{"title":"Infantile Fibrosarcoma of Tongue: A Rare Tumor.","authors":"Fazal I Wahid, Bakht Zada, Gul Rafique","doi":"10.21699/ajcr.v7i3.432","DOIUrl":"https://doi.org/10.21699/ajcr.v7i3.432","url":null,"abstract":"<p><p>Infantile fibrosarcoma is very rare tumor and seldom occurs in oral cavity. Overall good prognosis is reported in more than 80% cases. We present a 5-month old female patient with swelling of the tongue for four months. This was excised completely. Histopathology and immunohistochemistry revealed it as infantile fibrosarcoma of grade II. </p>","PeriodicalId":89657,"journal":{"name":"APSP journal of case reports","volume":"7 3","pages":"23"},"PeriodicalIF":0.0,"publicationDate":"2016-06-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4921220/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34654330","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Malignant Myopericytoma of Shoulder: A Rare Lesion.","authors":"Fariba Binesh, Reza Nafisi Moghadam, Masoud Shabani, Mohammad Reza Mortazavizadeh, Saeedeh Zare","doi":"10.21699/ajcr.v7i3.421","DOIUrl":"https://doi.org/10.21699/ajcr.v7i3.421","url":null,"abstract":"<p><p>Myopericytoma is a soft tissue tumor with perivascular myoid differentiation. It accounts for 1% of the vascular tumors and involves mostly cutaneous or subcutaneous tissue of the limbs in adults. Malignant myopericytoma is exceedingly rare. A 15-year old girl presented with slowly progressive mass over left shoulder region. Histopathology and immunohistochemistry after complete excision revealed it as malignant myopericytoma. </p>","PeriodicalId":89657,"journal":{"name":"APSP journal of case reports","volume":"7 3","pages":"21"},"PeriodicalIF":0.0,"publicationDate":"2016-06-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4921218/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34654328","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Preduodenal Portal Vein with Situs Inversus Totalis causing Duodenal Obstruction.","authors":"Flavia D'souza, Amol Nage, Pradnya Bendre","doi":"10.21699/ajcr.v7i3.435","DOIUrl":"https://doi.org/10.21699/ajcr.v7i3.435","url":null,"abstract":"<p><p>Congenital duodenal obstruction sometimes may be secondary to unusual entities like preduodenal portal vein (PDPV) the identification of which is very important to avoid inadvertent injury or incorrect surgery. A 6-day old neonate presented with congenital duodenal obstruction. Investigations revealed situs inversus totalis with many congenital cardiovascular anomalies. At operation preduodenal portal vein and malrotation were found. Correction of malrotation and bypass duodeno-duodenostomy were done. </p>","PeriodicalId":89657,"journal":{"name":"APSP journal of case reports","volume":"7 3","pages":"24"},"PeriodicalIF":0.0,"publicationDate":"2016-06-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4921221/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34654331","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Abhijeet D Sawant, Rasik Shah, Nitin Shah, Tarun Gupta
{"title":"A Rare Cause of Chronic Life Threatening Bleeding in a Girl: The Ulcerated Blind Loops.","authors":"Abhijeet D Sawant, Rasik Shah, Nitin Shah, Tarun Gupta","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Ulceration in a blind loop can lead to massive gastrointestinal tract (GIT) bleeding. A 13-year old girl presented with symptomatic melena requiring repeated blood transfusion since childhood. She was an operated case of small bowel atresia in neonatal life. Her upper and lower gastrointestinal endoscopies were normal. Operation showed presence of multiple ulcers in two blind loops (parts of previous side to side anastomosis) and at the anastomotic site. She underwent resection and end-to-end anastomosis of the small bowel leading to complete resolution of melena and anemia. </p>","PeriodicalId":89657,"journal":{"name":"APSP journal of case reports","volume":"7 2","pages":"13"},"PeriodicalIF":0.0,"publicationDate":"2016-04-24","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4852056/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34540782","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Rapidly Enlarging Intra-abdominal Ileal Duplication Cyst in a Newborn.","authors":"Emrah Aydın","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":89657,"journal":{"name":"APSP journal of case reports","volume":"7 2","pages":"18"},"PeriodicalIF":0.0,"publicationDate":"2016-04-24","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4852061/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34540788","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Renal Agenesis with Full Length Ipsilateral Refluxing Ureter.","authors":"Dilip Kumar Pal, Vipin Chandra, Manju Banerjee","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Unilateral renal agenesis with vesicoureteral reflux in the ipsilateral full length ureter is a rare phenomenon. Herein we report a case of 10-year old boy who presented with recurrent urinary tract infections. No renal tissue was identified on left side in various imaging studies. Micturating cystourethrogram (MCUG) showed left sided refluxing and blind ending ureter. Left ureterectomy was done because of recurrent UTI in the refluxing system. </p>","PeriodicalId":89657,"journal":{"name":"APSP journal of case reports","volume":"7 2","pages":"11"},"PeriodicalIF":0.0,"publicationDate":"2016-04-24","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4852054/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34540781","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Arzu Akdag, Karar Orkun Anadut, Omer Yalcin, Mete Kaya
{"title":"Fetal Bowel Dilatation due to Intestinal Neuronal Dysplasia: A Rarity.","authors":"Arzu Akdag, Karar Orkun Anadut, Omer Yalcin, Mete Kaya","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Intestinal neuronal dysplasia (IND) type B is characterized by malformation of parasympathetic plexus and manifests at more than 6 month of age with progressive severe constipation. We report a case of IND type B presented with bowel dilatation on antenatal scan and neonatal intestinal obstruction which is unusual with this type of IND. </p>","PeriodicalId":89657,"journal":{"name":"APSP journal of case reports","volume":"7 2","pages":"14"},"PeriodicalIF":0.0,"publicationDate":"2016-04-24","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4852057/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34540784","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
R Angotti, F Molinaro, M Sica, F Mariscoli, E Bindi, O Mazzei, F Ferrara, M Messina
{"title":"Association of Duodenal Atresia, Malrotation, and Atrial Septal Defect in a Down-Syndrome Patient.","authors":"R Angotti, F Molinaro, M Sica, F Mariscoli, E Bindi, O Mazzei, F Ferrara, M Messina","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Duodenal atresia is the frequent cause of neonatal intestinal obstruction. The association between duodenal atresia, intestinal malrotation, cardiac anomalies and Down syndrome is infrequently reported. We present a prenatally suspected case of duodenal atresia which was associated with malrotation and atrial septal defect in a patient of Down syndrome. Duodenotomy and resection of web was performed in addition to Ladd's procedure. Postoperative course remained uneventful. </p>","PeriodicalId":89657,"journal":{"name":"APSP journal of case reports","volume":"7 2","pages":"16"},"PeriodicalIF":0.0,"publicationDate":"2016-04-24","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4852059/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34540786","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Primary Testicular Pre-B Lymphoblastic Lymphoma.","authors":"Fariba Binesh, Mohammad Forat Yazdi, Alireza Jenabzadeh, Somayeh Hosseini, Roghayeh Massumi","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Primary testicular lymphoblastic lymphoma is a rare entity. We report a case of a 13-year-old boy referred with unilateral testicular swelling. After preliminary work-up orchiectomy was performed Histopathology detected primary testicular lymphoblastic lymphoma. Lymphoblastic lymphoma should be considered in the differential diagnosis of testicular masses in children. </p>","PeriodicalId":89657,"journal":{"name":"APSP journal of case reports","volume":"7 2","pages":"15"},"PeriodicalIF":0.0,"publicationDate":"2016-04-24","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4852058/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34540787","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Primary Synovial Sarcoma of Lung: A Rare Tumor.","authors":"Prince Raj, Parveen Kumar, Yogesh Kumar Sarin","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Synovial sarcoma of lung is a rare tumor with few case reports in literature. Though named synovial sarcoma due to its resemblance to synovium on light microscopy, it arises from mesenchymal tissue. Here, we present a case of synovial sarcoma of lung in a 7-year old boy, with main emphasis on difficulty faced in the management. </p>","PeriodicalId":89657,"journal":{"name":"APSP journal of case reports","volume":"7 2","pages":"12"},"PeriodicalIF":0.0,"publicationDate":"2016-04-24","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4852055/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"34540783","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}