. Angoli, J. Guo, S. Prabhakaran, S. Vidyasagar","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1990","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1990","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"14 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115630229","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
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