Sushil V. Yewale, Shruti A. Mondkar, Vaman Khadilkar, Anuradha V. Khadilkar
{"title":"Pallister-Hall syndrome: A 3-year-old girl with short stature and polydactyly","authors":"Sushil V. Yewale, Shruti A. Mondkar, Vaman Khadilkar, Anuradha V. Khadilkar","doi":"10.25259/wjwch_6_2023","DOIUrl":"https://doi.org/10.25259/wjwch_6_2023","url":null,"abstract":"A 3.1-year-old girl presented with short stature and developmental delay. She had a high-pitched voice, broad forehead, midfacial hypoplasia, hypoplastic labia, and bilateral mesoaxial polydactyly involving upper limbs. Biochemical reports were suggestive of isolated growth hormone deficiency (GHD) and magnetic resonance imaging revealed a large hypothalamic hamartoma (HH). The presence of auxological, clinical, and biochemical findings of GHD together with polydactyly and HH clinched the diagnosis of Pallister-Hall Syndrome. There are approximately 100 cases reported worldwide, which points toward the rarity of this disorder. Moreover, in contrast to most cases, our case had significant developmental delay.","PeriodicalId":485919,"journal":{"name":"Wadia Journal of Women and Child Health","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136292859","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Keith Peter D’souza, Anuradha Fakirappa Karegar, Veronique Dinand
{"title":"Cleaning is also caring – Dignity of the child even after death","authors":"Keith Peter D’souza, Anuradha Fakirappa Karegar, Veronique Dinand","doi":"10.25259/wjwch_31_2023","DOIUrl":"https://doi.org/10.25259/wjwch_31_2023","url":null,"abstract":"Bai Jerbai Wadia Hospital for Children in Mumbai is known for its specialized care for children. Its Pediatric Palliative and Supportive Care Unit works toward improving the quality of life for seriously ill children and enhances end-of-life care. This article focuses on the important role of “Maushis” (cleaning staff) in ensuring dignity for deceased children and supporting families at the hospital. Two workshops with “Maushis” led to positive changes in their practices, including attention to detail, cultural sensitivity, and the introduction of a comfortable trolley for transporting deceased children. This initiative promotes respect and dignity for non-medical staff, enhancing the overall care experience in the hospital.","PeriodicalId":485919,"journal":{"name":"Wadia Journal of Women and Child Health","volume":"55 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136292861","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"From Editors’ Desk","authors":"Sudha Rao, Dhruv Mamtora","doi":"10.25259/wjwch_41_2023","DOIUrl":"https://doi.org/10.25259/wjwch_41_2023","url":null,"abstract":"","PeriodicalId":485919,"journal":{"name":"Wadia Journal of Women and Child Health","volume":"36 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136353104","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Audit in surgical histopathology at Wadia hospitals - Study of pre-analytical, analytical, and post-analytical phase","authors":"Leena Milind Patwardhan, Sunita Sharma","doi":"10.25259/wjwch_8_2023","DOIUrl":"https://doi.org/10.25259/wjwch_8_2023","url":null,"abstract":"Objectives: This audit of surgical histopathology aims to verify conformance to required processes, assess their implementation, and define the targets of quality control with appropriate changes in the existing system by evaluating pre-analytical, analytical, and post-analytical phases of histopathology. Material and Methods: This study was an observational retrospective study done over a year, from March 15, 2022 to February 28, 2023. Small biopsies, large organ resections, and second opinion samples like paraffin blocks or slides received in the surgical histopathology department were categorized as I, II and III respectively. Samples were also segregated as per the department it was received from, namely, gastroenterology, neurology, pulmonology, nephrology, orthopedics, gynepathology, and others. Manual audit was done as a pre-analytical phase including adequacy of clinical information and grossing adequacy, analytical phase to study the turn around time (TAT) and tissue section quality, and the post-analytical phase in the form of report verification, approval and dispatch, and amendment if any, were studied. Results: During this audit period, 1752 surgical histopathology samples were received of which 80% were small biopsies (category I), 19.6% were large organ resection samples (category II) and 0.4% samples were received for second opinion (category III). General pediatrics ( n = 798) and Gynepathology ( n = 569) were the main departments from which the samples were received. Incomplete request forms, errors in sample fixation, wrong payment/barcode were some of the pre-analytical errors. Training of staff on one to one basis was done. In the analytical phase errors such as nicks, folds or air bubbles in the mounted sample were seen. Histotechnical staff were retrained to reduce errors. In the post analytical phase, the turnaround time was achieved as per the hospital quality process indicator, feedback from cases on second opinion was received only in 25% of samples. Conclusions: In this surgical histopathology audit of 1752 samples, quality indicators were achieved as per external quality assurance system (EQAS). Remedial actions were carried out to prevent errors.","PeriodicalId":485919,"journal":{"name":"Wadia Journal of Women and Child Health","volume":"47 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136292864","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"A toddler with testosterone: where did it come from?","authors":"Amrita Rajiv Mehta, Sudha Chandrashekhar Rao, Rajesh Joshi, Ajinkya Patil","doi":"10.25259/wjwch_20_2022","DOIUrl":"https://doi.org/10.25259/wjwch_20_2022","url":null,"abstract":"Precocious development of secondary sexual characters not involving pulsatile gonadotropin secretion is known as gonadotropin independent precocious puberty or peripheral precocious puberty (PPP). This form of sexual precocity in males can occur due to gonadal, adrenal, or other testosterone secreting tumors (teratomas, hepatomas, and choriocarcinomas), untreated congenital adrenal hyperplasia, testotoxicosis, and familial male limited precocious puberty. We report a case of a 2-year-old boy with PPP caused due to hepatoblastoma. Complete surgical resection of the tumor was done, and the child received cisplatin chemotherapy.","PeriodicalId":485919,"journal":{"name":"Wadia Journal of Women and Child Health","volume":"38 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136295667","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Parag Karkera, Arka Banerjee, Gayatri Munghate, Pradnya Bendre
{"title":"Organ-preserving enucleation in a case of solid pseudopapillary neoplasm of pancreas","authors":"Parag Karkera, Arka Banerjee, Gayatri Munghate, Pradnya Bendre","doi":"10.25259/wjwch_16_2023","DOIUrl":"https://doi.org/10.25259/wjwch_16_2023","url":null,"abstract":"Solid pseudopapillary neoplasm (SPN) is a rare pancreatic tumor affecting mostly females in the second or third decade of life. These tumors have a low malignant potential, and hence, surgical resection remains the main treatment. Large tumors may present with compressive symptoms such as abdominal pain or vomiting. Once resected completely, SPNs usually have an excellent long-term prognosis. We report a 16-year-old girl who presented with vomiting and abdominal pain localized to the right upper quadrant. Imaging showed an encapsulated tumor arising from the pancreatic head which prompted us to perform organ-preserving enucleation. Histopathology confirmed the tumor as an SPN.","PeriodicalId":485919,"journal":{"name":"Wadia Journal of Women and Child Health","volume":"4 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136292618","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Spectrum of World Health Organization global priority pathogens in hospitalized children - A single center experience","authors":"Samrin Sheikh, Swati Joshi Mulye","doi":"10.25259/wjwch_4_2023","DOIUrl":"https://doi.org/10.25259/wjwch_4_2023","url":null,"abstract":"Objectives: To study the spectrum of World Health Organization (WHO) global priority pathogens in hospitalized children at our center. Material and Methods: This cross-sectional study was conducted between April 2021 to September 2022 in the Department of Pediatrics at Sri Aurobindo Institute of Medical Sciences and Post Graduate Institute (SAMC), Indore. All children admitted to the Pediatric and Adolescent Medicine Department; Ward, Pediatric Intensive Care Unit, Neonatal Intensive Care Unit, and Pediatric Surgical intensive Care Unit and with culture (Blood, urine, cerebrospinal fluid, and other body fluids/tissue) having grown at least one of the WHO priority pathogens, were studied. Results: In this study period, 100 children had positive cultures. We found that urine specimens had the most bacterial isolations 35 (35%), followed by blood 24 (24%). Escherichia coli was the most often isolated organism [25 (25%)], followed by Staphylococcus aureus [18 (18%)]. About 80% of E. coli and 70.59% of Klebsiella spp. were resistant to third-generation cephalosporins due to extended-spectrum beta-lactamase (ESBL), while 50% of S. aureus were Methicillin-resistant. In all, over half of the Enterobacteriaceae were resistant to carbapenem (49.21%) or third generation cephalosporins (55.56%) due to ESBL. Pseudomonas aeruginosa carbapenem resistance was found in 11.11% cases. Conclusion: In this study, WHO priority list pathogens, Enterobacteriaceae, methicillin-resistant S. aureus, Klebsiella species, and E. coli all show significant antimicrobial resistance (AMR). On the other hand, AMR trends for Acinetobacter baumanni, P. aeruginosa , and S. aureus (vancomycin resistant) are lower than the estimations provided by the WHO globally.","PeriodicalId":485919,"journal":{"name":"Wadia Journal of Women and Child Health","volume":"8 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136353872","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"CEO’s Message","authors":"Minnie Bodhanwala","doi":"10.25259/wjwch_40_2023","DOIUrl":"https://doi.org/10.25259/wjwch_40_2023","url":null,"abstract":"","PeriodicalId":485919,"journal":{"name":"Wadia Journal of Women and Child Health","volume":"4 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136292865","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Transabdominal cerclage: The journey of turning bad into good","authors":"Amol Pawar, Sweta Shrivastava, Aishwarya Kadrekar","doi":"10.25259/wjwch_7_2023","DOIUrl":"https://doi.org/10.25259/wjwch_7_2023","url":null,"abstract":"Recurrent pregnancy loss is a challenging obstetric condition that requires thorough evaluation and vigilant antenatal care. Cervical insufficiency is a well-recognized cause of late miscarriage. Here, we are reporting a case of multiple pregnancy failures including both 1st- and 2nd-trimester losses with cervical insufficiency after ruling out all other probable causes. The patient had a history of 3 failed transvaginal cervical cerclage procedures, and hence, in her 7th pregnancy, transabdominal cervical cerclage was attempted that resulted in salvaging the pregnancy beyond viability and the patient delivered a healthy baby through an emergency cesarean section near term. The patient was reconceived with the transabdominal cerclage in situ and delivered with a successful fetal and maternal outcome despite having multiple high-risk factors. This highlights the effectiveness of transabdominal cervical cerclage to prevent spontaneous mid-trimester loss and preterm delivery when previous transvaginal cerclage has failed.","PeriodicalId":485919,"journal":{"name":"Wadia Journal of Women and Child Health","volume":"7 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-10-10","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"136294917","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}