CJC Pediatric and Congenital Heart Disease最新文献_第8页

Home-Based Resistance Training Programme in Fontan Patients: It Is Feasible, Safe, and Efficient Fontan患者的家庭阻力训练计划：可行、安全、有效

CJC Pediatric and Congenital Heart Disease Pub Date : 2023-10-01 DOI: 10.1016/j.cjcpc.2023.08.003

Joanie Gagnon MD candidate, PHT , Mickaël Martin MSc , Louise Gosselin RN , Philippe Chetaille MD, MSc

{"title":"Home-Based Resistance Training Programme in Fontan Patients: It Is Feasible, Safe, and Efficient","authors":"Joanie Gagnon MD candidate, PHT , Mickaël Martin MSc , Louise Gosselin RN , Philippe Chetaille MD, MSc","doi":"10.1016/j.cjcpc.2023.08.003","DOIUrl":"https://doi.org/10.1016/j.cjcpc.2023.08.003","url":null,"abstract":"<div><h3>Background</h3><p>Fontan physiology is characterized by a single functional systemic ventricle that reduces cardiac output adaptation and exercise capacity. Peripheral muscle pump is crucial for venous return, and resistance training of the peripheral muscles may be particularly beneficial for cardiac function in these patients. This study explores the feasibility of a training programme including safety and effectiveness, maximal exercise capacity, cardiorespiratory endurance, and quality of life in a Fontan population.</p></div><div><h3>Methods</h3><p>Twelve Fontan patients (18-32 years old) with New York Heart Association functional classes I and II were recruited. The intervention was 12 weeks of home-based exercise programme of 3 sessions per week supervised online by a physiotherapist. Pre- and postintervention evaluations assessed lean body mass, segmental forces with a hand-held dynamometer, maximal oxygen consumption (VO<sub>2</sub>max), cardiovascular endurance, leg endurance with a 1-minute-sit-to-stand test, and quality of life with a 36-item Short-Form Survey.</p></div><div><h3>Results</h3><p>A total of 11 of 12 participants completed 35 of 36 workouts, exceeding our 80% threshold for completion. No adverse events were reported. Leg muscle strength increased significantly (knee extensors improved by 22.8 ± 22.8 N m [17.7%], <em>P</em> = 0.019). Despite no change in VO<sub>2</sub>max, endurance time showed a significant improvement of 5.3 minutes (72%). Perceived physical condition evaluated with a self-perception scale improved significantly. There was no significant difference in the lean body mass and in quality of life.</p></div><div><h3>Conclusion</h3><p>In this small group of post-Fontan patients with mild functional impairments, we describe a structured, accessible, and feasible home-based resistance training programme that seems safe and show improvements in strength and perceived physical condition.</p></div>","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"67739333","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 0

Successful Use of Prostaglandin Infusion in a Two-Month-Old With Coarctation of the Aorta and Ventricular Dysfunction 前列腺素输注在2个月大合并主动脉缩窄和心室功能障碍患者中的成功应用

CJC Pediatric and Congenital Heart Disease Pub Date : 2023-10-01 DOI: 10.1016/j.cjcpc.2023.05.005

Stephanie Hosang MD , Luis Altamirano-Diaz MD

引用次数: 0

Cascade Screening in Familial Hypercholesterolemia: Achieving Buy-In and Turning Patients Into Partners 家族性高胆固醇血症的级联筛查：获得认同并将患者转变为伴侣

CJC Pediatric and Congenital Heart Disease Pub Date : 2023-10-01 DOI: 10.1016/j.cjcpc.2023.06.002

Michael Khoury MD, FRCPC

引用次数: 0

Empowering the Future: Transitioning to Adulthood With Congenital Heart Disease 赋予未来力量：先天性心脏病向成年过渡

CJC Pediatric and Congenital Heart Disease Pub Date : 2023-10-01 DOI: 10.1016/j.cjcpc.2023.09.007

Philip Moons PhD, RN

引用次数: 0

Exploring Barriers and Facilitators to Indirect Cascade Screening for Familial Hypercholesteraemia in a Paediatric/Parent Population 探讨儿童/父母群体中家族性高胆固醇血症间接级联筛查的障碍和促进因素

CJC Pediatric and Congenital Heart Disease Pub Date : 2023-10-01 DOI: 10.1016/j.cjcpc.2023.05.006

Megan A. Dickson MSc , Laura Zahavich MSc , Janet Rush PhD , Stacy Hewson MSc, MS , David Chitayat MD, FABMG, FACMG, FCCMG, FRCPC , Brian W. McCrindle MD, FRCPC, MPH, FACC , Nita Chahal PhD, NP

{"title":"Exploring Barriers and Facilitators to Indirect Cascade Screening for Familial Hypercholesteraemia in a Paediatric/Parent Population","authors":"Megan A. Dickson MSc , Laura Zahavich MSc , Janet Rush PhD , Stacy Hewson MSc, MS , David Chitayat MD, FABMG, FACMG, FCCMG, FRCPC , Brian W. McCrindle MD, FRCPC, MPH, FACC , Nita Chahal PhD, NP","doi":"10.1016/j.cjcpc.2023.05.006","DOIUrl":"https://doi.org/10.1016/j.cjcpc.2023.05.006","url":null,"abstract":"<div><h3>Background</h3><p>Familial hypercholesteraemia (FH), an inherited disorder of cholesterol metabolism, has a prevalence of 1:250 and an associated 6- to 22-fold increased risk for cardiovascular disease. Despite the prevalence and availability of effective risk-reduction treatments, 90% of at-risk Canadians are undiagnosed. Indirect cascade screening from an index case is useful but the uptake is low (<4%), suggesting that barriers may exist. Using the Theoretical Domains Framework, we sought to determine barriers and facilitators among parents of children diagnosed with FH that may influence the uptake of cascade screening among families.</p></div><div><h3>Methods</h3><p>A qualitative description approach was used for virtual interviews with 10 parents of children with FH, recruited from a regional Lipid Clinic in Toronto, Canada. Semistructured interviews were conducted. The data were analysed using a directed content analysis method.</p></div><div><h3>Results</h3><p>Five interconnecting themes were identified that captured both facilitators and barriers of indirect cascade screening: a high level of knowledge about FH after clinic attendance; parents’ surprise of their child’s diagnosis and ongoing worry; parents’ willingness to communicate the need for cholesterol screening; parents’ desire for educational materials, dictated by an external vs internal locus of control; and social and societal influences including the lack of awareness about FH in professional and public domains.</p></div><div><h3>Conclusions</h3><p>The themes identified will inform next steps in programme development. An urgent need was identified for strategies to educate the public and primary care providers about FH and blood cholesterol/genetic screening.</p></div>","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"67739351","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 1

Information for Readers 读者资讯

CJC Pediatric and Congenital Heart Disease Pub Date : 2023-08-01 DOI: 10.1016/S2772-8129(23)00106-9

引用次数: 0

Evaluating a Telemedicine Video Game–Linked High-Intensity Interval Training Exercise Programme in Paediatric Heart Transplant Recipients 评估儿童心脏移植受者与远程医疗视频游戏相关的高强度间歇训练运动计划

CJC Pediatric and Congenital Heart Disease Pub Date : 2023-08-01 DOI: 10.1016/j.cjcpc.2023.04.001

Christopher M. Spence MD , Rae Foshaug , Samira Rowland BSc , Amanda Krysler MSc , Jennifer Conway MD, MSc , Simon Urschel MD , Lori West MD, PhD , Michael Stickland PhD , Pierre Boulanger MSc, PhD , John C. Spence PhD , Michael Khoury MD

{"title":"Evaluating a Telemedicine Video Game–Linked High-Intensity Interval Training Exercise Programme in Paediatric Heart Transplant Recipients","authors":"Christopher M. Spence MD , Rae Foshaug , Samira Rowland BSc , Amanda Krysler MSc , Jennifer Conway MD, MSc , Simon Urschel MD , Lori West MD, PhD , Michael Stickland PhD , Pierre Boulanger MSc, PhD , John C. Spence PhD , Michael Khoury MD","doi":"10.1016/j.cjcpc.2023.04.001","DOIUrl":"https://doi.org/10.1016/j.cjcpc.2023.04.001","url":null,"abstract":"<div><p>Paediatric heart transplant recipients (HTRs) have reduced exercise capacity, physical activity (PA), health-related quality of life (HRQoL), and self-efficacy towards PA. Exercise interventions have demonstrated improvements in exercise capacity and functional status in adult HTRs, with a specific emerging interest in the role of high-intensity interval training (HIIT). Studies of exercise interventions in paediatric HTRs have been limited and nonrandomized to date. HIIT has not yet been evaluated in paediatric HTRs. We thus seek to evaluate the safety and feasibility of a randomized crossover trial of a 12-week, home-based, video game–linked HIIT intervention using a cycle ergometer with telemedicine and remote physiological monitoring capabilities (MedBIKE) in paediatric HTRs. The secondary objective is to evaluate the impact of the intervention on (1) exercise capacity, (2) PA, (3) HRQoL and self-efficacy towards PA, and (4) sustained changes in secondary outcomes at 6 and 12 months after intervention. After a baseline assessment of the secondary outcomes, participants will be randomized to receive the MedBIKE intervention (12 weeks, 36 sessions) or usual care. After the intervention and a repeated assessment, all participants will cross over. Follow-up assessments will be administered at 6 and 12 months after the MedBIKE intervention. We anticipate that the MedBIKE intervention will be feasible and safely yield sustained improvements in exercise capacity, PA, HRQoL, and self-efficacy towards PA in paediatric HTRs. This study will serve as the foundation for a larger, multicentre randomized crossover trial and will help inform exercise rehabilitation programmes for paediatric HTRs.</p></div>","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49737722","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 2

Long-term Outcome of Simultaneous Transcatheter Pulmonary and Tricuspid Valve-in-Valve Implantation in Ebstein Malformation With Pulmonary Insufficiency 经导管肺动脉瓣与三尖瓣瓣内植入治疗Ebstein畸形伴肺功能不全的远期疗效

CJC Pediatric and Congenital Heart Disease Pub Date : 2023-08-01 DOI: 10.1016/j.cjcpc.2023.03.003

Mohamed Al Nasef MD, FPCIS, Irfan Saleem MB, Ahmad Salim MD, Merna Atiyah MD, Khalid S. Al Najashi MD

引用次数: 0

Textile-based Wearable to Monitor Heart Activity in Paediatric Population: A Pilot Study 基于纺织品的可穿戴设备监测儿科人群的心脏活动:一项试点研究

CJC Pediatric and Congenital Heart Disease Pub Date : 2023-08-01 DOI: 10.1016/j.cjcpc.2023.05.007

Nasim Montazeri Ghahjaverstan PhD , Diana Balmer-Minnes MSc , Behrad Taghibeyglou MSc , Bastien Moineau PhD , Gabriela Chaves PhD , Milad Alizadeh-Meghrazi PhD , Barbara Cifra MD , Aamir Jeewa MB BCh , Azadeh Yadollahi PhD

{"title":"Textile-based Wearable to Monitor Heart Activity in Paediatric Population: A Pilot Study","authors":"Nasim Montazeri Ghahjaverstan PhD , Diana Balmer-Minnes MSc , Behrad Taghibeyglou MSc , Bastien Moineau PhD , Gabriela Chaves PhD , Milad Alizadeh-Meghrazi PhD , Barbara Cifra MD , Aamir Jeewa MB BCh , Azadeh Yadollahi PhD","doi":"10.1016/j.cjcpc.2023.05.007","DOIUrl":"https://doi.org/10.1016/j.cjcpc.2023.05.007","url":null,"abstract":"<div><h3>Background</h3><p>Cardiac monitoring for children with heart disease still employs common clinical techniques that require visits to hospital either in an ambulatory or inpatient setting. Frequent cardiac monitoring, such as heart rate monitoring, can limit children’s physical activity and quality of life. The main objective of this study is to evaluate the performance of a textile-based device (SKIIN) in measuring heart rate (HR) in different tasks: lying down, sitting, standing, exercising, and cooling down.</p></div><div><h3>Methods</h3><p>Twenty participants including healthy children and children with heart disease were included in this study. The difference between the HRs recorded by the SKIIN was compared with a reference electrocardiogram collection by normalized root mean squared error. Participants completed a questionnaire on their experience wearing the textile device with additional parental feedback on the textile device collected.</p></div><div><h3>Results</h3><p>Participants had the median age of 14 years (range: 10-17 years), with body mass index 23.1 ± 3.8 kg/m<sup>2</sup> and body surface area 1.70 ± 0.25 m<sup>2</sup>. The HR recorded by SKIIN and reference system significantly changes between tasks (<em>P</em> < 0.001), while not significantly different from each other (<em>P</em> > 0.05). The normalized root mean squared error was 3.8% ± 3.0% and 3.6% ± 3.7% for healthy and the heart disease groups, respectively. All participants found the textile device non-irritating and easy to wear.</p></div><div><h3>Conclusions</h3><p>This study provides proof of concept that HR can be robustly and conveniently monitored by smart textiles, with similar accuracy to standard-of-care devices.</p></div>","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"49725184","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

引用次数: 1

Advancing Wearable Technology for Monitoring Heart Activity in Paediatric Populations 推进可穿戴技术监测儿科人群的心脏活动

CJC Pediatric and Congenital Heart Disease Pub Date : 2023-08-01 DOI: 10.1016/j.cjcpc.2023.06.003

Colin K. Drummond PhD, MBA , Animesh Tandon MD, MS

引用次数: 0