{"title":"Analysis of Th2 Biomarkers to Identify a Th2-High Subgroup of Cystic Fibrosis Patients","authors":"J. Barry, P. Akuthota, D. Conrad","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1995","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1995","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"39 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122945963","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
H. Yin, N. Li, N. Shiner, S. Khanal, J. Schupp, G. Chupp, J. L. Gómez, C. Britto-Leon
{"title":"Sexually Dimorphic Innate Immune Programs of Airway Monocytes in Cystic Fibrosis","authors":"H. Yin, N. Li, N. Shiner, S. Khanal, J. Schupp, G. Chupp, J. L. Gómez, C. Britto-Leon","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1984","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1984","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"8 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"114781568","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
D. Liston, M. Hennig, D. Ishimaru, J. Eby, Salman Khalid Ahmed, X. Yu, A. Alfaifi, H. Lister, M. Sidhu, S. Comini, P. Gao, A. Ashworth, O.M. Mousa, M.J. Torres, D. Siegwart, V. Kharitonov, D. J. Lockhart, B. Wustman
{"title":"An mRNA-Based Therapy to Treat Primary Ciliary Dyskinesia: Aerosol Delivery, Biodistribution and Tolerability","authors":"D. Liston, M. Hennig, D. Ishimaru, J. Eby, Salman Khalid Ahmed, X. Yu, A. Alfaifi, H. Lister, M. Sidhu, S. Comini, P. Gao, A. Ashworth, O.M. Mousa, M.J. Torres, D. Siegwart, V. Kharitonov, D. J. Lockhart, B. Wustman","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2002","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2002","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"17 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"124493104","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
A. Lennox, E. Brutsaert, H. Weber, M. Gorgy, D. Lindsay-Adler, Z. Messer, J. Welter, S. Krishnan, A. Dozor
{"title":"Decline in Vitamin D Levels During Hospitalization for CF Pulmonary Exacerbations","authors":"A. Lennox, E. Brutsaert, H. Weber, M. Gorgy, D. Lindsay-Adler, Z. Messer, J. Welter, S. Krishnan, A. Dozor","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1994","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1994","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"130308432","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
C. Bojanowski, K. Choi, J. Bodnar, S. Lee, G. Trevejo-Nuñez, G. Kurland, J. Bomberger, R. Schleimer, J. Kolls
{"title":"IL-22 Binding Protein (IL-22RA2) Is Associated with Chronic Sinopulmonary Infections in Cystic Fibrosis","authors":"C. Bojanowski, K. Choi, J. Bodnar, S. Lee, G. Trevejo-Nuñez, G. Kurland, J. Bomberger, R. Schleimer, J. Kolls","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1991","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1991","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"14 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"126611634","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
M. Bottier, L. Delgado, M. Shuttleworth, D. Cassidy, M. Crichton, S. Gallant, L. Perrea, S. Aliberti, J. Altenburg, M. Shteinberg, T. Welte, F. Blasi, P. Goeminne, O. Sibila, E. Polverino, C. Hogg, S. Ollosson, M. Loebinger, N. Lorent, J. Chalmers, A. Shoemark
{"title":"Characterization of Ciliary Function in Bronchiectasis (EMBARC-BRIDGE Study)","authors":"M. Bottier, L. Delgado, M. Shuttleworth, D. Cassidy, M. Crichton, S. Gallant, L. Perrea, S. Aliberti, J. Altenburg, M. Shteinberg, T. Welte, F. Blasi, P. Goeminne, O. Sibila, E. Polverino, C. Hogg, S. Ollosson, M. Loebinger, N. Lorent, J. Chalmers, A. Shoemark","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2000","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2000","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"116 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"117229672","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Loss of Small Pulmonary Blood Vessels in Cystic Fibrosis","authors":"J. Amoakon, J. Lee, A. Naren","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1985","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1985","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"161 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122092926","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
T. Asakura, K. Okuda, G. Chen, T. Kato, Y. Mikami, G.C. Rodney, S. M. Barbosa Cardenas, M. Chua, Y. Masugi, P. Noone, C. Ribeiro, C. Doerschuk, K. Olivier, N. Hasegawa, S. Randell, W. O'Neal, R. C. Boucher
{"title":"MUC5B-Dominated Mucus Hyperproduction in the Bronchiolectatic Airway of Non-Cystic Fibrosis Bronchiectasis (NCFB)","authors":"T. Asakura, K. Okuda, G. Chen, T. Kato, Y. Mikami, G.C. Rodney, S. M. Barbosa Cardenas, M. Chua, Y. Masugi, P. Noone, C. Ribeiro, C. Doerschuk, K. Olivier, N. Hasegawa, S. Randell, W. O'Neal, R. C. Boucher","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2003","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a2003","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"63 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"127593713","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
M. Weckmann, G. Nissen, J. Sand, H. Jessen, D. Leeming, B. Tümmler, M. Kopp, G. Hansen, E. von Mutius, K. Rabe, T. Bahmer, A. Möller, A. Jung, A. Dittrich, and the ALLIANCE Study Group as part of the German
{"title":"Collagen Neoepitope Biomarkers Are Increased in Allergic Broncho-Pulmonary Aspergillosis in Cystic Fibrosis","authors":"M. Weckmann, G. Nissen, J. Sand, H. Jessen, D. Leeming, B. Tümmler, M. Kopp, G. Hansen, E. von Mutius, K. Rabe, T. Bahmer, A. Möller, A. Jung, A. Dittrich, and the ALLIANCE Study Group as part of the German","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1989","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1989","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"262 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"132866159","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
A. Grosche, X. Xu, D. Angoli, J. Guo, S. Prabhakaran, S. Vidyasagar
{"title":"Select Amino Acids Increased Anion Secretion in Primary F508del/F508del HBEC by Activating CFTR and Alternative Anion Secretory Pathways","authors":"A. Grosche, X. Xu, D. Angoli, J. Guo, S. Prabhakaran, S. Vidyasagar","doi":"10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1990","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2022.205.1_meetingabstracts.a1990","url":null,"abstract":"","PeriodicalId":129198,"journal":{"name":"A62. CYSTIC FIBROSIS AND NON-CF BRONCHIECTASIS: MECHANISTIC INSIGHTS","volume":"14 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2022-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115630229","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}