Perspectives in pediatric pathology最新文献

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Pathology of peroxisomal disorders. 过氧化物酶体疾病的病理学。
Perspectives in pediatric pathology Pub Date : 1993-01-01
J E Dimmick, D A Applegarth
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引用次数: 0
Neuronal ceroid-lipofuscinoses in childhood. 儿童神经性神经性脂褐素病。
Perspectives in pediatric pathology Pub Date : 1993-01-01
J Rapola
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引用次数: 0
Homocystinuria: clinical and pathologic review, with emphasis on thrombotic features, including pulmonary artery thrombosis. 同型半胱氨酸尿:临床和病理回顾,重点是血栓特征,包括肺动脉血栓形成。
Perspectives in pediatric pathology Pub Date : 1993-01-01
E R Lieberman, E D Gomperts, K N Shaw, B H Landing, G N Donnell
{"title":"Homocystinuria: clinical and pathologic review, with emphasis on thrombotic features, including pulmonary artery thrombosis.","authors":"E R Lieberman, E D Gomperts, K N Shaw, B H Landing, G N Donnell","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76320,"journal":{"name":"Perspectives in pediatric pathology","volume":"17 ","pages":"125-47"},"PeriodicalIF":0.0,"publicationDate":"1993-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"19304353","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Galactosemia: clinical and pathologic features, tissue staining patterns with labeled galactose- and galactosamine-binding lectins, and possible loci of nonenzymatic galactosylation. 半乳糖血症:临床和病理特征,半乳糖和半乳糖胺结合凝集素标记的组织染色模式,以及可能的非酶半乳糖基化位点。
Perspectives in pediatric pathology Pub Date : 1993-01-01
B H Landing, S M Ang, G Villarreal-Engelhardt, G N Donnell
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引用次数: 0
Founders of pediatric pathology: Malcolm Charles Fowler (1925-1974). 儿科病理学奠基人:马尔科姆·查尔斯·福勒(1925-1974)。
Perspectives in pediatric pathology Pub Date : 1993-01-01
R F Carter
{"title":"Founders of pediatric pathology: Malcolm Charles Fowler (1925-1974).","authors":"R F Carter","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76320,"journal":{"name":"Perspectives in pediatric pathology","volume":"17 ","pages":"1-6"},"PeriodicalIF":0.0,"publicationDate":"1993-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"19304352","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
The mucolipidoses. 粘液脂质。
Perspectives in pediatric pathology Pub Date : 1993-01-01
E F Gilbert-Barness, L A Barness
{"title":"The mucolipidoses.","authors":"E F Gilbert-Barness, L A Barness","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76320,"journal":{"name":"Perspectives in pediatric pathology","volume":"17 ","pages":"148-84"},"PeriodicalIF":0.0,"publicationDate":"1993-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"19304354","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Molecular and histological analysis of embryonic development. 胚胎发育的分子和组织学分析。
Perspectives in pediatric pathology Pub Date : 1992-01-01
D P Witte, B J Aronow, J A Harmony
{"title":"Molecular and histological analysis of embryonic development.","authors":"D P Witte, B J Aronow, J A Harmony","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76320,"journal":{"name":"Perspectives in pediatric pathology","volume":"16 ","pages":"7-26"},"PeriodicalIF":0.0,"publicationDate":"1992-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"12640138","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
A natural immune system in pregnancy serum lethal to human neuroblastoma cells: a possible mechanism of spontaneous regression. 妊娠血清中对人神经母细胞瘤细胞致命的自然免疫系统:一种可能的自发消退机制。
Perspectives in pediatric pathology Pub Date : 1992-01-01
R P Bolande
{"title":"A natural immune system in pregnancy serum lethal to human neuroblastoma cells: a possible mechanism of spontaneous regression.","authors":"R P Bolande","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76320,"journal":{"name":"Perspectives in pediatric pathology","volume":"16 ","pages":"120-33"},"PeriodicalIF":0.0,"publicationDate":"1992-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"12640135","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Founders of pediatric pathology: John Emery (1915-). 儿科病理学的创始人:约翰·埃默里(1915-)。
Perspectives in pediatric pathology Pub Date : 1992-01-01
A H Cameron
{"title":"Founders of pediatric pathology: John Emery (1915-).","authors":"A H Cameron","doi":"","DOIUrl":"","url":null,"abstract":"","PeriodicalId":76320,"journal":{"name":"Perspectives in pediatric pathology","volume":"16 ","pages":"1-6"},"PeriodicalIF":0.0,"publicationDate":"1992-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"12639502","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Peripheral primitive neuroectodermal tumors. Diagnosis, classification, and prognosis. 周围原始神经外胚层肿瘤。诊断、分类和预后。
Perspectives in pediatric pathology Pub Date : 1992-01-01
M Tsokos
{"title":"Peripheral primitive neuroectodermal tumors. Diagnosis, classification, and prognosis.","authors":"M Tsokos","doi":"","DOIUrl":"","url":null,"abstract":"<p><p>In conclusion, the group of peripheral primitive neuroectodermal tumors has been redefined in recent years on the basis of cytogenetic, molecular genetic and more precisely defined histopathologic characteristics. Although in the past, many tumors has been called Ewing's sarcoma, currently this diagnosis is limited to tumors which cannot be more specifically classified on the basis of their ultrastructural and immunophenotypic characteristics. Most small round cell tumors previously classified as Ewing's sarcoma are now classified as peripheral PNET. The consistent cytogenetic abnormality in Ewing's sarcoma and peripheral PNET and patterns of neurotransmitter enzymes have supported a common neuroectodermal origin. The precise characterization of soft tissue Ewing's sarcoma is further complicated by the several primitive rhabdomyosarcomas that may exhibit a similar light microscopic appearance. The importance of histopathologic distinction among these various round cell tumors of childhood is well recognized. Furthermore, primitive tumors with overlapping neural and mesenchymal features, known as malignant ectomesenchymoma, are now identified more often than previously. Finally, molecular biologic and cytogenetic differences between peripheral PNET and neuroblastoma have confirmed their clinical and biologic differences, in spite of their morphologic similarities. Molecular genetic and flow cytometric evaluation have contributed to the distinction of groups with prognostic significance and offer possibilities for new clinical trials.</p>","PeriodicalId":76320,"journal":{"name":"Perspectives in pediatric pathology","volume":"16 ","pages":"27-98"},"PeriodicalIF":0.0,"publicationDate":"1992-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"12509279","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
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