CJC Pediatric and Congenital Heart Disease最新文献

{"title":"Severe Inflammatory Heart Disease in Children With Lupus: A Case Series","authors":"Geena Kim MD , Deborah M. Levy MD , Dawn Nicolson MSc , Sunghoon Minn MSc , Andrea Knight MD , Linda T. Hiraki MD, ScD , Aine Lynch MBBCh , Emilie Jean-St-Michel MD , Jenna Ashkanase MD , Aamir Jeewa MBBCh, FRCPC","doi":"10.1016/j.cjcpc.2024.05.005","DOIUrl":"10.1016/j.cjcpc.2024.05.005","url":null,"abstract":"","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2024-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.sciencedirect.com/science/article/pii/S2772812924000435/pdfft?md5=e290183279c1422b7675774cabe923da&pid=1-s2.0-S2772812924000435-main.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142076711","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Nonfatal Isolated Cardiac Nonlysosomal Glycogenosis: A Rare Cause of Infantile Hypertrophic Cardiomyopathy","authors":"","doi":"10.1016/j.cjcpc.2024.02.003","DOIUrl":"10.1016/j.cjcpc.2024.02.003","url":null,"abstract":"","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2024-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.sciencedirect.com/science/article/pii/S2772812924000216/pdfft?md5=5f1bae0ed43d51d94298cf92d583604a&pid=1-s2.0-S2772812924000216-main.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"140464814","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Strategies to Overcome Barriers to Physical Activity Participation in Children and Adults Living With Congenital Heart Disease: A Narrative Review","authors":"","doi":"10.1016/j.cjcpc.2024.05.002","DOIUrl":"10.1016/j.cjcpc.2024.05.002","url":null,"abstract":"<div><p>Physical activity participation is critical for optimal physical, psychological, and cognitive health in children and adults living with congenital heart disease (CHD). Majority of the general population are not sufficiently active, and with the added psychological, physical, and socioeconomic barriers faced by individuals with CHD, it is unsurprising that many people living with CHD do not meet the recommendations for physical activity either. The aim of this review is to outline lifelong physical activity barriers faced by individuals living with CHD and provide age-appropriate strategies that can be used to ensure the development of long-term positive physical activity behaviours. Barriers to physical activity include safety fears, lack of encouragement, low exercise self-efficacy, body image concerns, limited education, socioeconomic status, reduced access to resources, and cardiac diagnosis and severity. These barriers are multifaceted and often begin in early childhood and continue to develop well into adulthood. Therefore, it is important for children to participate in physical activity from early stages of life as it has been shown to improve cardiorespiratory fitness, muscular endurance, and quality of life. Current literature demonstrates that participation in physical activity and higher intensity exercise after appropriate screening is safe and should be encouraged rather than dissuaded in people born with a congenital heart condition.</p></div>","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2024-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.sciencedirect.com/science/article/pii/S277281292400040X/pdfft?md5=94843d6f1f675657d4193d810858b3af&pid=1-s2.0-S277281292400040X-main.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"141049076","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Effective Management of Cor Triatriatum Dexter Using Double Balloon Dilatation in a Paediatric Age Group Case-Report Study","authors":"","doi":"10.1016/j.cjcpc.2024.06.001","DOIUrl":"10.1016/j.cjcpc.2024.06.001","url":null,"abstract":"","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2024-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.sciencedirect.com/science/article/pii/S2772812924000599/pdfft?md5=88b5260e75db582a0b79fa1d2314089e&pid=1-s2.0-S2772812924000599-main.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"141402863","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Radiation Reduction in Paediatric Cardiac Catheterization: We Can Go Even Lower","authors":"Talya Finke MBBS, BSc (Hons) ,&nbsp;Gur Mainzer MD ,&nbsp;Yonatan Yitzhak MRT ,&nbsp;Sunder Devadas MRT ,&nbsp;Dariusz Mroczek CVT, BioMed-Eng ,&nbsp;Lee N. Benson MD, FRCPC, MSCAI ,&nbsp;Sharon Borik MD","doi":"10.1016/j.cjcpc.2024.05.004","DOIUrl":"10.1016/j.cjcpc.2024.05.004","url":null,"abstract":"<div><h3>Background</h3><p>Radiation reduction is an integral component in the management of a paediatric cardiac catheterization laboratory. Simple and easily implementable protocol changes and technical upgrades have been shown to significantly reduce radiation exposure.</p></div><div><h3>Methods</h3><p>Radiation exposures (2020-2022) at Safra Children’s Hospital, Sheba Medical Center, Israel (unit A: n = 672) were retrospectively reviewed, including dose area product (DAP) (μGy m²), DAP/kg, Air Kerma (mGy), and fluoroscopy time (minutes) for 16 procedural types. Median doses were compared with those measured (2011-2014) at the Hospital for Sick Children, Toronto, Canada (unit B: n = 2033). Radiation reduction techniques included fluoroscopy acquisition at 7.5 frames/s, removal of antiscatter grids for children &lt;30 kg, limiting field of view, use of Philips ClarityIQ technology, and an institutional culture of radiation mindedness.</p></div><div><h3>Results</h3><p>Exposure was significantly lower in unit A in 14 of 16 procedure types. Total median doses were lower in unit A (DAP: 91.4 [44.7-205.4] vs 387 [138.2-1339] μGy m² [<em>P</em> &lt; 0.001], DAP/kg: 9.33 [4.3-16.4] vs 29.22 [12.8-65.9] μGy m²/kg [<em>P</em> &lt; 0.001], and Air Kerma: 14.9 [7.8-29] vs 61 [23-176.4] mGy [<em>P</em> &lt; 0.001]) despite higher fluoroscopy time (14.1 [4.2-24.6] vs 12.3 [6.8-23.3] minutes [<em>P</em> = 0.03]). DAP was lower for specific procedures including pulmonary valvuloplasty (46.3 [14.3-219.3] vs 127 [60-323] μGy m² [<em>P</em> &lt; 0.001]) and patent ductus arteriosus closure (51.9 [18.8-111.8] vs 178 [96-410] μGy m² [<em>P</em> &lt; 0.001]).</p></div><div><h3>Conclusions</h3><p>Enhanced radiation reduction techniques can lead to lower than previously published exposure levels across a wide range of procedure types when employing dose-limiting protocols and radiation reduction technology.</p></div>","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2024-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.sciencedirect.com/science/article/pii/S2772812924000423/pdfft?md5=f403cdb9a3b0d4b0ed13b335a2620191&pid=1-s2.0-S2772812924000423-main.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142076708","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Behaviour Concerns in Preschool Cardiac Surgery Survivors","authors":"Sabrina H.Y. Eliason MD ,&nbsp;Charlene M.T. Robertson MD ,&nbsp;Susan A. Bobbitt MD ,&nbsp;Sara Khademioureh MAct Sc ,&nbsp;Irina A. Dinu PhD ,&nbsp;Ari R. Joffe MD ,&nbsp;Bryan V. Acton PhD","doi":"10.1016/j.cjcpc.2024.04.001","DOIUrl":"10.1016/j.cjcpc.2024.04.001","url":null,"abstract":"<div><h3>Background</h3><p>Behaviour concerns (BC) are reported in survivors of complex cardiac surgery (CCSx) with inconsistent evidence about health and demographic variables that impact outcomes.</p></div><div><h3>Methods</h3><p>A prospective inception-cohort study of infants (without known chromosomal abnormalities) after CCSx from 2001 to 2017 determined Behaviour Assessment System for Children (BASC-II/III) parent rating scales at 4.5 years. <em>T</em> scores ≥60 for externalizing, internalizing, and the Behavioural Symptoms Index and ≤40 for adaptive behaviour defined BC. Potential predictive variables included demographic, acute care, and health factors after initial CCSx. Multiple logistic regression using the purposeful selection method gave odds ratios (ORs) with 95% confidence intervals (CIs).</p></div><div><h3>Results</h3><p>Survivors (n = 585; 61% boys, 40% single ventricle) were assessed at a median age of 55 months (interquartile range: 53, 57 months). Independent predictors were noncardiac hospitalizations (OR: 1.10, 95% CI: 1.02, 1.19; <em>P</em> = 0.015) for externalizing; noncardiac hospitalizations (OR: 1.14, 95% CI: 1.05, 1.24; <em>P</em> = 0.003), female sex (OR: 1.62, 95% CI: 1.04, 2.52; <em>P</em> = 0.031), and single ventricle (OR: 1.82, 95% CI: 1.04, 3.17; <em>P</em> = 0.035) for internalizing; noncardiac hospitalizations (OR: 1.10, 95% CI: 1.02, 1.19; <em>P</em> = 0.017), socioeconomic status (SES) (OR: 0.98, 95% CI: 0.96, 0.10; <em>P</em> = 0.031), and years of maternal schooling (OR: 0.91, 95% CI: 0.84, 0.10; <em>P</em> = 0.04) for adaptive; and extracorporeal life-saving support (OR: 2.03, 95% CI: 1.01, 3.96; <em>P</em> = 0.041) for the Behavioural Symptoms Index, indicating more pervasive behaviours.</p></div><div><h3>Conclusions</h3><p>The number of noncardiac hospitalizations predicted increased odds of BC and requires further attention. Improving inpatient trauma-informed care experiences and optimizing access to primary care to prevent noncardiac hospitalization may be modifiable.</p></div>","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2024-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.sciencedirect.com/science/article/pii/S2772812924000381/pdfft?md5=0b3e1115d1c09283c8fecaa3dfd03aa8&pid=1-s2.0-S2772812924000381-main.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"142076709","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Childhood Maltreatment and Body Mass Index in Older Adults With Chronic Illness","authors":"Vicki St-Arnaud MSc ,&nbsp;Ann Xiuli Chicoine BSc ,&nbsp;Jean-Claude Tardif MD ,&nbsp;David Busseuil PhD ,&nbsp;Bianca D’Antono PhD","doi":"10.1016/j.cjcpc.2024.03.002","DOIUrl":"10.1016/j.cjcpc.2024.03.002","url":null,"abstract":"<div><h3>Background</h3><p>Childhood trauma has been associated with greater psychological and physical morbidity, including a greater risk of developing coronary artery disease (CAD). Emotional dysregulation and increased body mass index (BMI) may be involved. This study evaluated whether (1) childhood maltreatment is associated with a higher BMI at study onset and with greater increases in BMI 5 years later among older adults with CAD or other chronic illnesses; (2) sex and/or CAD status moderate these results; and (3) baseline symptoms of anxiety, depression, and perceived stress (emotional dysregulation) mediate the association between childhood maltreatment and BMI at follow-up.</p></div><div><h3>Methods</h3><p>A total of 1232 men and women (aged 60.86 [6.95] years) completed validated questionnaires on childhood maltreatment and symptoms of psychological distress. The weight and height of the participant were measured, and the BMI was calculated using the weight (kg)/height (m²) ratio.</p></div><div><h3>Results</h3><p>Childhood maltreatment was not significantly associated with BMI at study onset nor at follow-up. This relation did not differ as a function of sex nor CAD status. Although childhood maltreatment was associated with significantly greater psychological distress at study onset (all <em>P</em> &lt; 0.001), there latter was not found to mediate the relation between maltreatment and change in BMI at follow-up.</p></div><div><h3>Conclusions</h3><p>In contrast to previous literature, childhood maltreatment was not associated with BMI nor with the change in BMI over 5 years in men and women with chronic disease. However, as psychological distress increases risk for morbidity and mortality, it may represent an important target for prevention and intervention in survivors of childhood maltreatment.</p></div>","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2024-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.sciencedirect.com/science/article/pii/S277281292400037X/pdfft?md5=8641f5ea353fcb65d3615aaa40356b5a&pid=1-s2.0-S277281292400037X-main.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"140781559","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"The Ross Procedure in Children and Infants: A Systematic Review With Pooled Analyses","authors":"Nabil Dib MD, MSc ,&nbsp;Walid Ben Ali MD, PhD ,&nbsp;Thierry Ducruet MSc ,&nbsp;Ofélie Trudeau MSc ,&nbsp;Pierre-Luc Bernier MD ,&nbsp;Nancy Poirier MD ,&nbsp;Paul Khairy MD, PhD","doi":"10.1016/j.cjcpc.2024.02.004","DOIUrl":"10.1016/j.cjcpc.2024.02.004","url":null,"abstract":"<div><h3>Background</h3><p>The Ross procedure is a surgical option for congenital aortic stenosis that involves replacing the diseased aortic valve with a pulmonary autograft. Little is known about outcomes in children, particularly those younger than 1 year.</p></div><div><h3>Methods</h3><p>A systematic review with pooled analyses was conducted according to Preferred Reporting Items for Systematic Reviews and Meta-Analyses (PRISMA) criteria. Inferred individual patient data were extracted from life tables. The primary end points were early (≤30 days) and late (&gt;30 days) mortality rates following the Ross procedure in children. Secondary end points were freedom from reintervention for the right ventricular outflow tract and pulmonary autograft. These end points were assessed in the overall population of children. Sensitivity analyses were performed in subgroups younger than 1 year of age (infants) and in noninfant children.</p></div><div><h3>Results</h3><p>A total of 25 studies on 2737 patients met inclusion criteria. The pooled early survival rate was 96.0% (95% confidence interval [CI]: 95.1%-96.8%) overall and 86.8% (95% CI: 82.1%-90.3%) among infants. Pooled overall 10-year survival, freedom from pulmonary autograft reintervention, and freedom from right ventricular outflow tract reintervention rates were 91.1%, 90.2%, and 79.7%, respectively. Corresponding pooled rates in infants were 79.3%, 87.1%, and 51.2%. Mortality was significantly higher among infants compared with noninfant children (hazard ratio: 3.38, 95% CI: 2.44-4.68; <em>P</em> &lt; 0.001). In metaregression analyses, younger age was strongly associated with poorer survival and higher reintervention rates.</p></div><div><h3>Conclusions</h3><p>Modest survival and autograft reoperation rates were observed following the Ross procedure in children. Surgery in infancy was strongly associated with poorer survival and higher reintervention rates.</p></div>","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2024-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.sciencedirect.com/science/article/pii/S2772812924000228/pdfft?md5=c39d3a451aed5c004aa2f4517c6ce8ab&pid=1-s2.0-S2772812924000228-main.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"140468316","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"Arrhythmia as a Presenting Feature of Atypical Cardiac Rhabdomyoma in Children","authors":"Biobelemoye Irabor BSc ,&nbsp;Aneal Khan MSc, MD ,&nbsp;Michelle Noga MD ,&nbsp;Kimberley Myers MD ,&nbsp;Steven C. Greenway MSc, MD ,&nbsp;Ali Fatehi Hassanabad MD, MSc","doi":"10.1016/j.cjcpc.2024.02.002","DOIUrl":"10.1016/j.cjcpc.2024.02.002","url":null,"abstract":"","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2024-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.sciencedirect.com/science/article/pii/S2772812924000204/pdfft?md5=de7a3d42c3efbec72ab4df93c3e6d29c&pid=1-s2.0-S2772812924000204-main.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139966962","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}

{"title":"The Weight of Trauma: Navigating Collider Stratification Bias in the Association Between Childhood Maltreatment and Adult Body Mass Index","authors":"Nicholas Grubic MSc ,&nbsp;Jayati Khattar MPH ,&nbsp;Vanessa De Rubeis PhD ,&nbsp;Hailey R. Banack PhD ,&nbsp;Julia Dabravolskaj PhD ,&nbsp;Katerina Maximova PhD","doi":"10.1016/j.cjcpc.2024.05.001","DOIUrl":"10.1016/j.cjcpc.2024.05.001","url":null,"abstract":"","PeriodicalId":100249,"journal":{"name":"CJC Pediatric and Congenital Heart Disease","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2024-06-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.sciencedirect.com/science/article/pii/S2772812924000393/pdfft?md5=27f78b3793bcb3024e5e25af45761362&pid=1-s2.0-S2772812924000393-main.pdf","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"141044997","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}