PAMJ Clinical Medicine最新文献

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Tumeurs neuroendocrines à cellules claires du pancréas : A propos de deux cas et revue de la littérature 胰腺清除细胞神经内分泌肿瘤:约2例及文献综述
PAMJ Clinical Medicine Pub Date : 2021-08-18 DOI: 10.11604/pamj-cm.2021.6.40.30402
Z. Samlani, Yassine Lemfadli, A. A. Errami, S. Oubaha, Abderrachid Hamdaoui, K. Krati
{"title":"Tumeurs neuroendocrines à cellules claires du pancréas : A propos de deux cas et revue de la littérature","authors":"Z. Samlani, Yassine Lemfadli, A. A. Errami, S. Oubaha, Abderrachid Hamdaoui, K. Krati","doi":"10.11604/pamj-cm.2021.6.40.30402","DOIUrl":"https://doi.org/10.11604/pamj-cm.2021.6.40.30402","url":null,"abstract":"Les tumeurs neuroendocrines a cellules claires du pancreas ont ete rarement rapportees dans la litterature. Cette entite nosologique rare pose un probleme de diagnostic differentiel avec de nombreuses tumeurs primitives et metastatiques du pancreas. Cependant, l´utilisation des techniques de l´immunohistochimie et de l´histologie pourra faciliter le diagnostic. Nous avons collige deux cas dans notre etablissement au cours de la derniere annee avec des tumeurs neuroendocrines pancreatiques primitives a cellules claires. Nous presentons leurs cas dans le but de contribuer aux donnees disponibles sur le sujet. Nous insistons sur l´interet de l´echoendoscopie dans le diagnostic positif et nous fournissons egalement une revue actualisee de la litterature disponible a ce jour concernant les tumeurs neuroendocrines a cellules claires du pancreas.","PeriodicalId":397112,"journal":{"name":"PAMJ Clinical Medicine","volume":"9 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-08-18","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115323380","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Bilateral exudative retinal detachment in HELLP syndrome, first description in North Africa: a case report 双侧渗出性视网膜脱离HELLP综合征,首次描述在北非:一个病例报告
PAMJ Clinical Medicine Pub Date : 2021-08-04 DOI: 10.11604/pamj-cm.2021.6.39.25913
A. Khallouli, R. Choura, R. Saidane, D. Gouider, A. Maalej, R. Rannen
{"title":"Bilateral exudative retinal detachment in HELLP syndrome, first description in North Africa: a case report","authors":"A. Khallouli, R. Choura, R. Saidane, D. Gouider, A. Maalej, R. Rannen","doi":"10.11604/pamj-cm.2021.6.39.25913","DOIUrl":"https://doi.org/10.11604/pamj-cm.2021.6.39.25913","url":null,"abstract":"HELLP syndrome (Hemolysis, Elevated Liver Enzymes, Low Platelets) is a pregnancy disorder representing a severe form of preeclampsia and associated with high maternal and fetal mortality. Serous retinal detachment has been reported in eclampsia. However, bilateral exudative retinal detachment associated with HELLP syndrome has rarely been described. We report a case of a 32-year-old patient, gravida III para III, with hypertensive HELLP syndrome who developed bilateral exudative bullous retinal detachment following caesarean delivery at 33 weeks. A comprehensive management and a scheduled monitoring of this potentially sight-threatening eye disease led to saving useful vision.","PeriodicalId":397112,"journal":{"name":"PAMJ Clinical Medicine","volume":"41 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-08-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125116174","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 1
One successful intrauterine device into a uterus, didelphys: a case report and literature review 宫内节育器成功植入子宫一例,didelphys: 1例报告及文献复习
PAMJ Clinical Medicine Pub Date : 2021-08-03 DOI: 10.11604/pamj-cm.2021.6.38.29179
Kasereka Muteke John, Kaboko Mbilika Kevin
{"title":"One successful intrauterine device into a uterus, didelphys: a case report and literature review","authors":"Kasereka Muteke John, Kaboko Mbilika Kevin","doi":"10.11604/pamj-cm.2021.6.38.29179","DOIUrl":"https://doi.org/10.11604/pamj-cm.2021.6.38.29179","url":null,"abstract":"Uterus didelphys represents a uterus malformation where the uterus is present as a double organ due to embryonic fusion failure of the mullerian ducts. As a result, there is a double uterus with separated cervices. This congenital malformation used to be a controversial contraindication of an intrauterine device (IUD) insertion. It is a category 4 WHO medical eligibility criteria: not being used because of its association with a high risk of IUD expulsion, malposition into the uterus, uterine perforation and its migration into the abdominal cavity and viscera. We present and discuss the case of a 35-year-old woman, P4+6, known with uterus didelphys who came to our outpatient clinic for family planning. She was counselled about all available methods and opted for a levonorgestrel IUD (LNG-IUD). We inserted the device into one of her double uterus and she is fully satisfied with the method now one year and three months ago. Levonorgestrel IUD is a long acting, highly effective and reversible form of contraception that works mainly by thickening of the cervical mucus and also by thinning the endometrial lining. Considering its effect on the endometrium and the cervical mucus; and its high level of progesterone pelvic release, we think one LNG-IUD contraception into one of the double uterus is enough and effective in individualized and known women with such condition instead of two IUDs, one being into each uterus, such published in all articles we read through. The purpose of this case report is to demonstrate that only one LNG-IUD contraception can be sufficient and effective method in known and selective women with uterus didelphys. However a case-series study is needed for more evidence.","PeriodicalId":397112,"journal":{"name":"PAMJ Clinical Medicine","volume":"31 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-08-03","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133469901","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Bilateral cataract in a teenage girl with type 1 diabetes (T1D): case report 少女合并1型糖尿病(T1D)双侧白内障1例
PAMJ Clinical Medicine Pub Date : 2021-07-29 DOI: 10.11604/pamj-cm.2021.6.35.30477
D. Boiro, Lamine Thiam, I. Basse, M. Ndiaye, A. A. Ndongo, N. Seck, A. Sow, B. Niang, D. Diédhiou, M. Guéye, O. Ndiaye
{"title":"Bilateral cataract in a teenage girl with type 1 diabetes (T1D): case report","authors":"D. Boiro, Lamine Thiam, I. Basse, M. Ndiaye, A. A. Ndongo, N. Seck, A. Sow, B. Niang, D. Diédhiou, M. Guéye, O. Ndiaye","doi":"10.11604/pamj-cm.2021.6.35.30477","DOIUrl":"https://doi.org/10.11604/pamj-cm.2021.6.35.30477","url":null,"abstract":"","PeriodicalId":397112,"journal":{"name":"PAMJ Clinical Medicine","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-07-29","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115967812","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Panniculite mésentérique, une cause inhabituelle de douleur abdominale : à propos de 2 cas diagnostiqués à la tomodensitométrie 肠系膜Panniculite,腹痛的不寻常原因:约2例ct诊断
PAMJ Clinical Medicine Pub Date : 2021-07-28 DOI: 10.11604/pamj-cm.2021.6.34.30415
P. Gbande, M. Tchaou, A. Amadou, L. Sonhaye, K. Adjenou
{"title":"Panniculite mésentérique, une cause inhabituelle de douleur abdominale : à propos de 2 cas diagnostiqués à la tomodensitométrie","authors":"P. Gbande, M. Tchaou, A. Amadou, L. Sonhaye, K. Adjenou","doi":"10.11604/pamj-cm.2021.6.34.30415","DOIUrl":"https://doi.org/10.11604/pamj-cm.2021.6.34.30415","url":null,"abstract":"La panniculite mesenterique est une maladie rare et benigne caracterisee par un processus inflammatoire et fibrotique chronique qui affecte le tissu adipeux mesenterique. Elle atteint souvent le sujet adulte de sexe masculin. Son etiologie reste inconnue. L´aspect tomodensitometrique de la PM varie selon l´importance de l´inflammation et de la fibrose. Nous rapportons deux cas de panniculite mesenterique reveles par une douleur abdominale. Le diagnostic a ete pose sur la base des donnees de la tomodensitometrie. Nous rappelons a travers ces cas, les aspects cliniques et tomodensitometriques de cette affection rare.","PeriodicalId":397112,"journal":{"name":"PAMJ Clinical Medicine","volume":"38 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-07-28","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115772162","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Dystrophie des cônes 锥体营养不良
PAMJ Clinical Medicine Pub Date : 2021-07-27 DOI: 10.11604/pamj-cm.2021.6.33.24149
Souhaila Karmoun, A. Berraho
{"title":"Dystrophie des cônes","authors":"Souhaila Karmoun, A. Berraho","doi":"10.11604/pamj-cm.2021.6.33.24149","DOIUrl":"https://doi.org/10.11604/pamj-cm.2021.6.33.24149","url":null,"abstract":"Nous rapportons le cas d´une jeune femme âgee de 30 ans, sans antecedents notables, qui se plaint d´une baisse d´acuite visuelle progressive depuis l´âge de 20 ans. L´acuite visuelle est chiffree a 1/10 non ameliorable en œil droit et gauche. L´examen du segment anterieur des deux yeux est sans particularites. L´examen du fond d´œil a revele l´existence d´une lesion maculaire jaunâtre arrondie avec une atrophie maculaire majeure au niveau des deux yeux (A, B). Le vitre est transparent, l´examen de la peripherie retinienne est normal. Les cliches en auto fluorescences decrivent un aspect granulaire des maculas avec une alternance de points hypo-autofluorescents (alteration de l´epithelium pigmentaire) et hyper-autofluorescents (depots de lipofuscine) (C, D). L´angiographie a la fluoresceine montre la presence d´une atrophie maculaire accompagnee d´un remaniement de l´epithelium pigmentaire. Il existe aussi un effet fenetre realisant l´aspect d´œil de bœuf au niveau maculaire (E, F). Une electro-retinographie a ete realisee confirmant le diagnostic de la dystrophie des cones. Sur le plan histologique, la dystrophie progressive des cones correspond a une atteinte selective des cones et il a longtemps ete debattu de l´origine du processus degeneratif, entre une atteinte primaire de l´EP et une atteinte primaire des cones, plus probable. La dystrophie progressive des cones concerne le plus souvent des adultes jeunes qui consultent pour une baisse de l´acuite visuelle centrale bilaterale et frequemment asymetrique. L´affection evolue rapidement vers une acuite comprise entre 3/10 et 1/20, puis vers un scotome central.","PeriodicalId":397112,"journal":{"name":"PAMJ Clinical Medicine","volume":"148 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-07-27","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"121766007","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Suspended morgagnian nucleus 悬浮摩根核
PAMJ Clinical Medicine Pub Date : 2021-07-26 DOI: 10.11604/pamj-cm.2021.6.30.30845
K. Madbouhi, L. O. Cherkaoui
{"title":"Suspended morgagnian nucleus","authors":"K. Madbouhi, L. O. Cherkaoui","doi":"10.11604/pamj-cm.2021.6.30.30845","DOIUrl":"https://doi.org/10.11604/pamj-cm.2021.6.30.30845","url":null,"abstract":"Morgagnian cataract is a cataract in which there is liquefaction of the cortex and sinking of the dense nucleus in the capsular bag. In some cases, liquified cortical matter gets completely resorbed leaving behind just the transparent lens capsule superiorly and the dense nucleus in the bag inferiorly. We report the case of a 70-year-old patient, with no history of ocular trauma, presented with diminution of vision in the right eye for 1 year. Slit lamp examination showed a small cataract nucleus, suspended in the anterior chamber by the vitreous after spontaneous rupture of the capsular bag in the inf-nasal area and resorption of the cortex (Figure 1). She underwent an anterior nucleus extraction followed by an anterior vitrectomy and implantation of an iris fixation lens.","PeriodicalId":397112,"journal":{"name":"PAMJ Clinical Medicine","volume":"87 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-07-26","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"121419111","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Challenging case of anal carcinoma with baseline chronic neutropenia - the importance of a multi-disciplinary team effort in the prevailing COVID-19 pandemic 肛门癌伴基线慢性中性粒细胞减少的挑战性病例——在当前的COVID-19大流行中,多学科团队努力的重要性
PAMJ Clinical Medicine Pub Date : 2021-07-26 DOI: 10.11604/pamj-cm.2021.6.31.30533
N. Shanbhag, H. Medina, J. Philip, S. Cordner, A. Duncan, Vonetta George, Raghunandan Gangappa, Preston Goodwin, Sekeena Goodwin, Lestor Simon, H. Agrawal, Mohammed Syed Ali, R. Hodge
{"title":"Challenging case of anal carcinoma with baseline chronic neutropenia - the importance of a multi-disciplinary team effort in the prevailing COVID-19 pandemic","authors":"N. Shanbhag, H. Medina, J. Philip, S. Cordner, A. Duncan, Vonetta George, Raghunandan Gangappa, Preston Goodwin, Sekeena Goodwin, Lestor Simon, H. Agrawal, Mohammed Syed Ali, R. Hodge","doi":"10.11604/pamj-cm.2021.6.31.30533","DOIUrl":"https://doi.org/10.11604/pamj-cm.2021.6.31.30533","url":null,"abstract":"The year 2020 has been a challenging time with the prevailing COVID19 pandemic. The pandemic has forced the cancer departments globally to re-think and rearrange the ways cancers are treated. There were delays in surgery, radiation and chemotherapy. This case demonstrates the importance of multi-disciplinary teamwork and how a scientifically sound strategy and meticulous treatment planning can overcome the extra challenges in Oncology during the COVID19 pandemic.","PeriodicalId":397112,"journal":{"name":"PAMJ Clinical Medicine","volume":"321 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-07-26","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"132910360","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Hémangiome caverneux du jéjunum mimant un corps étranger Hémangiome caverneux你jéjunum mimant联合国陆战队étranger
PAMJ Clinical Medicine Pub Date : 2021-07-26 DOI: 10.11604/pamj-cm.2021.6.32.27566
Khalil Maamar, M. Bouziane
{"title":"Hémangiome caverneux du jéjunum mimant un corps étranger","authors":"Khalil Maamar, M. Bouziane","doi":"10.11604/pamj-cm.2021.6.32.27566","DOIUrl":"https://doi.org/10.11604/pamj-cm.2021.6.32.27566","url":null,"abstract":"Les tumeurs primitives de l´intestin grele sont rares et le plus souvent benignes. Les angiomes caverneux du jejunum sont exceptionnels, ils representent moins de 5% de l´ensemble des tumeurs benignes de l´intestin grele et 0,3% de l´ensemble des tumeurs du tractus gastro-intestinal. L´aspect normal de la muqueuse rend le diagnostic endoscopique presque impossible. La Tomodensitometrie (TDM) avec injection du produit de contraste avec un temps arteriel precoce ou l´IRM peuvent suspecter le diagnostic, le traitement est essentiellement chirurgical si la tumeur est compliquee, le pronostic est excellent. Nous rapportons un cas d´une patiente de 43 ans suivi en psychiatrie pour psychose rapporte des douleurs chroniques epigastriques avec vomissements, les explorations endoscopiques haute et basse etaient normaux, la TDM a montre un aspect de corps etranger : piece de monnaie (A). L´exploration caleidoscopique a montre un aspect d´une tumeur angiomateuse de la paroi de la pemiere anse jejunale de 5cm. L´examen anatomopathologique de la piece (B) de resection a confirme l´angiome caverneux.","PeriodicalId":397112,"journal":{"name":"PAMJ Clinical Medicine","volume":"42 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-07-26","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"124750556","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Volvulus du caecum sur mésentère commun complet au cours de la grossesse: à propos d’un cas 妊娠期完全普通肠系膜上的盲肠卷:约1例
PAMJ Clinical Medicine Pub Date : 2021-07-23 DOI: 10.11604/pamj-cm.2021.6.29.30231
F. Khanfir, Amine Zouari, F. Chaker, A. Masmoudi, Hend Tebourbi, M. Abdelmoula, Taher Labidi, Houcen Harbi, Bassem Abid, Mohamed Derbel, R. Mzali, K. Chaabane
{"title":"Volvulus du caecum sur mésentère commun complet au cours de la grossesse: à propos d’un cas","authors":"F. Khanfir, Amine Zouari, F. Chaker, A. Masmoudi, Hend Tebourbi, M. Abdelmoula, Taher Labidi, Houcen Harbi, Bassem Abid, Mohamed Derbel, R. Mzali, K. Chaabane","doi":"10.11604/pamj-cm.2021.6.29.30231","DOIUrl":"https://doi.org/10.11604/pamj-cm.2021.6.29.30231","url":null,"abstract":"Un accident occlusif aigu pendant la grossesse est une complication rare mais potentiellement grave qui peut poser des difficultes diagnostiques et mettre en jeu le pronostic maternel et fœtal. Nous rapportons le cas d´une patiente âgee de 22 ans, sans antecedents, admise pour des contractions uterines au terme de 37 semaines d´amenorrhees. L´examen a l´admission etait sans anomalies. La patiente a presente 7 heures apres l´admission des vomissements repetitifs avec polypnee et fievre. Une cesarienne a ete decidee en urgence devant l´apparition d´une bradycardie fœtale a l´enregistrement du rythme cardiaque fœtal ERCF. Le diagnostic de volvulus du colon droit sur un mesentere commun complet a ete pose en per-operatoire apres l´extraction fœtale. Le colon droit etait distendu et necrose avec trois tours de spire. La decision etait de realiser une colectomie droite avec anastomose ileo-colique termino laterale. L´evolution de la patiente en post operatoire etait favorable. A travers cette observation ainsi qu´une revue de litterature nous essaierons de discuter les modalites diagnostiques et therapeutiques de cette pathologie.","PeriodicalId":397112,"journal":{"name":"PAMJ Clinical Medicine","volume":"11 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-07-23","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125773427","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
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