{"title":"Isolated Biventricular Noncompaction in an adult with severe pulmonary hypertension: An association reviewed.","authors":"N Awasthy, M Tomar, S Radhakrishnan","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Biventricular noncompaction is a recently recognized rare form of cardiomyopathy. It is characterized by altered structure of myocardial wall as a result of intrauterine arrest of compaction of the myocardial fibers in absence of coexisting congenital lesion. Left ventricle is the most affected site for noncompaction, but right ventricular involvement has been reported in a few cases. Diagnosis is made with 2-dimensional echocardiography or cardiac magnetic resonance imaging. While major clinical manifestations are heart failure, arrhythmias and embolic events,pulmonary artery hypertension (PAH) has not been well elaborated in the literature. We present a 13-year old boy who had Biventricular noncompaction complicated by severe pulmonary hypertension. Pulmonary hypertension may be a consequence of increased pulmonary venous pressures caused by systolic and diastolic left ventricular dysfunction secondary to noncompaction. We review the literature particularly with reference toPAH in the context of our case.</p>","PeriodicalId":89564,"journal":{"name":"Images in paediatric cardiology","volume":"14 1","pages":"1-5"},"PeriodicalIF":0.0,"publicationDate":"2012-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3663152/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"31467196","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Cor triatriatum sinister with situs inversus totalis in an infant.","authors":"A Taksande, A Gadekar, S Meshram, S Pathak","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Cor triatriatum sinister is a rare congenital cardiac malformation characterized by a membrane in the left atrium which separates the left atrium into the proximal and distal chambers. Association of cor triatriatum is extremely rare with situs inversus totalis. Here we report a rare case of cor triatriatum sinister with situs inversus totalis in a 5 month old female infant.</p>","PeriodicalId":89564,"journal":{"name":"Images in paediatric cardiology","volume":"14 1","pages":"6-10"},"PeriodicalIF":0.0,"publicationDate":"2012-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3663153/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"31468134","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Patent arterial duct occlusion with two Amplatzer Duct Occluder devices.","authors":"V Grech, Jv Degiovanni","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>It is accepted practice to close large patent arterial ducts (PDA) with Amplatzer duct occluder devices, with extremely low rates of residual PDA. We report a child who required device closure of PDA with two Amplatzer PDA devices on two separate occasions, despite the first device deployment being a standard placement of an appropriately sized Amplatzer device in the usual position.</p>","PeriodicalId":89564,"journal":{"name":"Images in paediatric cardiology","volume":"13 4","pages":"6-9"},"PeriodicalIF":0.0,"publicationDate":"2011-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3662088/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"31467195","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Y Shiina, S Slavik, H Uemura, Kp McCarthy, Ho S Yen
{"title":"The inferior caval vein draining into the left atrial cavity - a rare case.","authors":"Y Shiina, S Slavik, H Uemura, Kp McCarthy, Ho S Yen","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":89564,"journal":{"name":"Images in paediatric cardiology","volume":"13 4","pages":"1-5"},"PeriodicalIF":0.0,"publicationDate":"2011-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3662087/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"31467194","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Three-dimensional trans-esophageal Echocardiographic Evaluation of Atrial Septal Defects: A Pictorial Essay.","authors":"Vinay K Sharma, S Radhakrishnan, S Shrivastava","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>This pictorial assay illustrates the methodology of evaluating the atrial septal defects by three dimensional transesophageal echocardiography with the help of representative images. The article starts by discussing the technical details of how to acquire and crop the dataset to reconstruct the transesophageal three dimensional echocardiographic images of the inter atrial septum. Next, the anatomical details of the normal inter atrial septum are illustrated, followed by representative examples of all the possible defects of inter atrial septum. All the images have been reproduced in a uniform pattern which is similar to the view of the inter atrial septum that is seen in the real life situation by the surgeon.</p>","PeriodicalId":89564,"journal":{"name":"Images in paediatric cardiology","volume":"13 3","pages":"1-18"},"PeriodicalIF":0.0,"publicationDate":"2011-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3232598/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"30488959","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
N Datrice, J Milliken, M Kirsh, A Abolhoda, F Saremi, L Sender
{"title":"Metastatic Ewing's Sarcoma to the Right Ventricle.","authors":"N Datrice, J Milliken, M Kirsh, A Abolhoda, F Saremi, L Sender","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":89564,"journal":{"name":"Images in paediatric cardiology","volume":"13 2","pages":"4-7"},"PeriodicalIF":0.0,"publicationDate":"2011-04-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3232596/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"30488958","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Y Derraz, R Amri, D Mahjoubi, T El Houari, M Cherti
{"title":"Use of interventional catheterization before surgery in an adult with univentricular heart.","authors":"Y Derraz, R Amri, D Mahjoubi, T El Houari, M Cherti","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":89564,"journal":{"name":"Images in paediatric cardiology","volume":"13 2","pages":"1-3"},"PeriodicalIF":0.0,"publicationDate":"2011-04-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3232597/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"30488957","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Double orifice mitral valve associated with Ventricular Septal Defect in an infant: Case Report.","authors":"A Taksande, V Goutami, E Thomas","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Double orifice mitral valve (DOMV) is an uncommon anomaly characterized by a mitral valve with a single fibrous annulus with two orifices opening into the left ventricle. Here we present a rare case of DOMV with ventricular septal defect (VSD) which was detected by 2-D echocardiography.</p>","PeriodicalId":89564,"journal":{"name":"Images in paediatric cardiology","volume":"13 1","pages":"6-9"},"PeriodicalIF":0.0,"publicationDate":"2011-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3232594/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"30488956","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
K Iqbal, Sm Ali, Na Tramboo, Aa Lone, S Kaul, N Kaul, I Hafiz
{"title":"Patent ductus arteriosus device embolization.","authors":"K Iqbal, Sm Ali, Na Tramboo, Aa Lone, S Kaul, N Kaul, I Hafiz","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>Nonsurgical closure of patent ductus arteriosus (PDA) using a duct occluder placed percutaneously is currently the first line of therapy and the success rate is quite high. Several devices are currently available. An eight year child underwent device closure of the ductus. However after deployment of the device it, became dislodged into the left pulmonary artery. Several attempts at catheter retrieval failed. The child underwent successful surgical removal of the device without cardiopulmonary bypass.</p>","PeriodicalId":89564,"journal":{"name":"Images in paediatric cardiology","volume":"13 1","pages":"1-5"},"PeriodicalIF":0.0,"publicationDate":"2011-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3232595/pdf/","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"30488955","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"OA","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}