Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases最新文献

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Kawasaki Disease Presenting as Fever and Urinary Tract Infection. 川崎病表现为发热和尿路感染。
IF 3.4
Rakesh Kumar Pilania, Purbasha Misra, Sandesh Guleria, Manphool Singhal, Anju Gupta, Surjit Singh
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引用次数: 1
Calcified Saccular Coronary Artery Aneurysm of Kawasaki Disease. 川崎病的钙化囊状冠状动脉瘤。
IF 3.4
Manphool Singhal, Pandiarajan Vignesh, N Khandelwal, Surjit Singh
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引用次数: 1
Things Come in 3's… Or So It Seems. 事情都是三段式的,至少看起来是这样。
IF 3.4
Mariana Luís, Luísa Brites, Maria João Salvador, Mariana Santiago, Cátia Duarte
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引用次数: 1
An Adult With Fever and Facial Nerve Palsy: An Unusual Presentation of Kawasaki Disease. 成人发烧和面神经麻痹:川崎病的一个不寻常的表现。
IF 3.4
Ankur Kumar Jindal, Rakesh Kumar Pilania, Deepti Suri, Parul Chawla Gupta, Surjit Singh
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引用次数: 3
Hypotension in a Febrile Child-Beware of Kawasaki Disease Shock Syndrome. 温热儿童低血压当心川崎病休克综合征。
IF 3.4
Rakesh Kumar Pilania, Ankur Kumar Jindal, Vaddi Vamsi Srikrishna, Madhusudan Samprathi, Manphool Singhal, Surjit Singh
{"title":"Hypotension in a Febrile Child-Beware of Kawasaki Disease Shock Syndrome.","authors":"Rakesh Kumar Pilania, Ankur Kumar Jindal, Vaddi Vamsi Srikrishna, Madhusudan Samprathi, Manphool Singhal, Surjit Singh","doi":"10.1097/RHU.0000000000001002","DOIUrl":"https://doi.org/10.1097/RHU.0000000000001002","url":null,"abstract":"","PeriodicalId":520664,"journal":{"name":"Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases","volume":" ","pages":"e130-e131"},"PeriodicalIF":3.4,"publicationDate":"2020-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1097/RHU.0000000000001002","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"37076868","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 4
Healing of Mucocutaneous Lesions With Apremilast in Behçet Disease. 阿普雷米司特治疗皮肤粘膜病变的疗效。
IF 3.4
Patricia Moya, Ivan Castellví, Berta Magallares, Milena Millan, Nicholas Wilson, Hector Corominas
{"title":"Healing of Mucocutaneous Lesions With Apremilast in Behçet Disease.","authors":"Patricia Moya, Ivan Castellví, Berta Magallares, Milena Millan, Nicholas Wilson, Hector Corominas","doi":"10.1097/RHU.0000000000001005","DOIUrl":"https://doi.org/10.1097/RHU.0000000000001005","url":null,"abstract":"","PeriodicalId":520664,"journal":{"name":"Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases","volume":" ","pages":"e132"},"PeriodicalIF":3.4,"publicationDate":"2020-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1097/RHU.0000000000001005","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"37077770","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 2
PET/CT Findings of Granulomatosis With Polyangiitis Presenting as a Solitary Pulmonary Nodule and Mimicking Lung Cancer. 肉芽肿合并多血管炎的PET/CT表现为孤立性肺结节,类似肺癌。
IF 3.4
Luis Gorospe, Odile Ajuria-Illarramendi, Carlos de la Puente-Bujidos, Gemma María Muñoz-Molina, Alberto Cabañero-Sánchez, Nicolás Moreno-Mata, Amparo Benito-Berlinches
{"title":"PET/CT Findings of Granulomatosis With Polyangiitis Presenting as a Solitary Pulmonary Nodule and Mimicking Lung Cancer.","authors":"Luis Gorospe, Odile Ajuria-Illarramendi, Carlos de la Puente-Bujidos, Gemma María Muñoz-Molina, Alberto Cabañero-Sánchez, Nicolás Moreno-Mata, Amparo Benito-Berlinches","doi":"10.1097/RHU.0000000000000994","DOIUrl":"https://doi.org/10.1097/RHU.0000000000000994","url":null,"abstract":"","PeriodicalId":520664,"journal":{"name":"Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases","volume":" ","pages":"e122-e123"},"PeriodicalIF":3.4,"publicationDate":"2020-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"36883007","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 2
Late Onset Multiple Acyl-CoA Dehydrogenase Deficiency (MADD) Myopathy Misdiagnosed as Polymyositis. 迟发性多发性酰基辅酶a脱氢酶缺乏症(MADD)被误诊为多发性肌炎。
IF 3.4
Andrea Barp, Rémi Bellance, Edoardo Malfatti, Odile Rigal, Cécile Acquaviva-Bourdain, Pascal Laforet
{"title":"Late Onset Multiple Acyl-CoA Dehydrogenase Deficiency (MADD) Myopathy Misdiagnosed as Polymyositis.","authors":"Andrea Barp, Rémi Bellance, Edoardo Malfatti, Odile Rigal, Cécile Acquaviva-Bourdain, Pascal Laforet","doi":"10.1097/RHU.0000000000001000","DOIUrl":"https://doi.org/10.1097/RHU.0000000000001000","url":null,"abstract":"","PeriodicalId":520664,"journal":{"name":"Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases","volume":" ","pages":"e125-e127"},"PeriodicalIF":3.4,"publicationDate":"2020-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"37171051","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 2
Constrictive (Obliterative) Bronchiolitis as Presenting Manifestation of Connective Tissue Diseases. 缩窄性(闭塞性)细支气管炎是结缔组织疾病的表现。
IF 3.4
Antonella Arcadu, Jay H Ryu
{"title":"Constrictive (Obliterative) Bronchiolitis as Presenting Manifestation of Connective Tissue Diseases.","authors":"Antonella Arcadu,&nbsp;Jay H Ryu","doi":"10.1097/RHU.0000000000001387","DOIUrl":"https://doi.org/10.1097/RHU.0000000000001387","url":null,"abstract":"<p><strong>Background: </strong>Constrictive (obliterative) bronchiolitis (CB) is an uncommon form of obstructive lung disease that can occur in patients with identifiable causes including connective tissue diseases (CTDs) as a form of lung involvement. We explored whether CB can be the presenting manifestation of CTD.</p><p><strong>Methods: </strong>We identified 44 patients with cryptogenic CB and examined the presenting clinical, laboratory, and radiologic features, as well as their clinical course.</p><p><strong>Results: </strong>The mean age at presentation was 60.5 (SD, 13.8) years and included 38 women (86%); 32 (73%) were never smokers. All patients presented for evaluation of dyspnea, commonly associated with cough. An obstructive pattern on pulmonary function testing was demonstrated in 86% of patients. On chest high-resolution computed tomography, nearly all patients manifested a mosaic attenuation pattern with air trapping on expiratory views, characteristic of CB. Bronchoscopic lung biopsy (n = 10) was usually nondiagnostic (90%), whereas all 5 surgical lung biopsies yielded evidence of CB. Serologic testing for CTD was positive in 19 patients (43%) and most commonly included antinuclear antibody, rheumatoid factor, and anti-cyclic citrullinated antibodies. Seven of these patients with positive serologic results were eventually diagnosed to have CTD. Connective tissue diseases included rheumatoid arthritis in 4 patients, Sjögren syndrome in 2, and undifferentiated CTD in 1 patient.</p><p><strong>Conclusions: </strong>Nearly one-half of patients with cryptogenic CB manifest positive CTD serology, and some of these patients have CTD not previously diagnosed. These results suggest that CB can be the presenting manifestation of a CTD.</p>","PeriodicalId":520664,"journal":{"name":"Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases","volume":" ","pages":"176-180"},"PeriodicalIF":3.4,"publicationDate":"2020-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1097/RHU.0000000000001387","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"37869910","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 2
Thirty-Day Hospital Readmissions for Granulomatosis With Polyangiitis in the United States: A Nationwide Analysis. 在美国,肉芽肿病合并多血管炎的30天再入院:一项全国性的分析。
IF 3.4
Yiming Luo, Changchuan Jiang, Ana Belen Arevalo Molina, Shane Murray, Gustavo Contreras Anez, Maria Salgado, Jiehui Xu
{"title":"Thirty-Day Hospital Readmissions for Granulomatosis With Polyangiitis in the United States: A Nationwide Analysis.","authors":"Yiming Luo,&nbsp;Changchuan Jiang,&nbsp;Ana Belen Arevalo Molina,&nbsp;Shane Murray,&nbsp;Gustavo Contreras Anez,&nbsp;Maria Salgado,&nbsp;Jiehui Xu","doi":"10.1097/RHU.0000000000001045","DOIUrl":"https://doi.org/10.1097/RHU.0000000000001045","url":null,"abstract":"<p><strong>Background/objective: </strong>Granulomatosis with polyangiitis (GPA) is a systemic necrotizing vasculitis that often results in frequent hospitalizations. We investigated the characteristics and predictors of 30-day hospital readmissions in GPA.</p><p><strong>Methods: </strong>We performed a cross-sectional analysis using the 2014 National Readmission Database. We included nonelective admissions with a primary or secondary diagnosis of GPA. We compared characteristics between readmissions and nonreadmissions. Independent predictors for readmissions were studied using mixed-effects multivariable logistic regression.</p><p><strong>Results: </strong>We evaluated a total of 9749 hospital admissions with GPA, among which there were 2173 readmissions (22.3%) within 30 days of discharge. The top 5 primary reasons for readmissions were GPA, sepsis, pneumonia, acute respiratory failure, and acute kidney injury. Granulomatosis with polyangiitis readmissions were associated with higher length of stay (8.0 vs 7.2 days; p = 0.019) and less discharge home (50% vs 63%, p < 0.001). Independent predictors for readmissions were younger age (odds ratio [OR], 0.99; p = 0.013), no private insurance (OR, 0.50; p < 0.001), higher Charlson Comorbidity Index (OR, 1.12; p = 0.039), congestive heart failure (OR, 1.71; p = 0.001), acute kidney injury (OR, 1.39; p = 0.005), and discharge to home health care (OR, 1.29; p = 0.039).</p><p><strong>Conclusions: </strong>We found a significant burden of 30-day readmissions among GPA populations. Clinicians should be vigilant regarding patients with high risk of readmissions, including those with younger age, public insurance, higher comorbidity burden, cardiac and renal complications, and unfavorable discharge dispositions.</p>","PeriodicalId":520664,"journal":{"name":"Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases","volume":" ","pages":"192-196"},"PeriodicalIF":3.4,"publicationDate":"2020-08-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1097/RHU.0000000000001045","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"40559373","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 3
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